Class information for:
Level 1: FAMILIAL MEDITERRANEAN FEVER//MEFV//PERIODIC FEVER

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
1684 2535 30.1 79%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
449 3       FAMILIAL MEDITERRANEAN FEVER//TOLL LIKE RECEPTORS//INFLAMMASOME 25887
2102 2             FAMILIAL MEDITERRANEAN FEVER//INFLAMMASOME//NLRP3 5151
1684 1                   FAMILIAL MEDITERRANEAN FEVER//MEFV//PERIODIC FEVER 2535

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 FAMILIAL MEDITERRANEAN FEVER authKW 7903156 31% 84% 777
2 MEFV authKW 1246963 4% 93% 111
3 PERIODIC FEVER authKW 1242199 4% 90% 114
4 FMF authKW 1237230 5% 81% 127
5 MEFV GENE authKW 1108146 4% 99% 93
6 AUTOINFLAMMATORY DISEASE authKW 765942 4% 65% 98
7 PYRIN authKW 501635 2% 73% 57
8 FAMILIAL MEDITERRANEAN FEVER FMF authKW 448382 2% 85% 44
9 AUTOINFLAMMATORY SYNDROMES authKW 439136 2% 65% 56
10 MUCKLE WELLS SYNDROME authKW 424167 1% 93% 38

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Rheumatology 81985 33% 1% 828
2 Pediatrics 3160 13% 0% 328
3 Medicine, General & Internal 2304 15% 0% 385
4 Genetics & Heredity 758 9% 0% 216
5 Immunology 637 9% 0% 237
6 Dermatology 405 4% 0% 90
7 Medicine, Research & Experimental 245 5% 0% 123
8 Urology & Nephrology 164 3% 0% 79
9 Allergy 110 1% 0% 30
10 Otorhinolaryngology 52 1% 0% 35

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HELLER MED 321105 3% 33% 81
2 TRANSLAT AUTOINFLAMMATORY DIS SECT 144912 1% 63% 19
3 UO PEDIAT REUMATOL 2 96350 0% 100% 8
4 GENET GENOM BRANCH 95154 1% 44% 18
5 UNITE MED MALAD AUTOINFLAMMATOI 84796 1% 54% 13
6 PAEDIAT NEPHROL RHEUMATOL 81290 0% 75% 9
7 INTER SYST AUTOIMMUNE AUTOINFLAMMAT 75371 1% 48% 13
8 FMF CLIN 73766 0% 88% 7
9 MED F 72010 1% 18% 33
10 PEDIAT RHEUMATOL NEPHROL 70068 0% 73% 8

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 RHEUMATOLOGY INTERNATIONAL 22000 4% 2% 91
2 CLINICAL AND EXPERIMENTAL RHEUMATOLOGY 18857 4% 2% 93
3 CLINICAL RHEUMATOLOGY 17798 4% 2% 89
4 MODERN RHEUMATOLOGY 12115 1% 3% 36
5 ARTHRITIS AND RHEUMATISM 10254 4% 1% 94
6 PEDIATRIC RHEUMATOLOGY 9663 1% 5% 17
7 ARCHIVES OF RHEUMATOLOGY 8502 0% 6% 11
8 RHEUMATOLOGY 6095 2% 1% 49
9 ANNALS OF THE RHEUMATIC DISEASES 5287 2% 1% 63
10 SEMINARS IN ARTHRITIS AND RHEUMATISM 4777 1% 1% 28

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 FAMILIAL MEDITERRANEAN FEVER 7903156 31% 84% 777 Search FAMILIAL+MEDITERRANEAN+FEVER Search FAMILIAL+MEDITERRANEAN+FEVER
2 MEFV 1246963 4% 93% 111 Search MEFV Search MEFV
3 PERIODIC FEVER 1242199 4% 90% 114 Search PERIODIC+FEVER Search PERIODIC+FEVER
4 FMF 1237230 5% 81% 127 Search FMF Search FMF
5 MEFV GENE 1108146 4% 99% 93 Search MEFV+GENE Search MEFV+GENE
6 AUTOINFLAMMATORY DISEASE 765942 4% 65% 98 Search AUTOINFLAMMATORY+DISEASE Search AUTOINFLAMMATORY+DISEASE
7 PYRIN 501635 2% 73% 57 Search PYRIN Search PYRIN
8 FAMILIAL MEDITERRANEAN FEVER FMF 448382 2% 85% 44 Search FAMILIAL+MEDITERRANEAN+FEVER+FMF Search FAMILIAL+MEDITERRANEAN+FEVER+FMF
9 AUTOINFLAMMATORY SYNDROMES 439136 2% 65% 56 Search AUTOINFLAMMATORY+SYNDROMES Search AUTOINFLAMMATORY+SYNDROMES
10 MUCKLE WELLS SYNDROME 424167 1% 93% 38 Search MUCKLE+WELLS+SYNDROME Search MUCKLE+WELLS+SYNDROME

