Class information for:
Level 1: FUMARATE HYDRATASE//HLRCC//CUTANEOUS LEIOMYOSARCOMA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
19177 518 28.3 71%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
438 3       ENDOMETRIOSIS//LEIOMYOMA//OBSTETRICS & GYNECOLOGY 26743
1605 2             LEIOMYOSARCOMA//ENDOMETRIAL STROMAL SARCOMA//UTERINE SARCOMA 7106
19177 1                   FUMARATE HYDRATASE//HLRCC//CUTANEOUS LEIOMYOSARCOMA 518

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 FUMARATE HYDRATASE authKW 2790997 13% 72% 66
2 HLRCC authKW 1676721 6% 89% 32
3 CUTANEOUS LEIOMYOSARCOMA authKW 707370 2% 100% 12
4 CUTANEOUS LEIOMYOMA authKW 594385 2% 92% 11
5 HEREDITARY LEIOMYOMATOSIS AND RENAL CELL CANCER authKW 535884 2% 91% 10
6 SUCCINATION authKW 434064 2% 82% 9
7 FUMARASE DEFICIENCY authKW 361052 1% 88% 7
8 HEREDITARY LEIOMYOMATOSIS AND RENAL CELL CANCER HLRCC authKW 303157 1% 86% 6
9 CUTANEOUS LEIOMYOMATOSIS authKW 294737 1% 100% 5
10 FUMARATE HYDRATASE FH authKW 265261 1% 75% 6

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 9514 33% 0% 169
2 Pathology 1137 14% 0% 71
3 Oncology 543 18% 0% 95
4 Genetics & Heredity 361 12% 0% 63
5 Urology & Nephrology 303 8% 0% 40
6 Surgery 119 10% 0% 53
7 Medicine, Research & Experimental 39 4% 0% 23
8 Cell Biology 36 6% 0% 33
9 Endocrinology & Metabolism 16 3% 0% 18
10 Obstetrics & Gynecology 16 3% 0% 13

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 OXFORD KEIO METABOL CONSORTIUM 235790 1% 100% 4
2 CANC BIOL METAB GRP 184207 1% 63% 5
3 UROL ONCOL BRANCH 119647 7% 5% 38
4 HYPOXIA BIOL GRP 117895 0% 100% 2
5 INTERDISCIPLINARY UROL ONCOL 117895 0% 100% 2
6 MOL POPULAT GENET 82407 4% 7% 20
7 ST BARTHOLOMEWS LONDON MED DENT 81864 1% 28% 5
8 ABS REUS 3 58947 0% 100% 1
9 BIOMED HELINSKI 58947 0% 100% 1
10 CAN BIOL GENET 58947 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 FAMILIAL CANCER 5445 2% 1% 9
2 AMERICAN JOURNAL OF SURGICAL PATHOLOGY 3109 3% 0% 18
3 AMERICAN JOURNAL OF DERMATOPATHOLOGY 2710 3% 0% 13
4 JOURNAL OF CUTANEOUS PATHOLOGY 2287 2% 0% 12
5 VESTNIK DERMATOLOGII I VENEROLOGII 1396 2% 0% 8
6 CANCER CELL 1379 1% 0% 6
7 ARCHIVES OF DERMATOLOGY 1359 2% 0% 12
8 CHINESE JOURNAL OF CANCER 1337 1% 1% 3
9 DERMATOLOGY 1171 2% 0% 9
10 JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 1066 3% 0% 15

