Class information for:
Level 1: ATYPICAL HEMOLYTIC UREMIC SYNDROME//FACTOR H//ECULIZUMAB

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
4973 1694 39.1 79%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
350 3       COMPLEMENT//MANNOSE BINDING LECTIN//IMMUNOLOGY 35656
363 2             COMPLEMENT//MANNOSE BINDING LECTIN//PAROXYSMAL NOCTURNAL HEMOGLOBINURIA 17354
4973 1                   ATYPICAL HEMOLYTIC UREMIC SYNDROME//FACTOR H//ECULIZUMAB 1694

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ATYPICAL HEMOLYTIC UREMIC SYNDROME authKW 1771012 7% 81% 121
2 FACTOR H authKW 1412353 9% 54% 146
3 ECULIZUMAB authKW 1132220 8% 48% 130
4 DENSE DEPOSIT DISEASE authKW 909274 3% 86% 59
5 C3 GLOMERULOPATHY authKW 688588 2% 93% 41
6 COMPLEMENT FACTOR H authKW 592816 4% 45% 73
7 FACTOR I authKW 521189 2% 69% 42
8 MEMBRANOPROLIFERATIVE GLOMERULONEPHRITIS authKW 511589 5% 32% 89
9 ATYPICAL HAEMOLYTIC URAEMIC SYNDROME authKW 399294 1% 92% 24
10 C3 GLOMERULONEPHRITIS authKW 393028 2% 84% 26

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Urology & Nephrology 20949 33% 0% 552
2 Immunology 5545 28% 0% 479
3 Pediatrics 1842 12% 0% 206
4 Transplantation 1509 7% 0% 111
5 Hematology 491 6% 0% 101
6 Biochemistry & Molecular Biology 431 17% 0% 294
7 Medicine, General & Internal 118 6% 0% 95
8 Genetics & Heredity 111 5% 0% 82
9 Pathology 95 3% 0% 48
10 Peripheral Vascular Diseases 74 3% 0% 46

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SERV IMMUNOL BIOL 354495 4% 29% 69
2 JR GRP CELLULAR IMMUNOBIOL 236760 1% 77% 17
3 NO MOL GENET SERV 235510 1% 93% 14
4 COMPLEMENT INFLAMMAT 192414 2% 34% 31
5 MOL OTOLARYNGOL RENAL S 162191 1% 43% 21
6 RARE RENAL DIS CLIN 144191 0% 100% 8
7 INFECT BIOL 126776 5% 9% 78
8 GRP BIOMOL MED 112297 1% 69% 9
9 COMPLEMENT DIS TEAM 110394 0% 88% 7
10 MTA ELTE LENDULET COMPLEMENT GRP 104862 0% 73% 8

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PEDIATRIC NEPHROLOGY 46482 7% 2% 125
2 MOLECULAR IMMUNOLOGY 22080 5% 1% 93
3 AMERICAN JOURNAL OF KIDNEY DISEASES 10063 4% 1% 69
4 JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY 6909 3% 1% 53
5 CLINICAL JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY 4687 2% 1% 27
6 CLINICAL NEPHROLOGY 4174 2% 1% 34
7 NATURE REVIEWS NEPHROLOGY 3995 1% 2% 10
8 KIDNEY INTERNATIONAL 3684 3% 0% 55
9 SEMINARS IN THROMBOSIS AND HEMOSTASIS 3266 1% 1% 22
10 NEPHROLOGY DIALYSIS TRANSPLANTATION 2757 3% 0% 44

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 ATYPICAL HEMOLYTIC UREMIC SYNDROME 1771012 7% 81% 121 Search ATYPICAL+HEMOLYTIC+UREMIC+SYNDROME Search ATYPICAL+HEMOLYTIC+UREMIC+SYNDROME
2 FACTOR H 1412353 9% 54% 146 Search FACTOR+H Search FACTOR+H
3 ECULIZUMAB 1132220 8% 48% 130 Search ECULIZUMAB Search ECULIZUMAB
4 DENSE DEPOSIT DISEASE 909274 3% 86% 59 Search DENSE+DEPOSIT+DISEASE Search DENSE+DEPOSIT+DISEASE
5 C3 GLOMERULOPATHY 688588 2% 93% 41 Search C3+GLOMERULOPATHY Search C3+GLOMERULOPATHY
6 COMPLEMENT FACTOR H 592816 4% 45% 73 Search COMPLEMENT+FACTOR+H Search COMPLEMENT+FACTOR+H
7 FACTOR I 521189 2% 69% 42 Search FACTOR+I Search FACTOR+I
8 MEMBRANOPROLIFERATIVE GLOMERULONEPHRITIS 511589 5% 32% 89 Search MEMBRANOPROLIFERATIVE+GLOMERULONEPHRITIS Search MEMBRANOPROLIFERATIVE+GLOMERULONEPHRITIS
9 ATYPICAL HAEMOLYTIC URAEMIC SYNDROME 399294 1% 92% 24 Search ATYPICAL+HAEMOLYTIC+URAEMIC+SYNDROME Search ATYPICAL+HAEMOLYTIC+URAEMIC+SYNDROME
10 C3 GLOMERULONEPHRITIS 393028 2% 84% 26 Search C3+GLOMERULONEPHRITIS Search C3+GLOMERULONEPHRITIS

