Class information for:
Level 1: CONGENITAL HYPERINSULINISM//NESIDIOBLASTOSIS//HYPERINSULINISM

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
11430 982 29.9 73%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
537 3       BIOARTIFICIAL LIVER//HEPATOCYTES//HEPATOCYTE TRANSPLANTATION 19236
2578 2             MODY//CONGENITAL HYPERINSULINISM//NEONATAL DIABETES 3676
11430 1                   CONGENITAL HYPERINSULINISM//NESIDIOBLASTOSIS//HYPERINSULINISM 982

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CONGENITAL HYPERINSULINISM authKW 2727479 10% 88% 100
2 NESIDIOBLASTOSIS authKW 2281853 10% 73% 101
3 HYPERINSULINISM authKW 1374322 12% 39% 114
4 LONDON PAEDIAT ENDOCRINOL METAB address 507824 4% 47% 35
5 HYPERINSULINEMIC HYPOGLYCEMIA authKW 429963 2% 63% 22
6 HYPERINSULINAEMIC HYPOGLYCAEMIA authKW 390688 2% 74% 17
7 PERSISTENT HYPERINSULINEMIC HYPOGLYCEMIA OF INFANCY authKW 298493 1% 80% 12
8 ABCC8 authKW 224587 2% 33% 22
9 HYPOGLYCEMIA authKW 175869 13% 4% 129
10 DEV ENDOCRINOL GRP address 172751 3% 16% 34

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Pediatrics 10753 36% 0% 355
2 Endocrinology & Metabolism 10002 39% 0% 383
3 Surgery 463 14% 0% 133
4 Pathology 411 6% 0% 63
5 Genetics & Heredity 114 6% 0% 58
6 Medicine, Research & Experimental 76 4% 0% 44
7 Medical Laboratory Technology 49 1% 0% 14
8 Gastroenterology & Hepatology 39 3% 0% 27
9 Medicine, General & Internal 36 5% 0% 45
10 CYTOLOGY & HISTOLOGY 13 0% 0% 2

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 LONDON PAEDIAT ENDOCRINOL METAB 507824 4% 47% 35
2 DEV ENDOCRINOL GRP 172751 3% 16% 34
3 UNIT BIOCHEM ENDOCRINOL METAB 159908 1% 86% 6
4 LONDON PEDIAT ENDOCRINOL METAB 111046 1% 71% 5
5 GENET EPIGENET HLTH DIS GENET GENOM MED PRO 93281 0% 100% 3
6 GENET EPIGENET HLTH DIS 82913 0% 67% 4
7 BIOMED CLIN SCI 82512 5% 5% 51
8 UNITE 383 62187 0% 100% 2
9 PAEDIAT ENDOCRINOL 57565 4% 5% 38
10 CLIN MOL GENET UNIT 55780 3% 7% 27

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM 25384 5% 2% 54
2 HORMONE RESEARCH IN PAEDIATRICS 12191 2% 2% 18
3 SEMINARS IN PEDIATRIC SURGERY 11198 1% 3% 12
4 JOURNAL OF CLINICAL RESEARCH IN PEDIATRIC ENDOCRINOLOGY 10629 1% 3% 10
5 DIABETES 4307 4% 0% 41
6 JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM 3625 5% 0% 53
7 ARCHIVES OF DISEASE IN CHILDHOOD 3092 3% 0% 33
8 JOURNAL OF PEDIATRICS 2781 4% 0% 35
9 OBESITY SURGERY 2260 2% 0% 18
10 EUROPEAN JOURNAL OF PEDIATRICS 2180 2% 0% 23

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 CONGENITAL HYPERINSULINISM 2727479 10% 88% 100 Search CONGENITAL+HYPERINSULINISM Search CONGENITAL+HYPERINSULINISM
2 NESIDIOBLASTOSIS 2281853 10% 73% 101 Search NESIDIOBLASTOSIS Search NESIDIOBLASTOSIS
3 HYPERINSULINISM 1374322 12% 39% 114 Search HYPERINSULINISM Search HYPERINSULINISM
4 HYPERINSULINEMIC HYPOGLYCEMIA 429963 2% 63% 22 Search HYPERINSULINEMIC+HYPOGLYCEMIA Search HYPERINSULINEMIC+HYPOGLYCEMIA
5 HYPERINSULINAEMIC HYPOGLYCAEMIA 390688 2% 74% 17 Search HYPERINSULINAEMIC+HYPOGLYCAEMIA Search HYPERINSULINAEMIC+HYPOGLYCAEMIA
6 PERSISTENT HYPERINSULINEMIC HYPOGLYCEMIA OF INFANCY 298493 1% 80% 12 Search PERSISTENT+HYPERINSULINEMIC+HYPOGLYCEMIA+OF+INFANCY Search PERSISTENT+HYPERINSULINEMIC+HYPOGLYCEMIA+OF+INFANCY
7 ABCC8 224587 2% 33% 22 Search ABCC8 Search ABCC8
8 HYPOGLYCEMIA 175869 13% 4% 129 Search HYPOGLYCEMIA Search HYPOGLYCEMIA
9 HYPERINSULINISM HYPERAMMONEMIA SYNDROME 129555 1% 83% 5 Search HYPERINSULINISM+HYPERAMMONEMIA+SYNDROME Search HYPERINSULINISM+HYPERAMMONEMIA+SYNDROME
10 NEAR TOTAL PANCREATECTOMY 124374 0% 100% 4 Search NEAR+TOTAL+PANCREATECTOMY Search NEAR+TOTAL+PANCREATECTOMY

