Class information for:
Level 1: CUTIS LAXA//FIBULIN 1//FIBULIN 5

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
16395 656 31.7 79%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
12 4 POLYMER SCIENCE//MATERIALS SCIENCE, PAPER & WOOD//CHEMISTRY, PHYSICAL 1084170
195 3       MATERIALS SCIENCE, BIOMATERIALS//HYDROXYAPATITE//TISSUE ENGINEERING 53996
2693 2             ELASTIN//ELASTIN LIKE POLYPEPTIDE//TROPOELASTIN 3356
16395 1                   CUTIS LAXA//FIBULIN 1//FIBULIN 5 656

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CUTIS LAXA authKW 1370957 8% 55% 54
2 FIBULIN 1 authKW 1021737 5% 73% 30
3 FIBULIN 5 authKW 851004 5% 52% 35
4 FIBULIN 4 authKW 754050 3% 90% 18
5 EFEMP1 authKW 707993 3% 89% 17
6 FIBULIN authKW 558534 4% 50% 24
7 ARTERIAL TORTUOSITY SYNDROME authKW 478761 2% 86% 12
8 FIBULIN 3 authKW 380118 2% 58% 14
9 AUTOSOMAL RECESSIVE CUTIS LAXA authKW 325826 1% 100% 7
10 DE BARSY SYNDROME authKW 325826 1% 100% 7

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 2633 16% 0% 102
2 Genetics & Heredity 1621 21% 0% 141
3 Cell Biology 510 16% 0% 104
4 Ophthalmology 289 6% 0% 41
5 Biochemistry & Molecular Biology 270 21% 0% 135
6 Oncology 252 12% 0% 79
7 Pediatrics 163 6% 0% 42
8 Developmental Biology 91 3% 0% 18
9 Cardiac & Cardiovascular System 64 5% 0% 34
10 Medicine, Research & Experimental 49 4% 0% 29

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PROGRAM CELL STRUCT DEV 186186 1% 100% 4
2 GEN ONCOL B BREAST UNIT 93093 0% 100% 2
3 FG DEV DIS 72847 1% 26% 6
4 IMMUNO MICROENVIRONM DISEDUC MINIST 62061 0% 67% 2
5 SECT CLIN GENET DYSMORPHOL 59842 0% 43% 3
6 IN IDUALIZED MED ARTERIAL DIS 55405 1% 24% 5
7 ANESTHESIOL REHABIL 46547 0% 100% 1
8 CATALA CIENCIES CARDIOVASC INVEST BIOME 46547 0% 100% 1
9 CELL GENET DEV BIOL CGDB 46547 0% 100% 1
10 CELLULAR NEUROSCI CORE 46547 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 AMERICAN JOURNAL OF MEDICAL GENETICS PART A 4240 4% 0% 23
2 MATRIX BIOLOGY 4175 2% 1% 11
3 PEDIATRIC DERMATOLOGY 1797 2% 0% 12
4 CLINICAL DYSMORPHOLOGY 1492 1% 1% 6
5 JOURNAL OF INVESTIGATIVE DERMATOLOGY 1252 3% 0% 17
6 CLINICAL GENETICS 1089 2% 0% 11
7 EUROPEAN JOURNAL OF HUMAN GENETICS 803 1% 0% 8
8 ANNALES DE DERMATOLOGIE ET DE VENEREOLOGIE 802 2% 0% 10
9 AMERICAN JOURNAL OF MEDICAL GENETICS 746 2% 0% 12
10 HUMAN MOLECULAR GENETICS 668 2% 0% 12

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 CUTIS LAXA 1370957 8% 55% 54 Search CUTIS+LAXA Search CUTIS+LAXA
2 FIBULIN 1 1021737 5% 73% 30 Search FIBULIN+1 Search FIBULIN+1
3 FIBULIN 5 851004 5% 52% 35 Search FIBULIN+5 Search FIBULIN+5
4 FIBULIN 4 754050 3% 90% 18 Search FIBULIN+4 Search FIBULIN+4
5 EFEMP1 707993 3% 89% 17 Search EFEMP1 Search EFEMP1
6 FIBULIN 558534 4% 50% 24 Search FIBULIN Search FIBULIN
7 ARTERIAL TORTUOSITY SYNDROME 478761 2% 86% 12 Search ARTERIAL+TORTUOSITY+SYNDROME Search ARTERIAL+TORTUOSITY+SYNDROME
8 FIBULIN 3 380118 2% 58% 14 Search FIBULIN+3 Search FIBULIN+3
9 AUTOSOMAL RECESSIVE CUTIS LAXA 325826 1% 100% 7 Search AUTOSOMAL+RECESSIVE+CUTIS+LAXA Search AUTOSOMAL+RECESSIVE+CUTIS+LAXA
10 DE BARSY SYNDROME 325826 1% 100% 7 Search DE+BARSY+SYNDROME Search DE+BARSY+SYNDROME

