Class information for:
Level 1: SCHNITZLER SYNDROME//URTICARIAL VASCULITIS//HYPOCOMPLEMENTEMIC URTICARIAL VASCULITIS SYNDROME

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
23188 355 24.0 63%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
315 3       ALLERGY//MAST CELLS//BRADYKININ 39886
3057 2             CHRONIC URTICARIA//URTICARIA//CHRONIC IDIOPATHIC URTICARIA 2443
23188 1                   SCHNITZLER SYNDROME//URTICARIAL VASCULITIS//HYPOCOMPLEMENTEMIC URTICARIAL VASCULITIS SYNDROME 355

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SCHNITZLER SYNDROME authKW 4638531 17% 88% 61
2 URTICARIAL VASCULITIS authKW 1211346 7% 54% 26
3 HYPOCOMPLEMENTEMIC URTICARIAL VASCULITIS SYNDROME authKW 430072 1% 100% 5
4 HYPOCOMPLEMENTEMIC URTICARIAL VASCULITIS authKW 309647 2% 60% 6
5 NEUTROPHILIC URTICARIAL DERMATOSIS authKW 215031 1% 50% 5
6 HYPOCOMPLEMENTAEMIC URTICARIAL VASCULITIS authKW 172029 1% 100% 2
7 MCDUFFLE SYNDROME authKW 172029 1% 100% 2
8 MONOCLONAL DYSPROTEINEMIA authKW 172029 1% 100% 2
9 MONOCLONAL IGM GAMMOPATHY authKW 172029 1% 100% 2
10 RECURRENT HEREDITARY FEVERS authKW 172029 1% 100% 2

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 9172 39% 0% 137
2 Rheumatology 2165 14% 0% 51
3 Allergy 1535 10% 0% 35
4 Medicine, General & Internal 381 16% 0% 58
5 Urology & Nephrology 89 5% 0% 19
6 Immunology 46 7% 0% 26
7 Pediatrics 12 3% 0% 11
8 Ophthalmology 12 2% 0% 8
9 Primary Health Care 1 0% 0% 1
10 Hematology 1 1% 0% 5

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CEA LIFE SCI TECHNOL 86014 0% 100% 1
2 CONNECTICUT ASTHMA ALLERGY 86014 0% 100% 1
3 ETABLISSMENT TRANSFUS SANGUINE 86014 0% 100% 1
4 FOR 316 86014 0% 100% 1
5 FRENCH STUDY GRP CUTANEOUS LYMPHOMAS 86014 0% 100% 1
6 GERONTOL 3 86014 0% 100% 1
7 IGRD 86014 0% 100% 1
8 IMMUNOPATHOL CLIN DERMATOL 86014 0% 100% 1
9 INSERM 99 08 86014 0% 100% 1
10 INSERM U882 86014 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ANNALES DE DERMATOLOGIE ET DE VENEREOLOGIE 7309 6% 0% 22
2 DERMATOLOGICA 2679 2% 0% 7
3 JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 2528 5% 0% 19
4 REVUE DE MEDECINE INTERNE 1759 3% 0% 9
5 BRITISH JOURNAL OF DERMATOLOGY 1739 4% 0% 15
6 CLINICAL AND EXPERIMENTAL DERMATOLOGY 1723 3% 0% 10
7 ARCHIVES OF DERMATOLOGY 1117 3% 0% 9
8 VESTNIK DERMATOLOGII I VENEROLOGII 795 1% 0% 5
9 CLINICAL RHEUMATOLOGY 780 2% 0% 7
10 EXPERT OPINION ON ORPHAN DRUGS 780 1% 0% 2

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 SCHNITZLER SYNDROME 4638531 17% 88% 61 Search SCHNITZLER+SYNDROME Search SCHNITZLER+SYNDROME
2 URTICARIAL VASCULITIS 1211346 7% 54% 26 Search URTICARIAL+VASCULITIS Search URTICARIAL+VASCULITIS
3 HYPOCOMPLEMENTEMIC URTICARIAL VASCULITIS SYNDROME 430072 1% 100% 5 Search HYPOCOMPLEMENTEMIC+URTICARIAL+VASCULITIS+SYNDROME Search HYPOCOMPLEMENTEMIC+URTICARIAL+VASCULITIS+SYNDROME
4 HYPOCOMPLEMENTEMIC URTICARIAL VASCULITIS 309647 2% 60% 6 Search HYPOCOMPLEMENTEMIC+URTICARIAL+VASCULITIS Search HYPOCOMPLEMENTEMIC+URTICARIAL+VASCULITIS
5 NEUTROPHILIC URTICARIAL DERMATOSIS 215031 1% 50% 5 Search NEUTROPHILIC+URTICARIAL+DERMATOSIS Search NEUTROPHILIC+URTICARIAL+DERMATOSIS
6 HYPOCOMPLEMENTAEMIC URTICARIAL VASCULITIS 172029 1% 100% 2 Search HYPOCOMPLEMENTAEMIC+URTICARIAL+VASCULITIS Search HYPOCOMPLEMENTAEMIC+URTICARIAL+VASCULITIS
7 MCDUFFLE SYNDROME 172029 1% 100% 2 Search MCDUFFLE+SYNDROME Search MCDUFFLE+SYNDROME
8 MONOCLONAL DYSPROTEINEMIA 172029 1% 100% 2 Search MONOCLONAL+DYSPROTEINEMIA Search MONOCLONAL+DYSPROTEINEMIA
9 MONOCLONAL IGM GAMMOPATHY 172029 1% 100% 2 Search MONOCLONAL+IGM+GAMMOPATHY Search MONOCLONAL+IGM+GAMMOPATHY
10 RECURRENT HEREDITARY FEVERS 172029 1% 100% 2 Search RECURRENT+HEREDITARY+FEVERS Search RECURRENT+HEREDITARY+FEVERS

