Class information for:
Level 1: OSTEOGENESIS IMPERFECTA//BONE EXTRACELLULAR MATRIX BRANCH//BRUCK SYNDROME

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
3041 2081 33.8 67%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
593 3       JOURNAL OF THE AMERICAN LEATHER CHEMISTS ASSOCIATION//OSTEOGENESIS IMPERFECTA//JOURNAL OF THE SOCIETY OF LEATHER TECHNOLOGISTS AND CHEMISTS 14947
797 2             OSTEOGENESIS IMPERFECTA//EHLERS DANLOS SYNDROME//COLLAGEN 12085
3041 1                   OSTEOGENESIS IMPERFECTA//BONE EXTRACELLULAR MATRIX BRANCH//BRUCK SYNDROME 2081

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 OSTEOGENESIS IMPERFECTA authKW 8015093 34% 76% 717
2 BONE EXTRACELLULAR MATRIX BRANCH address 437541 2% 76% 39
3 BRUCK SYNDROME authKW 223160 1% 89% 17
4 COL1A2 authKW 210406 1% 46% 31
5 COL1A1 authKW 197954 2% 31% 43
6 BRITTLE BONE DISEASE authKW 194180 1% 88% 15
7 HYPERPLASTIC CALLUS authKW 190731 1% 100% 13
8 SECT CONNECT TISSUE DISORDERS address 165297 1% 87% 13
9 OSTEOGENESIS IMPERFECTA OI authKW 162515 1% 92% 12
10 CRTAP authKW 136556 1% 85% 11

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Orthopedics 3874 12% 0% 251
2 Genetics & Heredity 3860 19% 0% 392
3 Pediatrics 3119 14% 0% 293
4 Endocrinology & Metabolism 3013 16% 0% 324
5 Biochemistry & Molecular Biology 427 16% 0% 336
6 Medicine, Research & Experimental 206 5% 0% 102
7 Surgery 202 8% 0% 157
8 Otorhinolaryngology 159 2% 0% 47
9 Medicine, General & Internal 125 5% 0% 111
10 Rheumatology 119 2% 0% 35

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BONE EXTRACELLULAR MATRIX BRANCH 437541 2% 76% 39
2 SECT CONNECT TISSUE DISORDERS 165297 1% 87% 13
3 BONE OSTEOGENESIS IMPERFECTA 93895 0% 80% 8
4 FC DONDERS NEUROSCI 88030 0% 100% 6
5 SECT PHYS BIOCHEM 82538 1% 26% 22
6 BEMB 73358 0% 100% 5
7 GENET UNIT 55792 4% 5% 76
8 HOSP UNIV LA PAZ IDIPAZ 33004 0% 38% 6
9 BGI SHENZHEN BINHAI GENOM 29343 0% 100% 2
10 CHIRURG ABT 3 29343 0% 100% 2

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF BONE AND MINERAL RESEARCH 13691 4% 1% 79
2 BONE 10735 3% 1% 70
3 CALCIFIED TISSUE INTERNATIONAL 5051 2% 1% 41
4 MATRIX 4699 0% 4% 9
5 JOURNAL OF MEDICAL GENETICS 4623 2% 1% 43
6 HUMAN MUTATION 4473 2% 1% 35
7 JOURNAL OF PEDIATRIC ORTHOPAEDICS 4105 2% 1% 38
8 AMERICAN JOURNAL OF MEDICAL GENETICS 3031 2% 0% 43
9 HUMAN GENETICS 2599 2% 0% 38
10 HORMONE RESEARCH IN PAEDIATRICS 2540 1% 1% 12

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 OSTEOGENESIS IMPERFECTA 8015093 34% 76% 717 Search OSTEOGENESIS+IMPERFECTA Search OSTEOGENESIS+IMPERFECTA
2 BRUCK SYNDROME 223160 1% 89% 17 Search BRUCK+SYNDROME Search BRUCK+SYNDROME
3 COL1A2 210406 1% 46% 31 Search COL1A2 Search COL1A2
4 COL1A1 197954 2% 31% 43 Search COL1A1 Search COL1A1
5 BRITTLE BONE DISEASE 194180 1% 88% 15 Search BRITTLE+BONE+DISEASE Search BRITTLE+BONE+DISEASE
6 HYPERPLASTIC CALLUS 190731 1% 100% 13 Search HYPERPLASTIC+CALLUS Search HYPERPLASTIC+CALLUS
7 OSTEOGENESIS IMPERFECTA OI 162515 1% 92% 12 Search OSTEOGENESIS+IMPERFECTA+OI Search OSTEOGENESIS+IMPERFECTA+OI
8 CRTAP 136556 1% 85% 11 Search CRTAP Search CRTAP
9 IDIOPATHIC JUVENILE OSTEOPOROSIS 118838 0% 90% 9 Search IDIOPATHIC+JUVENILE+OSTEOPOROSIS Search IDIOPATHIC+JUVENILE+OSTEOPOROSIS
10 OSTEOGENESIS IMPERFECT 118838 0% 90% 9 Search OSTEOGENESIS+IMPERFECT Search OSTEOGENESIS+IMPERFECT

