Class information for:
Level 1: FACTOR VII DEFICIENCY//FACTOR X DEFICIENCY//FVII DEFICIENCY

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
17027 622 27.0 69%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
111 3       THROMBOSIS RESEARCH//THROMBOSIS AND HAEMOSTASIS//HEMATOLOGY 71244
637 2             TISSUE FACTOR//THROMBOMODULIN//PROTEIN C 13723
17027 1                   FACTOR VII DEFICIENCY//FACTOR X DEFICIENCY//FVII DEFICIENCY 622

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 FACTOR VII DEFICIENCY authKW 3488503 15% 75% 95
2 FACTOR X DEFICIENCY authKW 1979973 9% 73% 55
3 FVII DEFICIENCY authKW 1070491 4% 84% 26
4 FX DEFICIENCY authKW 349090 1% 89% 8
5 RARE BLEEDING DISORDERS authKW 338532 3% 34% 20
6 CONGENITAL FACTOR VII DEFICIENCY authKW 314179 1% 80% 8
7 FACTOR VII authKW 303584 9% 11% 55
8 INHERITED FACTOR VII DEFICIENCY authKW 245455 1% 100% 5
9 FACTOR X authKW 244054 5% 15% 33
10 IMPAIRED SECRETION authKW 204544 1% 83% 5

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 28299 64% 0% 401
2 Peripheral Vascular Diseases 2530 19% 0% 119
3 Pediatrics 176 7% 0% 42
4 Genetics & Heredity 53 5% 0% 33
5 Anesthesiology 53 2% 0% 13
6 Medicine, General & Internal 44 6% 0% 35
7 Medical Laboratory Technology 32 1% 0% 9
8 Obstetrics & Gynecology 25 3% 0% 17
9 Dentistry, Oral Surgery & Medicine 14 2% 0% 11
10 Transplantation 11 1% 0% 8

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 FONDAZ LUIGI VILLA 98182 0% 100% 2
2 ST GEORGES HAEMOPHILIA 98182 0% 100% 2
3 CIBF 65453 0% 67% 2
4 MED SCI HAEMATOL 63114 0% 43% 3
5 TRANSGENE 55224 0% 38% 3
6 ABRAMSON PEDIAT 310 49091 0% 100% 1
7 ANASTHESIE CHIRURG INTENS BEHANDLUNG PRAKLIN 49091 0% 100% 1
8 CHILDRENS HOSP ORG 49091 0% 100% 1
9 COAGULAT REFERENCE 49091 0% 100% 1
10 D DEN UNIV KLIN 49091 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HAEMOPHILIA 63302 10% 2% 63
2 BLOOD COAGULATION & FIBRINOLYSIS 38900 8% 2% 51
3 THROMBOSIS AND HAEMOSTASIS 8660 7% 0% 42
4 JOURNAL OF THROMBOSIS AND HAEMOSTASIS 5511 3% 1% 21
5 HAEMOSTASIS 4788 2% 1% 11
6 CLINICAL AND APPLIED THROMBOSIS-HEMOSTASIS 4318 2% 1% 12
7 BRITISH JOURNAL OF HAEMATOLOGY 3246 5% 0% 30
8 THROMBOSIS RESEARCH 2293 4% 0% 22
9 ACTA HAEMATOLOGICA 2035 2% 0% 12
10 BLUT 1866 1% 1% 6

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 FACTOR VII DEFICIENCY 3488503 15% 75% 95 Search FACTOR+VII+DEFICIENCY Search FACTOR+VII+DEFICIENCY
2 FACTOR X DEFICIENCY 1979973 9% 73% 55 Search FACTOR+X+DEFICIENCY Search FACTOR+X+DEFICIENCY
3 FVII DEFICIENCY 1070491 4% 84% 26 Search FVII+DEFICIENCY Search FVII+DEFICIENCY
4 FX DEFICIENCY 349090 1% 89% 8 Search FX+DEFICIENCY Search FX+DEFICIENCY
5 RARE BLEEDING DISORDERS 338532 3% 34% 20 Search RARE+BLEEDING+DISORDERS Search RARE+BLEEDING+DISORDERS
6 CONGENITAL FACTOR VII DEFICIENCY 314179 1% 80% 8 Search CONGENITAL+FACTOR+VII+DEFICIENCY Search CONGENITAL+FACTOR+VII+DEFICIENCY
7 FACTOR VII 303584 9% 11% 55 Search FACTOR+VII Search FACTOR+VII
8 INHERITED FACTOR VII DEFICIENCY 245455 1% 100% 5 Search INHERITED+FACTOR+VII+DEFICIENCY Search INHERITED+FACTOR+VII+DEFICIENCY
9 FACTOR X 244054 5% 15% 33 Search FACTOR+X Search FACTOR+X
10 IMPAIRED SECRETION 204544 1% 83% 5 Search IMPAIRED+SECRETION Search IMPAIRED+SECRETION

