Class information for:
Level 1: TYROSINEMIA//SUCCINYLACETONE//NTBC

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
12756 883 27.3 64%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
537 3       BIOARTIFICIAL LIVER//HEPATOCYTES//HEPATOCYTE TRANSPLANTATION 19236
3543 2             ALKAPTONURIA//OCHRONOSIS//HOMOGENTISIC ACID 1359
12756 1                   TYROSINEMIA//SUCCINYLACETONE//NTBC 883

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 TYROSINEMIA authKW 1400459 6% 75% 54
2 SUCCINYLACETONE authKW 985112 4% 81% 35
3 NTBC authKW 806064 3% 90% 26
4 TYROSINEMIA TYPE I authKW 619869 2% 81% 22
5 SULCOTRIONE authKW 603564 3% 73% 24
6 4 HYDROXYPHENYLPYRUVATE DIOXYGENASE authKW 540292 3% 63% 25
7 FUMARYLACETOACETATE HYDROLASE authKW 508312 2% 70% 21
8 TYROSINEMIA TYPE II authKW 449539 1% 100% 13
9 MESOTRIONE authKW 420531 3% 41% 30
10 HEREDITARY TYROSINEMIA TYPE 1 authKW 389597 1% 87% 13

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Genetics & Heredity 1785 20% 0% 173
2 Medicine, Research & Experimental 984 13% 0% 118
3 Pediatrics 876 12% 0% 103
4 Endocrinology & Metabolism 518 10% 0% 92
5 Medical Laboratory Technology 343 4% 0% 31
6 Biochemistry & Molecular Biology 307 19% 0% 171
7 Dermatology 73 3% 0% 24
8 Chemistry, Medicinal 63 3% 0% 29
9 Entomology 55 2% 0% 21
10 Biochemical Research Methods 46 3% 0% 30

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 MIDWEST FETAL CARE 69160 0% 100% 2
2 ERROS INATOS METAB 36267 1% 13% 8
3 GENET CELLULAIRE DEV 36013 1% 21% 5
4 ALLGEMEINE KINDERHEILKUNDE JUGENDMED 34580 0% 100% 1
5 AUTON UNIV MADRID 34580 0% 100% 1
6 BIOC TEURS ANALYSE ENVIRONM 34580 0% 100% 1
7 BIOCHEM GENET CLIN 34580 0% 100% 1
8 C FSIP 34580 0% 100% 1
9 CENT CHEM PESTICIDE 34580 0% 100% 1
10 CHILD HLTHBIOCHEM GENET UNIT 34580 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF INHERITED METABOLIC DISEASE 31266 7% 1% 64
2 MOLECULAR GENETICS AND METABOLISM 3563 2% 1% 18
3 BIOCHEMICAL MEDICINE AND METABOLIC BIOLOGY 796 0% 1% 4
4 CLINICA CHIMICA ACTA 777 2% 0% 16
5 PEDIATRIC RESEARCH 619 1% 0% 13
6 HUMAN MUTATION 543 1% 0% 8
7 PESTICIDE BIOCHEMISTRY AND PHYSIOLOGY 538 1% 0% 7
8 PEST MANAGEMENT SCIENCE 536 1% 0% 7
9 AMERICAN JOURNAL OF HUMAN GENETICS 502 1% 0% 11
10 ORPHANET JOURNAL OF RARE DISEASES 491 0% 0% 4

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 TYROSINEMIA 1400459 6% 75% 54 Search TYROSINEMIA Search TYROSINEMIA
2 SUCCINYLACETONE 985112 4% 81% 35 Search SUCCINYLACETONE Search SUCCINYLACETONE
3 NTBC 806064 3% 90% 26 Search NTBC Search NTBC
4 TYROSINEMIA TYPE I 619869 2% 81% 22 Search TYROSINEMIA+TYPE+I Search TYROSINEMIA+TYPE+I
5 SULCOTRIONE 603564 3% 73% 24 Search SULCOTRIONE Search SULCOTRIONE
6 4 HYDROXYPHENYLPYRUVATE DIOXYGENASE 540292 3% 63% 25 Search 4+HYDROXYPHENYLPYRUVATE+DIOXYGENASE Search 4+HYDROXYPHENYLPYRUVATE+DIOXYGENASE
7 FUMARYLACETOACETATE HYDROLASE 508312 2% 70% 21 Search FUMARYLACETOACETATE+HYDROLASE Search FUMARYLACETOACETATE+HYDROLASE
8 TYROSINEMIA TYPE II 449539 1% 100% 13 Search TYROSINEMIA+TYPE+II Search TYROSINEMIA+TYPE+II
9 MESOTRIONE 420531 3% 41% 30 Search MESOTRIONE Search MESOTRIONE
10 HEREDITARY TYROSINEMIA TYPE 1 389597 1% 87% 13 Search HEREDITARY+TYROSINEMIA+TYPE+1 Search HEREDITARY+TYROSINEMIA+TYPE+1

