Class information for:
Level 1: TUBEROUS SCLEROSIS//TUBEROUS SCLEROSIS COMPLEX//SUBEPENDYMAL GIANT CELL ASTROCYTOMA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
2838 2134 35.0 78%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
465 3       RENAL CELL CARCINOMA//ANGIOMYOLIPOMA//TUBEROUS SCLEROSIS 24387
1854 2             ANGIOMYOLIPOMA//TUBEROUS SCLEROSIS//TUBEROUS SCLEROSIS COMPLEX 6081
2838 1                   TUBEROUS SCLEROSIS//TUBEROUS SCLEROSIS COMPLEX//SUBEPENDYMAL GIANT CELL ASTROCYTOMA 2134

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 TUBEROUS SCLEROSIS authKW 3544965 23% 51% 488
2 TUBEROUS SCLEROSIS COMPLEX authKW 3055878 16% 63% 339
3 SUBEPENDYMAL GIANT CELL ASTROCYTOMA authKW 1274751 5% 90% 99
4 TUBERIN authKW 984475 4% 75% 92
5 HAMARTIN authKW 816848 3% 88% 65
6 TSC2 authKW 796552 5% 53% 105
7 TSC1 authKW 731570 4% 68% 75
8 SEGA authKW 284449 1% 76% 26
9 CORTICAL TUBER authKW 235440 1% 69% 24
10 TUBEROUS SCLEROSIS COMPLEX TSC authKW 224312 1% 56% 28

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 10282 31% 0% 657
2 Pediatrics 4231 16% 0% 342
3 Genetics & Heredity 2099 14% 0% 302
4 Pathology 1566 8% 0% 176
5 Dermatology 977 6% 0% 120
6 Neurosciences 915 14% 0% 305
7 Neuroimaging 463 2% 0% 42
8 Radiology, Nuclear Medicine & Medical Imaging 376 6% 0% 136
9 Urology & Nephrology 278 4% 0% 87
10 Oncology 241 8% 0% 163

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PENN EPILEPSY 169920 1% 42% 28
2 TUBEROUS SCLEROSIS CLIN 130064 0% 91% 10
3 CAROL JAMES HERSCOT TUBEROUS SCLEROSIS COMP 100150 0% 100% 7
4 BATH UNIT PAEDIAT 75292 0% 53% 10
5 HERSCOT TUBEROUS SCLEROSIS COMPLEX 59612 0% 83% 5
6 NEURODEV SERV NDS 59612 0% 83% 5
7 EXPT MED MED ONCOL 57229 0% 100% 4
8 EXPERTISE NEURODEV DISORDERS 51094 0% 71% 5
9 NEUROL EPILEPTOL 47365 1% 13% 26
10 DEV PSYCHIAT SECT 44330 1% 16% 20

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF CHILD NEUROLOGY 12773 3% 1% 66
2 EPILEPSIA 6488 3% 1% 64
3 PEDIATRIC NEUROLOGY 4326 2% 1% 36
4 EUROPEAN JOURNAL OF PAEDIATRIC NEUROLOGY 3719 1% 2% 17
5 BRAIN & DEVELOPMENT 3500 1% 1% 30
6 JOURNAL OF MEDICAL GENETICS 2973 2% 1% 35
7 HUMAN MOLECULAR GENETICS 2644 2% 0% 43
8 CHILDS NERVOUS SYSTEM 2047 1% 1% 27
9 ANNALS OF NEUROLOGY 1830 1% 0% 32
10 ACTA NEUROPATHOLOGICA 1493 1% 0% 25

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 TUBEROUS SCLEROSIS 3544965 23% 51% 488 Search TUBEROUS+SCLEROSIS Search TUBEROUS+SCLEROSIS
2 TUBEROUS SCLEROSIS COMPLEX 3055878 16% 63% 339 Search TUBEROUS+SCLEROSIS+COMPLEX Search TUBEROUS+SCLEROSIS+COMPLEX
3 SUBEPENDYMAL GIANT CELL ASTROCYTOMA 1274751 5% 90% 99 Search SUBEPENDYMAL+GIANT+CELL+ASTROCYTOMA Search SUBEPENDYMAL+GIANT+CELL+ASTROCYTOMA
4 TUBERIN 984475 4% 75% 92 Search TUBERIN Search TUBERIN
5 HAMARTIN 816848 3% 88% 65 Search HAMARTIN Search HAMARTIN
6 TSC2 796552 5% 53% 105 Search TSC2 Search TSC2
7 TSC1 731570 4% 68% 75 Search TSC1 Search TSC1
8 SEGA 284449 1% 76% 26 Search SEGA Search SEGA
9 CORTICAL TUBER 235440 1% 69% 24 Search CORTICAL+TUBER Search CORTICAL+TUBER
10 TUBEROUS SCLEROSIS COMPLEX TSC 224312 1% 56% 28 Search TUBEROUS+SCLEROSIS+COMPLEX+TSC Search TUBEROUS+SCLEROSIS+COMPLEX+TSC

