Class information for:
Level 1: WISKOTT ALDRICH SYNDROME//X LINKED THROMBOCYTOPENIA//WISKOTT ALDRICH SYNDROME PROTEIN

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
11252 996 41.3 87%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
458 3       DICTYOSTELIUM//DICTYOSTELIUM DISCOIDEUM//ACTIN 24720
405 2             WISKOTT ALDRICH SYNDROME//ACTIN//CELL MECHANICS 16651
11252 1                   WISKOTT ALDRICH SYNDROME//X LINKED THROMBOCYTOPENIA//WISKOTT ALDRICH SYNDROME PROTEIN 996

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 WISKOTT ALDRICH SYNDROME authKW 5010172 21% 77% 212
2 X LINKED THROMBOCYTOPENIA authKW 801152 3% 93% 28
3 WISKOTT ALDRICH SYNDROME PROTEIN authKW 566530 3% 60% 31
4 WASP authKW 501459 8% 20% 81
5 WIP authKW 399149 3% 52% 25
6 WAVE3 authKW 278693 1% 91% 10
7 N WASP authKW 265254 3% 29% 30
8 WAS GENE authKW 245252 1% 100% 8
9 ARP2 3 COMPLEX authKW 193805 3% 22% 29
10 DISORDERS IMMUN SECT address 178639 1% 45% 13

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 4303 20% 0% 204
2 Cell Biology 2197 25% 0% 250
3 Immunology 1355 19% 0% 189
4 Biochemistry & Molecular Biology 631 24% 0% 241
5 Pediatrics 388 8% 0% 77
6 Allergy 312 3% 0% 28
7 Genetics & Heredity 273 8% 0% 82
8 Medicine, Research & Experimental 250 7% 0% 70
9 Oncology 186 9% 0% 91
10 Biophysics 82 4% 0% 44

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 DISORDERS IMMUN SECT 178639 1% 45% 13
2 MOL IMMUNOL UNIT 108392 5% 8% 46
3 MIANATO KU 61313 0% 100% 2
4 SHAHID ABBAS ABDOLLAHI 61313 0% 100% 2
5 IMMUNOPHYSIOL SECT 54496 0% 44% 4
6 IMMUNODEFICIENCY 42098 1% 11% 13
7 IMMUNOREGULAT GRP 40874 0% 67% 2
8 LEUKAEMIA FUND CHILDHOOD LEUKAEMIA 40874 0% 67% 2
9 IMMUNOL INFECT DIS RHEUMATOL 40870 0% 33% 4
10 PROGRAMA GENS MALALTIA 40870 0% 33% 4

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BLOOD 6685 9% 0% 87
2 BRITISH JOURNAL OF HAEMATOLOGY 970 2% 0% 21
3 JOURNAL OF CELL SCIENCE 908 2% 0% 20
4 CURRENT BIOLOGY 859 2% 0% 16
5 PEDIATRIC BLOOD & CANCER 802 1% 0% 11
6 CELL MOTILITY AND THE CYTOSKELETON 700 1% 0% 7
7 BLOOD CELLS MOLECULES AND DISEASES 611 1% 0% 6
8 JOURNAL OF CLINICAL IMMUNOLOGY 584 1% 0% 7
9 JOURNAL OF CELL BIOLOGY 528 2% 0% 17
10 INTERNATIONAL JOURNAL OF HEMATOLOGY 506 1% 0% 8

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 WISKOTT ALDRICH SYNDROME 5010172 21% 77% 212 Search WISKOTT+ALDRICH+SYNDROME Search WISKOTT+ALDRICH+SYNDROME
2 X LINKED THROMBOCYTOPENIA 801152 3% 93% 28 Search X+LINKED+THROMBOCYTOPENIA Search X+LINKED+THROMBOCYTOPENIA
3 WISKOTT ALDRICH SYNDROME PROTEIN 566530 3% 60% 31 Search WISKOTT+ALDRICH+SYNDROME+PROTEIN Search WISKOTT+ALDRICH+SYNDROME+PROTEIN
4 WASP 501459 8% 20% 81 Search WASP Search WASP
5 WIP 399149 3% 52% 25 Search WIP Search WIP
6 WAVE3 278693 1% 91% 10 Search WAVE3 Search WAVE3
7 N WASP 265254 3% 29% 30 Search N+WASP Search N+WASP
8 WAS GENE 245252 1% 100% 8 Search WAS+GENE Search WAS+GENE
9 ARP2 3 COMPLEX 193805 3% 22% 29 Search ARP2+3+COMPLEX Search ARP2+3+COMPLEX
10 WAVE2 157648 1% 43% 12 Search WAVE2 Search WAVE2

