Class information for:
Level 1: KRABBE DISEASE//GLOBOID CELL LEUKODYSTROPHY//PSYCHOSINE

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
16795 635 32.9 68%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
551 3       FABRY DISEASE//GAUCHER DISEASE//LYSOSOMAL STORAGE DISEASE 18099
491 2             GAUCHER DISEASE//LYSOSOMAL STORAGE DISEASE//MUCOPOLYSACCHARIDOSIS 15457
16795 1                   KRABBE DISEASE//GLOBOID CELL LEUKODYSTROPHY//PSYCHOSINE 635

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 KRABBE DISEASE authKW 6948364 27% 85% 170
2 GLOBOID CELL LEUKODYSTROPHY authKW 4719670 16% 96% 102
3 PSYCHOSINE authKW 2567236 10% 86% 62
4 GALACTOCEREBROSIDASE authKW 1649628 6% 84% 41
5 TWITCHER MOUSE authKW 1400316 5% 94% 31
6 TWITCHER authKW 1017494 4% 92% 23
7 TWITCHER MICE authKW 625117 2% 100% 13
8 GALC authKW 569432 2% 79% 15
9 GALACTOSYLCERAMIDASE authKW 494595 2% 86% 12
10 GALC GENE authKW 288515 1% 100% 6

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 1968 25% 0% 159
2 Neurosciences 1928 33% 0% 210
3 Pathology 583 9% 0% 58
4 Genetics & Heredity 580 14% 0% 87
5 Pediatrics 574 11% 0% 71
6 Neuroimaging 415 3% 0% 21
7 Medicine, Research & Experimental 402 10% 0% 66
8 Biochemistry & Molecular Biology 226 20% 0% 124
9 Cell & Tissue Engineering 164 2% 0% 10
10 Medical Laboratory Technology 119 3% 0% 16

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HUNTER JAMES KELLY 204117 2% 28% 15
2 POPULAT HLTH OBSERV 173104 1% 60% 6
3 LYSOSOMAL DIS TESTING 171733 1% 71% 5
4 FDN GILLET MERIEUX 116351 2% 22% 11
5 NEUROL 2E311 96172 0% 100% 2
6 U189 77884 1% 18% 9
7 UNIT HUMAN ANAT HISTOL 54093 0% 38% 3
8 AXOGLIA INTERACT UNIT INSPE 48086 0% 100% 1
9 CHILD HEALTHCARE GENET SCI 48086 0% 100% 1
10 CHILD NEUROL PATHOL 48086 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF NEUROSCIENCE RESEARCH 13160 8% 1% 49
2 PEDIATRIC NEUROLOGY 5475 3% 1% 22
3 NEUROPEDIATRICS 2850 2% 1% 11
4 MOLECULAR GENETICS AND METABOLISM 2585 2% 0% 13
5 JOURNAL OF INHERITED METABOLIC DISEASE 1775 2% 0% 13
6 JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY 1515 2% 0% 10
7 ACTA NEUROPATHOLOGICA 1376 2% 0% 13
8 BRAIN & DEVELOPMENT 835 1% 0% 8
9 NEUROBIOLOGY OF DISEASE 827 1% 0% 8
10 BIOCHEMICAL AND MOLECULAR MEDICINE 804 0% 1% 2

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 KRABBE DISEASE 6948364 27% 85% 170 Search KRABBE+DISEASE Search KRABBE+DISEASE
2 GLOBOID CELL LEUKODYSTROPHY 4719670 16% 96% 102 Search GLOBOID+CELL+LEUKODYSTROPHY Search GLOBOID+CELL+LEUKODYSTROPHY
3 PSYCHOSINE 2567236 10% 86% 62 Search PSYCHOSINE Search PSYCHOSINE
4 GALACTOCEREBROSIDASE 1649628 6% 84% 41 Search GALACTOCEREBROSIDASE Search GALACTOCEREBROSIDASE
5 TWITCHER MOUSE 1400316 5% 94% 31 Search TWITCHER+MOUSE Search TWITCHER+MOUSE
6 TWITCHER 1017494 4% 92% 23 Search TWITCHER Search TWITCHER
7 TWITCHER MICE 625117 2% 100% 13 Search TWITCHER+MICE Search TWITCHER+MICE
8 GALC 569432 2% 79% 15 Search GALC Search GALC
9 GALACTOSYLCERAMIDASE 494595 2% 86% 12 Search GALACTOSYLCERAMIDASE Search GALACTOSYLCERAMIDASE
10 GALC GENE 288515 1% 100% 6 Search GALC+GENE Search GALC+GENE

