Class information for:
Level 1: PROPERDIN//COMPLEMENT DEFICIENCY//C7

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
7487 1362 35.1 58%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
350 3       COMPLEMENT//MANNOSE BINDING LECTIN//IMMUNOLOGY 35656
363 2             COMPLEMENT//MANNOSE BINDING LECTIN//PAROXYSMAL NOCTURNAL HEMOGLOBINURIA 17354
7487 1                   PROPERDIN//COMPLEMENT DEFICIENCY//C7 1362

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PROPERDIN authKW 252545 2% 43% 26
2 COMPLEMENT DEFICIENCY authKW 207959 2% 31% 30
3 C7 authKW 179819 1% 42% 19
4 PROPERDIN DEFICIENCY authKW 134507 0% 100% 6
5 C8 GAMMA authKW 115290 0% 86% 6
6 COMPLEMENT COMPONENT C6 authKW 112089 0% 100% 5
7 C7 DEFICIENCY authKW 93406 0% 83% 5
8 C8 authKW 91520 1% 29% 14
9 MEMBRANE ATTACK COMPLEX authKW 81431 2% 14% 26
10 C9 DEFICIENCY authKW 71735 0% 80% 4

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Immunology 13715 48% 0% 654
2 Infectious Diseases 632 7% 0% 97
3 Biochemistry & Molecular Biology 570 21% 0% 282
4 Microbiology 490 9% 0% 126
5 Genetics & Heredity 295 7% 0% 102
6 Allergy 124 2% 0% 22
7 Medicine, General & Internal 114 6% 0% 81
8 Medicine, Research & Experimental 100 4% 0% 60
9 Pathology 90 3% 0% 41
10 Rheumatology 70 2% 0% 22

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 REFRACTORY DIS 44836 0% 100% 2
2 4566 SCOTT AVE 22418 0% 100% 1
3 ABORATING BACTERIAL MENINGITIS 22418 0% 100% 1
4 BIOCHEM DEV GENET 22418 0% 100% 1
5 BIOCHEM HAEMOSTASIS 22418 0% 100% 1
6 BIOCHEM MRC IMMUNOCHEM UNIT S PARKS RD 22418 0% 100% 1
7 CAMBRIDGE HEPATOBILIARY RENAL TRANSPLANT UNIT 22418 0% 100% 1
8 CELL BIOL PHYSIOL IMMUNOLIMMUNOL 22418 0% 100% 1
9 CENT SANQUIN 22418 0% 100% 1
10 CHU CHR CITADELLE 22418 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 COMPLEMENT AND INFLAMMATION 27321 1% 12% 10
2 MOLECULAR IMMUNOLOGY 15107 5% 1% 69
3 PROGRESS IN ALLERGY 13568 1% 6% 10
4 EXPERIMENTAL AND CLINICAL IMMUNOGENETICS 11057 1% 3% 15
5 JOURNAL OF IMMUNOLOGY 9328 11% 0% 150
6 CLINICAL AND EXPERIMENTAL IMMUNOLOGY 4730 4% 0% 49
7 ACTA PATHOLOGICA MICROBIOLOGICA ET IMMUNOLOGICA SCANDINAVICA SECTION C-IMMUNOLOGY 2567 0% 2% 6
8 BIOLOGICAL MEMBRANES 2489 0% 11% 1
9 IMMUNOLOGY 1823 2% 0% 27
10 JAPANESE JOURNAL OF HUMAN GENETICS 1561 0% 1% 6

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 PROPERDIN 252545 2% 43% 26 Search PROPERDIN Search PROPERDIN
2 COMPLEMENT DEFICIENCY 207959 2% 31% 30 Search COMPLEMENT+DEFICIENCY Search COMPLEMENT+DEFICIENCY
3 C7 179819 1% 42% 19 Search C7 Search C7
4 PROPERDIN DEFICIENCY 134507 0% 100% 6 Search PROPERDIN+DEFICIENCY Search PROPERDIN+DEFICIENCY
5 C8 GAMMA 115290 0% 86% 6 Search C8+GAMMA Search C8+GAMMA
6 COMPLEMENT COMPONENT C6 112089 0% 100% 5 Search COMPLEMENT+COMPONENT+C6 Search COMPLEMENT+COMPONENT+C6
7 C7 DEFICIENCY 93406 0% 83% 5 Search C7+DEFICIENCY Search C7+DEFICIENCY
8 C8 91520 1% 29% 14 Search C8 Search C8
9 MEMBRANE ATTACK COMPLEX 81431 2% 14% 26 Search MEMBRANE+ATTACK+COMPLEX Search MEMBRANE+ATTACK+COMPLEX
10 C9 DEFICIENCY 71735 0% 80% 4 Search C9+DEFICIENCY Search C9+DEFICIENCY

