Class information for:
Level 1: HEMANGIOBLASTOMA//VON HIPPEL LINDAU DISEASE//VON HIPPEL LINDAU

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
3154 2052 32.6 77%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
465 3       RENAL CELL CARCINOMA//ANGIOMYOLIPOMA//TUBEROUS SCLEROSIS 24387
318 2             RENAL CELL CARCINOMA//PARTIAL NEPHRECTOMY//KIDNEY NEOPLASMS 18306
3154 1                   HEMANGIOBLASTOMA//VON HIPPEL LINDAU DISEASE//VON HIPPEL LINDAU 2052

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HEMANGIOBLASTOMA authKW 4471390 18% 81% 371
2 VON HIPPEL LINDAU DISEASE authKW 3803567 17% 74% 347
3 VON HIPPEL LINDAU authKW 866229 6% 46% 127
4 HAEMANGIOBLASTOMA authKW 692429 3% 85% 55
5 VHL authKW 671772 6% 34% 131
6 VON HIPPEL LINDAU SYNDROME authKW 671041 3% 72% 63
7 VHL GENE authKW 410585 2% 64% 43
8 HEMANGIOBLASTOMAS authKW 219121 1% 82% 18
9 RETINAL ANGIOMA authKW 167381 1% 75% 15
10 CEREBELLAR HEMANGIOBLASTOMA authKW 138486 1% 85% 11

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 4985 22% 0% 459
2 Pathology 3044 11% 0% 234
3 Oncology 2722 20% 0% 417
4 Surgery 1979 18% 0% 375
5 Ophthalmology 1521 8% 0% 162
6 Genetics & Heredity 1281 12% 0% 238
7 Urology & Nephrology 793 6% 0% 132
8 Cell Biology 454 10% 0% 196
9 Radiology, Nuclear Medicine & Medical Imaging 289 6% 0% 120
10 Neuroimaging 231 1% 0% 30

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SURG NEUROL BRANCH 93344 3% 10% 62
2 UROL ONCOL BRANCH 56490 3% 7% 52
3 GENET ONCOL EPHE 49995 1% 31% 11
4 CANC UK RENAL MOL ONCOL GRP 35257 0% 30% 8
5 EPHE FRE 2939 29758 0% 100% 2
6 NEUROONCOL EPHE 29758 0% 100% 2
7 AUGEN ZENTRUM 26447 0% 44% 4
8 METAB CHECKPOINT 22316 0% 50% 3
9 ABT VISZERALE CHIRURG 19837 0% 67% 2
10 BIOMED SCICANC 19837 0% 67% 2

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SURGICAL NEUROLOGY 3233 2% 1% 34
2 FAMILIAL CANCER 2852 1% 1% 13
3 NEUROSURGERY 2672 2% 0% 49
4 ACTA NEUROCHIRURGICA 2494 2% 0% 35
5 BRITISH JOURNAL OF NEUROSURGERY 1829 1% 1% 19
6 JOURNAL OF NEUROSURGERY 1709 2% 0% 40
7 NEUROLOGIA MEDICO-CHIRURGICA 1597 1% 1% 17
8 NEUROSURGICAL REVIEW 1376 1% 1% 12
9 JOURNAL OF CLINICAL NEUROSCIENCE 1305 1% 0% 23
10 CANCER RESEARCH 1279 3% 0% 60

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 HEMANGIOBLASTOMA 4471390 18% 81% 371 Search HEMANGIOBLASTOMA Search HEMANGIOBLASTOMA
2 VON HIPPEL LINDAU DISEASE 3803567 17% 74% 347 Search VON+HIPPEL+LINDAU+DISEASE Search VON+HIPPEL+LINDAU+DISEASE
3 VON HIPPEL LINDAU 866229 6% 46% 127 Search VON+HIPPEL+LINDAU Search VON+HIPPEL+LINDAU
4 HAEMANGIOBLASTOMA 692429 3% 85% 55 Search HAEMANGIOBLASTOMA Search HAEMANGIOBLASTOMA
5 VHL 671772 6% 34% 131 Search VHL Search VHL
6 VON HIPPEL LINDAU SYNDROME 671041 3% 72% 63 Search VON+HIPPEL+LINDAU+SYNDROME Search VON+HIPPEL+LINDAU+SYNDROME
7 VHL GENE 410585 2% 64% 43 Search VHL+GENE Search VHL+GENE
8 HEMANGIOBLASTOMAS 219121 1% 82% 18 Search HEMANGIOBLASTOMAS Search HEMANGIOBLASTOMAS
9 RETINAL ANGIOMA 167381 1% 75% 15 Search RETINAL+ANGIOMA Search RETINAL+ANGIOMA
10 CEREBELLAR HEMANGIOBLASTOMA 138486 1% 85% 11 Search CEREBELLAR+HEMANGIOBLASTOMA Search CEREBELLAR+HEMANGIOBLASTOMA