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 DUMAS, E , GIRAUDO, M , GOUJON, E , HALMA, M , KNHILI, E , STAUFFERT, M , BATISSON, I , BESSE-HOGGAN, P , BOHATIER, JT , BOUCHARD, P , ET AL (2017) FATE AND ECOTOXICOLOGICAL IMPACT OF NEW GENERATION HERBICIDES FROM THE TRIKETONE FAMILY: AN OVERVIEW TO ASSESS THE ENVIRONMENTAL RISKS.JOURNAL OF HAZARDOUS MATERIALS. VOL. 325. ISSUE . P. 136 -156 87 52% 0
2 SANTRA, S , BAUMANN, U , (2008) EXPERIENCE OF NITISINONE FOR THE PHARMACOLOGICAL TREATMENT OF HEREDITARY TYROSINAEMIA TYPE 1.EXPERT OPINION ON PHARMACOTHERAPY. VOL. 9. ISSUE 7. P. 1229-1236 46 94% 19
3 PITKANEN, ST , SALO, MK , HEIKINHEIMO, M , (2000) HEREDITARY TYROSINAEMIA TYPE I: FROM BASICS TO PROGRESS IN TREATMENT.ANNALS OF MEDICINE. VOL. 32. ISSUE 8. P. 530 -538 62 86% 9
4 MAYORANDAN, S , MEYER, U , GOKCAY, G , SEGARRA, NG , DE BAULNY, HO , VAN SPRONSEN, F , ZEMAN, J , DE LAET, C , SPIEKERKOETTER, U , THIMM, E , ET AL (2014) CROSS-SECTIONAL STUDY OF 168 PATIENTS WITH HEPATORENAL TYROSINAEMIA AND IMPLICATIONS FOR CLINICAL PRACTICE.ORPHANET JOURNAL OF RARE DISEASES. VOL. 9. ISSUE . P. - 35 95% 12
5 RUSSO, PA , MITCHELL, GA , TANGUAY, RM , (2001) TYROSINEMIA: A REVIEW.PEDIATRIC AND DEVELOPMENTAL PATHOLOGY. VOL. 4. ISSUE 3. P. 212-221 57 81% 73
6 ZEYBEK, ACA , KIYKIM, E , SOYUCEN, E , CANSEVER, S , ALTAY, S , ZUBARIOGLU, T , ERKAN, T , AYDIN, A , (2015) HEREDITARY TYROSINEMIA TYPE 1 IN TURKEY: TWENTY YEAR SINGLE-CENTER EXPERIENCE.PEDIATRICS INTERNATIONAL. VOL. 57. ISSUE 2. P. 281 -289 33 94% 4
7 MCKIERNAN, PJ , (2006) NITISINONE IN THE TREATMENT OF HEREDITARY TYROSINAEMIA TYPE 1.DRUGS. VOL. 66. ISSUE 6. P. 743-750 38 97% 39
8 GROMPE, M , (2001) THE PATHOPHYSIOLOGY AND TREATMENT OF HEREDITARY TYROSINEMIA TYPE 1.SEMINARS IN LIVER DISEASE. VOL. 21. ISSUE 4. P. 563-571 53 77% 63
9 DE LAET, C , DIONISI-VICI, C , LEONARD, JV , MCKIERNAN, P , MITCHELL, G , MONTI, L , DE BAULNY, HO , PINTOS-MORELL, G , SPIEKERKOTTER, U , (2013) RECOMMENDATIONS FOR THE MANAGEMENT OF TYROSINAEMIA TYPE 1.ORPHANET JOURNAL OF RARE DISEASES. VOL. 8. ISSUE . P. - 29 94% 24
10 NASRALLAH, F , HAMMAMI, MB , BEN RHOUMA, H , FRADJ, SH , AZZOUZ, H , OMAR, S , FEKI, M , BEN YOUSSEF, IT , MESSAOUD, T , TEBIB, N , ET AL (2015) CLINICAL AND BIOCHEMICAL PROFILE OF TYROSINEMIA TYPE 1 IN TUNISIA.CLINICAL LABORATORY. VOL. 61. ISSUE 5-6. P. 487 -492 29 100% 0

Classes with closest relation at Level 1



Rank Class id link
1 21992 ALKAPTONURIA//OCHRONOSIS//HOMOGENTISIC ACID
2 29439 ALPHA GLUTATHIONE S TRANSFERASE//ENZYMES GLUTATHIONE S TRANSFERASE//ALPHA GLUTATHIONE TRANSFERASES
3 18536 HOMOGENTISATE PHYTYLTRANSFERASE//GAMMA TOCOPHEROL METHYLTRANSFERASE//TOCOCHROMANOLS
4 10958 PHOSPHOENOLPYRUVATE CARBOXYKINASE//GLYCERONEOGENESIS//BROWN ADIPOSE TISSUE HEMIDENERVATION
5 24639 8 AZASTEROID//1 ALKYL 3 4 DIHYDROISOQUINOLINES//2 ACYLCYCLOHEXANE 1 3 DIONES
6 32585 JOURNAL OF PESTICIDE SCIENCE//3 TRIAZOLYLTHIOACETIC ACID//5H 1 3 4THIADIAZOLO3 2 APYRIMIDINE 6 CARBOXYLATE
7 29283 HEMATOLOGICAL AND CLINICOCHEMICAL PARAMETERS//URINOMETER//WHOLE BLOOD WATER
8 16858 MAMMALIAN GENET UNIT//ENU MUTAGENESIS//PHENOTYPE DRIVEN SCREEN
9 20380 TERT BUTYLDIMETHYLSILYLATION//PROTEINOUS AMINO ACIDS//STAR SYMBOL PLOT
10 29066 INTERMEDIATE VOLTAGE EM//BIOCI ENGN//CELL CALCIUM TMB 8

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