Class information for: |
Basic class information |
Class id | #P | Avg. number of references |
Database coverage of references |
---|---|---|---|
21807 | 405 | 30.6 | 72% |
Hierarchy of classes |
The table includes all classes above and classes immediately below the current class. |
Cluster id | Level | Cluster label | #P |
---|---|---|---|
0 | 4 | BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY | 4064930 |
631 | 3 | KYNURENINE//NEOPTERIN//INDOLEAMINE 2 3 DIOXYGENASE | 12928 |
1475 | 2 | THIAMINE//THIAMINE DEFICIENCY//WERNICKES ENCEPHALOPATHY | 7673 |
21807 | 1 | BENFOTIAMINE//SLC19A2//SLC19A3 | 405 |
Terms with highest relevance score |
rank | Term | termType | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|---|
1 | BENFOTIAMINE | authKW | 1115252 | 7% | 53% | 28 |
2 | SLC19A2 | authKW | 892830 | 4% | 79% | 15 |
3 | SLC19A3 | authKW | 796356 | 3% | 81% | 13 |
4 | TRMA | authKW | 707869 | 3% | 72% | 13 |
5 | THIAMINE RESPONSIVE MEGALOBLASTIC ANEMIA | authKW | 608181 | 3% | 73% | 11 |
6 | THIAMINE | authKW | 530539 | 18% | 10% | 74 |
7 | SLC19A2 GENE | authKW | 376976 | 1% | 100% | 5 |
8 | THIAMINE TRANSPORT | authKW | 369432 | 2% | 70% | 7 |
9 | BIOTIN RESPONSIVE BASAL GANGLIA DISEASE | authKW | 301580 | 1% | 100% | 4 |
10 | THIAMINE TRANSPORTER 2 DEFICIENCY | authKW | 301580 | 1% | 100% | 4 |
Web of Science journal categories |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|
1 | Endocrinology & Metabolism | 714 | 17% | 0% | 69 |
2 | Pediatrics | 416 | 12% | 0% | 48 |
3 | Physiology | 278 | 10% | 0% | 40 |
4 | Clinical Neurology | 260 | 12% | 0% | 50 |
5 | Genetics & Heredity | 241 | 11% | 0% | 46 |
6 | Nutrition & Dietetics | 182 | 6% | 0% | 25 |
7 | Gastroenterology & Hepatology | 155 | 7% | 0% | 27 |
8 | Medicine, Research & Experimental | 98 | 7% | 0% | 28 |
9 | Pharmacology & Pharmacy | 68 | 10% | 0% | 41 |
10 | Biochemistry & Molecular Biology | 48 | 14% | 0% | 55 |
Address terms |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|
1 | DIAGNOST ENFERMEDADES MOL CEDEM BIOL MOL | 150790 | 0% | 100% | 2 |
2 | TAMKIN HUMAN MOL GENET IL | 86160 | 1% | 29% | 4 |
3 | ADFELING FARMACOL | 75395 | 0% | 100% | 1 |
4 | BIOMED SCI HEALTH | 75395 | 0% | 100% | 1 |
5 | BIOPHARMACEUT SCI THER EUT | 75395 | 0% | 100% | 1 |
6 | CEFALU PA | 75395 | 0% | 100% | 1 |
7 | CIMA NEUROSCI | 75395 | 0% | 100% | 1 |
8 | DIGEST DISPRINCE WALES HOSP | 75395 | 0% | 100% | 1 |
9 | GENET CYTOGENETFEDERAT GENET | 75395 | 0% | 100% | 1 |
10 | INBORN ERRORS METABOLISM IBC | 75395 | 0% | 100% | 1 |
