Class information for:
Level 2: HEREDITARY ANGIOEDEMA//C1 INHIBITOR//ANGIOEDEMA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
3090 2362 30.4 71%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
315 3       ALLERGY//MAST CELLS//BRADYKININ 39886
3090 2             HEREDITARY ANGIOEDEMA//C1 INHIBITOR//ANGIOEDEMA 2362
3345 1                   HEREDITARY ANGIOEDEMA//C1 INHIBITOR//ANGIOEDEMA 2003
25829 1                   COUGH//24 HOUR MONITORING OF ARTERIAL PRESSURE//ACE II INHIBITOR 271
35991 1                   MOEXIPRIL//CAS 82586 52 5//24 HOUR BLOOD PRESSURE MEASUREMENT ABPM 88

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HEREDITARY ANGIOEDEMA authKW 4484496 15% 95% 365
2 C1 INHIBITOR authKW 2051252 9% 77% 207
3 ANGIOEDEMA authKW 2027435 12% 53% 294
4 C1 INHIBITOR DEFICIENCY authKW 1024772 4% 94% 84
5 C1 ESTERASE INHIBITOR authKW 721437 3% 72% 78
6 ACQUIRED ANGIOEDEMA authKW 491507 2% 98% 39
7 HAE authKW 429534 2% 92% 36
8 ECALLANTIDE authKW 426556 1% 100% 33
9 ICATIBANT authKW 401092 3% 52% 60
10 C1 INH authKW 376487 2% 79% 37

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Allergy 46274 21% 1% 490
2 Immunology 5541 24% 0% 573
3 Medicine, General & Internal 2507 16% 0% 384
4 Dermatology 753 5% 0% 113
5 Emergency Medicine 496 2% 0% 50
6 Otorhinolaryngology 421 3% 0% 76
7 Peripheral Vascular Diseases 412 5% 0% 109
8 Pharmacology & Pharmacy 366 10% 0% 232
9 Hematology 201 4% 0% 86
10 Medicine, Research & Experimental 188 5% 0% 107

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 REFERENCE ANGIOEDEMA 180963 1% 100% 14
2 ANGIOEDEMA 155111 1% 100% 12
3 MU CTY HOSP 132949 1% 86% 12
4 HUNGARIAN ANGIOEDEMA 130335 0% 92% 11
5 HAE DENMARK 116334 0% 100% 9
6 REFERENCE ANGIOEDEMES CREAK 103408 0% 100% 8
7 CLIN UNIV MED INTERNE 84595 1% 55% 12
8 BIOMED NETWORK RARE DIS CIBERER U754 77556 0% 100% 6
9 GREPI AGIM CNRS FRE 3405 66475 0% 86% 6
10 ALLERGOL ANGIOEDEMA OUTPATIENT CLIN 64630 0% 100% 5

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ALLERGY AND ASTHMA PROCEEDINGS 45963 3% 5% 75
2 ANNALS OF ALLERGY ASTHMA & IMMUNOLOGY 18849 3% 2% 73
3 IMMUNOLOGY AND ALLERGY CLINICS OF NORTH AMERICA 8014 1% 2% 29
4 JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY-IN PRACTICE 6858 1% 4% 14
5 JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY 6061 3% 1% 71
6 ALLERGY 4522 2% 1% 47
7 CLINICAL REVIEWS IN ALLERGY & IMMUNOLOGY 2876 1% 1% 15
8 EXPERT REVIEW OF CLINICAL IMMUNOLOGY 2733 1% 2% 13
9 ALLERGY ASTHMA AND CLINICAL IMMUNOLOGY 2551 0% 3% 7
10 PEDIATRIC ALLERGY IMMUNOLOGY AND PULMONOLOGY 1944 0% 3% 6

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 HEREDITARY ANGIOEDEMA 4484496 15% 95% 365 Search HEREDITARY+ANGIOEDEMA Search HEREDITARY+ANGIOEDEMA
2 C1 INHIBITOR 2051252 9% 77% 207 Search C1+INHIBITOR Search C1+INHIBITOR
3 ANGIOEDEMA 2027435 12% 53% 294 Search ANGIOEDEMA Search ANGIOEDEMA
4 C1 INHIBITOR DEFICIENCY 1024772 4% 94% 84 Search C1+INHIBITOR+DEFICIENCY Search C1+INHIBITOR+DEFICIENCY
5 C1 ESTERASE INHIBITOR 721437 3% 72% 78 Search C1+ESTERASE+INHIBITOR Search C1+ESTERASE+INHIBITOR
6 ACQUIRED ANGIOEDEMA 491507 2% 98% 39 Search ACQUIRED+ANGIOEDEMA Search ACQUIRED+ANGIOEDEMA
7 HAE 429534 2% 92% 36 Search HAE Search HAE
8 ECALLANTIDE 426556 1% 100% 33 Search ECALLANTIDE Search ECALLANTIDE
9 ICATIBANT 401092 3% 52% 60 Search ICATIBANT Search ICATIBANT
10 C1 INH 376487 2% 79% 37 Search C1+INH Search C1+INH