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 DE VEGA, S , IWAMOTO, T , YAMADA, Y , (2009) FIBULINS: MULTIPLE ROLES IN MATRIX STRUCTURES AND TISSUE FUNCTIONS.CELLULAR AND MOLECULAR LIFE SCIENCES. VOL. 66. ISSUE 11-12. P. 1890 -1902 72 71% 101
2 TIMPL, R , SASAKI, T , KOSTKA, G , CHU, ML , (2003) FIBULINS: A VERSATILE FAMILY OF EXTRACELLULAR MATRIX PROTEINS.NATURE REVIEWS MOLECULAR CELL BIOLOGY. VOL. 4. ISSUE 6. P. 479-489 61 70% 225
3 CANGEMI, C , HANSEN, ML , ARGRAVES, WS , RASMUSSEN, LM , (2014) FIBULINS AND THEIR ROLE IN CARDIOVASCULAR BIOLOGY AND DISEASE.ADVANCES IN CLINICAL CHEMISTRY, VOL 67. VOL. 67. ISSUE . P. 245 -265 57 71% 3
4 BERK, DR , BENTLEY, DD , BAYLISS, SJ , LIND, A , URBAN, Z , (2012) CUTIS LAXA: A REVIEW.JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY. VOL. 66. ISSUE 5. P. - 69 60% 0
5 OBAYA, AJ , RUA, S , MONCADA-PAZOS, A , CAL, S , (2012) THE DUAL ROLE OF FIBULINS IN TUMORIGENESIS.CANCER LETTERS. VOL. 325. ISSUE 2. P. 132-138 56 68% 15
6 FISCHER-ZIRNSAK, B , ESCANDE-BEILLARD, N , GANESH, J , TAN, YX , AL BUGHAILI, M , LIN, AE , SAHAI, I , BAHENA, P , REICHERT, SL , LOH, A , ET AL (2015) RECURRENT DE NOVO MUTATIONS AFFECTING RESIDUE ARG1 38 OF PYRROLINE-5-CARBOXYLATE SYNTHASE CAUSE A PROGEROID FORM OF AUTOSOMAL-DOMINANT CUTIS LAXA.AMERICAN JOURNAL OF HUMAN GENETICS. VOL. 97. ISSUE 3. P. 483 -492 32 82% 4
7 URBAN, Z , DAVIS, EC , (2014) CUTIS LAXA: INTERSECTION OF ELASTIC FIBER BIOGENESIS, TGF BETA SIGNALING, THE SECRETORY PATHWAY AND METABOLISM.MATRIX BIOLOGY. VOL. 33. ISSUE . P. 16-22 48 54% 11
8 GALLAGHER, WM , CURRID, CA , WHELAN, LC , (2005) FIBULINS AND CANCER: FRIEND OR FOE?.TRENDS IN MOLECULAR MEDICINE. VOL. 11. ISSUE 7. P. 336-340 32 91% 86
9 PAPKE, CL , YANAGISAWA, H , (2014) FIBULIN-4 AND FIBULIN-5 IN ELASTOGENESIS AND BEYOND: INSIGHTS FROM MOUSE AND HUMAN STUDIES.MATRIX BIOLOGY. VOL. 37. ISSUE . P. 142 -149 43 51% 20
10 YANAGISAWA, H , DAVIS, EC , (2010) UNRAVELING THE MECHANISM OF ELASTIC FIBER ASSEMBLY: THE ROLES OF SHORT FIBULINS.INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY. VOL. 42. ISSUE 7. P. 1084-1093 49 50% 40

Classes with closest relation at Level 1



Rank Class id link
1 22334 ANETODERMA//MID DERMAL ELASTOLYSIS//ELASTOPHAGOCYTOSIS
2 2309 MARFAN SYNDROME//FIBRILLIN//FBN1
3 7939 DESMOSINE//RECH OPHTALMOL//ELASTIN PEPTIDES
4 19200 LTBP//ALPHA V BETA 6//INTEGRIN ALPHA V BETA 6
5 16539 LYSYL OXIDASE//LOXL2//LYSYL OXIDASE LIKE 2
6 15993 CONGENITAL DISORDERS OF GLYCOSYLATION//CDG//CARBOHYDRATE DEFICIENT GLYCOPROTEIN SYNDROME
7 26133 FLOPPY EYELID SYNDROME//ASCHER SYNDROME//BLEPHAROCHALASIS
8 7639 EHLERS DANLOS SYNDROME//JOINT HYPERMOBILITY//HYPERMOBILITY
9 27558 LIPOID PROTEINOSIS//EXTRACELLULAR MATRIX PROTEIN 1//HYALINOSIS CUTIS ET MUCOSAE
10 18488 BEST DISEASE//BEST VITELLIFORM MACULAR DYSTROPHY//BEST1

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