Class information for:
Level 1: CONGENITAL DYSERYTHROPOIETIC ANEMIA//CONGENITAL DYSERYTHROPOIETIC ANAEMIA//HEMPAS

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
24056 325 25.1 51%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
455 3       HEMOGLOBIN//SICKLE CELL DISEASE//SICKLE CELL ANEMIA 25359
1768 2             HEMOGLOBIN//ALPHA THALASSEMIA//HEMOGLOBINOPATHIES 6399
24056 1                   CONGENITAL DYSERYTHROPOIETIC ANEMIA//CONGENITAL DYSERYTHROPOIETIC ANAEMIA//HEMPAS 325

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CONGENITAL DYSERYTHROPOIETIC ANEMIA authKW 1835036 8% 78% 25
2 CONGENITAL DYSERYTHROPOIETIC ANAEMIA authKW 882120 4% 72% 13
3 HEMPAS authKW 712067 4% 63% 12
4 CDA II authKW 626356 3% 67% 10
5 CONGENITAL DYSERYTHROPOIETIC ANEMIA TYPE II authKW 563726 2% 100% 6
6 DYSERYTHROPOIESIS authKW 524824 6% 31% 18
7 SEC23B authKW 422792 2% 75% 6
8 CDA I authKW 375818 1% 100% 4
9 CDA TYPE I authKW 375818 1% 100% 4
10 CDA TYPE III authKW 281863 1% 100% 3

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 15143 65% 0% 212
2 Pediatrics 270 11% 0% 35
3 Pathology 154 7% 0% 22
4 Oncology 42 8% 0% 26
5 Genetics & Heredity 22 5% 0% 16
6 Medicine, Research & Experimental 18 4% 0% 13
7 Medical Laboratory Technology 11 1% 0% 4
8 Microscopy 7 1% 0% 2
9 Medicine, General & Internal 5 4% 0% 12
10 Transplantation 5 1% 0% 4

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 EFRATI BLOOD CELLS CYTOL 260980 2% 56% 5
2 GERMAN REGISTRY CONGENITAL DYSERYTHROPOIET ANEMIA 187909 1% 100% 2
3 U 473 140929 1% 50% 3
4 THALASSEMIAS 125271 1% 67% 2
5 U 779 125271 1% 67% 2
6 ABT BIOMETRIE 93954 0% 100% 1
7 ABT HAMATOL HAMATOL 93954 0% 100% 1
8 ABT PADIAT HAMATOL ONKOL ENDOKRINOL 93954 0% 100% 1
9 ADV PAAEDITR 93954 0% 100% 1
10 ASSISTANCE PUBL HOPITAUX PARIS MED PARIS SUD 93954 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BRITISH JOURNAL OF HAEMATOLOGY 18903 16% 0% 52
2 ACTA HAEMATOLOGICA 5335 4% 0% 14
3 CLINICAL AND LABORATORY HAEMATOLOGY 5131 3% 1% 9
4 EUROPEAN JOURNAL OF HAEMATOLOGY 4150 4% 0% 13
5 JOURNAL OF THE JAPANESE SOCIETY OF INTERNAL MEDICINE 3478 0% 4% 1
6 HAEMATOLOGIA 3204 1% 1% 4
7 HAEMATOLOGICA 3120 3% 0% 11
8 AMERICAN JOURNAL OF HEMATOLOGY 2659 4% 0% 13
9 INDIAN JOURNAL OF HEMATOLOGY AND BLOOD TRANSFUSION 2575 1% 1% 4
10 BLUT 2486 2% 1% 5

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 CONGENITAL DYSERYTHROPOIETIC ANEMIA 1835036 8% 78% 25 Search CONGENITAL+DYSERYTHROPOIETIC+ANEMIA Search CONGENITAL+DYSERYTHROPOIETIC+ANEMIA
2 CONGENITAL DYSERYTHROPOIETIC ANAEMIA 882120 4% 72% 13 Search CONGENITAL+DYSERYTHROPOIETIC+ANAEMIA Search CONGENITAL+DYSERYTHROPOIETIC+ANAEMIA
3 HEMPAS 712067 4% 63% 12 Search HEMPAS Search HEMPAS
4 CDA II 626356 3% 67% 10 Search CDA+II Search CDA+II
5 CONGENITAL DYSERYTHROPOIETIC ANEMIA TYPE II 563726 2% 100% 6 Search CONGENITAL+DYSERYTHROPOIETIC+ANEMIA+TYPE+II Search CONGENITAL+DYSERYTHROPOIETIC+ANEMIA+TYPE+II
6 DYSERYTHROPOIESIS 524824 6% 31% 18 Search DYSERYTHROPOIESIS Search DYSERYTHROPOIESIS
7 SEC23B 422792 2% 75% 6 Search SEC23B Search SEC23B
8 CDA I 375818 1% 100% 4 Search CDA+I Search CDA+I
9 CDA TYPE I 375818 1% 100% 4 Search CDA+TYPE+I Search CDA+TYPE+I
10 CDA TYPE III 281863 1% 100% 3 Search CDA+TYPE+III Search CDA+TYPE+III

