Class information for:
Level 1: ALKAPTONURIA//OCHRONOSIS//HOMOGENTISIC ACID

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
21992 398 21.4 55%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
537 3       BIOARTIFICIAL LIVER//HEPATOCYTES//HEPATOCYTE TRANSPLANTATION 19236
3543 2             ALKAPTONURIA//OCHRONOSIS//HOMOGENTISIC ACID 1359
21992 1                   ALKAPTONURIA//OCHRONOSIS//HOMOGENTISIC ACID 398

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ALKAPTONURIA authKW 9245648 34% 90% 134
2 OCHRONOSIS authKW 7594179 28% 88% 113
3 HOMOGENTISIC ACID authKW 2797608 14% 65% 56
4 OCHRONOTIC ARTHROPATHY authKW 1457702 5% 100% 19
5 INTERDIPARTIMENTALE STUDIO BIOCHIM PATOL OSTE address 545571 2% 89% 8
6 ALCAPTONURIA authKW 517863 2% 75% 9
7 CHROMHIDROSIS authKW 469915 2% 88% 7
8 HOMOGENTISATE 1 2 DIOXYGENASE authKW 469915 2% 88% 7
9 OCHRONOTIC ARTHRITIS authKW 460327 2% 100% 6
10 ALK TONURIA OFF address 306885 1% 100% 4

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Rheumatology 4692 20% 0% 79
2 Orthopedics 708 12% 0% 47
3 Dermatology 425 8% 0% 33
4 Genetics & Heredity 356 14% 0% 54
5 Medical Laboratory Technology 180 4% 0% 15
6 Medicine, Research & Experimental 171 9% 0% 35
7 Pathology 145 6% 0% 24
8 Endocrinology & Metabolism 127 8% 0% 32
9 Medicine, General & Internal 65 8% 0% 30
10 Cardiac & Cardiovascular System 46 6% 0% 22

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 INTERDIPARTIMENTALE STUDIO BIOCHIM PATOL OSTE 545571 2% 89% 8
2 ALK TONURIA OFF 306885 1% 100% 4
3 CLIN BIOCHEM METAB 92056 2% 20% 6
4 UNIDAD PATOL MOL 87175 1% 23% 5
5 ADOLESCENT MED YOUNG PARENTS PROGRAM 76721 0% 100% 1
6 AIMAKU 76721 0% 100% 1
7 ALKPTONURIA OFF 76721 0% 100% 1
8 DIAG TREATMENT PREVENT KIDNEY STONES 76721 0% 100% 1
9 DIPARTIMENTO PEDIAT OSTET MED 76721 0% 100% 1
10 HNO KLIN POLIKLIN OTTO KOMER 76721 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF INHERITED METABOLIC DISEASE 7457 5% 0% 21
2 CLINICAL RHEUMATOLOGY 4143 4% 0% 17
3 ACTA ORTHOPAEDICA ET TRAUMATOLOGICA TURCICA 2323 1% 1% 5
4 ZEITSCHRIFT FUR RHEUMATOLOGIE 2093 2% 0% 8
5 RHEUMATOLOGY INTERNATIONAL 2042 3% 0% 11
6 GENE GEOGRAPHY 1143 0% 1% 1
7 ARCHIVES D ANATOMIE ET DE CYTOLOGIE PATHOLOGIQUES 860 0% 1% 1
8 JCR-JOURNAL OF CLINICAL RHEUMATOLOGY 823 1% 0% 4
9 ZEITSCHRIFT FUR ORTHOPADIE UND IHRE GRENZGEBIETE 796 1% 0% 5
10 JOURNAL OF HEART VALVE DISEASE 777 1% 0% 5

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 ALKAPTONURIA 9245648 34% 90% 134 Search ALKAPTONURIA Search ALKAPTONURIA
2 OCHRONOSIS 7594179 28% 88% 113 Search OCHRONOSIS Search OCHRONOSIS
3 HOMOGENTISIC ACID 2797608 14% 65% 56 Search HOMOGENTISIC+ACID Search HOMOGENTISIC+ACID
4 OCHRONOTIC ARTHROPATHY 1457702 5% 100% 19 Search OCHRONOTIC+ARTHROPATHY Search OCHRONOTIC+ARTHROPATHY
5 ALCAPTONURIA 517863 2% 75% 9 Search ALCAPTONURIA Search ALCAPTONURIA
6 CHROMHIDROSIS 469915 2% 88% 7 Search CHROMHIDROSIS Search CHROMHIDROSIS
7 HOMOGENTISATE 1 2 DIOXYGENASE 469915 2% 88% 7 Search HOMOGENTISATE+1+2+DIOXYGENASE Search HOMOGENTISATE+1+2+DIOXYGENASE
8 OCHRONOTIC ARTHRITIS 460327 2% 100% 6 Search OCHRONOTIC+ARTHRITIS Search OCHRONOTIC+ARTHRITIS
9 DARK URINE 245506 1% 80% 4 Search DARK+URINE Search DARK+URINE
10 ALKAPTONURIA COMPLICATIONS 230164 1% 100% 3 Search ALKAPTONURIA+COMPLICATIONS Search ALKAPTONURIA+COMPLICATIONS