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 GRAZIANO, ACE , CARDILE, V , (2015) HISTORY, GENETIC, AND RECENT ADVANCES ON KRABBE DISEASE.GENE. VOL. 555. ISSUE 1. P. 2 -13 111 93% 13
2 WON, JS , SINGH, AK , SINGH, I , (2016) BIOCHEMICAL, CELL BIOLOGICAL, PATHOLOGICAL, AND THERAPEUTIC ASPECTS OF KRABBE'S DISEASE.JOURNAL OF NEUROSCIENCE RESEARCH. VOL. 94. ISSUE 11. P. 990 -1006 110 55% 1
3 BONGARZONE, ER , ESCOLAR, ML , GRAY, SJ , KAFRI, T , VITE, CH , SANDS, MS , (2016) INSIGHTS INTO THE PATHOGENESIS AND TREATMENT OF KRABBE DISEASE.PEDIATRIC ENDOCRINOLOGY REVIEWS PER. VOL. 13. ISSUE . P. 689 -696 58 89% 1
4 WENGER, DA , RAFI, MA , LUZI, P , (2016) KRABBE DISEASE: ONE HUNDRED YEARS FROM THE BEDSIDE TO THE BENCH TO THE BEDSIDE.JOURNAL OF NEUROSCIENCE RESEARCH. VOL. 94. ISSUE 11. P. 982 -989 55 98% 0
5 MIKULKA, CR , SANDS, MS , (2016) TREATMENT FOR KRABBE'S DISEASE: FINDING THE COMBINATION.JOURNAL OF NEUROSCIENCE RESEARCH. VOL. 94. ISSUE 11. P. 1126 -1137 63 82% 0
6 POTTER, GB , SANTOS, M , DAVISSON, MT , ROWITCH, DH , MARKS, DL , BONGARZONE, ER , PETRYNIAK, MA , (2013) MISSENSE MUTATION IN MOUSE GALC MIMICS HUMAN GENE DEFECT AND OFFERS NEW INSIGHTS INTO KRABBE DISEASE.HUMAN MOLECULAR GENETICS. VOL. 22. ISSUE 17. P. 3397-3414 56 88% 12
7 RICCA, A , GRITTI, A , (2016) PERSPECTIVE ON INNOVATIVE THERAPIES FOR GLOBOID CELL LEUKODYSTROPHY.JOURNAL OF NEUROSCIENCE RESEARCH. VOL. 94. ISSUE 11. P. 1304 -1317 82 59% 0
8 LI, YD , SANDS, MS , (2014) EXPERIMENTAL THERAPIES IN THE MURINE MODEL OF GLOBOID CELL LEUKODYSTROPHY.PEDIATRIC NEUROLOGY. VOL. 51. ISSUE 5. P. 600 -606 49 82% 12
9 KARUMUTHIL-MELETHIL, S , GRAY, SJ , (2016) IMMUNOLOGICAL CONSIDERATIONS FOR TREATING GLOBOID CELL LEUKODYSTROPHY.JOURNAL OF NEUROSCIENCE RESEARCH. VOL. 94. ISSUE 11. P. 1349 -1358 54 78% 0
10 LIAO, P , GELINAS, J , SIRRS, S , (2014) PHENOTYPIC VARIABILITY OF KRABBE DISEASE ACROSS THE LIFESPAN.CANADIAN JOURNAL OF NEUROLOGICAL SCIENCES. VOL. 41. ISSUE 1. P. 5 -12 48 89% 1

Classes with closest relation at Level 1



Rank Class id link
1 11213 METACHROMATIC LEUKODYSTROPHY//ARYLSULFATASE A//MULTIPLE SULFATASE DEFICIENCY
2 12781 ALEXANDER DISEASE//LEUKODYSTROPHY//ROSENTHAL FIBERS
3 17857 PROSAPOSIN//SPHINGOLIPID ACTIVATOR PROTEINS//SAPOSIN
4 12163 SANDHOFF DISEASE//GM2 GANGLIOSIDOSIS//TAY SACHS DISEASE
5 24263 FUCOSIDOSIS//ALPHA L FUCOSIDASE//CANINE FUCOSIDOSIS
6 1052 MUCOPOLYSACCHARIDOSIS//MUCOPOLYSACCHARIDOSES//HUNTER SYNDROME
7 18342 SULFATIDE//BIOMED ANAL RADIOISOTOPE//SEMINOLIPID
8 29918 ABNORMAL FUNCTION//ABT ENTWICKLUNGSNEUROL NEUROPADIAT//ASPHYXIA BRAIN PERINATAL
9 1959 GAUCHER DISEASE//GLUCOCEREBROSIDASE//GAUCHER CLIN
10 21054 ALPHA MANNOSIDOSIS//BETA MANNOSIDOSIS//MANNOSIDOSIS

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