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 WICKRAMASINGHE, SN , WOOD, WG , (2005) ADVANCES IN THE UNDERSTANDING OF THE CONGENITAL DYSERYTHROPOIETIC ANAEMIAS.BRITISH JOURNAL OF HAEMATOLOGY. VOL. 131. ISSUE 4. P. 431-446 93 90% 51
2 RENELLA, R , WOOD, WG , (2009) THE CONGENITAL DYSERYTHROPOIETIC ANEMIAS.HEMATOLOGY-ONCOLOGY CLINICS OF NORTH AMERICA. VOL. 23. ISSUE 2. P. 283-+ 82 91% 16
3 WICKRAMASINGHE, SN , (1998) CONGENITAL DYSERYTHROPOIETIC ANAEMIAS: CLINICAL FEATURES, HAEMATOLOGICAL MORPHOLOGY AND NEW BIOCHEMICAL DATA.BLOOD REVIEWS. VOL. 12. ISSUE 3. P. 178 -200 59 86% 39
4 IOLASCON, A , ESPOSITO, MR , RUSSO, R , (2012) CLINICAL ASPECTS AND PATHOGENESIS OF CONGENITAL DYSERYTHROPOIETIC ANEMIAS: FROM MORPHOLOGY TO MOLECULAR APPROACH.HAEMATOLOGICA-THE HEMATOLOGY JOURNAL. VOL. 97. ISSUE 12. P. 1786-1794 50 66% 19
5 HEIMPEL, H , (2004) CONGENITAL DYSERYTHROPOIETIC ANEMIAS: EPIDEMIOLOGY, CLINICAL SIGNIFICANCE, AND PROGRESS IN UNDERSTANDING THEIR PATHOGENESIS.ANNALS OF HEMATOLOGY. VOL. 83. ISSUE 10. P. 613-621 48 87% 22
6 KAMIYA, T , MANABE, A , (2010) CONGENITAL DYSERYTHROPOIETIC ANEMIA.INTERNATIONAL JOURNAL OF HEMATOLOGY. VOL. 92. ISSUE 3. P. 432-438 36 90% 6
7 GAMBALE, A , IOLASCON, A , ANDOLFO, I , RUSSO, R , (2016) DIAGNOSIS AND MANAGEMENT OF CONGENITAL DYSERYTHROPOIETIC ANEMIAS.EXPERT REVIEW OF HEMATOLOGY. VOL. 9. ISSUE 3. P. 283 -296 40 60% 1
8 WICKRAMASINGHE, SN , (2000) CONGENITAL DYSERYTHROPOIETIC ANEMIAS.CURRENT OPINION IN HEMATOLOGY. VOL. 7. ISSUE 2. P. 71 -78 38 97% 19
9 WICKRAMASINGHE, SN , (1997) DYSERYTHROPOIESIS AND CONGENITAL DYSERYTHROPOIETIC ANAEMIAS.BRITISH JOURNAL OF HAEMATOLOGY. VOL. 98. ISSUE 4. P. 785-797 51 75% 44
10 DELAUNAY, J , (1999) RECOGNIZING TYPES I, II AND III CONGENITAL DYSERYTHROPOIETIC ANEMIAS NOW THAT THE CAUSATIVE GENES HAVE BEEN IDENTIFIED..ANNALES DE PEDIATRIE. VOL. 46. ISSUE 1. P. 64 -72 39 98% 0

Classes with closest relation at Level 1



Rank Class id link
1 15993 CONGENITAL DISORDERS OF GLYCOSYLATION//CDG//CARBOHYDRATE DEFICIENT GLYCOPROTEIN SYNDROME
2 36392 26 KDA HELICOBACTER SPECIES SPECIFIC ANTIGEN GENE//AMOL THALASSEMIA//CANCER ADVERSE EFFECTS
3 28007 ACUTE ERYTHROLEUKEMIA//PURE ERYTHROID LEUKEMIA//ACUTE ERYTHROID LEUKEMIA
4 28087 FOLLICULAR DYSPLASIA//HAIRLESS DOGS//COLOUR DILUTION ALOPECIA
5 16240 X LINKED SIDEROBLASTIC ANEMIA//ALAS2//5 AMINOLEVULINATE SYNTHASE
6 9537 SENESCENT CELL ANTIGEN//ERYTHROCYTE AGING//SENESCENT ERYTHROCYTES
7 35917 PHOTIC SNEEZE REFLEX//ACHOO SYNDROME//INTRACTABLE SNEEZING
8 9383 FETAL HEMOGLOBIN//HEMOGLOBINOPATHY THALASSEMIA UNIT//GAMMA GLOBIN
9 30174 T ACTIVATION//ERYTHROCYTE CHARGE//ERYTHROCYTE T ANTIGEN
10 16788 EXTRAMEDULLARY HEMATOPOIESIS//EXTRAMEDULLARY HAEMATOPOIESIS//HEMATOPOIESIS EXTRAMEDULLARY

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