Class information for:
Level 1: HEREDITARY ANGIOEDEMA//C1 INHIBITOR//ANGIOEDEMA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
3345 2003 30.8 71%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
315 3       ALLERGY//MAST CELLS//BRADYKININ 39886
3090 2             HEREDITARY ANGIOEDEMA//C1 INHIBITOR//ANGIOEDEMA 2362
3345 1                   HEREDITARY ANGIOEDEMA//C1 INHIBITOR//ANGIOEDEMA 2003

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HEREDITARY ANGIOEDEMA authKW 5288388 18% 95% 365
2 C1 INHIBITOR authKW 2418975 10% 77% 207
3 ANGIOEDEMA authKW 2358497 15% 53% 292
4 C1 INHIBITOR DEFICIENCY authKW 1208473 4% 94% 84
5 C1 ESTERASE INHIBITOR authKW 850769 4% 72% 78
6 ACQUIRED ANGIOEDEMA authKW 579615 2% 98% 39
7 HAE authKW 506533 2% 92% 36
8 ECALLANTIDE authKW 503021 2% 100% 33
9 ICATIBANT authKW 473002 3% 52% 60
10 C1 INH authKW 443978 2% 79% 37

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Allergy 52291 24% 1% 479
2 Immunology 6522 28% 0% 565
3 Medicine, General & Internal 2000 16% 0% 317
4 Dermatology 924 6% 0% 113
5 Emergency Medicine 576 2% 0% 49
6 Otorhinolaryngology 505 4% 0% 75
7 Hematology 254 4% 0% 85
8 Anesthesiology 225 2% 0% 47
9 Medicine, Research & Experimental 176 5% 0% 94
10 Peripheral Vascular Diseases 90 3% 0% 55

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 REFERENCE ANGIOEDEMA 213403 1% 100% 14
2 ANGIOEDEMA 182917 1% 100% 12
3 MU CTY HOSP 156782 1% 86% 12
4 HUNGARIAN ANGIOEDEMA 153699 1% 92% 11
5 HAE DENMARK 137187 0% 100% 9
6 REFERENCE ANGIOEDEMES CREAK 121944 0% 100% 8
7 CLIN UNIV MED INTERNE 99762 1% 55% 12
8 BIOMED NETWORK RARE DIS CIBERER U754 91458 0% 100% 6
9 GREPI AGIM CNRS FRE 3405 78391 0% 86% 6
10 ALLERGOL ANGIOEDEMA OUTPATIENT CLIN 76215 0% 100% 5

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ALLERGY AND ASTHMA PROCEEDINGS 54228 4% 5% 75
2 ANNALS OF ALLERGY ASTHMA & IMMUNOLOGY 22253 4% 2% 73
3 IMMUNOLOGY AND ALLERGY CLINICS OF NORTH AMERICA 9460 1% 2% 29
4 JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY-IN PRACTICE 8092 1% 4% 14
5 JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY 6573 3% 1% 68
6 ALLERGY 5122 2% 1% 46
7 CLINICAL REVIEWS IN ALLERGY & IMMUNOLOGY 3397 1% 1% 15
8 EXPERT REVIEW OF CLINICAL IMMUNOLOGY 3227 1% 2% 13
9 ALLERGY ASTHMA AND CLINICAL IMMUNOLOGY 3010 0% 3% 7
10 PEDIATRIC ALLERGY IMMUNOLOGY AND PULMONOLOGY 2294 0% 3% 6

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 HEREDITARY ANGIOEDEMA 5288388 18% 95% 365 Search HEREDITARY+ANGIOEDEMA Search HEREDITARY+ANGIOEDEMA
2 C1 INHIBITOR 2418975 10% 77% 207 Search C1+INHIBITOR Search C1+INHIBITOR
3 ANGIOEDEMA 2358497 15% 53% 292 Search ANGIOEDEMA Search ANGIOEDEMA
4 C1 INHIBITOR DEFICIENCY 1208473 4% 94% 84 Search C1+INHIBITOR+DEFICIENCY Search C1+INHIBITOR+DEFICIENCY
5 C1 ESTERASE INHIBITOR 850769 4% 72% 78 Search C1+ESTERASE+INHIBITOR Search C1+ESTERASE+INHIBITOR
6 ACQUIRED ANGIOEDEMA 579615 2% 98% 39 Search ACQUIRED+ANGIOEDEMA Search ACQUIRED+ANGIOEDEMA
7 HAE 506533 2% 92% 36 Search HAE Search HAE
8 ECALLANTIDE 503021 2% 100% 33 Search ECALLANTIDE Search ECALLANTIDE
9 ICATIBANT 473002 3% 52% 60 Search ICATIBANT Search ICATIBANT
10 C1 INH 443978 2% 79% 37 Search C1+INH Search C1+INH