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 KHALED, A , KERKENI, N , HAWILO, A , FAZAA, B , KAMOUN, MR , (2011) ENDOGENOUS OCHRONOSIS: CASE REPORT AND A SYSTEMATIC REVIEW OF THE LITERATURE.INTERNATIONAL JOURNAL OF DERMATOLOGY. VOL. 50. ISSUE 3. P. 262 -267 34 100% 7
2 RANGANATH, LR , PSARELLI, EE , COX, TF , GALLAGHER, JA , (2015) DIAGNOSTIC TOOLS AND STRATEGIES FOR ASSESSING DISEASE PROGRESSION IN ALKAPTONURIA.EXPERT OPINION ON ORPHAN DRUGS. VOL. 3. ISSUE 6. P. 705 -717 41 68% 0
3 ZATKOVA, A , (2011) AN UPDATE ON MOLECULAR GENETICS OF ALKAPTONURIA (AKU).JOURNAL OF INHERITED METABOLIC DISEASE. VOL. 34. ISSUE 6. P. 1127-1136 29 88% 23
4 BRACONI, D , MILLUCCI, L , BERNARDINI, G , SANTUCCI, A , (2015) OXIDATIVE STRESS AND MECHANISMS OF OCHRONOSIS IN ALKAPTONURIA.FREE RADICAL BIOLOGY AND MEDICINE. VOL. 88. ISSUE . P. 70 -80 38 56% 2
5 RANGANATH, LR , JARVIS, JC , GALLAGHER, JA , (2013) RECENT ADVANCES IN MANAGEMENT OF ALKAPTONURIA (INVITED REVIEW; BEST PRACTICE ARTICLE).JOURNAL OF CLINICAL PATHOLOGY. VOL. 66. ISSUE 5. P. 367-373 21 95% 14
6 GIL, JA , WAWRZYNSKI, J , WARYASZ, GR , (2016) ORTHOPEDIC MANIFESTATIONS OF OCHRONOSIS: PATHOPHYSIOLOGY, PRESENTATION, DIAGNOSIS, AND MANAGEMENT.AMERICAN JOURNAL OF MEDICINE. VOL. 129. ISSUE 5. P. - 18 100% 1
7 VENTURA-RIOS, L , HERNANDEZ-DIAZ, C , GUTIERREZ-PEREZ, L , BERNAL-GONZALEZ, A , PICHARDO-BAHENA, R , CEDENO-GARCIDUENAS, AL , PINEDA, C , (2016) OCHRONOTIC ARTHROPATHY AS A PARADIGM OF METABOLICALLY INDUCED DEGENERATIVE JOINT DISEASE. A CASE-BASED REVIEW.CLINICAL RHEUMATOLOGY. VOL. 35. ISSUE 5. P. 1389 -1395 20 91% 0
8 AQUARON, RR , (2011) ALKAPTONURIA IN FRANCE: PAST EXPERIENCE AND LESSONS FOR THE FUTURE.JOURNAL OF INHERITED METABOLIC DISEASE. VOL. 34. ISSUE 6. P. 1115-1126 19 100% 7
9 NEMETHOVA, M , RADVANSZKY, J , KADASI, L , ASCHER, DB , PIRES, DEV , BLUNDELL, TL , PORFIRIO, B , MANNONI, A , SANTUCCI, A , MILUCCI, L , ET AL (2016) TWELVE NOVEL HGD GENE VARIANTS IDENTIFIED IN 99 ALKAPTONURIA PATIENTS: FOCUS ON 'BLACK BONE DISEASE' IN ITALY.EUROPEAN JOURNAL OF HUMAN GENETICS. VOL. 24. ISSUE 1. P. 66 -72 19 76% 2
10 MANNONI, A , SELVI, E , LORENZINI, S , GIORGI, M , AIRO, P , CAMMELLI, D , ANDREOTTI, L , MARCOLONGO, R , PORFIRIO, B , (2004) ALKAPTONURIA, OCHRONOSIS, AND OCHRONOTIC ARTHROPATHY.SEMINARS IN ARTHRITIS AND RHEUMATISM. VOL. 33. ISSUE 4. P. 239-248 22 92% 35

Classes with closest relation at Level 1



Rank Class id link
1 12756 TYROSINEMIA//SUCCINYLACETONE//NTBC
2 36591 PURPLE URINE BAG SYNDROME//PURPLE URINE//URINARY BAG
3 21834 BLACK THYROID//MINOCYCLINE//MINOCYCLINE PIGMENTATION
4 7922 MELASMA//NEVUS OF OTA//CHLOASMA
5 36907 PACHYDERMODACTYLY//ATROPHIA MACULOSA VARIOLIFORMIS CUTIS//DIGITAL FIBROMATOSIS
6 35736 ST PETERSBURG INFORMAT AUTOMAT//CULTURAL RULES//MATHEMATICAL ANTHROPOLOGY
7 23275 SYNOVIAL BIOPSY//SYNOVIAL TISSUE//SYNOVIAL BIOMARKERS
8 12466 DIFFUSE IDIOPATHIC SKELETAL HYPEROSTOSIS//DISH//FORESTIERS DISEASE
9 13786 TUMORAL CALCINOSIS//CALCINOSIS//CALCINOSIS CUTIS
10 28711 SYNTHET INORGAN METALLOORGAN//SYNTHET INORG METALLOORGAN//1 PHENYL 2 3 DIMETHYL 4 AMINOPYRAZOL 5 ONE

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