Class information for:
Level 2: MODY//CONGENITAL HYPERINSULINISM//NEONATAL DIABETES

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
2578 3676 32.9 79%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
537 3       BIOARTIFICIAL LIVER//HEPATOCYTES//HEPATOCYTE TRANSPLANTATION 19236
2578 2             MODY//CONGENITAL HYPERINSULINISM//NEONATAL DIABETES 3676
6916 1                   MODY//MATURITY ONSET DIABETES OF THE YOUNG//MONOGENIC DIABETES 1429
11430 1                   CONGENITAL HYPERINSULINISM//NESIDIOBLASTOSIS//HYPERINSULINISM 982
16491 1                   NEONATAL DIABETES//NEONATAL DIABETES MELLITUS//WOLCOTT RALLISON SYNDROME 650
17143 1                   NEONATAL HYPOGLYCEMIA//NEONATAL HYPOGLYCAEMIA//ADDENBROOKES UNIV HOSP NHS TRUST 615

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 MODY authKW 1085087 5% 78% 168
2 CONGENITAL HYPERINSULINISM authKW 757902 3% 89% 102
3 NEONATAL DIABETES authKW 653879 3% 79% 100
4 NESIDIOBLASTOSIS authKW 621552 3% 73% 102
5 MATURITY ONSET DIABETES OF THE YOUNG authKW 581995 2% 81% 87
6 MONOGENIC DIABETES authKW 543173 2% 87% 75
7 HYPERINSULINISM authKW 413431 3% 41% 121
8 NEONATAL DIABETES MELLITUS authKW 366792 2% 79% 56
9 BIOMED CLIN SCI address 359657 6% 21% 206
10 HNF 1 ALPHA authKW 309187 2% 58% 64

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 Endocrinology & Metabolism 31190 36% 0% 1313
2 Pediatrics 21441 27% 0% 981
3 Genetics & Heredity 1295 9% 0% 335
4 Biochemistry & Molecular Biology 342 13% 0% 466
5 Cell Biology 226 6% 0% 226
6 Developmental Biology 212 2% 0% 70
7 Medicine, Research & Experimental 192 4% 0% 144
8 Pathology 179 3% 0% 99
9 Obstetrics & Gynecology 174 3% 0% 107
10 Medical Laboratory Technology 162 1% 0% 50

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BIOMED CLIN SCI 359657 6% 21% 206
2 LONDON PAEDIAT ENDOCRINOL METAB 159858 1% 51% 38
3 VASC MED DIABET 81522 0% 55% 18
4 DEV ENDOCRINOL GRP 57592 1% 18% 38
5 CHILDREN DIABET 45212 0% 78% 7
6 UNIT BIOCHEM ENDOCRINOL METAB 42709 0% 86% 6
7 WESSEX REG GENET S 41524 0% 100% 5
8 DIABET VASC MED 34517 1% 20% 21
9 MENDELIAN DIABET 33905 0% 58% 7
10 PAEDIAT ENDOCRINOL 33329 2% 7% 56

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PEDIATRIC DIABETES 34912 2% 6% 67
2 JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM 30123 3% 3% 114
3 DIABETES 26128 5% 2% 195
4 DIABETOLOGIA 9282 3% 1% 97
5 DIABETIC MEDICINE 8767 2% 1% 78
6 HORMONE RESEARCH IN PAEDIATRICS 7848 1% 3% 28
7 JOURNAL OF CLINICAL RESEARCH IN PEDIATRIC ENDOCRINOLOGY 7251 0% 5% 16
8 ARCHIVES OF DISEASE IN CHILDHOOD 4323 2% 1% 76
9 DIABETES CARE 3766 2% 1% 73
10 JOURNAL OF PEDIATRICS 3534 2% 1% 77

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 MODY 1085087 5% 78% 168 Search MODY Search MODY
2 CONGENITAL HYPERINSULINISM 757902 3% 89% 102 Search CONGENITAL+HYPERINSULINISM Search CONGENITAL+HYPERINSULINISM
3 NEONATAL DIABETES 653879 3% 79% 100 Search NEONATAL+DIABETES Search NEONATAL+DIABETES
4 NESIDIOBLASTOSIS 621552 3% 73% 102 Search NESIDIOBLASTOSIS Search NESIDIOBLASTOSIS
5 MATURITY ONSET DIABETES OF THE YOUNG 581995 2% 81% 87 Search MATURITY+ONSET+DIABETES+OF+THE+YOUNG Search MATURITY+ONSET+DIABETES+OF+THE+YOUNG
6 MONOGENIC DIABETES 543173 2% 87% 75 Search MONOGENIC+DIABETES Search MONOGENIC+DIABETES
7 HYPERINSULINISM 413431 3% 41% 121 Search HYPERINSULINISM Search HYPERINSULINISM
8 NEONATAL DIABETES MELLITUS 366792 2% 79% 56 Search NEONATAL+DIABETES+MELLITUS Search NEONATAL+DIABETES+MELLITUS
9 HNF 1 ALPHA 309187 2% 58% 64 Search HNF+1+ALPHA Search HNF+1+ALPHA
10 MATURITY ONSET DIABETES OF THE YOUNG MODY 205413 1% 85% 29 Search MATURITY+ONSET+DIABETES+OF+THE+YOUNG+MODY Search MATURITY+ONSET+DIABETES+OF+THE+YOUNG+MODY

