Class information for:
Level 1: HYPER IGE SYNDROME//JOBS SYNDROME//HYPERIMMUNOGLOBULIN E SYNDROME

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
20465 459 33.1 74%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
530 3       SPLENECTOMY//COMMON VARIABLE IMMUNODEFICIENCY//IMMUNE THROMBOCYTOPENIA 19898
1704 2             COMMON VARIABLE IMMUNODEFICIENCY//PRIMARY IMMUNODEFICIENCY//INTRAVENOUS IMMUNOGLOBULIN 6726
20465 1                   HYPER IGE SYNDROME//JOBS SYNDROME//HYPERIMMUNOGLOBULIN E SYNDROME 459

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HYPER IGE SYNDROME authKW 4653397 20% 76% 92
2 JOBS SYNDROME authKW 3035623 11% 89% 51
3 HYPERIMMUNOGLOBULIN E SYNDROME authKW 1645503 6% 85% 29
4 DOCK8 authKW 1047756 5% 75% 21
5 DOCK8 DEFICIENCY authKW 864823 3% 100% 13
6 DEDICATOR OF CYTOKINESIS 8 authKW 489862 2% 82% 9
7 HYPER IGE authKW 449696 3% 52% 13
8 HIES authKW 425756 2% 80% 8
9 STAT3 MUTATION authKW 407463 2% 88% 7
10 BUCKLEY SYNDROME authKW 332624 1% 100% 5

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Allergy 9335 21% 0% 97
2 Immunology 3692 43% 0% 198
3 Pediatrics 869 16% 0% 72
4 Dermatology 435 8% 0% 36
5 Medicine, General & Internal 83 8% 0% 36
6 Medicine, Research & Experimental 54 5% 0% 24
7 Hematology 41 4% 0% 17
8 Otorhinolaryngology 41 2% 0% 11
9 Respiratory System 27 3% 0% 12
10 Infectious Diseases 26 3% 0% 14

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SCUOLA DOTTORATO SCI RIPRODUZ SVILUPPO 133050 0% 100% 2
2 PICAR 88698 0% 67% 2
3 HUMAN IMMUNOL DIS UNIT 85529 1% 43% 3
4 IMMUNODEFICIENCIES UNIT 70954 1% 27% 4
5 KIPPER ALLERGY IMMUNOL 70954 1% 27% 4
6 ADULT IMMUNOHEMATOL 66525 0% 100% 1
7 BOWMAN GRAY MED PEDIAT 300 HAWTHORNE RD 66525 0% 100% 1
8 CLIN B34141 66525 0% 100% 1
9 CLIN IMMUNOL MINIST EDUC CHILD DEV 66525 0% 100% 1
10 FDN IRCCS POLICLIN MILANO 66525 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF CLINICAL IMMUNOLOGY 12774 5% 1% 22
2 JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY 6419 7% 0% 32
3 CLINICAL IMMUNOLOGY 4191 3% 0% 13
4 ANNALS OF ALLERGY 1811 2% 0% 8
5 ALLERGOLOGIA ET IMMUNOPATHOLOGIA 1591 1% 0% 5
6 IRANIAN JOURNAL OF ALLERGY ASTHMA AND IMMUNOLOGY 1330 1% 1% 3
7 ANNALS OF ALLERGY ASTHMA & IMMUNOLOGY 1158 2% 0% 8
8 CURRENT OPINION IN ALLERGY AND CLINICAL IMMUNOLOGY 1016 1% 0% 4
9 JOURNAL OF INFORMATION ETHICS 830 0% 1% 1
10 IMMUNOLOGY AND ALLERGY CLINICS OF NORTH AMERICA 782 1% 0% 4

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 HYPER IGE SYNDROME 4653397 20% 76% 92 Search HYPER+IGE+SYNDROME Search HYPER+IGE+SYNDROME
2 JOBS SYNDROME 3035623 11% 89% 51 Search JOBS+SYNDROME Search JOBS+SYNDROME
3 HYPERIMMUNOGLOBULIN E SYNDROME 1645503 6% 85% 29 Search HYPERIMMUNOGLOBULIN+E+SYNDROME Search HYPERIMMUNOGLOBULIN+E+SYNDROME
4 DOCK8 1047756 5% 75% 21 Search DOCK8 Search DOCK8
5 DOCK8 DEFICIENCY 864823 3% 100% 13 Search DOCK8+DEFICIENCY Search DOCK8+DEFICIENCY
6 DEDICATOR OF CYTOKINESIS 8 489862 2% 82% 9 Search DEDICATOR+OF+CYTOKINESIS+8 Search DEDICATOR+OF+CYTOKINESIS+8
7 HYPER IGE 449696 3% 52% 13 Search HYPER+IGE Search HYPER+IGE
8 HIES 425756 2% 80% 8 Search HIES Search HIES
9 STAT3 MUTATION 407463 2% 88% 7 Search STAT3+MUTATION Search STAT3+MUTATION
10 BUCKLEY SYNDROME 332624 1% 100% 5 Search BUCKLEY+SYNDROME Search BUCKLEY+SYNDROME