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 CICARDI, M , ABERER, W , BANERJI, A , BAS, M , BERNSTEIN, JA , BORK, K , CABALLERO, T , FARKAS, H , GRUMACH, A , KAPLAN, AP , ET AL (2014) CLASSIFICATION, DIAGNOSIS, AND APPROACH TO TREATMENT FOR ANGIOEDEMA: CONSENSUS REPORT FROM THE HEREDITARY ANGIOEDEMA INTERNATIONAL WORKING GROUP.ALLERGY. VOL. 69. ISSUE 5. P. 602-616 97 96% 100
2 FARKAS, H , MARTINEZ-SAGUER, I , BORK, K , BOWEN, T , CRAIG, T , FRANK, M , GERMENIS, AE , GRUMACH, AS , LUCZAY, A , VARGA, L , ET AL (2017) INTERNATIONAL CONSENSUS ON THE DIAGNOSIS AND MANAGEMENT OF PEDIATRIC PATIENTS WITH HEREDITARY ANGIOEDEMA WITH C1 INHIBITOR DEFICIENCY.ALLERGY. VOL. 72. ISSUE 2. P. 300 -313 90 94% 1
3 AGOSTONI, A , AYGOREN-PURSUN, E , BINKLEY, KE , BLANCH, A , BORK, K , BOUILLET, L , BUCHER, C , CASTALDO, AJ , CICARDI, M , DAVIS, AE , ET AL (2004) HEREDITARY AND ACQUIRED ANGIOEDEMA: PROBLEMS AND PROGRESS: PROCEEDINGS OF THE THIRD C1 ESTERASE INHIBITOR DEFICIENCY WORKSHOP AND BEYOND.JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY. VOL. 114. ISSUE 3. P. S51 -S131 220 66% 211
4 ZURAW, BL , BERNSTEIN, JA , LANG, DM , CRAIG, T , DREYFUS, D , HSIEH, F , KHAN, D , SHEIKH, J , WELDON, D , BERNSTEIN, DI , ET AL (2013) A FOCUSED PARAMETER UPDATE: HEREDITARY ANGIOEDEMA, ACQUIRED C1 INHIBITOR DEFICIENCY, AND ANGIOTENSIN-CONVERTING ENZYME INHIBITOR-ASSOCIATED ANGIOEDEMA.JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY. VOL. 131. ISSUE 6. P. 1491 -+ 111 97% 28
5 CABALLERO, T , BAEZA, ML , CABANAS, R , CAMPOS, A , CIMBOLLEK, S , GOMEZ-TRASEIRA, C , GONZALEZ-QUEVEDO, T , GUILARTE, M , JURADO-PALOMO, J , LARCO, JI , ET AL (2011) CONSENSUS STATEMENT ON THE DIAGNOSIS, MANAGEMENT, AND TREATMENT OF ANGIOEDEMA MEDIATED BY BRADYKININ. PART II. TREATMENT, FOLLOW-UP, AND SPECIAL SITUATIONS.JOURNAL OF INVESTIGATIONAL ALLERGOLOGY AND CLINICAL IMMUNOLOGY. VOL. 21. ISSUE 6. P. 422 -441 120 86% 32
6 FARKAS, H , (2013) CURRENT PHARMACOTHERAPY OF BRADYKININ-MEDIATED ANGIOEDEMA.EXPERT OPINION ON PHARMACOTHERAPY. VOL. 14. ISSUE 5. P. 571 -586 104 94% 11
7 CABALLERO, T , BAEZA, ML , CABANAS, R , CAMPOS, A , CIMBOLLEK, S , GOMEZ-TRASEIRA, C , GONZALEZ-QUEVEDO, T , GUILARTE, M , SALA-CUNILL, A , RUBIO, M , ET AL (2011) CONSENSUS STATEMENT ON THE DIAGNOSIS, MANAGEMENT, AND TREATMENT OF ANGIOEDEMA MEDIATED BY BRADYKININ. PART I. CLASSIFICATION, EPIDEMIOLOGY, PATHOPHYSIOLOGY, GENETICS, CLINICAL SYMPTOMS, AND DIAGNOSIS.JOURNAL OF INVESTIGATIONAL ALLERGOLOGY AND CLINICAL IMMUNOLOGY. VOL. 21. ISSUE 5. P. 333 -347 107 82% 57
8 ZURAW, BL , CHRISTIANSEN, SC , (2016) HOW WE MANAGE PERSONS WITH HEREDITARY ANGIOEDEMA.BRITISH JOURNAL OF HAEMATOLOGY. VOL. 173. ISSUE 6. P. 831 -843 87 98% 1
9 LONGHURST, H , CICARDI, M , (2012) HEREDITARY ANGIO-OEDEMA.LANCET. VOL. 379. ISSUE 9814. P. 474 -481 71 97% 103
10 WU, MA , ZANICHELLI, A , MANSI, M , CICARDI, M , (2016) CURRENT TREATMENT OPTIONS FOR HEREDITARY ANGIOEDEMA DUE TO C1 INHIBITOR DEFICIENCY.EXPERT OPINION ON PHARMACOTHERAPY. VOL. 17. ISSUE 1. P. 27 -40 73 94% 4

Classes with closest relation at Level 1



Rank Class id link
1 25829 COUGH//24 HOUR MONITORING OF ARTERIAL PRESSURE//ACE II INHIBITOR
2 3705 FACTOR XII//FACTOR XI//FACTOR XI DEFICIENCY
3 3827 CHRONIC URTICARIA//URTICARIA//CHRONIC IDIOPATHIC URTICARIA
4 33647 CRYOFIBRINOGEN//CRYOFIBRINOGENEMIA//CRYOFIBRINOGENAEMIA
5 7412 C1Q//ANTI C1Q ANTIBODIES//C1Q DEFICIENCY
6 27726 DANAZOL//ALPHA 1 ANTITRYPSIN P GLYCOPROTEIN//CATTEDRA GINECOL ENDOCRINOL
7 3467 C5A//C5A RECEPTOR//ANAPHYLATOXIN
8 23188 SCHNITZLER SYNDROME//URTICARIAL VASCULITIS//HYPOCOMPLEMENTEMIC URTICARIAL VASCULITIS SYNDROME
9 36704 ALLERGY LIVER TRANSPLANTATION//ARA H 1 ALLERGEN PEANUT//ARA H 2 ALLERGEN PEANUT
10 881 BRADYKININ//KININS//B 2 RECEPTOR

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