Journals |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|
1 | DIABETES STOFFWECHSEL UND HERZ | 4779 | 1% | 2% | 4 |
2 | AMERICAN JOURNAL OF PHYSIOLOGY-GASTROINTESTINAL AND LIVER PHYSIOLOGY | 3897 | 4% | 0% | 18 |
3 | CARDIOVASCULAR TOXICOLOGY | 1621 | 1% | 1% | 3 |
4 | MOLECULAR GENETICS AND METABOLISM | 1173 | 2% | 0% | 7 |
5 | JOURNAL OF NUTRITIONAL SCIENCE AND VITAMINOLOGY | 1026 | 1% | 0% | 6 |
6 | PEDIATRIC NEUROLOGY | 862 | 2% | 0% | 7 |
7 | AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY | 837 | 2% | 0% | 9 |
8 | DIABETES-METABOLISM RESEARCH AND REVIEWS | 834 | 1% | 0% | 4 |
9 | ACTA DIABETOLOGICA | 767 | 1% | 0% | 4 |
10 | INTERNATIONAL JOURNAL OF DIABETES IN DEVELOPING COUNTRIES | 696 | 0% | 0% | 2 |
Author Key Words |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
LCSH search | Wikipedia search |
---|---|---|---|---|---|---|---|
1 | BENFOTIAMINE | 1115252 | 7% | 53% | 28 | Search BENFOTIAMINE | Search BENFOTIAMINE |
2 | SLC19A2 | 892830 | 4% | 79% | 15 | Search SLC19A2 | Search SLC19A2 |
3 | SLC19A3 | 796356 | 3% | 81% | 13 | Search SLC19A3 | Search SLC19A3 |
4 | TRMA | 707869 | 3% | 72% | 13 | Search TRMA | Search TRMA |
5 | THIAMINE RESPONSIVE MEGALOBLASTIC ANEMIA | 608181 | 3% | 73% | 11 | Search THIAMINE+RESPONSIVE+MEGALOBLASTIC+ANEMIA | Search THIAMINE+RESPONSIVE+MEGALOBLASTIC+ANEMIA |
6 | THIAMINE | 530539 | 18% | 10% | 74 | Search THIAMINE | Search THIAMINE |
7 | SLC19A2 GENE | 376976 | 1% | 100% | 5 | Search SLC19A2+GENE | Search SLC19A2+GENE |
8 | THIAMINE TRANSPORT | 369432 | 2% | 70% | 7 | Search THIAMINE+TRANSPORT | Search THIAMINE+TRANSPORT |
9 | BIOTIN RESPONSIVE BASAL GANGLIA DISEASE | 301580 | 1% | 100% | 4 | Search BIOTIN+RESPONSIVE+BASAL+GANGLIA+DISEASE | Search BIOTIN+RESPONSIVE+BASAL+GANGLIA+DISEASE |
10 | THIAMINE TRANSPORTER 2 DEFICIENCY | 301580 | 1% | 100% | 4 | Search THIAMINE+TRANSPORTER+2+DEFICIENCY | Search THIAMINE+TRANSPORTER+2+DEFICIENCY |
Core articles |
The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c: (1) Number of references referring to publications in the class. (2) Share of total number of active references referring to publications in the class. (3) Age of the article. New articles get higher score than old articles. (4) Citation rate, normalized to year. |
Rank | Reference | # ref. in cl. |
Shr. of ref. in cl. |
Citations |
---|---|---|---|---|
1 | ORTIGOZA-ESCOBAR, JD , MOLERO-LUIS, M , ARIAS, A , MARTI-SANCHEZ, L , RODRIGUEZ-POMBO, P , ARTUCH, R , PEREZ-DUENAS, B , (2016) TREATMENT OF GENETIC DEFECTS OF THIAMINE TRANSPORT AND METABOLISM.EXPERT REVIEW OF NEUROTHERAPEUTICS. VOL. 16. ISSUE 7. P. 755 -763 | 50 | 86% | 0 |
