Class information for:
Level 1: MUCOLIPIDOSIS TYPE IV//MUCOLIPIN//MUCOLIPIDOSIS IV

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
23712 337 49.7 85%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
262 3       AUTOPHAGY//RESVERATROL//HISTONE DEACETYLASE INHIBITOR 44558
1128 2             AUTOPHAGY//BECLIN 1//LC3 9655
23712 1                   MUCOLIPIDOSIS TYPE IV//MUCOLIPIN//MUCOLIPIDOSIS IV 337

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 MUCOLIPIDOSIS TYPE IV authKW 1843534 7% 88% 23
2 MUCOLIPIN authKW 1449732 6% 80% 20
3 MUCOLIPIDOSIS IV authKW 1003664 4% 92% 12
4 TFEB authKW 756156 8% 32% 26
5 TRPML1 authKW 724862 4% 67% 12
6 MLIV authKW 634261 2% 100% 7
7 TRPML3 authKW 634261 2% 100% 7
8 MUCOLIPIN 1 authKW 493311 2% 78% 7
9 TRPML authKW 443979 2% 70% 7
10 TRANSCRIPTION FACTOR EB authKW 296532 2% 55% 6

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Cell Biology 1823 38% 0% 128
2 Biochemistry & Molecular Biology 480 34% 0% 113
3 Genetics & Heredity 276 13% 0% 44
4 Medicine, Research & Experimental 106 8% 0% 26
5 Developmental Biology 56 3% 0% 10
6 Physiology 54 5% 0% 18
7 Pathology 35 4% 0% 12
8 Endocrinology & Metabolism 32 5% 0% 17
9 Ophthalmology 32 3% 0% 11
10 Neurosciences 29 8% 0% 27

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 DAN JAN DUNCAN NEUROL 181218 1% 100% 2
2 DIABET HYPERTENS MEMBRANE BIOL PROGRAM 181218 1% 100% 2
3 JAN DAN DUNCAN NEUROL 157629 7% 8% 23
4 PROGRAM CELL REGULATORY BIOL 111513 1% 31% 4
5 DEV METAB NEUROL BRANCH 92221 4% 7% 15
6 A HARTMAN CONTEMPORARY JEWRY 90609 0% 100% 1
7 ADDENBROOKES HOSP STUDY MOL MECHANISMS DIS 90609 0% 100% 1
8 ANATOMOPATHOL OPERAT UNIT 90609 0% 100% 1
9 BK PLUS PROJECT 12 90609 0% 100% 1
10 DIPARTIMENTALE MALATTIE RARE 90609 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 AUTOPHAGY 4823 3% 1% 9
2 CELL CALCIUM 3824 3% 0% 11
3 TRAFFIC 3009 2% 0% 8
4 BIRTH DEFECTS-ORIGINAL ARTICLE SERIES 1333 1% 1% 2
5 EMBO MOLECULAR MEDICINE 1264 1% 0% 3
6 SCIENCE SIGNALING 932 1% 0% 4
7 NATURE CELL BIOLOGY 833 1% 0% 5
8 MOLECULAR GENETICS AND METABOLISM 718 1% 0% 5
9 INVERTEBRATE NEUROSCIENCE 706 0% 1% 1
10 BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE 688 1% 0% 5

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 MUCOLIPIDOSIS TYPE IV 1843534 7% 88% 23 Search MUCOLIPIDOSIS+TYPE+IV Search MUCOLIPIDOSIS+TYPE+IV
2 MUCOLIPIN 1449732 6% 80% 20 Search MUCOLIPIN Search MUCOLIPIN
3 MUCOLIPIDOSIS IV 1003664 4% 92% 12 Search MUCOLIPIDOSIS+IV Search MUCOLIPIDOSIS+IV
4 TFEB 756156 8% 32% 26 Search TFEB Search TFEB
5 TRPML1 724862 4% 67% 12 Search TRPML1 Search TRPML1
6 MLIV 634261 2% 100% 7 Search MLIV Search MLIV
7 TRPML3 634261 2% 100% 7 Search TRPML3 Search TRPML3
8 MUCOLIPIN 1 493311 2% 78% 7 Search MUCOLIPIN+1 Search MUCOLIPIN+1
9 TRPML 443979 2% 70% 7 Search TRPML Search TRPML
10 TRANSCRIPTION FACTOR EB 296532 2% 55% 6 Search TRANSCRIPTION+FACTOR+EB Search TRANSCRIPTION+FACTOR+EB