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 FUMARATE HYDRATASE 2790997 13% 72% 66 Search FUMARATE+HYDRATASE Search FUMARATE+HYDRATASE
2 HLRCC 1676721 6% 89% 32 Search HLRCC Search HLRCC
3 CUTANEOUS LEIOMYOSARCOMA 707370 2% 100% 12 Search CUTANEOUS+LEIOMYOSARCOMA Search CUTANEOUS+LEIOMYOSARCOMA
4 CUTANEOUS LEIOMYOMA 594385 2% 92% 11 Search CUTANEOUS+LEIOMYOMA Search CUTANEOUS+LEIOMYOMA
5 HEREDITARY LEIOMYOMATOSIS AND RENAL CELL CANCER 535884 2% 91% 10 Search HEREDITARY+LEIOMYOMATOSIS+AND+RENAL+CELL+CANCER Search HEREDITARY+LEIOMYOMATOSIS+AND+RENAL+CELL+CANCER
6 SUCCINATION 434064 2% 82% 9 Search SUCCINATION Search SUCCINATION
7 FUMARASE DEFICIENCY 361052 1% 88% 7 Search FUMARASE+DEFICIENCY Search FUMARASE+DEFICIENCY
8 HEREDITARY LEIOMYOMATOSIS AND RENAL CELL CANCER HLRCC 303157 1% 86% 6 Search HEREDITARY+LEIOMYOMATOSIS+AND+RENAL+CELL+CANCER+HLRCC Search HEREDITARY+LEIOMYOMATOSIS+AND+RENAL+CELL+CANCER+HLRCC
9 CUTANEOUS LEIOMYOMATOSIS 294737 1% 100% 5 Search CUTANEOUS+LEIOMYOMATOSIS Search CUTANEOUS+LEIOMYOMATOSIS
10 FUMARATE HYDRATASE FH 265261 1% 75% 6 Search FUMARATE+HYDRATASE+FH Search FUMARATE+HYDRATASE+FH

