Class information for:
Level 1: CUTIS VERTICIS GYRATA//CONGENITAL HYPERTRICHOSIS//HYPERTRICHOSIS CUBITI

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
21558 414 17.5 56%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
442 3       DERMATOLOGY//VITILIGO//DERMATOL 26460
2116 2             VITILIGO//INCONTINENTIA PIGMENTI//DERMATOLOGY 5103
21558 1                   CUTIS VERTICIS GYRATA//CONGENITAL HYPERTRICHOSIS//HYPERTRICHOSIS CUBITI 414

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CUTIS VERTICIS GYRATA authKW 1024064 5% 73% 19
2 CONGENITAL HYPERTRICHOSIS authKW 811316 3% 100% 11
3 HYPERTRICHOSIS CUBITI authKW 516292 2% 100% 7
4 HYPERTRICHOSIS authKW 462856 7% 22% 29
5 WIEDEMANN STEINER SYNDROME authKW 442536 1% 100% 6
6 SEGMENTAL ODONTOMAXILLARY DYSPLASIA authKW 368780 1% 100% 5
7 AMBRAS SYNDROME authKW 307315 1% 83% 5
8 KMT2A authKW 301165 2% 58% 7
9 SMOOTH MUSCLE HAMARTOMA authKW 265517 1% 60% 6
10 CANTU SYNDROME authKW 258139 2% 50% 7

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 21395 54% 0% 225
2 Pediatrics 1037 18% 0% 74
3 Genetics & Heredity 903 20% 0% 84
4 Dentistry, Oral Surgery & Medicine 84 4% 0% 17
5 Pathology 25 3% 0% 12
6 Medical Ethics 22 0% 0% 2
7 Medicine, General & Internal 10 4% 0% 17
8 Literary Reviews 7 0% 0% 1
9 Surgery 7 5% 0% 19
10 Primary Health Care 6 0% 0% 2

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CYTOL EMBRYOL 73756 0% 100% 1
2 DENT ORO IAL SCI 73756 0% 100% 1
3 DERMATOL STD PATHOL 73756 0% 100% 1
4 HOSP A PERRINO BRINDISI 73756 0% 100% 1
5 HOSP DESTERRO 73756 0% 100% 1
6 KLIN POLIKLIN DEMATOL VENEROL ALLERGOL 73756 0% 100% 1
7 MED OCCIDENTE MEXICANO SEGURO SOCIAL 73756 0% 100% 1
8 NEBRASKA MED 983335 73756 0% 100% 1
9 OU HISTOPATHOL 73756 0% 100% 1
10 PAEDIAT PUBL HLTH 73756 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PEDIATRIC DERMATOLOGY 44169 11% 1% 47
2 CLINICAL DYSMORPHOLOGY 11164 3% 1% 13
3 ANNALES DE DERMATOLOGIE ET DE VENEREOLOGIE 4665 5% 0% 19
4 AMERICAN JOURNAL OF MEDICAL GENETICS 4057 5% 0% 22
5 INTERNATIONAL JOURNAL OF DERMATOLOGY 3637 5% 0% 19
6 HAUTARZT 3454 4% 0% 15
7 AMERICAN JOURNAL OF MEDICAL GENETICS PART A 2859 4% 0% 15
8 JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 2646 5% 0% 21
9 CLINICAL AND EXPERIMENTAL DERMATOLOGY 2128 3% 0% 12
10 ANNALS OF DERMATOLOGY 1945 1% 1% 5

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 CUTIS VERTICIS GYRATA 1024064 5% 73% 19 Search CUTIS+VERTICIS+GYRATA Search CUTIS+VERTICIS+GYRATA
2 CONGENITAL HYPERTRICHOSIS 811316 3% 100% 11 Search CONGENITAL+HYPERTRICHOSIS Search CONGENITAL+HYPERTRICHOSIS
3 HYPERTRICHOSIS CUBITI 516292 2% 100% 7 Search HYPERTRICHOSIS+CUBITI Search HYPERTRICHOSIS+CUBITI
4 HYPERTRICHOSIS 462856 7% 22% 29 Search HYPERTRICHOSIS Search HYPERTRICHOSIS
5 WIEDEMANN STEINER SYNDROME 442536 1% 100% 6 Search WIEDEMANN+STEINER+SYNDROME Search WIEDEMANN+STEINER+SYNDROME
6 SEGMENTAL ODONTOMAXILLARY DYSPLASIA 368780 1% 100% 5 Search SEGMENTAL+ODONTOMAXILLARY+DYSPLASIA Search SEGMENTAL+ODONTOMAXILLARY+DYSPLASIA
7 AMBRAS SYNDROME 307315 1% 83% 5 Search AMBRAS+SYNDROME Search AMBRAS+SYNDROME
8 KMT2A 301165 2% 58% 7 Search KMT2A Search KMT2A
9 SMOOTH MUSCLE HAMARTOMA 265517 1% 60% 6 Search SMOOTH+MUSCLE+HAMARTOMA Search SMOOTH+MUSCLE+HAMARTOMA
10 CANTU SYNDROME 258139 2% 50% 7 Search CANTU+SYNDROME Search CANTU+SYNDROME

