Class information for:
Level 1: LIPOID PROTEINOSIS//EXTRACELLULAR MATRIX PROTEIN 1//HYALINOSIS CUTIS ET MUCOSAE

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
27558 226 23.2 62%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
382 3       DUPUYTRENS DISEASE//PRESSURE ULCER//VARICOSE VEINS 31698
3791 2             LIPOID PROTEINOSIS//JUVENILE HYALINE FIBROMATOSIS//HAJDU CHENEY SYNDROME 968
27558 1                   LIPOID PROTEINOSIS//EXTRACELLULAR MATRIX PROTEIN 1//HYALINOSIS CUTIS ET MUCOSAE 226

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 LIPOID PROTEINOSIS authKW 7838762 26% 98% 59
2 EXTRACELLULAR MATRIX PROTEIN 1 authKW 2084584 8% 86% 18
3 HYALINOSIS CUTIS ET MUCOSAE authKW 2034630 7% 94% 16
4 URBACH WIETHE DISEASE authKW 2001653 9% 74% 20
5 ECM1 authKW 972799 5% 60% 12
6 ECM1 GENE authKW 675561 2% 100% 5
7 MONILIFORM BLEPHAROSIS authKW 540449 2% 100% 4
8 URBACH WIETHE SYNDROME authKW 540449 2% 100% 4
9 EXTRACELLULAR MATRIX PROTEIN 1 ECM1 authKW 405337 1% 100% 3
10 EXTRACELLULAR MATRIX PROTEIN 1 GENE authKW 270225 1% 100% 2

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 6797 42% 0% 94
2 Otorhinolaryngology 330 8% 0% 19
3 Pathology 118 7% 0% 16
4 Pediatrics 83 8% 0% 17
5 Ophthalmology 69 5% 0% 12
6 Neuroimaging 63 2% 0% 5
7 Clinical Neurology 57 8% 0% 19
8 Dentistry, Oral Surgery & Medicine 43 4% 0% 9
9 Genetics & Heredity 8 4% 0% 9
10 Oncology 8 5% 0% 12

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CHILDRENS HOSP SHANXI PROVINCE 135112 0% 100% 1
2 DERMATOLCHILDRENS HOSPCHONGQING INT SCI 135112 0% 100% 1
3 EYE EAR NOSE THORAT HOSP 135112 0% 100% 1
4 GENET SKI DIS GRP 135112 0% 100% 1
5 GENET SKIN CANC 135112 0% 100% 1
6 GENET SKIN DIS GRP SKIN SCI 135112 0% 100% 1
7 HAZART RASOUL AKRAM HOSP 135112 0% 100% 1
8 HELM HOLTZ 135112 0% 100% 1
9 HNO KLIN BONN 135112 0% 100% 1
10 HOSP CRUZ AZUL 135112 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 INTERNATIONAL JOURNAL OF DERMATOLOGY 2661 5% 0% 12
2 HAUTARZT 1800 4% 0% 8
3 PEDIATRIC DERMATOLOGY 1785 3% 0% 7
4 CLINICAL AND EXPERIMENTAL DERMATOLOGY 1736 4% 0% 8
5 BRITISH JOURNAL OF DERMATOLOGY 982 4% 0% 9
6 JOURNAL OF DERMATOLOGY 946 2% 0% 4
7 MATRIX BIOLOGY 900 1% 0% 3
8 ANNALES DE DERMATOLOGIE ET DE VENEREOLOGIE 847 3% 0% 6
9 EXPERIMENTAL DERMATOLOGY 821 2% 0% 4
10 EUROPEAN JOURNAL OF DERMATOLOGY 810 2% 0% 4

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 LIPOID PROTEINOSIS 7838762 26% 98% 59 Search LIPOID+PROTEINOSIS Search LIPOID+PROTEINOSIS
2 EXTRACELLULAR MATRIX PROTEIN 1 2084584 8% 86% 18 Search EXTRACELLULAR+MATRIX+PROTEIN+1 Search EXTRACELLULAR+MATRIX+PROTEIN+1
3 HYALINOSIS CUTIS ET MUCOSAE 2034630 7% 94% 16 Search HYALINOSIS+CUTIS+ET+MUCOSAE Search HYALINOSIS+CUTIS+ET+MUCOSAE
4 URBACH WIETHE DISEASE 2001653 9% 74% 20 Search URBACH+WIETHE+DISEASE Search URBACH+WIETHE+DISEASE
5 ECM1 972799 5% 60% 12 Search ECM1 Search ECM1
6 ECM1 GENE 675561 2% 100% 5 Search ECM1+GENE Search ECM1+GENE
7 MONILIFORM BLEPHAROSIS 540449 2% 100% 4 Search MONILIFORM+BLEPHAROSIS Search MONILIFORM+BLEPHAROSIS
8 URBACH WIETHE SYNDROME 540449 2% 100% 4 Search URBACH+WIETHE+SYNDROME Search URBACH+WIETHE+SYNDROME
9 EXTRACELLULAR MATRIX PROTEIN 1 ECM1 405337 1% 100% 3 Search EXTRACELLULAR+MATRIX+PROTEIN+1+ECM1 Search EXTRACELLULAR+MATRIX+PROTEIN+1+ECM1
10 EXTRACELLULAR MATRIX PROTEIN 1 GENE 270225 1% 100% 2 Search EXTRACELLULAR+MATRIX+PROTEIN+1+GENE Search EXTRACELLULAR+MATRIX+PROTEIN+1+GENE

