Class information for:
Level 1: AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME//ALPS UNIT//DN T CELLS

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
23365 348 38.0 91%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
441 3       TRAIL//SURVIVIN//APOPTOSIS 26474
306 2             TRAIL//SURVIVIN//APOPTOSIS 18497
23365 1                   AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME//ALPS UNIT//DN T CELLS 348

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME authKW 3295269 15% 72% 52
2 ALPS UNIT address 710730 3% 90% 9
3 DN T CELLS authKW 558785 3% 58% 11
4 MULTI ORGAN TRANSPLANTAT PROGRAM address 510510 2% 73% 8
5 AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME ALPS authKW 467966 2% 67% 8
6 DOUBLE NEGATIVE T CELLS authKW 358933 4% 27% 15
7 MOL DEV SECT address 286625 2% 47% 7
8 CANALE SMITH SYNDROME authKW 274198 1% 63% 5
9 DOUBLE NEGATIVE REGULATORY T CELLS authKW 263234 1% 100% 3
10 FAS DEFICIENCY authKW 263234 1% 100% 3

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 2732 27% 0% 95
2 Immunology 2564 41% 0% 144
3 Allergy 311 5% 0% 16
4 Pediatrics 298 11% 0% 38
5 Medicine, Research & Experimental 67 6% 0% 22
6 Rheumatology 55 3% 0% 9
7 Transplantation 50 3% 0% 10
8 Pathology 26 3% 0% 11
9 Oncology 25 7% 0% 23
10 Cell Biology 17 6% 0% 20

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ALPS UNIT 710730 3% 90% 9
2 MULTI ORGAN TRANSPLANTAT PROGRAM 510510 2% 73% 8
3 MOL DEV SECT 286625 2% 47% 7
4 CLINICIAN SCIENTIST TRAINING PROGRAM 131614 1% 50% 3
5 LCID 90242 2% 17% 6
6 ADULT HEMATOL MED HP 87745 0% 100% 1
7 AIDS RATORY 87745 0% 100% 1
8 ALLERGY IMMUNOL PEDIAT RHEUMATOL PEDIA 87745 0% 100% 1
9 ALPS CLIN 87745 0% 100% 1
10 BRANCH GENET MOL BIOL 87745 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BLOOD 3107 10% 0% 35
2 CLINICAL IMMUNOLOGY 2648 3% 0% 9
3 IMMUNOLOGIC RESEARCH 1834 2% 0% 6
4 PEDIATRIC BLOOD & CANCER 1561 3% 0% 9
5 BRITISH JOURNAL OF HAEMATOLOGY 1259 4% 0% 14
6 JOURNAL OF CLINICAL IMMUNOLOGY 1246 2% 0% 6
7 JOURNAL OF IMMUNOLOGY 917 7% 0% 24
8 CURRENT ALLERGY AND ASTHMA REPORTS 805 1% 0% 3
9 TRANSFUSION MEDICINE AND HEMOTHERAPY 568 1% 0% 2
10 PEDIATRIC ASTHMA ALLERGY & IMMUNOLOGY 483 0% 1% 1

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME 3295269 15% 72% 52 Search AUTOIMMUNE+LYMPHOPROLIFERATIVE+SYNDROME Search AUTOIMMUNE+LYMPHOPROLIFERATIVE+SYNDROME
2 DN T CELLS 558785 3% 58% 11 Search DN+T+CELLS Search DN+T+CELLS
3 AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME ALPS 467966 2% 67% 8 Search AUTOIMMUNE+LYMPHOPROLIFERATIVE+SYNDROME+ALPS Search AUTOIMMUNE+LYMPHOPROLIFERATIVE+SYNDROME+ALPS
4 DOUBLE NEGATIVE T CELLS 358933 4% 27% 15 Search DOUBLE+NEGATIVE+T+CELLS Search DOUBLE+NEGATIVE+T+CELLS
5 CANALE SMITH SYNDROME 274198 1% 63% 5 Search CANALE+SMITH+SYNDROME Search CANALE+SMITH+SYNDROME
6 DOUBLE NEGATIVE REGULATORY T CELLS 263234 1% 100% 3 Search DOUBLE+NEGATIVE+REGULATORY+T+CELLS Search DOUBLE+NEGATIVE+REGULATORY+T+CELLS
7 FAS DEFICIENCY 263234 1% 100% 3 Search FAS+DEFICIENCY Search FAS+DEFICIENCY
8 FAS MUTATION 263234 1% 100% 3 Search FAS+MUTATION Search FAS+MUTATION
9 ALPS TYPE III 175489 1% 100% 2 Search ALPS+TYPE+III Search ALPS+TYPE+III
10 CD4 CD8 REGULATORY T CELLS 175489 1% 100% 2 Search CD4+CD8+REGULATORY+T+CELLS Search CD4+CD8+REGULATORY+T+CELLS