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 CICARDI, M , ABERER, W , BANERJI, A , BAS, M , BERNSTEIN, JA , BORK, K , CABALLERO, T , FARKAS, H , GRUMACH, A , KAPLAN, AP , ET AL (2014) CLASSIFICATION, DIAGNOSIS, AND APPROACH TO TREATMENT FOR ANGIOEDEMA: CONSENSUS REPORT FROM THE HEREDITARY ANGIOEDEMA INTERNATIONAL WORKING GROUP.ALLERGY. VOL. 69. ISSUE 5. P. 602-616 97 96% 100
2 FARKAS, H , MARTINEZ-SAGUER, I , BORK, K , BOWEN, T , CRAIG, T , FRANK, M , GERMENIS, AE , GRUMACH, AS , LUCZAY, A , VARGA, L , ET AL (2017) INTERNATIONAL CONSENSUS ON THE DIAGNOSIS AND MANAGEMENT OF PEDIATRIC PATIENTS WITH HEREDITARY ANGIOEDEMA WITH C1 INHIBITOR DEFICIENCY.ALLERGY. VOL. 72. ISSUE 2. P. 300 -313 90 94% 1
3 AGOSTONI, A , AYGOREN-PURSUN, E , BINKLEY, KE , BLANCH, A , BORK, K , BOUILLET, L , BUCHER, C , CASTALDO, AJ , CICARDI, M , DAVIS, AE , ET AL (2004) HEREDITARY AND ACQUIRED ANGIOEDEMA: PROBLEMS AND PROGRESS: PROCEEDINGS OF THE THIRD C1 ESTERASE INHIBITOR DEFICIENCY WORKSHOP AND BEYOND.JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY. VOL. 114. ISSUE 3. P. S51 -S131 220 66% 211
4 ZURAW, BL , BERNSTEIN, JA , LANG, DM , CRAIG, T , DREYFUS, D , HSIEH, F , KHAN, D , SHEIKH, J , WELDON, D , BERNSTEIN, DI , ET AL (2013) A FOCUSED PARAMETER UPDATE: HEREDITARY ANGIOEDEMA, ACQUIRED C1 INHIBITOR DEFICIENCY, AND ANGIOTENSIN-CONVERTING ENZYME INHIBITOR-ASSOCIATED ANGIOEDEMA.JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY. VOL. 131. ISSUE 6. P. 1491 -+ 111 97% 28
5 CABALLERO, T , BAEZA, ML , CABANAS, R , CAMPOS, A , CIMBOLLEK, S , GOMEZ-TRASEIRA, C , GONZALEZ-QUEVEDO, T , GUILARTE, M , JURADO-PALOMO, J , LARCO, JI , ET AL (2011) CONSENSUS STATEMENT ON THE DIAGNOSIS, MANAGEMENT, AND TREATMENT OF ANGIOEDEMA MEDIATED BY BRADYKININ. PART II. TREATMENT, FOLLOW-UP, AND SPECIAL SITUATIONS.JOURNAL OF INVESTIGATIONAL ALLERGOLOGY AND CLINICAL IMMUNOLOGY. VOL. 21. ISSUE 6. P. 422 -441 120 86% 32
6 FARKAS, H , (2013) CURRENT PHARMACOTHERAPY OF BRADYKININ-MEDIATED ANGIOEDEMA.EXPERT OPINION ON PHARMACOTHERAPY. VOL. 14. ISSUE 5. P. 571 -586 105 95% 11
7 CABALLERO, T , BAEZA, ML , CABANAS, R , CAMPOS, A , CIMBOLLEK, S , GOMEZ-TRASEIRA, C , GONZALEZ-QUEVEDO, T , GUILARTE, M , SALA-CUNILL, A , RUBIO, M , ET AL (2011) CONSENSUS STATEMENT ON THE DIAGNOSIS, MANAGEMENT, AND TREATMENT OF ANGIOEDEMA MEDIATED BY BRADYKININ. PART I. CLASSIFICATION, EPIDEMIOLOGY, PATHOPHYSIOLOGY, GENETICS, CLINICAL SYMPTOMS, AND DIAGNOSIS.JOURNAL OF INVESTIGATIONAL ALLERGOLOGY AND CLINICAL IMMUNOLOGY. VOL. 21. ISSUE 5. P. 333 -347 107 82% 57
8 ZURAW, BL , CHRISTIANSEN, SC , (2016) HOW WE MANAGE PERSONS WITH HEREDITARY ANGIOEDEMA.BRITISH JOURNAL OF HAEMATOLOGY. VOL. 173. ISSUE 6. P. 831 -843 87 98% 1
9 LONGHURST, H , CICARDI, M , (2012) HEREDITARY ANGIO-OEDEMA.LANCET. VOL. 379. ISSUE 9814. P. 474 -481 71 97% 103
10 WU, MA , ZANICHELLI, A , MANSI, M , CICARDI, M , (2016) CURRENT TREATMENT OPTIONS FOR HEREDITARY ANGIOEDEMA DUE TO C1 INHIBITOR DEFICIENCY.EXPERT OPINION ON PHARMACOTHERAPY. VOL. 17. ISSUE 1. P. 27 -40 73 94% 4

Classes with closest relation at Level 2



Rank Class id link
1 3057 CHRONIC URTICARIA//URTICARIA//CHRONIC IDIOPATHIC URTICARIA
2 1619 BRADYKININ//KININS//FACTOR XII
3 363 COMPLEMENT//MANNOSE BINDING LECTIN//PAROXYSMAL NOCTURNAL HEMOGLOBINURIA
4 1906 ALPHA 1 ANTITRYPSIN DEFICIENCY//ALPHA 1 ANTITRYPSIN//ALPHA1 ANTITRYPSIN DEFICIENCY
5 85 ANGIOTENSIN II//RENIN ANGIOTENSIN SYSTEM//ANGIOTENSIN
6 1550 TOXIC EPIDERMAL NECROLYSIS//STEVENS JOHNSON SYNDROME//DRUG ALLERGY
7 2978 PHARMACOVIGILANCE//ADVERSE DRUG REACTIONS//DRUG SAFETY
8 3661 EPIGLOTTITIS//CROUP//LARYNGOTRACHEOBRONCHITIS
9 406 HYPERTENSION//MEDICATION ADHERENCE//JOURNAL OF HUMAN HYPERTENSION
10 112 ASTHMA//EOSINOPHILS//ALLERGY

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