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 FORLINO, A , MARINI, JC , (2016) OSTEOGENESIS IMPERFECTA.LANCET. VOL. 387. ISSUE 10028. P. 1657 -1671 95 75% 32
2 FORLINO, A , CABRAL, WA , BARNES, AM , MARINI, JC , (2011) NEW PERSPECTIVES ON OSTEOGENESIS IMPERFECTA.NATURE REVIEWS ENDOCRINOLOGY. VOL. 7. ISSUE 9. P. 540 -557 144 76% 170
3 TREJO, P , RAUCH, F , (2016) OSTEOGENESIS IMPERFECTA IN CHILDREN AND ADOLESCENTS-NEW DEVELOPMENTS IN DIAGNOSIS AND TREATMENT.OSTEOPOROSIS INTERNATIONAL. VOL. 27. ISSUE 12. P. 3427 -3437 83 91% 1
4 MAROM, R , LEE, YC , GRAFE, I , LEE, B , (2016) PHARMACOLOGICAL AND BIOLOGICAL THERAPEUTIC STRATEGIES FOR OSTEOGENESIS IMPERFECTA.AMERICAN JOURNAL OF MEDICAL GENETICS PART C-SEMINARS IN MEDICAL GENETICS. VOL. 172. ISSUE 4. P. 367 -383 111 66% 0
5 RAUCH, F , GLORIEUX, FH , (2004) OSTEOGENESIS IMPERFECTA.LANCET. VOL. 363. ISSUE 9418. P. 1377-1385 81 70% 466
6 VAN DIJK, FS , SILLENCE, DO , (2014) OSTEOGENESIS IMPERFECTA: CLINICAL DIAGNOSIS, NOMENCLATURE AND SEVERITY ASSESSMENT.AMERICAN JOURNAL OF MEDICAL GENETICS PART A. VOL. 164. ISSUE 6. P. 1470 -1481 47 94% 70
7 MONTI, E , MOTTES, M , FRASCHINI, P , BRUNELLI, P , FORLINO, A , VENTURI, G , DORO, F , PERLINI, S , CAVARZERE, P , ANTONIAZZI, F , (2010) CURRENT AND EMERGING TREATMENTS FOR THE MANAGEMENT OF OSTEOGENESIS IMPERFECTA.THERAPEUTICS AND CLINICAL RISK MANAGEMENT. VOL. 6. ISSUE . P. 367 -381 88 77% 22
8 PRIMORAC, D , ROWE, DW , MOTTES, M , BARISIC, I , ANTICEVIC, D , MIRANDOLA, S , LIRA, MG , KALAJZIC, I , KUSEC, V , GLORIEUX, FH , (2001) OSTEOGENESIS IMPERFECTA AT THE BEGINNING OF BONE AND JOINT DECADE.CROATIAN MEDICAL JOURNAL. VOL. 42. ISSUE 4. P. 393 -415 113 75% 27
9 BESIO, R , FORLINO, A , (2015) TREATMENT OPTIONS FOR OSTEOGENESIS IMPERFECTA.EXPERT OPINION ON ORPHAN DRUGS. VOL. 3. ISSUE 2. P. 165 -181 79 73% 1
10 ROHRBACH, M , GIUNTA, C , (2012) RECESSIVE OSTEOGENESIS IMPERFECTA: CLINICAL, RADIOLOGICAL, AND MOLECULAR FINDINGS.AMERICAN JOURNAL OF MEDICAL GENETICS PART C-SEMINARS IN MEDICAL GENETICS. VOL. 160C. ISSUE 3. P. 175-189 72 76% 19

Classes with closest relation at Level 1



Rank Class id link
1 20193 FIBRIL GROWTH//COLLAGEN FIBRIL SEGMENTS//COLLAGEN LIPID INTERACTION
2 11104 LARP6//COLLAGEN GENES//ALPHA 2I COLLAGEN
3 17301 LYSYL HYDROXYLASE//EHLERS DANLOS SYNDROME TYPE VI//AGEN UNIT
4 7639 EHLERS DANLOS SYNDROME//JOINT HYPERMOBILITY//HYPERMOBILITY
5 10915 STICKLER SYNDROME//COL2A1//PROGRESSIVE PSEUDORHEUMATOID DYSPLASIA
6 24934 HSP47//HEAT SHOCK PROTEIN 47//UMB GREENEBAUM CANC
7 8944 TYPE V COLLAGEN//COLLAGEN XII//TYPE XI COLLAGEN
8 9510 TRIPLE HELIX//COLLAGEN LIKE PEPTIDE//FLUOROPROLINE
9 30620 CUTANEOUS ASTHENIA//DERMATOSPARAXIS//HEREDITARY EQUINE REGIONAL DERMAL ASTHENIA
10 9853 ACHONDROPLASIA//HYPOCHONDROPLASIA//THANATOPHORIC DYSPLASIA

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