Class information for:
Level 1: PAPILLON LEFEVRE SYNDROME//CATHEPSIN C//HAIM MUNK SYNDROME

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
24803 301 29.7 65%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
427 3       JOURNAL OF THE INSTITUTE OF BREWING//KERATINASE//CYSTATIN 27946
1744 2             CATHEPSIN//CATHEPSIN K//CATHEPSIN B 6503
24803 1                   PAPILLON LEFEVRE SYNDROME//CATHEPSIN C//HAIM MUNK SYNDROME 301

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PAPILLON LEFEVRE SYNDROME authKW 8437841 29% 96% 87
2 CATHEPSIN C authKW 3607479 18% 66% 54
3 HAIM MUNK SYNDROME authKW 608676 2% 100% 6
4 DIPEPTIDYL PEPTIDASE I authKW 608664 4% 50% 12
5 CATHEPSIN C MUTATION authKW 507230 2% 100% 5
6 CATHEPSIN C GENE authKW 304338 1% 100% 3
7 ORAL DIAG PERIODONTOL address 304338 1% 100% 3
8 PAPILLON LEFEVRE authKW 304338 1% 100% 3
9 PRE PUBERTAL PERIODONTITIS authKW 304338 1% 100% 3
10 PALMAR PLANTAR HYPERKERATOSIS authKW 228252 1% 75% 3

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dentistry, Oral Surgery & Medicine 4090 29% 0% 88
2 Dermatology 1563 18% 0% 53
3 Pediatrics 103 7% 0% 22
4 Biochemistry & Molecular Biology 89 18% 0% 55
5 Genetics & Heredity 54 7% 0% 21
6 Chemistry, Medicinal 36 4% 0% 12
7 Immunology 26 6% 0% 19
8 Biophysics 19 4% 0% 12
9 Medicine, Research & Experimental 13 4% 0% 11
10 Rheumatology 4 1% 0% 3

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ORAL DIAG PERIODONTOL 304338 1% 100% 3
2 BAHRAMI CHILDRENS MED HOSP 101446 0% 100% 1
3 BELFAST CITY HOSP TOWER 101446 0% 100% 1
4 BONE JOINT CONNECT TISSUE DIS BJCRC 101446 0% 100% 1
5 EISU AQUACULTURE 101446 0% 100% 1
6 EXPT VASC PATHOL CARDIOVASC MAASTRICHT 101446 0% 100% 1
7 HLTH BIOSCI NUTR PHYSIOL 101446 0% 100% 1
8 IMMUNOPHARMACOL GRPSOUTHAMPTON GEN HOSP 101446 0% 100% 1
9 INFECT IMMUNITY REPAIR 101446 0% 100% 1
10 INRA VAL DE LOIRE 101446 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF CLINICAL PERIODONTOLOGY 17919 10% 1% 29
2 JOURNAL OF PERIODONTOLOGY 9748 8% 0% 25
3 INTERNATIONAL JOURNAL OF DERMATOLOGY 1672 4% 0% 11
4 JOURNAL OF DENTISTRY FOR CHILDREN 1197 1% 0% 4
5 PERIODONTOLOGY 2000 1138 1% 0% 3
6 DERMATOLOGICA 1029 1% 0% 4
7 DEUTSCHE ZAHNARZTLICHE ZEITSCHRIFT 841 1% 0% 3
8 REVISTA ESPANOLA DE FISIOLOGIA 452 1% 0% 2
9 PEDIATRIC DERMATOLOGY 433 1% 0% 4
10 JOURNAL OF MEDICAL GENETICS 430 2% 0% 5

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 PAPILLON LEFEVRE SYNDROME 8437841 29% 96% 87 Search PAPILLON+LEFEVRE+SYNDROME Search PAPILLON+LEFEVRE+SYNDROME
2 CATHEPSIN C 3607479 18% 66% 54 Search CATHEPSIN+C Search CATHEPSIN+C
3 HAIM MUNK SYNDROME 608676 2% 100% 6 Search HAIM+MUNK+SYNDROME Search HAIM+MUNK+SYNDROME
4 DIPEPTIDYL PEPTIDASE I 608664 4% 50% 12 Search DIPEPTIDYL+PEPTIDASE+I Search DIPEPTIDYL+PEPTIDASE+I
5 CATHEPSIN C MUTATION 507230 2% 100% 5 Search CATHEPSIN+C+MUTATION Search CATHEPSIN+C+MUTATION
6 CATHEPSIN C GENE 304338 1% 100% 3 Search CATHEPSIN+C+GENE Search CATHEPSIN+C+GENE
7 PAPILLON LEFEVRE 304338 1% 100% 3 Search PAPILLON+LEFEVRE Search PAPILLON+LEFEVRE
8 PRE PUBERTAL PERIODONTITIS 304338 1% 100% 3 Search PRE+PUBERTAL+PERIODONTITIS Search PRE+PUBERTAL+PERIODONTITIS
9 PALMAR PLANTAR HYPERKERATOSIS 228252 1% 75% 3 Search PALMAR+PLANTAR+HYPERKERATOSIS Search PALMAR+PLANTAR+HYPERKERATOSIS
10 CATHEPSIN C GENE MUTATION 202892 1% 100% 2 Search CATHEPSIN+C+GENE+MUTATION Search CATHEPSIN+C+GENE+MUTATION