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 FARMAND, S , SUNDIN, M , (2015) HYPER-IGE SYNDROMES: RECENT ADVANCES IN PATHOGENESIS, DIAGNOSTICS AND CLINICAL CARE.CURRENT OPINION IN HEMATOLOGY. VOL. 22. ISSUE 1. P. 12 -22 58 75% 8
2 YONG, PFK , FREEMAN, AF , ENGELHARDT, KR , HOLLAND, S , PUCK, JM , GRIMBACHER, B , (2012) AN UPDATE ON THE HYPER-IGE SYNDROMES.ARTHRITIS RESEARCH & THERAPY. VOL. 14. ISSUE 6. P. - 59 78% 25
3 FREEMAN, AF , OLIVIER, KN , (2016) HYPER-IGE SYNDROMES AND THE LUNG.CLINICS IN CHEST MEDICINE. VOL. 37. ISSUE 3. P. 557 -+ 45 82% 0
4 FREEMAN, AF , HOLLAND, SM , (2010) CLINICAL MANIFESTATIONS OF HYPER IGE SYNDROMES.DISEASE MARKERS. VOL. 29. ISSUE 3-4. P. 123 -130 39 95% 26
5 DEWITT, CA , BISHOP, AB , BUESCHER, LS , STONE, SP , (2006) HYPERIMMUNOGLOBULIN E SYNDROME: TWO CASES AND A REVIEW OF THE LITERATURE.JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY. VOL. 54. ISSUE 5. P. 855-865 49 79% 32
6 DIMITROVA, D , FREEMAN, AF , (2017) CURRENT STATUS OF DEDICATOR OF CYTOKINESIS-ASSOCIATED IMMUNODEFICIENCY DOCK8 AND DOCK2.DERMATOLOGIC CLINICS. VOL. 35. ISSUE 1. P. 11 -+ 38 79% 0
7 HAGL, B , HEINZ, V , SCHLESINGER, A , SPIELBERGER, BD , SAWALLE-BELOHRADSKY, J , SENN-RAUH, M , MAGG, T , BOOS, AC , HONIG, M , SCHWARZ, K , ET AL (2016) KEY FINDINGS TO EXPEDITE THE DIAGNOSIS OF HYPER-IGE SYNDROMES IN INFANTS AND YOUNG CHILDREN.PEDIATRIC ALLERGY AND IMMUNOLOGY. VOL. 27. ISSUE 2. P. 177 -184 28 80% 5
8 ZHANG, Q , JING, H , SU, HC , (2016) RECENT ADVANCES IN DOCK8 IMMUNODEFICIENCY SYNDROME.JOURNAL OF CLINICAL IMMUNOLOGY. VOL. 36. ISSUE 5. P. 441 -449 33 80% 1
9 SOWERWINE, KJ , HOLLAND, SM , FREEMAN, AF , (2012) HYPER-IGE SYNDROME UPDATE.YEAR IN HUMAN AND MEDICAL GENETICS: INBORN ERRORS OF IMMUNITY III. VOL. 1250. ISSUE . P. 25 -32 41 68% 26
10 FREEMAN, AF , HOLLAND, SM , (2008) THE HYPER-IGE SYNDROMES.IMMUNOLOGY AND ALLERGY CLINICS OF NORTH AMERICA. VOL. 28. ISSUE 2. P. 277-+ 35 85% 55

Classes with closest relation at Level 1



Rank Class id link
1 13755 HUMAN GENET INFECT DIS//MENDELIAN SUSCEPTIBILITY TO MYCOBACTERIAL DISEASE//PEDIAT IMMUNOL HEMATOL UNIT
2 12297 SEVERE COMBINED IMMUNODEFICIENCY//OMENN SYNDROME//PRIMARY IMMUNODEFICIENCY
3 29646 AIDS SYNDROME//ALLERGIC RESPONSE TO HIV 1//ANTI HIV IGE
4 10295 CHRONIC GRANULOMATOUS DISEASE//CGD//CYBB
5 3006 COMMON VARIABLE IMMUNODEFICIENCY//IGA DEFICIENCY//CVID
6 36029 MCKITTRICK WHEELOCK SYNDROME//ABNORMAL DEFECATION//COLONIC WATER TRANSPORT
7 30073 BOTRYOMYCOSIS//BREVUNDIMONAS VESICULARIS//BACTERIAL PSEUDOMYCOSIS
8 11252 WISKOTT ALDRICH SYNDROME//X LINKED THROMBOCYTOPENIA//WISKOTT ALDRICH SYNDROME PROTEIN
9 8274 INTERLEUKIN 4//IL 4//IGE SYNTHESIS
10 19094 ECZEMA HERPETICUM//ATOPIC DERMATITIS//MICROBIAL SCI HOST DEF

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