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 CHAN, I , LIU, L , HAMADA, T , SETHURAMAN, G , MCGRATH, JA , (2007) THE MOLECULAR BASIS OF LIPOID PROTEINOSIS: MUTATIONS IN EXTRACELLULAR MATRIX PROTEIN 1.EXPERIMENTAL DERMATOLOGY. VOL. 16. ISSUE 11. P. 881-890 40 69% 52
2 LI, Y , LI, YQ , ZHAO, JL , WANG, DY , MAO, QW , XIA, HB , (2016) PRODUCTION AND CHARACTERIZATION OF DOMAIN-SPECIFIC MONOCLONAL ANTIBODIES AGAINST HUMAN ECM1.PROTEIN EXPRESSION AND PURIFICATION. VOL. 121. ISSUE . P. 103 -111 28 88% 0
3 HAMADA, T , (2002) LIPOID PROTEINOSIS.CLINICAL AND EXPERIMENTAL DERMATOLOGY. VOL. 27. ISSUE 8. P. 624-629 23 96% 59
4 BAYKAL, C , TOPKARCI, Z , YAZGANOGLU, D , AZIZLERLI, G , BAYKAN, B , (2007) LIPOID PROTEINOSIS: A CASE SERIES FROM ISTANBUL.INTERNATIONAL JOURNAL OF DERMATOLOGY. VOL. 46. ISSUE 10. P. 1011-1016 20 100% 12
5 STEPHAN, F , MOUTRAN, R , MAATOUK, I , SLEILATY, F , ABADJIAN, G , HADDAD, A , (2013) HYALINOSIS CUTIS ET MUCOSAE MANIFESTS IN DIFFERENT FEATURES IN TWO SISTERS.INTERNATIONAL JOURNAL OF DERMATOLOGY. VOL. 52. ISSUE 7. P. 843-845 17 100% 0
6 DERTLIOGLU, SB , CALIK, M , CICEK, D , (2014) DEMOGRAPHIC, CLINICAL, AND RADIOLOGIC SIGNS AND TREATMENT RESPONSES OF LIPOID PROTEINOSIS PATIENTS: A 10-CASE SERIES FROM SANLIURFA.INTERNATIONAL JOURNAL OF DERMATOLOGY. VOL. 53. ISSUE 4. P. 516-523 16 100% 1
7 KOWALEWSKI, C , KOZLOWSKA, A , CHAN, I , GORSKA, M , WOZNIAK, K , JABLONSKA, S , MCGRATH, JA , (2005) THREE-DIMENSIONAL IMAGING REVEALS MAJOR CHANGES IN SKIN MICROVASCULATURE IN LIPOID PROTEINOSIS AND LICHEN SCLEROSUS.JOURNAL OF DERMATOLOGICAL SCIENCE. VOL. 38. ISSUE 3. P. 215-224 22 79% 13
8 XU, XT , CHEN, QP , LEE, JSS , (2014) LIPOID PROTEINOSIS IN A CHINESE PATIENT.AMERICAN JOURNAL OF DERMATOPATHOLOGY. VOL. 36. ISSUE 6. P. E108-E113 18 72% 1
9 STAVRIANEAS, N , KARPOUZIS, A , VAMVASSAKIS, E , PATROU, A , KOUMANTAKIMATHIOUDAKI, E , PAPADOPOULOS, O , (1997) HYALINOSIS CUTIS AND MUCOSAE: REPORT OF THREE CASES..ANNALES DE DERMATOLOGIE ET DE VENEREOLOGIE. VOL. 124. ISSUE 2. P. 171-175 22 96% 2
10 SALIH, MA , ABU-AMERO, KK , ALRASHEED, S , ALORAINY, IA , LIU, L , MCGRATH, JA , VAN MALDERGEM, L , AL-FAKEY, YH , ALSUHAIBANI, AH , OYSTRECK, DT , ET AL (2011) MOLECULAR AND NEUROLOGICAL CHARACTERIZATIONS OF THREE SAUDI FAMILIES WITH LIPOID PROTEINOSIS.BMC MEDICAL GENETICS. VOL. 12. ISSUE . P. - 16 84% 4

Classes with closest relation at Level 1



Rank Class id link
1 27465 JUVENILE HYALINE FIBROMATOSIS//INFANTILE SYSTEMIC HYALINOSIS//HYALINE FIBROMATOSIS SYNDROME
2 19602 CUTANEOUS AMYLOIDOSIS//LICHEN AMYLOIDOSIS//MACULAR AMYLOIDOSIS
3 36814 ALPHA KETOGLUTARIC ACID DEHYDROGENASE//ALPHA KETOGLUTARIC ACIDURIA//CHOROID PLEXUS CALCIFICATIONS
4 11852 LICHEN SCLEROSUS//LICHEN SCLEROSUS ET ATROPHICUS//VULVAR LICHEN SCLEROSUS
5 24500 LIGNEOUS CONJUNCTIVITIS//PLASMINOGEN DEFICIENCY//HYPOPLASMINOGENEMIA
6 37522 DIFFERENTIAL GENE EXPRESSION DETECTION//CANC GENOME DISCOVERY CCGD//CANCER GENE ACTIVATION HETEROGENEITY
7 20445 PERLECAN//SCHWARTZ JAMPEL SYNDROME//STUVE WIEDEMANN SYNDROME
8 37128 C MANNOSYLATION//MESIR PASTE//ACONOGONON MOLLE
9 16395 CUTIS LAXA//FIBULIN 1//FIBULIN 5
10 30234 MEGALOCORNEA//NEUHAUSER SYNDROME//ANTERIOR MEGALOPHTHALMOS

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