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 DE KONING, HD , (2014) SCHNITZLER'S SYNDROME: LESSONS FROM 281 CASES.CLINICAL AND TRANSLATIONAL ALLERGY. VOL. 4. ISSUE . P. - 78 78% 6
2 DAVIS, MDP , BREWER, JD , (2004) URTICARIAL VASCULITIS AND HYPOCOMPLEMENTEMIC URTICARIAL VASCULITIS SYNDROME.IMMUNOLOGY AND ALLERGY CLINICS OF NORTH AMERICA. VOL. 24. ISSUE 2. P. 183-+ 88 66% 46
3 PERONI, A , COLATO, C , ZANONI, G , GIROLOMONI, G , (2010) URTICARIAL LESIONS: IF NOT URTICARIA, WHAT ELSE? THE DIFFERENTIAL DIAGNOSIS OF URTICARIA PART II. SYSTEMIC DISEASES.JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY. VOL. 62. ISSUE 4. P. 557 -570 73 64% 17
4 LIPSKER, D , LENORMAND, C , (2014) MANAGEMENT OF SCHNITZLER'S SYNDROME.EXPERT OPINION ON ORPHAN DRUGS. VOL. 2. ISSUE 9. P. 947 -955 45 92% 0
5 LIPSKER, D , (2010) THE SCHNITZLER SYNDROME.ORPHANET JOURNAL OF RARE DISEASES. VOL. 5. ISSUE . P. - 43 90% 46
6 DE KONING, HD , BODAR, EJ , VAN DER MEER, JWM , SIMON, A , (2007) SCHNITZLER SYNDROME: BEYOND THE CASE REPORTS: REVIEW AND FOLLOW-UP OF 94 PATIENTS WITH AN EMPHASIS ON PROGNOSIS AND TREATMENT.SEMINARS IN ARTHRITIS AND RHEUMATISM. VOL. 37. ISSUE 3. P. 137-148 49 78% 100
7 LIPSKER, D , VERAN, Y , GRUNENBERGER, F , CRIBIER, B , HEID, E , GROSSHANS, E , (2001) THE SCHNITZLER SYNDROME - FOUR NEW CASES AND REVIEW OF THE LITERATURE.MEDICINE. VOL. 80. ISSUE 1. P. 37 -44 33 100% 129
8 VENZOR, J , LEE, WL , HUSTON, DP , (2002) URTICARIAL VASCULITIS.CLINICAL REVIEWS IN ALLERGY & IMMUNOLOGY. VOL. 23. ISSUE 2. P. 201-216 46 73% 41
9 TINAZZI, E , PUCCETTI, A , PATUZZO, G , SORLETO, M , BARBIERI, A , LUNARDI, C , (2011) SCHNITZLER SYNDROME, AN AUTOIMMUNE-AUTOINFLAMMATORY SYNDROME: REPORT OF TWO NEW CASES AND REVIEW OF THE LITERATURE.AUTOIMMUNITY REVIEWS. VOL. 10. ISSUE 7. P. 404-409 32 82% 16
10 SOUBRIER, M , (2008) SCHNITZLER SYNDROME.JOINT BONE SPINE. VOL. 75. ISSUE 3. P. 263-266 27 90% 12

Classes with closest relation at Level 1



Rank Class id link
1 3827 CHRONIC URTICARIA//URTICARIA//CHRONIC IDIOPATHIC URTICARIA
2 29293 JACCOUDS ARTHROPATHY//RHUPUS//DEFORMING ARTHROPATHY
3 32990 ERYTHEMA ANNULARE CENTRIFUGUM//FIGURATE ERYTHEMA//311NM ULTRAVIOLET B NARROW BAND PHOTOTHERAPY
4 6267 HENOCH SCHONLEIN PURPURA//HENOCH SCHONLEIN PURPURA NEPHRITIS//LEUKOCYTOCLASTIC VASCULITIS
5 28905 GRANULOMA FACIALE//ERYTHEMA ELEVATUM DIUTINUM//EOSINOPHILIC ANGIOCENTRIC FIBROSIS
6 7412 C1Q//ANTI C1Q ANTIBODIES//C1Q DEFICIENCY
7 1684 FAMILIAL MEDITERRANEAN FEVER//MEFV//PERIODIC FEVER
8 17196 PALMAR FASCIITIS//PARANEOPLASTIC VASCULITIS//LEUKEMIC ARTHRITIS
9 11761 WALDENSTROMS MACROGLOBULINEMIA//WALDENSTROM MACROGLOBULINEMIA//LYMPHOPLASMACYTIC LYMPHOMA
10 15548 ADULT ONSET STILLS DISEASE//STILLS DISEASE//ADULT STILLS DISEASE

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