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 ROTHMAN, IL , (2014) MICHELIN TIRE BABY SYNDROME: A REVIEW OF THE LITERATURE AND A PROPOSAL FOR DIAGNOSTIC CRITERIA WITH ADOPTION OF THE NAME CIRCUMFERENTIAL SKIN FOLDS SYNDROME.PEDIATRIC DERMATOLOGY. VOL. 31. ISSUE 6. P. 659 -663 21 100% 0
2 KHATAMI, A , SERADJ, MH , GOROUHI, F , FIROOZ, A , DOWLATI, Y , (2008) GIANT BILATERAL BECKER NEVUS: A RARE PRESENTATION.PEDIATRIC DERMATOLOGY. VOL. 25. ISSUE 1. P. 47 -51 28 80% 10
3 SCHMIDT, CS , BENTZ, ML , (2005) CONGENITAL SMOOTH MUSCLE HAMARTOMA: THE IMPORTANCE OF DIFFERENTIATION FROM MELANOCYTIC NEVI.JOURNAL OF CRANIOFACIAL SURGERY. VOL. 16. ISSUE 5. P. 926-929 23 88% 6
4 DANARTI, R , KONIG, A , SALHI, M , BITTAR, M , HAPPLE, R , (2004) BECKER'S NEVUS SYNDROME REVISITED.JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY. VOL. 51. ISSUE 6. P. 965-969 22 88% 26
5 CHEN, WC , RING, J , HAPPLE, R , (2015) CONGENITAL GENERALIZED HYPERTRICHOSIS TERMINALIS: A PROPOSED CLASSIFICATION AND A PLEA TO AVOID THE AMBIGUOUS TERM "AMBRAS SYNDROME".EUROPEAN JOURNAL OF DERMATOLOGY. VOL. 25. ISSUE 3. P. 223 -227 17 81% 0
6 ZARINEH, A , KOZOVSKA, ME , BROWN, WG , ELDER, DE , RABKIN, MS , (2008) SMOOTH MUSCLE HAMARTOMA ASSOCIATED WITH A CONGENITAL PATTERN MELANOCYTIC NEVUS, A CASE REPORT AND REVIEW OF THE LITERATURE.JOURNAL OF CUTANEOUS PATHOLOGY. VOL. 35. ISSUE . P. 83-86 16 100% 4
7 CZESCHIK, JC , VOIGT, C , GOECKE, TO , LUDECKE, HJ , WAGNER, N , KUECHLER, A , WIECZOREK, D , (2013) WIDE CLINICAL VARIABILITY IN CONDITIONS WITH COARSE FACIAL FEATURES AND HYPERTRICHOSIS CAUSED BY MUTATIONS IN ABCC9.AMERICAN JOURNAL OF MEDICAL GENETICS PART A. VOL. 161A. ISSUE 2. P. 295-300 16 80% 8
8 WENDELIN, DS , POPE, DN , MALLORY, SB , (2003) HYPERTRICHOSIS.JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY. VOL. 48. ISSUE 2. P. 161-179 42 37% 56
9 HOLLAND, KE , GALBRAITH, SS , (2008) GENERALIZED CONGENITAL SMOOTH MUSCLE HAMARTOMA PRESENTING WITH HYPERTRICHOSIS, EXCESS SKIN FOLDS, AND FOLLICULAR DIMPLING.PEDIATRIC DERMATOLOGY. VOL. 25. ISSUE 2. P. 236 -239 14 100% 5
10 AFIFI, HH , ABDEL-HAMID, MS , EID, MM , MOSTAFA, IS , ABDEL-SALAM, GMH , (2016) DE NOVO MUTATION IN ABCC9 CAUSES HYPERTRICHOSIS ACROMEGALOID FACIAL FEATURES DISORDER.PEDIATRIC DERMATOLOGY. VOL. 33. ISSUE 2. P. E109 -E113 11 100% 0

Classes with closest relation at Level 1



Rank Class id link
1 36345 ENAMEL PEARLS//REGIONAL ODONTODYSPLASIA//GHOST TEETH
2 13864 EPIDERMAL NEVUS SYNDROME//LICHEN STRIATUS//NEVUS SEBACEUS
3 19177 FUMARATE HYDRATASE//HLRCC//CUTANEOUS LEIOMYOSARCOMA
4 25749 TRICHORHINOPHALANGEAL SYNDROME//TRPS1//LANGER GIEDION SYNDROME
5 10328 GINGIVAL OVERGROWTH//GINGIVAL HYPERPLASIA ETIOLOGY//GINGIVAL HYPERPLASIA
6 36200 ACRAL PEELING SKIN SYNDROME//KERATOLYTIC WINTER ERYTHEMA//PEELING SKIN SYNDROME
7 14318 ACANTHOSIS NIGRICANS//BAZEX SYNDROME//ACROKERATOSIS PARANEOPLASTICA
8 22392 ECTOPIC BREAST//ANOGENITAL MAMMARY LIKE GLANDS//HIDRADENOMA PAPILLIFERUM
9 24795 FRASER SYNDROME//CRYPTOPHTHALMOS//FRAS1
10 32276 WOLFGANG AMADEUS MOZART//REWRITING RULE//AFT OOGHEELKUNDE

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