Class information for:
Level 1: TRICHOEPITHELIOMA//CYLD//BROOKE SPIEGLER SYNDROME

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
13445 836 23.6 66%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
375 3       MELANOMA//DERMATOLOGY//DERMATOL 32727
1048 2             BASAL CELL CARCINOMA//DERMATOLOGY//SEBACEOUS CARCINOMA 10099
13445 1                   TRICHOEPITHELIOMA//CYLD//BROOKE SPIEGLER SYNDROME 836

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 TRICHOEPITHELIOMA authKW 1788215 7% 80% 61
2 CYLD authKW 1202654 7% 54% 61
3 BROOKE SPIEGLER SYNDROME authKW 1032338 4% 91% 31
4 CYLINDROMA authKW 813610 5% 52% 43
5 TRICHOBLASTOMA authKW 653114 5% 44% 41
6 BASALOID FOLLICULAR HAMARTOMA authKW 438289 1% 100% 12
7 DESMOPLASTIC TRICHOEPITHELIOMA authKW 410889 2% 75% 15
8 FAMILIAL CYLINDROMATOSIS authKW 404573 1% 92% 12
9 SPIRADENOMA authKW 378823 3% 45% 23
10 CYLD GENE authKW 365241 1% 100% 10

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 56961 62% 0% 521
2 Pathology 2395 16% 0% 130
3 Surgery 89 8% 0% 65
4 Oncology 86 7% 0% 62
5 Cell Biology 57 6% 0% 53
6 Ophthalmology 45 3% 0% 22
7 Genetics & Heredity 38 4% 0% 36
8 Otorhinolaryngology 36 2% 0% 15
9 Pediatrics 30 3% 0% 26
10 Medicine, Research & Experimental 13 3% 0% 23

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ANIM ISTANCE SHANDONG PROV MOL 73048 0% 100% 2
2 GRP RECH INFLAMMAT CANC 73048 0% 100% 2
3 SIKLS PATHOL 43663 2% 7% 16
4 ABORAT INNOVAT CANC MED DIAGNOST IMA 36524 0% 100% 1
5 ANATOMOPATHOL CLIN 36524 0% 100% 1
6 ANDREAS SYGROS HOSP DERMATOL 36524 0% 100% 1
7 CELL THER YQILU HOSP 36524 0% 100% 1
8 CHARLES UNIV MED HOSP 36524 0% 100% 1
9 DERMATOL COSMET LASER DERMATOL 36524 0% 100% 1
10 DERMATOLCLIN MOL MED 36524 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 AMERICAN JOURNAL OF DERMATOPATHOLOGY 56279 9% 2% 75
2 JOURNAL OF CUTANEOUS PATHOLOGY 49975 8% 2% 71
3 ANNALES DE DERMATOLOGIE ET DE VENEREOLOGIE 10762 5% 1% 41
4 CLINICAL AND EXPERIMENTAL DERMATOLOGY 4950 3% 1% 26
5 HAUTARZT 4011 3% 0% 23
6 JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 3841 4% 0% 36
7 ARCHIVES OF DERMATOLOGY 3670 3% 0% 25
8 PEDIATRIC DERMATOLOGY 3544 2% 1% 19
9 INTERNATIONAL JOURNAL OF DERMATOLOGY 2621 3% 0% 23
10 BRITISH JOURNAL OF DERMATOLOGY 2380 3% 0% 27

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 TRICHOEPITHELIOMA 1788215 7% 80% 61 Search TRICHOEPITHELIOMA Search TRICHOEPITHELIOMA
2 CYLD 1202654 7% 54% 61 Search CYLD Search CYLD
3 BROOKE SPIEGLER SYNDROME 1032338 4% 91% 31 Search BROOKE+SPIEGLER+SYNDROME Search BROOKE+SPIEGLER+SYNDROME
4 CYLINDROMA 813610 5% 52% 43 Search CYLINDROMA Search CYLINDROMA
5 TRICHOBLASTOMA 653114 5% 44% 41 Search TRICHOBLASTOMA Search TRICHOBLASTOMA
6 BASALOID FOLLICULAR HAMARTOMA 438289 1% 100% 12 Search BASALOID+FOLLICULAR+HAMARTOMA Search BASALOID+FOLLICULAR+HAMARTOMA
7 DESMOPLASTIC TRICHOEPITHELIOMA 410889 2% 75% 15 Search DESMOPLASTIC+TRICHOEPITHELIOMA Search DESMOPLASTIC+TRICHOEPITHELIOMA
8 FAMILIAL CYLINDROMATOSIS 404573 1% 92% 12 Search FAMILIAL+CYLINDROMATOSIS Search FAMILIAL+CYLINDROMATOSIS
9 SPIRADENOMA 378823 3% 45% 23 Search SPIRADENOMA Search SPIRADENOMA
10 CYLD GENE 365241 1% 100% 10 Search CYLD+GENE Search CYLD+GENE