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 WURZNER, R , WITZEL-SCHLOMP, K , TOKUNAGA, K , FERNIE, BA , HOBART, MJ , ORREN, A , (1998) REFERENCE TYPING REPORT FOR COMPLEMENT COMPONENTS C6, C7 AND C9 INCLUDING MUTATIONS LEADING TO DEFICIENCIES.EXPERIMENTAL AND CLINICAL IMMUNOGENETICS. VOL. 15. ISSUE 4. P. 268 -285 74 95% 15
2 WITZELSCHLOMP, K , SPATH, PJ , HOBART, MJ , FERNIE, BA , RITTNER, C , KAUFMANN, T , SCHNEIDER, PM , (1997) THE HUMAN COMPLEMENT C9 GENE - IDENTIFICATION OF TWO MUTATIONS CAUSING DEFICIENCY AND REVISION OF THE GENE STRUCTURE.JOURNAL OF IMMUNOLOGY. VOL. 158. ISSUE 10. P. 5043-5049 46 94% 16
3 RAMEIX-WELTI, MA , REGNIER, CH , BIENAIME, F , BLOUIN, J , SCHIFFERLI, J , FRIDMAN, WH , SAUTES-FRIDMAN, C , FREMEAUX-BACCHI, V , (2007) HEREDITARY COMPLEMENT C7 DEFICIENCY IN NINE FAMILIES: SUBTOTAL C7 DEFICIENCY REVISITED.EUROPEAN JOURNAL OF IMMUNOLOGY. VOL. 37. ISSUE 5. P. 1377-1385 35 85% 12
4 GARRED, P , VALERIUS, NH , MARQUART, H , ROSENFELDT, V , SCHEJBEL, L , (2009) PROPERDIN DEFICIENCY ASSOCIATED WITH RECURRENT OTITIS MEDIA AND PNEUMONIA, AND IDENTIFICATION OF MATE CARRIER WITH KLINEFELTER SYNDROME.CLINICAL IMMUNOLOGY. VOL. 131. ISSUE 3. P. 456-462 32 86% 14
5 ROSSI, V , WANG, YX , ESSER, AF , (2010) TOPOLOGY OF THE MEMBRANE-BOUND FORM OF COMPLEMENT PROTEIN C9 PROBED BY GLYCOSYLATION MAPPING, ANTI-PEPTIDE ANTIBODY BINDING, AND DISULFIDE MODIFICATION.MOLECULAR IMMUNOLOGY. VOL. 47. ISSUE 7-8. P. 1553-1560 33 83% 4
6 SHIN, ML , CARNEY, DF , (1988) CYTO-TOXIC ACTION AND OTHER METABOLIC CONSEQUENCES OF TERMINAL COMPLEMENT PROTEINS.PROGRESS IN ALLERGY. VOL. 40. ISSUE . P. 44-81 65 78% 46
7 MORGAN, BP , WALTERS, D , SERNA, M , BUBECK, D , (2016) TERMINAL COMPLEXES OF THE COMPLEMENT SYSTEM: NEW STRUCTURAL INSIGHTS AND THEIR RELEVANCE TO FUNCTION.IMMUNOLOGICAL REVIEWS. VOL. 274. ISSUE 1. P. 141 -151 40 48% 1
8 FERNIE, BA , WURZNER, R , ORREN, A , MORGAN, BP , POTTER, PC , PLATONOV, AE , VERSHININA, IV , SHIPULIN, GA , LACHMANN, PJ , HOBART, MJ , (1996) MOLECULAR BASES OF COMBINED SUBTOTAL DEFICIENCIES OF C6 AND C7 - THEIR EFFECTS IN COMBINATION WITH OTHER C6 AND C7 DEFICIENCIES.JOURNAL OF IMMUNOLOGY. VOL. 157. ISSUE 8. P. 3648-3657 38 93% 18
9 TEGLA, CA , CUDRICI, C , PATEL, S , TRIPPE, R , RUS, V , NICULESCU, F , RUS, H , (2011) MEMBRANE ATTACK BY COMPLEMENT: THE ASSEMBLY AND BIOLOGY OF TERMINAL COMPLEMENT COMPLEXES.IMMUNOLOGIC RESEARCH. VOL. 51. ISSUE 1. P. 45-60 55 34% 61
10 RAM, S , LEWIS, LA , RICE, PA , (2010) INFECTIONS OF PEOPLE WITH COMPLEMENT DEFICIENCIES AND PATIENTS WHO HAVE UNDERGONE SPLENECTOMY.CLINICAL MICROBIOLOGY REVIEWS. VOL. 23. ISSUE 4. P. 740 -+ 88 21% 86

Classes with closest relation at Level 1



Rank Class id link
1 2629 C2 DEFICIENCY//COMPLEMENT GENETICS//COMPLEMENT AND INFLAMMATION
2 8410 CD59//CD55//CD46
3 30260 CAMEL COMPLEMENT//AP DEPENDENT PHAGOCYTOSIS//AP LYTIC ACTIVITY
4 36876 C2 FUNCTIONAL ASSAY//C4 SYNTHESIS//CHOLINE PHOSPHOLIPID METABOLITES
5 19715 VITRONECTIN//KERCKHOFF KLIN HAEMOSTASIS UNIT//BIOL BUNKYO KU
6 16201 COMPLEMENT//BIIG//VACCINIA VIRUS COMPLEMENT CONTROL PROTEIN
7 4973 ATYPICAL HEMOLYTIC UREMIC SYNDROME//FACTOR H//ECULIZUMAB
8 18292 ACYLATION STIMULATING PROTEIN//C3ADESARG//RGC 32
9 3467 C5A//C5A RECEPTOR//ANAPHYLATOXIN
10 14680 COELOMOCYTES//THIOESTER CONTAINING PROTEIN TEP//COMPLEMENT LYTIC PATHWAY

Go to start page