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 MASSAAD, MJ , RAMESH, N , GEHA, RS , (2013) WISKOTT-ALDRICH SYNDROME: A COMPREHENSIVE REVIEW.YEAR IN IMMUNOLOGY. VOL. 1285. ISSUE . P. 26-43 163 82% 56
2 BLUNDELL, MP , WORTH, A , BOUMA, G , THRASHER, AJ , (2010) THE WISKOTT-ALDRICH SYNDROME: THE ACTIN CYTOSKELETON AND IMMUNE CELL FUNCTION.DISEASE MARKERS. VOL. 29. ISSUE 3-4. P. 157 -175 167 80% 20
3 THRASHER, AJ , BURNS, SO , (2010) WASP: A KEY IMMUNOLOGICAL MULTITASKER.NATURE REVIEWS IMMUNOLOGY. VOL. 10. ISSUE 3. P. 182 -192 86 90% 142
4 WORTH, AJJ , THRASHER, AJ , (2015) CURRENT AND EMERGING TREATMENT OPTIONS FOR WISKOTT-ALDRICH SYNDROME.EXPERT REVIEW OF CLINICAL IMMUNOLOGY. VOL. 11. ISSUE 9. P. 1015 -1032 100 81% 3
5 OCHS, HD , THRASHER, AJ , (2006) THE WISKOTT-ALDRICH SYNDROME.JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY. VOL. 117. ISSUE 4. P. 725 -738 99 80% 169
6 BOSTICARDO, M , MARANGONI, F , AIUTI, A , VILLA, A , RONCAROLO, MG , (2009) RECENT ADVANCES IN UNDERSTANDING THE PATHOPHYSIOLOGY OF WISKOTT-ALDRICH SYNDROME.BLOOD. VOL. 113. ISSUE 25. P. 6288-6295 78 79% 98
7 BOUMA, G , BURNS, SO , THRASHER, AJ , (2009) WISKOTT-ALDRICH SYNDROME: IMMUNODEFICIENCY RESULTING FROM DEFECTIVE CELL MIGRATION AND IMPAIRED IMMUNOSTIMULATORY ACTIVATION.IMMUNOBIOLOGY. VOL. 214. ISSUE 9-10. P. 778 -790 83 81% 31
8 COTTA-DE-ALMEIDA, V , DUPRE, L , GUIPOUY, D , VASCONCELOS, Z , (2015) SIGNAL INTEGRATION DURING T LYMPHOCYTE ACTIVATION AND FUNCTION: LESSONS FROM THE WISKOTT-ALDRICH SYNDROME.FRONTIERS IN IMMUNOLOGY. VOL. 6. ISSUE . P. - 76 78% 3
9 BURNS, S , CORY, GO , VAINCHENKER, W , THRASHER, AJ , (2004) MECHANISMS OF WASP-MEDIATED HEMATOLOGIC AND IMMUNOLOGIC DISEASE.BLOOD. VOL. 104. ISSUE 12. P. 3454 -3462 90 80% 86
10 ORANGE, JS , STONE, KD , TURVEY, SE , KRZEWSKI, K , (2004) THE WISKOTT-ALDRICH SYNDROME.CELLULAR AND MOLECULAR LIFE SCIENCES. VOL. 61. ISSUE 18. P. 2361-2385 122 60% 33

Classes with closest relation at Level 1



Rank Class id link
1 13975 PODOSOME//INVADOPODIA//CORTACTIN
2 4138 FORMIN//CELL STRUCT SIGNAL INTEGRAT//LAMELLIPODIUM
3 12297 SEVERE COMBINED IMMUNODEFICIENCY//OMENN SYNDROME//PRIMARY IMMUNODEFICIENCY
4 17746 CD43//LEUKOSIALIN//SIALOPHORIN
5 8624 DYNAMIN//BAR DOMAIN//AMPHIPHYSIN
6 19310 LASP 1//PALLADIN//ZYXIN
7 4230 IMMUNOLOGICAL SYNAPSE//LYMPHOCYTE INTERACT//PROGRAM MOL PATHOGENESIS
8 31783 CORONIN//CORONIN 1A//CORONIN 1C
9 15313 MAY HEGGLIN ANOMALY//INHERITED THROMBOCYTOPENIA//EPSTEIN SYNDROME
10 20465 HYPER IGE SYNDROME//JOBS SYNDROME//HYPERIMMUNOGLOBULIN E SYNDROME

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