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 LI, P , HUANG, P , YANG, Y , HAO, M , PENG, HW , LI, F , (2016) UPDATED UNDERSTANDING OF AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME (ALPS).CLINICAL REVIEWS IN ALLERGY & IMMUNOLOGY. VOL. 50. ISSUE 1. P. 55 -63 39 83% 3
2 PRICE, S , SHAW, PA , SEITZ, A , JOSHI, G , DAVIS, J , NIEMELA, JE , PERKINS, K , HORNUNG, RL , FOLIO, L , ROSENBERG, PS , ET AL (2014) NATURAL HISTORY OF AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME ASSOCIATED WITH FAS GENE MUTATIONS.BLOOD. VOL. 123. ISSUE 13. P. 1989-1999 37 79% 31
3 SU, HC , LENARDO, MJ , (2008) GENETIC DEFECTS OF APOPTOSIS AND PRIMARY IMMUNODEFICIENCY.IMMUNOLOGY AND ALLERGY CLINICS OF NORTH AMERICA. VOL. 28. ISSUE 2. P. 329-+ 58 68% 9
4 TEACHEY, DT , SEIF, AE , GRUPP, SA , (2010) ADVANCES IN THE MANAGEMENT AND UNDERSTANDING OF AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME (ALPS).BRITISH JOURNAL OF HAEMATOLOGY. VOL. 148. ISSUE 2. P. 205 -216 46 67% 33
5 RAO, VK , OLIVEIRA, JB , (2011) HOW I TREAT AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME.BLOOD. VOL. 118. ISSUE 22. P. 5741-5751 45 63% 26
6 FLEISHER, TA , OLIVEIRA, JB , (2012) MONOGENIC DEFECTS IN LYMPHOCYTE APOPTOSIS.CURRENT OPINION IN ALLERGY AND CLINICAL IMMUNOLOGY. VOL. 12. ISSUE 6. P. 609-615 37 76% 7
7 NEVEN, B , MAGERUS-CHATINET, A , FLORKIN, B , GOBERT, D , LAMBOTTE, O , DE SOMER, L , LANZAROTTI, N , STOLZENBERG, MC , BADER-MEUNIER, B , ALADJIDI, N , ET AL (2011) A SURVEY OF 90 PATIENTS WITH AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME RELATED TO TNFRSF6 MUTATION.BLOOD. VOL. 118. ISSUE 18. P. 4798 -4807 29 85% 31
8 SHAH, S , WU, E , RAO, VK , TARRANT, TK , (2014) AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME: AN UPDATE AND REVIEW OF THE LITERATURE.CURRENT ALLERGY AND ASTHMA REPORTS. VOL. 14. ISSUE 9. P. - 25 89% 8
9 TEACHEY, DT , (2012) NEW ADVANCES IN THE DIAGNOSIS AND TREATMENT OF AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME.CURRENT OPINION IN PEDIATRICS. VOL. 24. ISSUE 1. P. 1-8 32 70% 27
10 MADKAIKAR, M , MHATRE, S , GUPTA, M , GHOSH, K , (2011) ADVANCES IN AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROMES.EUROPEAN JOURNAL OF HAEMATOLOGY. VOL. 87. ISSUE 1. P. 1 -9 25 83% 19

Classes with closest relation at Level 1



Rank Class id link
1 1319 FAS//FAS LIGAND//FASL
2 26875 APO 1 ANTIBODY//APO I FAS APOPTOSIS//APOPTOSIS CYTOKINES
3 23671 EXTRATHYMIC T CELLS//INTERMEDIATE TCR CELL//TCRINT CELLS
4 14699 C FLIP//FADD//DEATH EFFECTOR DOMAIN
5 5991 NEW ZEALAND MICE//RHEUMATOL CLIN MED//MURINE LUPUS
6 9337 AUTOIMMUNE HEMOLYTIC ANEMIA//COLD AGGLUTININ DISEASE//EVANS SYNDROME
7 3006 COMMON VARIABLE IMMUNODEFICIENCY//IGA DEFICIENCY//CVID
8 32410 FIBRINOGEN LIKE PROTEIN 2//FGL2//SOLUBLE FIBRINOGEN LIKE PROTEIN 2
9 31953 DOUBLE POSITIVE T CELLS//GMP UNIT CELLULAR THER Y//CD8 INFECTION
10 110 FOXP3//REGULATORY T CELLS//TREG

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