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 ARYA, VB , MOHAMMED, Z , BLANKENSTEIN, O , DE LONLAY, P , HUSSAIN, K , (2014) HYPERINSULINAEMIC HYPOGLYCAEMIA.HORMONE AND METABOLIC RESEARCH. VOL. 46. ISSUE 3. P. 157 -170 91 66% 9
2 SHAH, P , DEMIRBILEK, H , HUSSAIN, K , (2014) PERSISTENT HYPERINSULINAEMIC HYPOGLYCAEMIA IN INFANCY.SEMINARS IN PEDIATRIC SURGERY. VOL. 23. ISSUE 2. P. 76 -82 65 96% 4
3 YORIFUJI, T , MASUE, M , NISHIBORI, H , (2014) CONGENITAL HYPERINSULINISM: GLOBAL AND JAPANESE PERSPECTIVES.PEDIATRICS INTERNATIONAL. VOL. 56. ISSUE 4. P. 467 -476 72 84% 0
4 ROZENKOVA, K , GUEMES, M , SHAH, P , HUSSAIN, K , (2015) THE DIAGNOSIS AND MANAGEMENT OF HYPERINSULINAEMIC HYPOGLYCAEMIA.JOURNAL OF CLINICAL RESEARCH IN PEDIATRIC ENDOCRINOLOGY. VOL. 7. ISSUE 2. P. 86 -97 68 76% 4
5 STANLEY, CA , (2016) PERSPECTIVE ON THE GENETICS AND DIAGNOSIS OF CONGENITAL HYPERINSULINISM DISORDERS.JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM. VOL. 101. ISSUE 3. P. 815 -826 55 71% 5
6 MEISSNER, T , MAYATEPEK, E , (2002) CLINICAL AND GENETIC HETEROGENEITY IN CONGENITAL HYPERINSULINISM.EUROPEAN JOURNAL OF PEDIATRICS. VOL. 161. ISSUE 1. P. 6 -20 86 73% 21
7 ARNOUX, JB , VERKARRE, V , SAINT-MARTIN, C , MONTRAVERS, F , BRASSIER, A , VALAYANNOPOULOS, V , BRUNELLE, F , FOURNET, JC , ROBERT, JJ , AIGRAIN, Y , ET AL (2011) CONGENITAL HYPERINSULINISM: CURRENT TRENDS IN DIAGNOSIS AND THERAPY.ORPHANET JOURNAL OF RARE DISEASES. VOL. 6. ISSUE . P. - 54 71% 68
8 ARNOUX, JB , SAINT-MARTIN, C , MONTRAVERS, F , VERKARRE, V , GALMICHE, L , TELION, C , CAPITO, C , ROBERT, JJ , HUSSAIN, K , AIGRAIN, Y , ET AL (2014) AN UPDATE ON CONGENITAL HYPERINSULINISM: ADVANCES IN DIAGNOSIS AND MANAGEMENT.EXPERT OPINION ON ORPHAN DRUGS. VOL. 2. ISSUE 8. P. 779 -795 67 64% 0
9 MOHAMED, Z , ARYA, VB , HUSSAIN, K , (2012) HYPERINSULINAEMIC HYPOGLYCAEMIA: GENETIC MECHANISMS, DIAGNOSIS AND MANAGEMENT.JOURNAL OF CLINICAL RESEARCH IN PEDIATRIC ENDOCRINOLOGY. VOL. 4. ISSUE 4. P. 169-181 57 72% 13
10 KAPOOR, RR , JAMES, C , HUSSAIN, K , (2009) ADVANCES IN THE DIAGNOSIS AND MANAGEMENT OF HYPERINSULINEMIC HYPOGLYCEMIA.NATURE CLINICAL PRACTICE ENDOCRINOLOGY & METABOLISM. VOL. 5. ISSUE 2. P. 101-112 62 67% 42

Classes with closest relation at Level 1



Rank Class id link
1 17143 NEONATAL HYPOGLYCEMIA//NEONATAL HYPOGLYCAEMIA//ADDENBROOKES UNIV HOSP NHS TRUST
2 3436 INSULINOMA//GASTRINOMA//ZOLLINGER ELLISON SYNDROME
3 23415 INSULIN OVERDOSE//BIOCHEMICAL HYPOGLYCEMIA//LETHAL HYPOGLYCAEMIA
4 16491 NEONATAL DIABETES//NEONATAL DIABETES MELLITUS//WOLCOTT RALLISON SYNDROME
5 14928 GLUTAMATE DEHYDROGENASE//GLUTAMATE DEHYDROGENASE ISOPROTEINS//CLOSTRIDIUM SYMBIOSUM
6 27571 PHARMACODYNAM THER EUT//PHARMACODYNAMIE THER EUT//SERV CHIM PHARMACEUT
7 761 ATP SENSITIVE K CHANNEL//K ATP CHANNEL//ATP SENSITIVE POTASSIUM CHANNEL
8 18947 DUMPING SYNDROME//OCTREOTIDE//REFRACTORY DIARRHEA
9 24537 FETAL CARDIAC FUNCTION//MYOCARDIAL PERFORMANCE INDEX//MODIFIED MYOCARDIAL PERFORMANCE INDEX
10 10494 GLUCOKINASE//GLUCOKINASE ACTIVATOR//GLUCOKINASE REGULATORY PROTEIN

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