Class information for:
Level 1: BIRT HOGG DUBE SYNDROME//FOLLICULIN//FIBROFOLLICULOMA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
20503 457 25.2 72%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
465 3       RENAL CELL CARCINOMA//ANGIOMYOLIPOMA//TUBEROUS SCLEROSIS 24387
1854 2             ANGIOMYOLIPOMA//TUBEROUS SCLEROSIS//TUBEROUS SCLEROSIS COMPLEX 6081
20503 1                   BIRT HOGG DUBE SYNDROME//FOLLICULIN//FIBROFOLLICULOMA 457

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BIRT HOGG DUBE SYNDROME authKW 4256080 18% 79% 81
2 FOLLICULIN authKW 2521271 9% 88% 43
3 FIBROFOLLICULOMA authKW 2278773 8% 95% 36
4 FLCN authKW 1359443 5% 88% 23
5 FOLLICULOSEBACEOUS CYSTIC HAMARTOMA authKW 1202688 4% 100% 18
6 BHD authKW 1016052 5% 72% 21
7 BIRT HOGG DUBE authKW 809875 4% 61% 20
8 TRICHODISCOMA authKW 621899 2% 85% 11
9 PERIFOLLICULAR FIBROMA authKW 475134 2% 89% 8
10 FOLLICULIN GENE authKW 467712 2% 100% 7

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 13297 41% 0% 187
2 Pathology 852 13% 0% 58
3 Genetics & Heredity 683 17% 0% 78
4 Oncology 304 15% 0% 69
5 Veterinary Sciences 162 8% 0% 35
6 Respiratory System 121 5% 0% 22
7 Cell Biology 75 9% 0% 39
8 Urology & Nephrology 18 3% 0% 12
9 Critical Care Medicine 6 1% 0% 5
10 Developmental Biology 6 1% 0% 5

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 UROL MOL GENET 160351 1% 40% 6
2 UNIT SKIN HISTOPATHOL 133632 0% 100% 2
3 PNEUMOTHORAX 120260 1% 30% 6
4 UROL ONCOL BRANCH 96169 7% 5% 32
5 GENET EAU INCA 89087 0% 67% 2
6 TOXICOL TERATOL 75164 1% 38% 3
7 ABT KLIN WISSEN 66816 0% 100% 1
8 ANAT HUMAN PATHOL 66816 0% 100% 1
9 AUTONOMA MED VET CONVENIO CONSULTORIA DERMATOPATO 66816 0% 100% 1
10 BIRT HOGG DUBE WORKING GRP 66816 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 AMERICAN JOURNAL OF DERMATOPATHOLOGY 11420 5% 1% 25
2 FAMILIAL CANCER 9229 2% 1% 11
3 JOURNAL OF CUTANEOUS PATHOLOGY 7978 5% 1% 21
4 ANNALS OF DERMATOLOGY 3458 2% 1% 7
5 ANNALES DE DERMATOLOGIE ET DE VENEREOLOGIE 2989 4% 0% 16
6 ARCHIVES OF DERMATOLOGY 2106 3% 0% 14
7 INTERNATIONAL JOURNAL OF DERMATOLOGY 2045 3% 0% 15
8 HAUTARZT 1383 2% 0% 10
9 JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 1382 4% 0% 16
10 EUROPEAN JOURNAL OF DERMATOLOGY 1224 2% 0% 7

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 BIRT HOGG DUBE SYNDROME 4256080 18% 79% 81 Search BIRT+HOGG+DUBE+SYNDROME Search BIRT+HOGG+DUBE+SYNDROME
2 FOLLICULIN 2521271 9% 88% 43 Search FOLLICULIN Search FOLLICULIN
3 FIBROFOLLICULOMA 2278773 8% 95% 36 Search FIBROFOLLICULOMA Search FIBROFOLLICULOMA
4 FLCN 1359443 5% 88% 23 Search FLCN Search FLCN
5 FOLLICULOSEBACEOUS CYSTIC HAMARTOMA 1202688 4% 100% 18 Search FOLLICULOSEBACEOUS+CYSTIC+HAMARTOMA Search FOLLICULOSEBACEOUS+CYSTIC+HAMARTOMA
6 BHD 1016052 5% 72% 21 Search BHD Search BHD
7 BIRT HOGG DUBE 809875 4% 61% 20 Search BIRT+HOGG+DUBE Search BIRT+HOGG+DUBE
8 TRICHODISCOMA 621899 2% 85% 11 Search TRICHODISCOMA Search TRICHODISCOMA
9 PERIFOLLICULAR FIBROMA 475134 2% 89% 8 Search PERIFOLLICULAR+FIBROMA Search PERIFOLLICULAR+FIBROMA
10 FOLLICULIN GENE 467712 2% 100% 7 Search FOLLICULIN+GENE Search FOLLICULIN+GENE

