Class information for:
Level 1: ACUTE INTERMITTENT PORPHYRIA//PORPHYRIA//ERYTHROPOIETIC PROTOPORPHYRIA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
2758 2156 30.7 59%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
468 3       GLUCOSINOLATES//BILIRUBIN//HEME OXYGENASE 24157
1296 2             HEME OXYGENASE//PORPHYRIA//HEME OXYGENASE 1 8624
2758 1                   ACUTE INTERMITTENT PORPHYRIA//PORPHYRIA//ERYTHROPOIETIC PROTOPORPHYRIA 2156

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ACUTE INTERMITTENT PORPHYRIA authKW 2134785 8% 90% 167
2 PORPHYRIA authKW 1578369 10% 52% 213
3 ERYTHROPOIETIC PROTOPORPHYRIA authKW 1168766 4% 85% 97
4 FERROCHELATASE authKW 799980 5% 56% 100
5 VARIEGATE PORPHYRIA authKW 655445 3% 86% 54
6 CONGENITAL ERYTHROPOIETIC PORPHYRIA authKW 595997 2% 96% 44
7 FRANCAIS PORPHYRIES address 509933 3% 65% 55
8 ACUTE PORPHYRIA authKW 498744 2% 93% 38
9 PORPHOBILINOGEN DEAMINASE authKW 427683 2% 57% 53
10 COPROPORPHYRINOGEN OXIDASE authKW 385483 2% 78% 35

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 4690 12% 0% 250
2 Medical Laboratory Technology 2440 6% 0% 125
3 Medicine, General & Internal 1251 13% 0% 270
4 Medicine, Research & Experimental 1215 10% 0% 213
5 Genetics & Heredity 1199 11% 0% 238
6 Biochemistry & Molecular Biology 884 21% 0% 443
7 Gastroenterology & Hepatology 421 5% 0% 108
8 Hematology 308 4% 0% 96
9 Anesthesiology 138 2% 0% 40
10 Biophysics 104 4% 0% 79

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 FRANCAIS PORPHYRIES 509933 3% 65% 55
2 PORPHYRIA SWEDEN 340263 1% 83% 29
3 PORPHYRIA 126153 1% 64% 14
4 BIOCHEM MOL GENET UNIT 113289 0% 100% 8
5 EUREG PORPHYRIA MAASTRICHT 86736 0% 88% 7
6 PORPHYRIA UNIT 72827 0% 86% 6
7 BIOCHEM DIAGNOSES PORPHYRIAS 70806 0% 100% 5
8 EUROPAI ES PORPHYRIEZENTRUM 70806 0% 100% 5
9 NORWEGIAN PORPHYRIA 70806 0% 100% 5
10 LENNOX EALES PORPHYRIA S 69386 0% 70% 7

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CELLULAR AND MOLECULAR BIOLOGY 7429 2% 1% 41
2 INTERNATIONAL JOURNAL OF BIOCHEMISTRY 4442 1% 1% 31
3 JOURNAL OF INHERITED METABOLIC DISEASE 3353 2% 1% 33
4 PHOTODERMATOLOGY PHOTOIMMUNOLOGY & PHOTOMEDICINE 3310 1% 1% 17
5 HUMAN GENETICS 3220 2% 1% 43
6 CLINICS IN HAEMATOLOGY 2595 0% 3% 7
7 EUROPEAN JOURNAL OF CLINICAL CHEMISTRY AND CLINICAL BIOCHEMISTRY 2240 1% 1% 12
8 BRITISH JOURNAL OF DERMATOLOGY 2200 2% 0% 42
9 SEMINARS IN DERMATOLOGY 1872 0% 2% 8
10 ANNALS OF CLINICAL BIOCHEMISTRY 1643 1% 1% 20

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 ACUTE INTERMITTENT PORPHYRIA 2134785 8% 90% 167 Search ACUTE+INTERMITTENT+PORPHYRIA Search ACUTE+INTERMITTENT+PORPHYRIA
2 PORPHYRIA 1578369 10% 52% 213 Search PORPHYRIA Search PORPHYRIA
3 ERYTHROPOIETIC PROTOPORPHYRIA 1168766 4% 85% 97 Search ERYTHROPOIETIC+PROTOPORPHYRIA Search ERYTHROPOIETIC+PROTOPORPHYRIA
4 FERROCHELATASE 799980 5% 56% 100 Search FERROCHELATASE Search FERROCHELATASE
5 VARIEGATE PORPHYRIA 655445 3% 86% 54 Search VARIEGATE+PORPHYRIA Search VARIEGATE+PORPHYRIA
6 CONGENITAL ERYTHROPOIETIC PORPHYRIA 595997 2% 96% 44 Search CONGENITAL+ERYTHROPOIETIC+PORPHYRIA Search CONGENITAL+ERYTHROPOIETIC+PORPHYRIA
7 ACUTE PORPHYRIA 498744 2% 93% 38 Search ACUTE+PORPHYRIA Search ACUTE+PORPHYRIA
8 PORPHOBILINOGEN DEAMINASE 427683 2% 57% 53 Search PORPHOBILINOGEN+DEAMINASE Search PORPHOBILINOGEN+DEAMINASE
9 COPROPORPHYRINOGEN OXIDASE 385483 2% 78% 35 Search COPROPORPHYRINOGEN+OXIDASE Search COPROPORPHYRINOGEN+OXIDASE
10 HEREDITARY COPROPORPHYRIA 326272 1% 96% 24 Search HEREDITARY+COPROPORPHYRIA Search HEREDITARY+COPROPORPHYRIA

