Class information for:
Level 1: CREUTZFELDT JAKOB DISEASE//CJD SURVEILLANCE UNIT//PRION DISEASE

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
641 3217 32.5 76%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
11 4 NEUROSCIENCES//CLINICAL NEUROLOGY//NEUROL 1112395
653 3       PRION//PRION PROTEIN//CREUTZFELDT JAKOB DISEASE 11471
876 2             PRION//PRION PROTEIN//CREUTZFELDT JAKOB DISEASE 11471
641 1                   CREUTZFELDT JAKOB DISEASE//CJD SURVEILLANCE UNIT//PRION DISEASE 3217

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CREUTZFELDT JAKOB DISEASE authKW 4554802 22% 66% 723
2 CJD SURVEILLANCE UNIT address 1198251 5% 77% 164
3 PRION DISEASE authKW 860403 9% 31% 292
4 CJD authKW 453566 3% 54% 88
5 VARIANT CREUTZFELDT JAKOB DISEASE authKW 388608 2% 69% 59
6 CREUTZFELDT JAKOB DIS SURVEILLANCE UNIT address 368942 2% 72% 54
7 PRION authKW 357590 9% 13% 300
8 GERSTMANN STRAUSSLER SCHEINKER DISEASE authKW 324928 1% 80% 43
9 SPORADIC CREUTZFELDT JAKOB DISEASE authKW 324928 1% 80% 43
10 FATAL FAMILIAL INSOMNIA authKW 312859 1% 70% 47

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 Clinical Neurology 30609 43% 0% 1369
2 Neurosciences 5724 26% 0% 837
3 Pathology 5233 12% 0% 383
4 Medicine, General & Internal 1179 10% 0% 333
5 Hematology 760 5% 0% 176
6 Neuroimaging 666 2% 0% 62
7 Psychiatry 664 6% 0% 201
8 Virology 501 4% 0% 113
9 Infectious Diseases 409 4% 0% 133
10 Public, Environmental & Occupational Health 159 4% 0% 139

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CJD SURVEILLANCE UNIT 1198251 5% 77% 164
2 CREUTZFELDT JAKOB DIS SURVEILLANCE UNIT 368942 2% 72% 54
3 CJD SCI TECHNOL 179285 1% 82% 23
4 PRION CLIN 160758 1% 71% 24
5 MRC PRION UNIT 156000 2% 34% 49
6 CENT NERVOUS SYST STUDIES 147064 1% 50% 31
7 AUSTRALIAN CREUTZFELDT JAKOB DIS REGISTRY 139756 1% 82% 18
8 CNS STUDIES 125600 0% 88% 15
9 U360 88691 1% 27% 35
10 REFERENCE TSE SURVEILLANCE 72996 0% 77% 10

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PRION 23268 1% 7% 33
2 NEUROLOGY 15137 6% 1% 185
3 NEUROPATHOLOGY 12196 1% 3% 43
4 FOLIA NEUROPATHOLOGICA 11452 1% 4% 32
5 ACTA NEUROPATHOLOGICA 10580 3% 1% 81
6 NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY 7390 1% 2% 38
7 JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY 7222 3% 1% 85
8 ANNALS OF NEUROLOGY 6932 2% 1% 76
9 BRAIN PATHOLOGY 6429 1% 2% 32
10 NEUROEPIDEMIOLOGY 4785 1% 2% 27

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 CREUTZFELDT JAKOB DISEASE 4554802 22% 66% 723 Search CREUTZFELDT+JAKOB+DISEASE Search CREUTZFELDT+JAKOB+DISEASE
2 PRION DISEASE 860403 9% 31% 292 Search PRION+DISEASE Search PRION+DISEASE
3 CJD 453566 3% 54% 88 Search CJD Search CJD
4 VARIANT CREUTZFELDT JAKOB DISEASE 388608 2% 69% 59 Search VARIANT+CREUTZFELDT+JAKOB+DISEASE Search VARIANT+CREUTZFELDT+JAKOB+DISEASE
5 PRION 357590 9% 13% 300 Search PRION Search PRION
6 GERSTMANN STRAUSSLER SCHEINKER DISEASE 324928 1% 80% 43 Search GERSTMANN+STRAUSSLER+SCHEINKER+DISEASE Search GERSTMANN+STRAUSSLER+SCHEINKER+DISEASE
7 SPORADIC CREUTZFELDT JAKOB DISEASE 324928 1% 80% 43 Search SPORADIC+CREUTZFELDT+JAKOB+DISEASE Search SPORADIC+CREUTZFELDT+JAKOB+DISEASE
8 FATAL FAMILIAL INSOMNIA 312859 1% 70% 47 Search FATAL+FAMILIAL+INSOMNIA Search FATAL+FAMILIAL+INSOMNIA
9 PRION PROTEIN 287674 6% 15% 200 Search PRION+PROTEIN Search PRION+PROTEIN
10 VCJD 268725 1% 60% 47 Search VCJD Search VCJD