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 SCHMIDT, LS , LINEHAN, WM , (2015) CLINICAL FEATURES, GENETICS AND POTENTIAL THERAPEUTIC APPROACHES FOR BIRT-HOGG-DUBE SYNDROME.EXPERT OPINION ON ORPHAN DRUGS. VOL. 3. ISSUE 1. P. 15 -29 81 92% 5
2 SCHMIDT, LS , LINEHAN, WM , (2015) MOLECULAR GENETICS AND CLINICAL FEATURES OF BIRT-HOGG-DUBE SYNDROME.NATURE REVIEWS UROLOGY. VOL. 12. ISSUE 10. P. 558 -569 78 76% 10
3 HASUMI, H , BABA, M , HASUMI, Y , FURUYA, M , YAO, M , (2016) BIRT-HOGG-DUBE SYNDROME: CLINICAL AND MOLECULAR ASPECTS OF RECENTLY IDENTIFIED KIDNEY CANCER SYNDROME.INTERNATIONAL JOURNAL OF UROLOGY. VOL. 23. ISSUE 3. P. 204 -210 58 92% 2
4 MENKO, FH , VAN STEENSEL, MAM , GIRAUD, S , FRIIS-HANSEN, L , RICHARD, S , UNGARI, S , NORDENSKJOLD, M , HANSEN, TV , SOLLY, J , MAHER, ER , (2009) BIRT-HOGG-DUBE SYNDROME: DIAGNOSIS AND MANAGEMENT.LANCET ONCOLOGY. VOL. 10. ISSUE 12. P. 1199-1206 58 81% 121
5 GUPTA, N , SUNWOO, BY , KOTLOFF, RM , (2016) BIRT-HOGG-DUBE SYNDROME.CLINICS IN CHEST MEDICINE. VOL. 37. ISSUE 3. P. 475 -+ 59 81% 0
6 PALMIROTTA, R , SAVONAROLA, A , LUDOVICI, G , DONATI, P , CAVALIERE, F , DE MARCHIS, ML , FERRONI, P , GUADAGNI, F , (2010) ASSOCIATION BETWEEN BIRT HOGG DUBE SYNDROME AND CANCER PREDISPOSITION.ANTICANCER RESEARCH. VOL. 30. ISSUE 3. P. 751 -757 46 100% 11
7 SCHMIDT, LS , (2013) BIRT-HOGG-DUBE SYNDROME: FROM GENE DISCOVERY TO MOLECULARLY TARGETED THERAPIES.FAMILIAL CANCER. VOL. 12. ISSUE 3. P. 357-364 41 98% 11
8 FURUYA, M , NAKATANI, Y , (2013) BIRT-HOGG-DUBE SYNDROME: CLINICOPATHOLOGICAL FEATURES OF THE LUNG.JOURNAL OF CLINICAL PATHOLOGY. VOL. 66. ISSUE 3. P. 178-186 38 95% 18
9 KENNEDY, JC , KHABIBULLIN, D , HENSKE, EP , (2016) MECHANISMS OF PULMONARY CYST PATHOGENESIS IN BIRT-HOGG-DUBE SYNDROME: THE STRETCH HYPOTHESIS.SEMINARS IN CELL & DEVELOPMENTAL BIOLOGY. VOL. 52. ISSUE . P. 47 -52 41 76% 2
10 TORO, JR , WEI, MH , GLENN, GM , WEINREICH, M , TOURE, O , VOCKE, C , TURNER, M , CHOYKE, P , MERINO, MJ , PINTO, PA , ET AL (2008) BHD MUTATIONS, CLINICAL AND MOLECULAR GENETIC INVESTIGATIONS OF BIRT-HOGG-DUBE SYNDROME: A NEW SERIES OF 50 FAMILIES AND A REVIEW OF PUBLISHED REPORTS.JOURNAL OF MEDICAL GENETICS. VOL. 45. ISSUE 6. P. 321-331 32 84% 157

Classes with closest relation at Level 1



Rank Class id link
1 19177 FUMARATE HYDRATASE//HLRCC//CUTANEOUS LEIOMYOSARCOMA
2 13445 TRICHOEPITHELIOMA//CYLD//BROOKE SPIEGLER SYNDROME
3 15283 LYMPHANGIOLEIOMYOMATOSIS//LYMPHANGIOMYOMATOSIS//PULMONARY LYMPHANGIOLEIOMYOMATOSIS
4 2032 CHROMOPHOBE RENAL CELL CARCINOMA//RENAL ONCOCYTOMA//COLLECTING DUCT CARCINOMA
5 11613 SPONTANEOUS PNEUMOTHORAX//PRIMARY SPONTANEOUS PNEUMOTHORAX//PNEUMOTHORAX
6 31230 SKIN TAGS//CLEAR CELL ACANTHOMA//ACROCHORDON
7 13169 SEBACEOUS CARCINOMA//MUIR TORRE SYNDROME//SEBACEOMA
8 24588 SMITH MAGENIS SYNDROME//RAI1//POTOCKI LUPSKI SYNDROME
9 3154 HEMANGIOBLASTOMA//VON HIPPEL LINDAU DISEASE//VON HIPPEL LINDAU
10 2838 TUBEROUS SCLEROSIS//TUBEROUS SCLEROSIS COMPLEX//SUBEPENDYMAL GIANT CELL ASTROCYTOMA

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