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 VENKATACHALAM, K , WONG, CO , ZHU, MX , (2015) THE ROLE OF TRPMLS IN ENDOLYSOSOMAL TRAFFICKING AND FUNCTION.CELL CALCIUM. VOL. 58. ISSUE 1. P. 48 -56 109 86% 11
2 WAKABAYASHI, K , GUSTAFSON, AM , SIDRANSKY, E , GOLDIN, E , (2011) MUCOLIPIDOSIS TYPE IV: AN UPDATE.MOLECULAR GENETICS AND METABOLISM. VOL. 104. ISSUE 3. P. 206 -213 55 87% 22
3 BACH, G , ZEEVI, DA , FRUMKIN, A , LEVIN, AK , (2010) MUCOLIPIDOSIS TYPE IV AND THE MUCOLIPINS.BIOCHEMICAL SOCIETY TRANSACTIONS. VOL. 38. ISSUE . P. 1432 -1435 52 90% 10
4 COLLETTI, GA , KISELYOV, K , (2011) TRPML1.TRANSIENT RECEPTOR POTENTIAL CHANNELS. VOL. 704. ISSUE . P. 209 -219 45 94% 8
5 CHEN, CC , KELLER, M , HESS, M , SCHIFFMANN, R , URBAN, N , WOLFGARDT, A , SCHAEFER, M , BRACHER, F , BIEL, M , WAHL-SCHOTT, C , ET AL (2014) A SMALL MOLECULE RESTORES FUNCTION TO TRPML1 MUTANT ISOFORMS RESPONSIBLE FOR MUCOLIPIDOSIS TYPE IV.NATURE COMMUNICATIONS. VOL. 5. ISSUE . P. - 37 80% 12
6 ZEEVI, DA , LEV, S , FRUMKIN, A , MINKE, B , BACH, G , (2010) HETEROMULTIMERIC TRPML CHANNEL ASSEMBLIES PLAY A CRUCIAL ROLE IN THE REGULATION OF CELL VIABILITY MODELS AND STARVATION-INDUCED AUTOPHAGY.JOURNAL OF CELL SCIENCE. VOL. 123. ISSUE 18. P. 3112 -3124 39 85% 22
7 CHENG, XP , SHEN, DB , SAMIE, M , XU, HX , (2010) MUCOLIPINS: INTRACELLULAR TRPML1-3 CHANNELS.FEBS LETTERS. VOL. 584. ISSUE 10. P. 2013 -2021 47 62% 54
8 ZEEVI, DA , FRUMKIN, A , BACH, G , (2007) TRPML AND LYSOSOMAL FUNCTION.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE. VOL. 1772. ISSUE 8. P. 851-858 38 76% 38
9 GRISHCHUK, Y , STEMBER, KG , MATSUNAGA, A , OLIVARES, AM , CRUZ, NM , KING, VE , HUMPHREY, DM , WANG, SL , MUZIKANSKY, A , BETENSKY, RA , ET AL (2016) RETINAL DYSTROPHY AND OPTIC NERVE PATHOLOGY IN THE MOUSE MODEL OF MUCOLIPIDOSIS IV.AMERICAN JOURNAL OF PATHOLOGY. VOL. 186. ISSUE 1. P. 199 -209 33 69% 1
10 BACH, G , (2005) MUCOLIPIN 1: ENDOCYTOSIS AND CATION CHANNEL - A REVIEW.PFLUGERS ARCHIV-EUROPEAN JOURNAL OF PHYSIOLOGY. VOL. 451. ISSUE 1. P. 313-317 35 83% 47

Classes with closest relation at Level 1



Rank Class id link
1 6900 CYCLIC ADP RIBOSE//ADP RIBOSYL CYCLASE//NAADP
2 19319 DANON DISEASE//LAMP 2//LAMP 2 DEFICIENCY
3 18351 LYSOSOME//OSMOTIC SENSITIVITY//CALPAIN CATHEPSIN HYPOTHESIS
4 36006 NANO EU2O3//ANTI MIGRATION AND ANTI INVASION//AUTOPHAGY MODULATING EFFECT
5 6069 NIEMANN PICK DISEASE TYPE C//NIEMANN PICK TYPE C//NIEMANN PICK DISEASE
6 59 AUTOPHAGY//BECLIN 1//LC3
7 35322 LAPTM4B//LAPTM4B 35//LYSOSOMAL PROTEIN TRANSMEMBRANE 4 BETA
8 3008 TRPA1//TRPM8//TRPV4
9 6422 RHEB//RICTOR//REDD1
10 11351 GALACTOSIALIDOSIS//SIALIDASE//SIALIDOSIS

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