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 KAVANAGH, D , GOODSHIP, TH , RICHARDS, A , (2013) ATYPICAL HEMOLYTIC UREMIC SYNDROME.SEMINARS IN NEPHROLOGY. VOL. 33. ISSUE 6. P. 508-530 150 85% 47
2 LOIRAT, C , FREMEAUX-BACCHI, V , (2011) ATYPICAL HEMOLYTIC UREMIC SYNDROME.ORPHANET JOURNAL OF RARE DISEASES. VOL. 6. ISSUE . P. - 114 81% 163
3 LOIRAT, C , FAKHOURI, F , ARICETA, G , BESBAS, N , BITZAN, M , BJERRE, A , COPPO, R , EMMA, F , JOHNSON, S , KARPMAN, D , ET AL (2016) AN INTERNATIONAL CONSENSUS APPROACH TO THE MANAGEMENT OF ATYPICAL HEMOLYTIC UREMIC SYNDROME IN CHILDREN.PEDIATRIC NEPHROLOGY. VOL. 31. ISSUE 1. P. 15 -39 76 73% 16
4 RIEDL, M , THORNER, P , LICHT, C , (2017) C3 GLOMERULOPATHY.PEDIATRIC NEPHROLOGY. VOL. 32. ISSUE 1. P. 43 -57 79 78% 1
5 DUREY, MAD , SINHA, A , TOGARSIMALEMATH, SK , BAGGA, A , (2016) ANTI-COMPLEMENT-FACTOR H-ASSOCIATED GLOMERULOPATHIES.NATURE REVIEWS NEPHROLOGY. VOL. 12. ISSUE 9. P. 563 -578 112 92% 0
6 DE VRIESE, AS , SETHI, S , VAN PRAET, J , NATH, KA , FERVENZA, FC , (2015) KIDNEY DISEASE CAUSED BY DYSREGULATION OF THE COMPLEMENT ALTERNATIVE PATHWAY: AN ETIOLOGIC APPROACH.JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY. VOL. 26. ISSUE 12. P. 2917 -2929 101 94% 4
7 DE CORDOBA, SR , HIDALGO, MS , PINTO, S , TORTAJADA, A , (2014) GENETICS OF ATYPICAL HEMOLYTIC UREMIC SYNDROME (AHUS).SEMINARS IN THROMBOSIS AND HEMOSTASIS. VOL. 40. ISSUE 4. P. 422-430 85 98% 23
8 WONG, EKS , GOODSHIP, THJ , KAVANAGH, D , (2013) COMPLEMENT THERAPY IN ATYPICAL HAEMOLYTIC URAEMIC SYNDROME (AHUS).MOLECULAR IMMUNOLOGY. VOL. 56. ISSUE 3. P. 199-212 100 88% 21
9 BARBOUR, TD , PICKERING, MC , COOK, HT , (2013) DENSE DEPOSIT DISEASE AND C3 GLOMERULOPATHY.SEMINARS IN NEPHROLOGY. VOL. 33. ISSUE 6. P. 493-507 95 92% 13
10 NORIS, M , REMUZZI, G , (2009) MEDICAL PROGRESS ATYPICAL HEMOLYTIC-UREMIC SYNDROME.NEW ENGLAND JOURNAL OF MEDICINE. VOL. 361. ISSUE 17. P. 1676-1687 67 78% 380

Classes with closest relation at Level 1



Rank Class id link
1 8410 CD59//CD55//CD46
2 2629 C2 DEFICIENCY//COMPLEMENT GENETICS//COMPLEMENT AND INFLAMMATION
3 23079 RECURRENT GLOMERULONEPHRITIS//RECURRENT IGA NEPHROPATHY//DE NOVO GLOMERULONEPHRITIS
4 30174 T ACTIVATION//ERYTHROCYTE CHARGE//ERYTHROCYTE T ANTIGEN
5 15400 THROMBOTIC MICROANGIOPATHY//SCHISTOCYTES//FRAGMENTED RED CELL
6 1709 THROMBOTIC THROMBOCYTOPENIC PURPURA//ADAMTS13//TTP
7 7487 PROPERDIN//COMPLEMENT DEFICIENCY//C7
8 3467 C5A//C5A RECEPTOR//ANAPHYLATOXIN
9 17790 ACUTE POSTSTREPTOCOCCAL GLOMERULONEPHRITIS//POSTSTREPTOCOCCAL GLOMERULONEPHRITIS//POSTINFECTIOUS GLOMERULONEPHRITIS
10 9804 COMPLEMENT RECEPTOR 1//COMPLEMENT RECEPTOR TYPE 1//CR1

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