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 BLAKE, PW , TORO, JR , (2009) UPDATE OF CYLINDROMATOSIS GENE (CYLD) MUTATIONS IN BROOKE-SPIEGLER SYNDROME: NOVEL INSIGHTS INTO THE ROLE OF DEUBIQUITINATION IN CELL SIGNALING.HUMAN MUTATION. VOL. 30. ISSUE 7. P. 1025-1036 71 68% 48
2 GUARDOLI, D , ARGENZIANO, G , PONTI, G , NASTI, S , ZALAUDEK, I , MOSCARELLA, E , LALLAS, A , PIANA, S , SPECCHIO, F , MARTINUZZI, C , ET AL (2015) A NOVEL CYLD GERMLINE MUTATION IN BROOKE-SPIEGLER SYNDROME.JOURNAL OF THE EUROPEAN ACADEMY OF DERMATOLOGY AND VENEREOLOGY. VOL. 29. ISSUE 3. P. 457 -462 42 98% 1
3 NAGY, N , FARKAS, K , KEMENY, L , SZELL, M , (2015) PHENOTYPE-GENOTYPE CORRELATIONS FOR CLINICAL VARIANTS CAUSED BY CYLD MUTATIONS.EUROPEAN JOURNAL OF MEDICAL GENETICS. VOL. 58. ISSUE 5. P. 271 -278 41 84% 4
4 DUBOIS, A , HODGSON, K , RAJAN, N , (2017) UNDERSTANDING INHERITED CYLINDROMAS CLINICAL IMPLICATIONS OF GENE DISCOVERY.DERMATOLOGIC CLINICS. VOL. 35. ISSUE 1. P. 61 -+ 38 79% 0
5 RAJAN, N , ASHWORTH, A , (2015) INHERITED CYLINDROMAS: LESSONS FROM A RARE TUMOUR.LANCET ONCOLOGY. VOL. 16. ISSUE 9. P. E460 -E469 43 69% 2
6 GROSSMANN, P , VANECEK, T , STEINER, P , KACEROVSKA, D , SPAGNOLO, DV , CRIBIER, B , ROSE, C , VAZMITEL, M , CARLSON, JA , EMBERGER, M , ET AL (2013) NOVEL AND RECURRENT GERMLINE AND SOMATIC MUTATIONS IN A COHORT OF 67 PATIENTS FROM 48 FAMILIES WITH BROOKE-SPIEGLER SYNDROME INCLUDING THE PHENOTYPIC VARIANT OF MULTIPLE FAMILIAL TRICHOEPITHELIOMAS AND CORRELATION WITH THE HISTOPATHOLOGIC FINDINGS IN 379 BIOPSY SPECIMENS.AMERICAN JOURNAL OF DERMATOPATHOLOGY. VOL. 35. ISSUE 1. P. 34 -44 29 97% 15
7 KAZAKOV, DV , VANECEK, T , ZELGER, B , CARLSON, JA , SPAGNOLO, DV , SCHALLER, J , NEMCOVA, J , KACEROVSKA, D , VAZMITEL, M , SANGUEZA, M , ET AL (2011) MULTIPLE (FAMILIAL) TRICHOEPITHELIOMAS: A CLINICOPATHOLOGICAL AND MOLECULAR BIOLOGICAL STUDY, INCLUDING CYLD AND PTCH GENE ANALYSIS, OF A SERIES OF 16 PATIENTS.AMERICAN JOURNAL OF DERMATOPATHOLOGY. VOL. 33. ISSUE 3. P. 251 -265 35 81% 14
8 VANECEK, T , HALBHUBER, Z , KACEROVSKA, D , MARTINEK, P , SEDIVCOVA, M , CARR, RA , SLOUKA, D , MICHAL, M , KAZAKOV, DV , (2014) LARGE GERMLINE DELETIONS OF THE CYLD GENE IN PATIENTS WITH BROOKE-SPIEGLER SYNDROME AND MULTIPLE FAMILIAL TRICHOEPITHELIOMA.AMERICAN JOURNAL OF DERMATOPATHOLOGY. VOL. 36. ISSUE 11. P. 868 -874 35 71% 2
9 DU TOIT, JP , SCHNEIDER, JW , VISSER, WI , JORDAAN, HF , (2016) THE CLINICOPATHOLOGICAL SPECTRUM OF TRICHOEPITHELIOMAS: A RETROSPECTIVE DESCRIPTIVE STUDY.INTERNATIONAL JOURNAL OF DERMATOLOGY. VOL. 55. ISSUE 3. P. 270 -277 27 90% 0
10 KAZAKOV, DV , VANECEK, T , NEMCOVA, J , KACEROVSKA, D , SPAGNOLO, DV , MUKENSNABL, P , MICHAL, M , (2009) SPECTRUM OF TUMORS WITH FOLLICULAR DIFFERENTIATION IN A PATIENT WITH THE CLINICAL PHENOTYPE OF MULTIPLE FAMILIAL TRICHOEPITHELIOMAS: A CLINICOPATHOLOGICAL AND MOLECULAR BIOLOGICAL STUDY, INCLUDING ANALYSIS OF THE CYLD AND PTCH GENES.AMERICAN JOURNAL OF DERMATOPATHOLOGY. VOL. 31. ISSUE 8. P. 819 -827 30 91% 4

Classes with closest relation at Level 1



Rank Class id link
1 5644 MICROCYSTIC ADNEXAL CARCINOMA//SWEAT GLAND NEOPLASMS//CHONDROID SYRINGOMA
2 20181 PILOMATRICOMA//PILOMATRIXOMA//PILOMATRIX CARCINOMA
3 17696 ERUPTIVE VELLUS HAIR CYST//EPIDERMAL CYST//STEATOCYSTOMA MULTIPLEX
4 20944 SYRINGOMA//ECCRINE SYRINGOFIBROADENOMA//HIDROCYSTOMA
5 26962 LARGE CELL ACANTHOMA//SEBORRHEIC KERATOSIS//INVERTED FOLLICULAR KERATOSIS
6 20503 BIRT HOGG DUBE SYNDROME//FOLLICULIN//FIBROFOLLICULOMA
7 13169 SEBACEOUS CARCINOMA//MUIR TORRE SYNDROME//SEBACEOMA
8 13864 EPIDERMAL NEVUS SYNDROME//LICHEN STRIATUS//NEVUS SEBACEUS
9 32051 CD10//CD10 EXPRESSION//BIOPATHOLUMR 599
10 18887 MARJOLINS ULCER//BURN SCAR//SQUAMOMELANOCYTIC TUMOR

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