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 NORDSTROM-O'BRIEN, M , VAN DER LUIJT, RB , VAN ROOIJEN, E , VAN DEN OUWELAND, AM , MAJOOR-KRAKAUER, DF , LOLKEMA, MP , VAN BRUSSEL, A , VOEST, EE , GILES, RH , (2010) GENETIC ANALYSIS OF VON HIPPEL-LINDAU DISEASE.HUMAN MUTATION. VOL. 31. ISSUE 5. P. 521 -537 154 74% 73
2 GOSSAGE, L , EISEN, T , MAHER, ER , (2015) VHL, THE STORY OF A TUMOUR SUPPRESSOR GENE.NATURE REVIEWS CANCER. VOL. 15. ISSUE 1. P. 55 -64 110 53% 65
3 RICHARD, S , DAVID, P , MARSOT-DUPUCH, K , GIRAUD, S , BEROUD, C , RESCHE, F , (2000) CENTRAL NERVOUS SYSTEM HEMANGIOBLASTOMAS, ENDOLYMPHATIC SAC TUMORS, AND VON HIPPEL-LINDAU DISEASE.NEUROSURGICAL REVIEW. VOL. 23. ISSUE 1. P. 1 -22 151 75% 74
4 LONSER, RR , GLENN, GM , WALTHER, M , CHEW, EY , LIBUTTI, SK , LINEHAN, WM , OLDFIELD, EH , (2003) VON HIPPEL-LINDAU DISEASE.LANCET. VOL. 361. ISSUE 9374. P. 2059-2067 77 86% 544
5 MILLS, SA , OH, MC , RUTKOWSKI, MJ , SUGHRUE, ME , BARANI, IJ , PARSA, AT , (2012) SUPRATENTORIAL HEMANGIOBLASTOMA: CLINICAL FEATURES, PROGNOSIS, AND PREDICTIVE VALUE OF LOCATION FOR VON HIPPEL-LINDAU DISEASE.NEURO-ONCOLOGY. VOL. 14. ISSUE 8. P. 1097-1104 84 94% 9
6 KIM, WY , KAELIN, WG , (2004) ROLE OF VHL GENE MUTATION IN HUMAN CANCER.JOURNAL OF CLINICAL ONCOLOGY. VOL. 22. ISSUE 24. P. 4991 -5004 97 60% 519
7 NIELSEN, SM , RHODES, L , BLANCO, I , CHUNG, WK , ENG, C , MAHER, ER , RICHARD, S , GILES, RH , (2016) VON HIPPEL-LINDAU DISEASE: GENETICS AND ROLE OF GENETIC COUNSELING IN A MULTIPLE NEOPLASIA SYNDROME.JOURNAL OF CLINICAL ONCOLOGY. VOL. 34. ISSUE 18. P. 2172 -+ 72 75% 3
8 RICHARD, S , GARDIE, B , COUVE, S , GAD, S , (2013) VON HIPPEL-LINDAU: HOW A RARE DISEASE ILLUMINATES CANCER BIOLOGY.SEMINARS IN CANCER BIOLOGY. VOL. 23. ISSUE 1. P. 26-37 83 72% 22
9 KAELIN, WG , (2007) VON HIPPEL-LINDAU DISEASE.ANNUAL REVIEW OF PATHOLOGY-MECHANISMS OF DISEASE. VOL. 2. ISSUE . P. 145 -173 115 51% 142
10 CHOU, A , TOON, C , PICKETT, J , GILL, AJ , (2013) VON HIPPEL-LINDAU SYNDROME.ENDOCRINE TUMOR SYNDROMES AND THEIR GENETICS. VOL. 41. ISSUE . P. 30-49 78 74% 10

Classes with closest relation at Level 1



Rank Class id link
1 27586 BAP1//SETD2//BRCA1 ASSOCIATED PROTEIN 1
2 36730 ANGIOGLIOMA//ANGIOGANGLIOGLIOMA//ANGIOGRAPHICALLY OCCULT CEREBROVASCULAR MALFORMATION
3 15101 ENDOLYMPHATIC SAC TUMOR//MIDDLE EAR ADENOMA//EXTERNAL AUDITORY CANAL
4 268 HIF 1 ALPHA//HYPOXIA INDUCIBLE FACTOR//HYPOXIA INDUCIBLE FACTOR 1
5 2032 CHROMOPHOBE RENAL CELL CARCINOMA//RENAL ONCOCYTOMA//COLLECTING DUCT CARCINOMA
6 19177 FUMARATE HYDRATASE//HLRCC//CUTANEOUS LEIOMYOSARCOMA
7 19028 COATS DISEASE//IDIOPATHIC MACULAR TELANGIECTASIA//MACULAR TELANGIECTASIA
8 27370 TUMOR TO TUMOR METASTASIS//TUMOR TO TUMOR//TUMOUR TO TUMOUR METASTASIS
9 20503 BIRT HOGG DUBE SYNDROME//FOLLICULIN//FIBROFOLLICULOMA
10 371 PHEOCHROMOCYTOMA//PARAGANGLIOMA//PHAEOCHROMOCYTOMA

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