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 MALIK, K , PATEL, P , CHEN, J , KHACHEMOUNE, A , (2015) LEIOMYOMA CUTIS: A FOCUSED REVIEW ON PRESENTATION, MANAGEMENT, AND ASSOCIATION WITH MALIGNANCY.AMERICAN JOURNAL OF CLINICAL DERMATOLOGY. VOL. 16. ISSUE 1. P. 35 -46 62 69% 2
2 LEHTONEN, HJ , (2011) HEREDITARY LEIOMYOMATOSIS AND RENAL CELL CANCER: UPDATE ON CLINICAL AND MOLECULAR CHARACTERISTICS.FAMILIAL CANCER. VOL. 10. ISSUE 2. P. 397 -411 59 63% 41
3 BADELOE, S , FRANK, J , (2009) CLINICAL AND MOLECULAR GENETIC ASPECTS OF HEREDITARY MULTIPLE CUTANEOUS LEIOMYOMATOSIS.EUROPEAN JOURNAL OF DERMATOLOGY. VOL. 19. ISSUE 6. P. 545 -551 52 75% 21
4 MENKO, FH , MAHER, ER , SCHMIDT, LS , MIDDELTON, LA , AITTOMAKI, K , TOMLINSON, I , RICHARD, S , LINEHAN, WM , (2014) HEREDITARY LEIOMYOMATOSIS AND RENAL CELL CANCER (HLRCC): RENAL CANCER RISK, SURVEILLANCE AND TREATMENT.FAMILIAL CANCER. VOL. 13. ISSUE 4. P. 637 -644 33 73% 15
5 GARDIE, B , REMENIERAS, A , KATTYGNARATH, D , BOMBLED, J , LEFEVRE, S , PERRIER-TRUDOVA, V , RUSTIN, P , BARROIS, M , SLAMA, A , AVRIL, MF , ET AL (2011) NOVEL FH MUTATIONS IN FAMILIES WITH HEREDITARY LEIOMYOMATOSIS AND RENAL CELL CANCER (HLRCC) AND PATIENTS WITH ISOLATED TYPE 2 PAPILLARY RENAL CELL CARCINOMA.JOURNAL OF MEDICAL GENETICS. VOL. 48. ISSUE 4. P. 226 -234 32 82% 33
6 SMIT, DL , MENSENKAMP, AR , BADELOE, S , BREUNING, MH , SIMON, MEH , VAN SPAENDONCK, KY , AALFS, CM , POST, JG , SHANLEY, S , KRAPELS, IPC , ET AL (2011) HEREDITARY LEIOMYOMATOSIS AND RENAL CELL CANCER IN FAMILIES REFERRED FOR FUMARATE HYDRATASE GERMLINE MUTATION ANALYSIS.CLINICAL GENETICS. VOL. 79. ISSUE 1. P. 49 -59 27 93% 35
7 REYES, C , KARAMURZIN, Y , FRIZZELL, N , GARG, K , NONAKA, D , CHEN, YB , SOSLOW, RA , (2014) UTERINE SMOOTH MUSCLE TUMORS WITH FEATURES SUGGESTING FUMARATE HYDRATASE ABERRATION: DETAILED MORPHOLOGIC ANALYSIS AND CORRELATION WITH S-(2-SUCCINO)-CYSTEINE IMMUNOHISTOCHEMISTRY.MODERN PATHOLOGY. VOL. 27. ISSUE 7. P. 1020 -1027 32 74% 7
8 ANEIROS-FERNANDEZ, J , ANTONIO RETAMERO, J , HUSEIN-ELAHMED, H , OVALLE, F , ANEIROS-CACHAZA, J , (2016) PRIMARY CUTANEOUS AND SUBCUTANEOUS LEIOMYOSARCOMAS: EVOLUTION AND PROGNOSTIC FACTORS.EUROPEAN JOURNAL OF DERMATOLOGY. VOL. 26. ISSUE 1. P. 9 -12 23 92% 1
9 TRPKOV, K , HES, O , AGAIMY, A , BONERT, M , MARTINEK, P , MAGI-GALLUZZI, C , KRISTIANSEN, G , LUDERS, C , NESI, G , COMPERAT, E , ET AL (2016) FUMARATE HYDRATASE-DEFICIENT RENAL CELL CARCINOMA IS STRONGLY CORRELATED WITH FUMARATE HYDRATASE MUTATION AND HEREDITARY LEIOMYOMATOSIS AND RENAL CELL CARCINOMA SYNDROME.AMERICAN JOURNAL OF SURGICAL PATHOLOGY. VOL. 40. ISSUE 7. P. 865 -875 23 96% 0
10 MASSI, D , FRANCHI, A , ALOS, L , COOK, M , DI PALMA, S , ENGUITA, AB , FERRARA, G , KAZAKOV, DV , MENTZEL, T , MICHAL, M , ET AL (2010) PRIMARY CUTANEOUS LEIOMYOSARCOMA: CLINICOPATHOLOGICAL ANALYSIS OF 36 CASES.HISTOPATHOLOGY. VOL. 56. ISSUE 2. P. 251 -262 24 89% 23

Classes with closest relation at Level 1



Rank Class id link
1 17906 ANGIOLEIOMYOMA//VASCULAR LEIOMYOMA//ANGIOMYOMA
2 20503 BIRT HOGG DUBE SYNDROME//FOLLICULIN//FIBROFOLLICULOMA
3 23900 ASPARTASE//MALEATE CIS TRANS ISOMERASE//MALEATE HYDRATASE
4 21395 SMOOTH MUSCLE TUMOR//PRIMARY HEPATIC LEIOMYOSARCOMA//LEIOMYOSARCOMA
5 27586 BAP1//SETD2//BRCA1 ASSOCIATED PROTEIN 1
6 21558 CUTIS VERTICIS GYRATA//CONGENITAL HYPERTRICHOSIS//HYPERTRICHOSIS CUBITI
7 19914 SPERMATIC CORD//PROSTATIC STROMAL SARCOMA//PARATESTICULAR
8 6633 UTERINE LEIOMYOMA//LEIOMYOMA//FIBROIDS
9 7269 DERMATOFIBROSARCOMA PROTUBERANS//DERMATOFIBROMA//ATYPICAL FIBROXANTHOMA
10 2032 CHROMOPHOBE RENAL CELL CARCINOMA//RENAL ONCOCYTOMA//COLLECTING DUCT CARCINOMA

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