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 HARPER, P , SARDH, E , (2014) MANAGEMENT OF ACUTE INTERMITTENT PORPHYRIA.EXPERT OPINION ON ORPHAN DRUGS. VOL. 2. ISSUE 4. P. 349 -368 97 89% 3
2 PUY, H , GOUYA, L , DEYBACH, JC , (2010) PORPHYRIAS.LANCET. VOL. 375. ISSUE 9718. P. 924 -937 87 72% 167
3 ANSTEY, AV , HIFT, RJ , (2007) LIVER DISEASE IN ERYTHROPOIETIC PROTOPORPHYRIA: INSIGHTS AND IMPLICATIONS FOR MANAGEMENT.GUT. VOL. 56. ISSUE 7. P. 1009-1018 85 98% 32
4 VENTURA, P , CAPPELLINI, MD , BIOLCATI, G , GUIDA, CC , ROCCHI, E , (2014) A CHALLENGING DIAGNOSIS FOR POTENTIAL FATAL DISEASES: RECOMMENDATIONS FOR DIAGNOSING ACUTE PORPHYRIAS.EUROPEAN JOURNAL OF INTERNAL MEDICINE. VOL. 25. ISSUE 6. P. 497 -505 76 90% 5
5 WHATLEY, SD , BADMINTON, MN , (2013) ROLE OF GENETIC TESTING IN THE MANAGEMENT OF PATIENTS WITH INHERITED PORPHYRIA AND THEIR FAMILIES.ANNALS OF CLINICAL BIOCHEMISTRY. VOL. 50. ISSUE 3. P. 204-216 81 78% 3
6 KAUPPINEN, R , (2005) PORPHYRIAS.LANCET. VOL. 365. ISSUE 9455. P. 241 -252 84 72% 129
7 HRDINKA, M , PUY, H , MARTASEK, P , (2006) MAY 2006 UPDATE IN PORPHOBILINOGEN DEAMINASE GENE POLYMORPHISMS AND MUTATIONS CAUSING ACUTE INTERMITTENT PORPHYRIA. COMPARISON WITH THE SITUATION IN SLAVIC POPULATION.PHYSIOLOGICAL RESEARCH. VOL. 55. ISSUE . P. S119 -S136 63 100% 27
8 FARFARAS, A , ZAGOURI, F , ZOGRAFOS, G , KOSTOPOULOU, A , SERGENTANIS, TN , ANTONIOU, S , (2010) ACUTE INTERMITTENT PORPHYRIA IN PREGNANCY: A COMMON MISDIAGNOSIS.CLINICAL AND EXPERIMENTAL OBSTETRICS & GYNECOLOGY. VOL. 37. ISSUE 4. P. 256 -260 59 98% 4
9 SASSA, S , (2000) HEMATOLOGIC ASPECTS OF THE PORPHYRIAS.INTERNATIONAL JOURNAL OF HEMATOLOGY. VOL. 71. ISSUE 1. P. 1-17 101 74% 18
10 SCHULENBURG-BRAND, D , KATUGAMPOLA, R , ANSTEY, AV , BADMINTON, MN , (2014) THE CUTANEOUS PORPHYRIAS.DERMATOLOGIC CLINICS. VOL. 32. ISSUE 3. P. 369 -+ 58 75% 10

Classes with closest relation at Level 1



Rank Class id link
1 6691 PORPHYRIA CUTANEA TARDA//UROPORPHYRINOGEN DECARBOXYLASE//PORPHYRIA
2 16240 X LINKED SIDEROBLASTIC ANEMIA//ALAS2//5 AMINOLEVULINATE SYNTHASE
3 13840 PSEUDOMONAS DENITRIFICANS//PRECORRIN 2//UROPORPHYRINOGEN III METHYLTRANSFERASE
4 16401 PROTOPORPHYRINOGEN OXIDASE//PEROXIDIZING HERBICIDES//PROTOPORPHYRINOGEN IX OXIDASE
5 21839 SN MESOPORPHYRIN//HEME OXYGENASE INHIBITOR//TIN MESOPORPHYRIN
6 29283 HEMATOLOGICAL AND CLINICOCHEMICAL PARAMETERS//URINOMETER//WHOLE BLOOD WATER
7 17456 N ALKYLPROTOPORPHYRIN//N ALKYLPROTOPORPHYRIN IX//TAPE PORPHYRIN
8 11897 PORPHOBILINOGEN SYNTHASE//C 5 PATHWAY//5 AMINOLEVULINIC ACID
9 26978 FLEISCHWIRTSCHAFT//PARMA HAM//HBEREICH LANDWIRT AFT OKOTROPHOL LANDESPFLEG
10 33937 ROTOR SYNDROME//BLUE DIVISION//DUBIN JOHNSON

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