2 | BERGMANN, AK , SAHAI, I , FALCONE, JF , FLEMING, J , BAGG, A , BORGNA-PIGNATI, C , CASEY, R , FABRIS, L , HEXNER, E , MATHEWS, L , ET AL (2009) THIAMINE-RESPONSIVE MEGALOBLASTIC ANEMIA: IDENTIFICATION OF NOVEL COMPOUND HETEROZYGOTES AND MUTATION UPDATE.JOURNAL OF PEDIATRICS. VOL. 155. ISSUE 6. P. 888 -U356 | 23 | 96% | 21 |
3 | ALGAHTANI, H , GHAMDI, S , SHIRAH, B , ALHARBI, B , ALGAHTANI, R , BAZAID, A , (2017) BIOTIN-THIAMINE-RESPONSIVE BASAL GANGLIA DISEASE: CATASTROPHIC CONSEQUENCES OF DELAY IN DIAGNOSIS AND TREATMENT.NEUROLOGICAL RESEARCH. VOL. 39. ISSUE 2. P. 117 -125 | 18 | 95% | 0 |
4 | SRIKRUPA, NN , MEENAKSHI, S , AROKIASAMY, T , MURALI, K , SOUMITTRA, N , (2014) LEBER'S CONGENITAL AMAUROSIS AS THE RETINAL DEGENERATIVE PHENOTYPE IN THIAMINE RESPONSIVE MEGALOBLASTIC ANEMIA: A CASE REPORT.OPHTHALMIC GENETICS. VOL. 35. ISSUE 2. P. 119-124 | 21 | 81% | 3 |
5 | BROWN, G , (2014) DEFECTS OF THIAMINE TRANSPORT AND METABOLISM.JOURNAL OF INHERITED METABOLIC DISEASE. VOL. 37. ISSUE 4. P. 577 -585 | 26 | 58% | 12 |
6 | AGLADIOGLU, SY , AYCAN, Z , BAS, VN , KENDIRCI, HNP , ONDER, A , (2012) THIAMINE-RESPONSIVE MEGALOBLASTIC ANEMIA SYNDROME: A NOVEL MUTATION.GENETIC COUNSELING. VOL. 23. ISSUE 2. P. 149-156 | 17 | 100% | 5 |
7 | MEE, L , NABOKINA, SM , SEKAR, VT , SUBRAMANIAN, VS , MAEDLER, K , SAID, HM , (2009) PANCREATIC BETA CELLS AND ISLETS TAKE UP THIAMIN BY A REGULATED CARRIER-MEDIATED PROCESS: STUDIES USING MICE AND HUMAN PANCREATIC PREPARATIONS.AMERICAN JOURNAL OF PHYSIOLOGY-GASTROINTESTINAL AND LIVER PHYSIOLOGY. VOL. 297. ISSUE 1. P. G197-G206 | 25 | 74% | 6 |
8 | MOZZILLO, E , MELIS, D , FALCO, M , FATTORUSSO, V , TAURISANO, R , FLANAGAN, SE , ELLARD, S , FRANZESE, A , (2013) THIAMINE RESPONSIVE MEGALOBLASTIC ANEMIA: A NOVEL SLC19A2 COMPOUND HETEROZYGOUS MUTATION IN TWO SIBLINGS.PEDIATRIC DIABETES. VOL. 14. ISSUE 5. P. 384-387 | 15 | 100% | 2 |
9 | ONAL, H , BARIS, S , OZDIL, M , YESIL, G , ALTUN, G , OZYILMAZ, I , AYDIN, A , CELKAN, T , (2009) THIAMINE-RESPONSIVE MEGALOBLASTIC ANEMIA: EARLY DIAGNOSIS MAY BE EFFECTIVE IN PREVENTING DEAFNESS.TURKISH JOURNAL OF PEDIATRICS. VOL. 51. ISSUE 3. P. 301-304 | 16 | 100% | 12 |
10 | RABBANI, N , THORNALLEY, PJ , (2011) EMERGING ROLE OF THIAMINE THERAPY FOR PREVENTION AND TREATMENT OF EARLY-STAGE DIABETIC NEPHROPATHY.DIABETES OBESITY & METABOLISM. VOL. 13. ISSUE 7. P. 577 -583 | 30 | 49% | 16 |
Classes with closest relation at Level 1 |