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 BORENSZTAJN, K , SPEK, CA , (2005) INHERITED COAGULATION FACTOR VII AND X DEFICIENCIES ASSOCIATED WITH SEVERE BLEEDING DIATHESIS: MOLECULAR GENETICS AND PATHOPHYSIOLOGY.CURRENT GENOMICS. VOL. 6. ISSUE 6. P. 383-400 77 63% 0
2 MENEGATTI, M , PEYVANDI, F , (2009) FACTOR X DEFICIENCY.SEMINARS IN THROMBOSIS AND HEMOSTASIS. VOL. 35. ISSUE 4. P. 407-415 38 76% 43
3 GIROLAMI, A , COSI, E , SAMBADO, L , GIROLAMI, B , RANDI, ML , (2015) COMPLEX HISTORY OF THE DISCOVERY AND CHARACTERIZATION OF CONGENITAL FACTOR X DEFICIENCY.SEMINARS IN THROMBOSIS AND HEMOSTASIS. VOL. 41. ISSUE 4. P. 359 -365 28 90% 2
4 GIROLAMI, A , SCANDELLARI, R , SCAPIN, M , VETTORE, S , (2008) CONGENITAL BLEEDING DISORDERS OF THE VITAMIN K-DEPENDENT CLOTTING FACTORS.VITAMIN K. VOL. 78. ISSUE . P. 281-+ 73 41% 12
5 SIBONI, SM , BIGUZZI, E , MISTRETTA, C , GARAGIOLA, I , PEYVANDI, F , (2015) LONG-TERM PROPHYLAXIS IN SEVERE FACTOR VII DEFICIENCY.HAEMOPHILIA. VOL. 21. ISSUE 6. P. 812 -819 26 93% 1
6 HERRMANN, FH , WULFF, K , AUERSWALD, G , SCHULMAN, S , ASTERMARK, J , BATOROVA, A , KREUZ, W , POLLMANN, H , RUIZ-SAEZ, A , BOSCH, N , ET AL (2009) FACTOR VII DEFICIENCY: CLINICAL MANIFESTATION OF 717 SUBJECTS FROM EUROPE AND LATIN AMERICA WITH MUTATIONS IN THE FACTOR 7 GENE.HAEMOPHILIA. VOL. 15. ISSUE 1. P. 267-280 24 100% 46
7 KREUZIGER, LMB , MORTON, CT , REDING, MT , (2013) IS PROPHYLAXIS REQUIRED FOR DELIVERY IN WOMEN WITH FACTOR VII DEFICIENCY?.HAEMOPHILIA. VOL. 19. ISSUE 6. P. 827-832 26 87% 6
8 GIROLAMI, A , SCARPARO, P , VETTORE, S , CANDEO, N , SCANDELLARI, R , LOMBARDI, AM , (2009) UNEXPLAINED DISCREPANCIES IN THE ACTIVITY-ANTIGEN RATIO IN CONGENITAL FX DEFICIENCIES WITH DEFECTS IN THE CATALYTIC DOMAIN.CLINICAL AND APPLIED THROMBOSIS-HEMOSTASIS. VOL. 15. ISSUE 6. P. 621-627 25 100% 5
9 GIROLAMI, A , COSI, E , SANTAROSSA, C , FERRARI, S , GIROLAMI, B , LOMBARDI, AM , (2016) PREVALENCE OF BLEEDING MANIFESTATIONS IN 128 HETEROZYGOTES FOR FACTOR X DEFICIENCY, MAINLY FOR FX FRIULI, MATCHED VERSUS 128 UNAFFECTED FAMILY MEMBERS, DURING A LONG SEQUENTIAL OBSERVATION PERIOD (23.5 YEARS).EUROPEAN JOURNAL OF HAEMATOLOGY. VOL. 97. ISSUE 6. P. 547 -553 21 100% 0
10 UPRICHARD, J , PERRY, DJ , (2002) FACTOR X DEFICIENCY.BLOOD REVIEWS. VOL. 16. ISSUE 2. P. 97-110 46 58% 83

Classes with closest relation at Level 1



Rank Class id link
1 3016 FACTOR VA//FACTOR V DEFICIENCY//PROTHROMBINASE
2 11335 RECOMBINANT ACTIVATED FACTOR VII//RECOMBINANT FACTOR VIIA//RFVIIA
3 23637 PROTEIN C INHIBITOR//F5F8D//LMAN1
4 4791 FIBRINOGEN//FACTOR VII//FIBRINOGEN ASSAYS
5 25757 INTRACRANIAL HAEMORRHAGE//PSEUDOTUMOUR//HEMOPHILIC PSEUDOTUMOR
6 17915 THROMBIN GENERATION//THROMBIN GENERATION ASSAY//ENDOGENOUS THROMBIN POTENTIAL
7 942 TISSUE FACTOR//TISSUE FACTOR PATHWAY INHIBITOR//TFPI
8 8500 HEMOPHILIA A//FACTOR VIII GENE//HAEMOPHILIA A
9 11284 FACTOR XIII//FACTOR XIII DEFICIENCY//MOL PATHOBIOCHEM PATHOBIOL
10 3705 FACTOR XII//FACTOR XI//FACTOR XI DEFICIENCY

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