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 SHOHAT, M , HALPERN, GJ , (2011) FAMILIAL MEDITERRANEAN FEVER-A REVIEW.GENETICS IN MEDICINE. VOL. 13. ISSUE 6. P. 487 -498 115 92% 40
2 DE JESUS, AA , GOLDBACH-MANSKY, R , (2013) MONOGENIC AUTOINFLAMMATORY DISEASES: CONCEPT AND CLINICAL MANIFESTATIONS.CLINICAL IMMUNOLOGY. VOL. 147. ISSUE 3. P. 155-174 112 82% 40
3 RUSSO, RAG , BROGAN, PA , (2014) MONOGENIC AUTOINFLAMMATORY DISEASES.RHEUMATOLOGY. VOL. 53. ISSUE 11. P. 1927 -1939 123 84% 4
4 VITALE, A , RIGANTE, D , LUCHERINI, OM , CASO, F , MUSCARI, I , MAGNOTTI, F , BRIZI, MG , GUERRINI, S , PATTI, M , PUNZI, L , ET AL (2013) BIOLOGICAL TREATMENTS: NEW WEAPONS IN THE MANAGEMENT OF MONOGENIC AUTOINFLAMMATORY DISORDERS.MEDIATORS OF INFLAMMATION. VOL. . ISSUE . P. - 108 84% 10
5 BILGINER, Y , OZEN, S , (2014) A CLINICAL GUIDE TO AUTOINFLAMMATORY DISEASES: FAMILIAL MEDITERRANEAN FEVER AND NEXT-OF-KIN.NATURE REVIEWS RHEUMATOLOGY. VOL. 10. ISSUE 3. P. 135 -147 79 90% 37
6 EL-SHANTI, H , MAJEED, HA , EL-KHATEEB, M , (2006) FAMILIAL MEDITERRANEAN FEVER IN ARABS.LANCET. VOL. 367. ISSUE 9515. P. 1016-1024 99 98% 69
7 STOJANOV, S , KASTNER, DL , (2005) FAMILIAL AUTOINFLAMMATORY DISEASES: GENETICS, PATHOGENESIS AND TREATMENT.CURRENT OPINION IN RHEUMATOLOGY. VOL. 17. ISSUE 5. P. 586-599 96 88% 193
8 FARASAT, S , AKSENTIJEVICH, I , TORO, JR , (2008) AUTOINFLAMMATORY DISEASES - CLINICAL AND GENETIC ADVANCES.ARCHIVES OF DERMATOLOGY. VOL. 144. ISSUE 3. P. 392-402 104 84% 65
9 PORTINCASA, P , (2016) COLCHICINE, BIOLOGIC AGENTS AND MORE FOR THE TREATMENT OF FAMILIAL MEDITERRANEAN FEVER. THE OLD, THE NEW, AND THE RARE.CURRENT MEDICINAL CHEMISTRY. VOL. 23. ISSUE 1. P. 60 -86 91 66% 5
10 BODAR, EJ , DRENTH, JPH , VAN DER MEER, JWM , SIMON, A , (2009) DYSREGULATION OF INNATE IMMUNITY: HEREDITARY PERIODIC FEVER SYNDROMES.BRITISH JOURNAL OF HAEMATOLOGY. VOL. 144. ISSUE 3. P. 279 -302 129 70% 19

Classes with closest relation at Level 1



Rank Class id link
1 20741 COLCHICINE//COLCHICINE POISONING//COLCHICUM AUTUMNALE
2 2156 INFLAMMASOME//NLRP3//CASPASE 1
3 23188 SCHNITZLER SYNDROME//URTICARIAL VASCULITIS//HYPOCOMPLEMENTEMIC URTICARIAL VASCULITIS SYNDROME
4 26333 IGD RECEPTOR//IGD MYELOMA//IGD
5 10685 NOD2//NOD1//BLAU SYNDROME
6 29002 AMYLOID GOITER//PARATHYROID LIPOADENOMA//THYROLIPOMA
7 24016 MEVALONATE DIPHOSPHATE DECARBOXYLASE//MEVALONATE PYROPHOSPHATE DECARBOXYLASE//MEVALONATE KINASE
8 15548 ADULT ONSET STILLS DISEASE//STILLS DISEASE//ADULT STILLS DISEASE
9 32401 PALINDROMIC RHEUMATISM//RELAPSING ARTHRITIS//ANTICITRULLINATED PEPTIDE PROTEIN ANTIBODIES
10 403 AMYLOIDOSIS//AL AMYLOIDOSIS//CARDIAC AMYLOIDOSIS

Go to start page