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 LUNDGREN, T , RENVERT, S , (2004) PERIODONTAL TREATMENT OF PATIENTS WITH PAPILLON-LEFEVRE SYNDROME: A 3-YEAR FOLLOW-UP.JOURNAL OF CLINICAL PERIODONTOLOGY. VOL. 31. ISSUE 11. P. 933-938 46 98% 12
2 HATTAB, FN , AMIN, WM , (2005) PAPILLON-LEFEVRE SYNDROME WITH ALBINISM: A REVIEW OF THE LITERATURE AND REPORT OF 2 BROTHERS.ORAL SURGERY ORAL MEDICINE ORAL PATHOLOGY ORAL RADIOLOGY AND ENDODONTOLOGY. VOL. 100. ISSUE 6. P. 709-716 43 96% 3
3 HAMON, Y , LEGOWSKA, M , FERGELOT, P , DALLET-CHOISY, S , NEWELL, L , VANDERLYNDEN, L , VALESHABAD, AK , ACRICH, K , KORD, H , CHARALAMPOS, T , ET AL (2016) ANALYSIS OF URINARY CATHEPSIN C FOR DIAGNOSING PAPILLON-LEFEVRE SYNDROME.FEBS JOURNAL. VOL. 283. ISSUE 3. P. 498 -509 34 89% 0
4 SADIK, CD , NOACK, B , SCHACHER, B , PFEILSCHIFTER, J , MUHL, H , EICKHOLZ, P , (2012) CYTOKINE PRODUCTION BY LEUKOCYTES OF PAPILLON-LEFEVRE SYNDROME PATIENTS IN WHOLE BLOOD CULTURES.CLINICAL ORAL INVESTIGATIONS. VOL. 16. ISSUE 2. P. 591-597 34 87% 1
5 NOACK, B , GORGENS, H , SCHACHER, B , PUKLO, M , EICKHOLZ, P , HOFFMANN, T , SCHACKERT, HK , (2008) FUNCTIONAL CATHEPSIN C MUTATIONS CAUSE DIFFERENT PAPILLON-LEFEVRE SYNDROME PHENOTYPES.JOURNAL OF CLINICAL PERIODONTOLOGY. VOL. 35. ISSUE 4. P. 311 -316 29 100% 11
6 NICKLES, K , SCHACHER, B , RATKA-KRUGER, P , KREBS, M , EICKHOLZ, P , (2013) LONG-TERM RESULTS AFTER TREATMENT OF PERIODONTITIS IN PATIENTS WITH PAPILLON-LEFEVRE SYNDROME: SUCCESS AND FAILURE.JOURNAL OF CLINICAL PERIODONTOLOGY. VOL. 40. ISSUE 8. P. 789-798 28 85% 2
7 ULLBRO, C , BROWN, A , TWETMAN, S , (2005) PREVENTIVE PERIODONTAL REGIMEN IN PAPILLON-LEFEVRE SYNDROME.PEDIATRIC DENTISTRY. VOL. 27. ISSUE 3. P. 226-232 30 91% 11
8 SCHACHER, B , BARON, F , LUDWIG, B , VALESKY, E , NOACK, B , EICKHOLZ, P , (2006) PERIODONTAL THERAPY IN SIBLINGS WITH PAPILLON-LEFEVRE SYNDROME AND TINEA CAPITIS: A REPORT OF TWO CASES.JOURNAL OF CLINICAL PERIODONTOLOGY. VOL. 33. ISSUE 11. P. 829-836 29 85% 14
9 KOSEM, R , DEBELJAK, M , LAMPRET, BR , KANSKY, A , BATTELINO, T , PODKRAJSEK, KT , (2012) CATHEPSIN C GENE 5 '-UNTRANSLATED REGION MUTATION IN PAPILLON-LEFEVRE SYNDROME.DERMATOLOGY. VOL. 225. ISSUE 3. P. 193-203 26 81% 1
10 CAGLI, NA , HAKKI, SS , DURSUN, R , TOY, H , GOKALP, A , RYU, OH , HART, PS , HART, TC , (2005) CLINICAL, GENETIC, AND BIOCHEMICAL FINDINGS IN TWO SIBLINGS WITH PAPILLON-LEFEVRE SYNDROME.JOURNAL OF PERIODONTOLOGY. VOL. 76. ISSUE 12. P. 2322-2329 24 92% 9

Classes with closest relation at Level 1



Rank Class id link
1 14769 KID SYNDROME//MAL DE MELEDA//PALMOPLANTAR KERATODERMA
2 752 CATHEPSIN B//CYSTATIN//CATHEPSIN L
3 5979 PERIODONTITIS//AGGRESSIVE PERIODONTITIS//JOURNAL OF PERIODONTAL RESEARCH
4 23573 CAP37//CATIONIC ANTIMICROBIAL PROTEIN//AZUROPHIL GRANULE
5 28105 EPSTEIN BARR VIRUS TYPE 1 AND TYPE 2//CLIN ORAL SURG IMPLANTOL//GINGIVAL BIOPSIES
6 3875 GRANZYME//GRANZYME B//PERFORIN
7 11865 CATHEPSIN K//PYCNODYSOSTOSIS//CATHEPSIN K INHIBITOR
8 2733 ACTINOBACILLUS ACTINOMYCETEMCOMITANS//AGGREGATIBACTER ACTINOMYCETEMCOMITANS//ORAL MICROBIOLOGY AND IMMUNOLOGY
9 19379 SALIVARY CLIN//PERIODONTOL GRP//SALIVA
10 36029 MCKITTRICK WHEELOCK SYNDROME//ABNORMAL DEFECATION//COLONIC WATER TRANSPORT

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