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 CURATOLO, P , BOMBARDIERI, R , JOZWIAK, S , (2008) TUBEROUS SCLEROSIS.LANCET. VOL. 372. ISSUE 9639. P. 657 -668 100 73% 295
2 HENSKE, EP , JOZWIAK, S , KINGSWOOD, JC , SAMPSON, JR , THIELE, EA , (2016) TUBEROUS SCLEROSIS COMPLEX.NATURE REVIEWS DISEASE PRIMERS. VOL. 2. ISSUE . P. - 122 68% 2
3 FELICIANO, DM , LIN, TV , HARTMAN, NW , BARTLEY, CM , KUBERA, C , HSIEH, L , LAFOURCADE, C , O'KEEFE, RA , BORDEY, A , (2013) A CIRCUITRY AND BIOCHEMICAL BASIS FOR TUBEROUS SCLEROSIS SYMPTOMS: FROM EPILEPSY TO NEUROCOGNITIVE DEFICITS.INTERNATIONAL JOURNAL OF DEVELOPMENTAL NEUROSCIENCE. VOL. 31. ISSUE 7. P. 667-678 109 73% 17
4 CURATOLO, P , MOAVERO, R , DE VRIES, PJ , (2015) NEUROLOGICAL AND NEUROPSYCHIATRIC ASPECTS OF TUBEROUS SCLEROSIS COMPLEX.LANCET NEUROLOGY. VOL. 14. ISSUE 7. P. 733 -745 71 80% 30
5 HOLMES, GL , STAFSTROM, CE , (2007) TUBEROUS SCLEROSIS COMPLEX AND EPILEPSY: RECENT DEVELOPMENTS AND FUTURE CHALLENGES.EPILEPSIA. VOL. 48. ISSUE 4. P. 617-630 93 84% 118
6 CRINO, PB , NATHANSON, KL , HENSKE, EP , (2006) THE TUBEROUS SCLEROSIS COMPLEX.NEW ENGLAND JOURNAL OF MEDICINE. VOL. 355. ISSUE 13. P. 1345-1356 69 73% 685
7 CRINO, PB , (2013) EVOLVING NEUROBIOLOGY OF TUBEROUS SCLEROSIS COMPLEX.ACTA NEUROPATHOLOGICA. VOL. 125. ISSUE 3. P. 317 -332 80 80% 41
8 CHEADLE, JP , REEVE, MP , SAMPSON, JR , KWIATKOWSKI, DJ , (2000) MOLECULAR GENETIC ADVANCES IN TUBEROUS SCLEROSIS.HUMAN GENETICS. VOL. 107. ISSUE 2. P. 97 -114 107 76% 185
9 CITRARO, R , LEO, A , CONSTANTI, A , RUSSO, E , DE SARRO, G , (2016) MTOR PATHWAY INHIBITION AS A NEW THERAPEUTIC STRATEGY IN EPILEPSY AND EPILEPTOGENESIS.PHARMACOLOGICAL RESEARCH. VOL. 107. ISSUE . P. 333 -343 72 58% 8
10 CURATOLO, P , (2015) MECHANISTIC TARGET OF RAPAMYCIN (MTOR) IN TUBEROUS SCLEROSIS COMPLEX-ASSOCIATED EPILEPSY.PEDIATRIC NEUROLOGY. VOL. 52. ISSUE 3. P. 281 -289 56 89% 17

Classes with closest relation at Level 1



Rank Class id link
1 15283 LYMPHANGIOLEIOMYOMATOSIS//LYMPHANGIOMYOMATOSIS//PULMONARY LYMPHANGIOLEIOMYOMATOSIS
2 13042 RHABDOMYOMA//CARDIAC RHABDOMYOMA//CARDIAC TUMOR
3 5499 ANGIOMYOLIPOMA//PECOMA//PERIVASCULAR EPITHELIOID CELL TUMOR
4 6422 RHEB//RICTOR//REDD1
5 4602 CORTICAL DYSPLASIA//FOCAL CORTICAL DYSPLASIA//SCHIZENCEPHALY
6 10778 WEST SYNDROME//INFANTILE SPASMS//HYPSARRHYTHMIA
7 20503 BIRT HOGG DUBE SYNDROME//FOLLICULIN//FIBROFOLLICULOMA
8 17613 STURGE WEBER SYNDROME//CHOROIDAL HEMANGIOMA//CIRCUMSCRIBED CHOROIDAL HEMANGIOMA
9 19028 COATS DISEASE//IDIOPATHIC MACULAR TELANGIECTASIA//MACULAR TELANGIECTASIA
10 28347 MESOTHELIN//ERC MESOTHELIN//MORAB 009

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