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 LEUCK, CJ , MCILWAINE, GG , ZEIDLER, M , (2000) CREUTZFELDT-JAKOB DISEASE AND THE EYE. I. BACKGROUND AND PATIENT MANAGEMENT.EYE. VOL. 14. ISSUE . P. 263 -290 297 83% 0
2 MINIKEL, EV , VALLABH, SM , LEK, M , ESTRADA, K , SAMOCHA, KE , SATHIRAPONGSASUTI, JF , MCLEAN, CY , TUNG, JY , YU, LPC , GAMBETTI, P , ET AL (2016) QUANTIFYING PRION DISEASE PENETRANCE USING LARGE POPULATION CONTROL COHORTS.SCIENCE TRANSLATIONAL MEDICINE. VOL. 8. ISSUE 322. P. - 99 66% 19
3 TAKADA, LT , KIM, MO , CLEVELAND, RW , WONG, K , FORNER, SA , GALA, II , FONG, JC , GESCHWIND, MD , (2017) GENETIC PRION DISEASE: EXPERIENCE OF A RAPIDLY PROGRESSIVE DEMENTIA CENTER IN THE UNITED STATES AND A REVIEW OF THE LITERATURE.AMERICAN JOURNAL OF MEDICAL GENETICS PART B-NEUROPSYCHIATRIC GENETICS. VOL. 174. ISSUE 1. P. 36 -69 137 81% 0
4 KOVACS, GG , TRABATTONI, G , HAINFELLNER, JA , IRONSIDE, JW , KNIGHT, RSG , BUDKA, H , (2002) MUTATIONS OF THE PRION PROTEIN GENE - PHENOTYPIC SPECTRUM.JOURNAL OF NEUROLOGY. VOL. 249. ISSUE 11. P. 1567-1582 126 98% 134
5 BROWN, K , MASTRIANNI, JA , (2010) THE PRION DISEASES.JOURNAL OF GERIATRIC PSYCHIATRY AND NEUROLOGY. VOL. 23. ISSUE 4. P. 277-298 137 68% 38
6 LUECK, CJ , MCILWAINE, GG , ZEIDLER, M , (2000) CREUTZFELDT-JAKOB DISEASE AND THE EYE. II. OPHTHALMIC AND NEURO-OPHTHALMIC FEATURES.EYE. VOL. 14. ISSUE . P. 291 -301 132 92% 14
7 CHEN, C , DONG, XP , (2016) EPIDEMIOLOGICAL CHARACTERISTICS OF HUMAN PRION DISEASES.INFECTIOUS DISEASES OF POVERTY. VOL. 5. ISSUE . P. - 73 95% 2
8 MEAD, S , (2006) PRION DISEASE GENETICS.EUROPEAN JOURNAL OF HUMAN GENETICS. VOL. 14. ISSUE 3. P. 273 -281 80 95% 156
9 TAKADA, LT , GESCHWIND, MD , (2013) PRION DISEASES.SEMINARS IN NEUROLOGY. VOL. 33. ISSUE 4. P. 348-356 74 88% 7
10 WADSWORTH, JDF , COLLINGE, J , (2007) UPDATE ON HUMAN PRION DISEASE.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE. VOL. 1772. ISSUE 6. P. 598 -609 96 72% 42

Classes with closest relation at Level 1



Rank Class id link
1 13 PRION PROTEIN//PRION//SCRAPIE
2 35292 301C//ADAPTED SCRAPIE STRAIN//AMYOTROPHICLATERAL SCLEROSIS
3 1746 SCRAPIE//CHRONIC WASTING DISEASE//BSE
4 29429 SPECIFIED RISK MATERIAL//CENTRAL NERVOUS SYSTEM TISSUES//CNS DETECTION
5 25551 HASHIMOTOS ENCEPHALOPATHY//HASHIMOTO ENCEPHALOPATHY//STEROID RESPONSIVE ENCEPHALOPATHY
6 34395 DISPOSABLE PRISMS//TONOMETER TIPS//TONOSAFE
7 5058 CEREBROSPINAL FLUID//PSYCHIAT NEUROCHEM//CLIN MEMORY UNIT
8 14129 NEUROFIBRILLARY TANGLES//SENILE PLAQUES//BETA A4 DEPOSITS
9 31869 FAMILIAL BRITISH DEMENTIA//FAMILIAL DANISH DEMENTIA//BRI2
10 20963 GLUTAMINYL CYCLASE//INTRANEURONAL A BETA//PYROGLUTAMATE

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