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 COLCLOUGH, K , BELLANNE-CHANTELOT, C , SAINT-MARTIN, C , FLANAGAN, SE , ELLARD, S , (2013) MUTATIONS IN THE GENES ENCODING THE TRANSCRIPTION FACTORS HEPATOCYTE NUCLEAR FACTOR 1 ALPHA AND 4 ALPHA IN MATURITY-ONSET DIABETES OF THE YOUNG AND HYPERINSULINEMIC HYPOGLYCEMIA.HUMAN MUTATION. VOL. 34. ISSUE 5. P. 669-685 131 86% 22
2 ANIK, A , CATLI, G , ABACI, A , BOBER, E , (2015) MATURITY-ONSET DIABETES OF THE YOUNG (MODY): AN UPDATE.JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM. VOL. 28. ISSUE 3-4. P. 251 -263 86 90% 6
3 RUBIO-CABEZAS, O , HATTERSLEY, AT , NJOLSTAD, PR , MLYNARSKI, W , ELLARD, S , WHITE, N , CHI, DV , CRAIG, ME , (2014) THE DIAGNOSIS AND MANAGEMENT OF MONOGENIC DIABETES IN CHILDREN AND ADOLESCENTS.PEDIATRIC DIABETES. VOL. 15. ISSUE . P. 47 -64 112 64% 23
4 ELLARD, S , COLCLOUGH, K , (2006) MUTATIONS IN THE GENES ENCODING THE TRANSCRIPTION FACTORS HEPATOCYTE NUCLEAR FACTOR 1 ALPHA (HNF1A) AND 4 ALPHA (HNF4A) IN MATURITY-ONSET DIABETES OF THE YOUNG.HUMAN MUTATION. VOL. 27. ISSUE 9. P. 854-869 98 92% 83
5 RYFFEL, GU , (2001) MUTATIONS IN THE HUMAN GENES ENCODING THE TRANSCRIPTION FACTORS OF THE HEPATOCYTE NUCLEAR FACTOR (HNF)1 AND HNF4 FAMILIES: FUNCTIONAL AND PATHOLOGICAL CONSEQUENCES.JOURNAL OF MOLECULAR ENDOCRINOLOGY. VOL. 27. ISSUE 1. P. 11 -29 102 83% 172
6 MCDONALD, TJ , ELLARD, S , (2013) MATURITY ONSET DIABETES OF THE YOUNG: IDENTIFICATION AND DIAGNOSIS.ANNALS OF CLINICAL BIOCHEMISTRY. VOL. 50. ISSUE 5. P. 403-415 80 82% 22
7 ARYA, VB , MOHAMMED, Z , BLANKENSTEIN, O , DE LONLAY, P , HUSSAIN, K , (2014) HYPERINSULINAEMIC HYPOGLYCAEMIA.HORMONE AND METABOLIC RESEARCH. VOL. 46. ISSUE 3. P. 157 -170 96 70% 9
8 YAMAGATA, K , (2014) ROLES OF HNF1 ALPHA AND HNF4 ALPHA IN PANCREATIC BETA-CELLS: LESSONS FROM A MONOGENIC FORM OF DIABETES (MODY).PANCREATIC BETA CELL. VOL. 95. ISSUE . P. 407 -423 78 86% 7
9 TIMSIT, J , SAINT-MARTIN, C , DUBOIS-LAFORGUE, D , BELLANNE-CHANTELOT, C , (2016) SEARCHING FOR MATURITY-ONSET DIABETES OF THE YOUNG (MODY): WHEN AND WHAT FOR?.CANADIAN JOURNAL OF DIABETES. VOL. 40. ISSUE 5. P. 455 -461 59 98% 2
10 LACHANCE, CH , (2016) PRACTICAL ASPECTS OF MONOGENIC DIABETES: A CLINICAL POINT OF VIEW.CANADIAN JOURNAL OF DIABETES. VOL. 40. ISSUE 5. P. 368 -375 68 85% 2

Classes with closest relation at Level 2



Rank Class id link
1 3379 ALPHA FETOPROTEIN//COSALANE//AFP RECEPTOR
2 457 BETA CELL//INSULIN SECRETION//PANCREATIC ISLETS
3 2439 GENOMIC IMPRINTING//BECKWITH WIEDEMANN SYNDROME//SILVER RUSSELL SYNDROME
4 3108 FOXM1//FOXO1//FOXO
5 1189 NICORANDIL//ISCHEMIC PRECONDITIONING//K ATP CHANNEL
6 3581 PHOSPHOENOLPYRUVATE CARBOXYKINASE//GLYCERONEOGENESIS//BROWN ADIPOSE TISSUE HEMIDENERVATION
7 257 GENETIC EPIDEMIOLOGY//HUMAN HEREDITY//GENETICS & HEREDITY
8 1495 KIDNEY DEVELOPMENT//FETAL PROGRAMMING//URETERIC BUD
9 789 TYPE 1 DIABETES//BARBARA DAVIS CHILDHOOD DIABET//PTPN22
10 2654 NURR1//NUR77//PGC 1 ALPHA

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