Class information for:
Level 3: POLYCYSTIC KIDNEY DISEASE//AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE//HEDGEHOG

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
642 12305 39.4 80%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
642 3       POLYCYSTIC KIDNEY DISEASE//AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE//HEDGEHOG 12305
1658 2             HEDGEHOG//GLI//CILIOPATHY 6876
2024 2             AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE//POLYCYSTIC KIDNEY DISEASE//ADPKD 5429

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 POLYCYSTIC KIDNEY DISEASE authKW 795847 4% 65% 494
2 AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE authKW 775862 3% 80% 390
3 HEDGEHOG authKW 552459 4% 42% 536
4 ADPKD authKW 522199 2% 85% 248
5 CILIOPATHY authKW 361615 2% 75% 194
6 GLI authKW 315167 1% 71% 179
7 PRIMARY CILIA authKW 308658 1% 68% 182
8 SMOOTHENED authKW 288446 1% 73% 160
9 HEDGEHOG SIGNALING authKW 287926 2% 62% 187
10 BARDET BIEDL SYNDROME authKW 263517 1% 78% 136

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 Urology & Nephrology 29581 15% 1% 1824
2 Genetics & Heredity 11631 14% 0% 1711
3 Developmental Biology 11416 6% 1% 794
4 Cell Biology 11207 17% 0% 2088
5 Gastroenterology & Hepatology 4703 7% 0% 819
6 Pathology 2464 5% 0% 575
7 Oncology 1966 9% 0% 1062
8 Biochemistry & Molecular Biology 1914 15% 0% 1818
9 Pediatrics 1814 5% 0% 638
10 Transplantation 1195 2% 0% 301

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HUMAN DIS MODELING 35273 0% 30% 47
2 KHA CARI GUIDELINES 29755 0% 100% 12
3 KIDNEY GENET GRP 28583 0% 82% 14
4 GENET TRANSLAT MED 24246 0% 65% 15
5 RAINBOW CHILDHOOD PKD 24246 0% 65% 15
6 EDUC ANIM MODELS HUMAN DIS 23101 0% 55% 17
7 SECT OPHTHALMOL NEUROSCI 21238 0% 30% 29
8 NEPHROL 20489 6% 1% 743
9 WESTERN SYDNEY LOCAL HLTH DIST 19428 0% 56% 14
10 SHIMIZU KU 17478 0% 14% 49

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY 22372 2% 4% 258
2 KIDNEY INTERNATIONAL 8990 2% 2% 234
3 DEVELOPMENT 7350 2% 2% 198
4 AMERICAN JOURNAL OF KIDNEY DISEASES 6691 1% 2% 154
5 AMERICAN JOURNAL OF MEDICAL GENETICS 6542 1% 2% 155
6 HUMAN MOLECULAR GENETICS 6158 1% 2% 159
7 PEDIATRIC NEPHROLOGY 5692 1% 2% 120
8 NEPHROLOGY DIALYSIS TRANSPLANTATION 5182 1% 1% 165
9 JOURNAL OF MEDICAL GENETICS 4901 1% 2% 109
10 VITAMINS AND HORMONES 4462 0% 9% 21

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 POLYCYSTIC KIDNEY DISEASE 795847 4% 65% 494 Search POLYCYSTIC+KIDNEY+DISEASE Search POLYCYSTIC+KIDNEY+DISEASE
2 AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE 775862 3% 80% 390 Search AUTOSOMAL+DOMINANT+POLYCYSTIC+KIDNEY+DISEASE Search AUTOSOMAL+DOMINANT+POLYCYSTIC+KIDNEY+DISEASE
3 HEDGEHOG 552459 4% 42% 536 Search HEDGEHOG Search HEDGEHOG
4 ADPKD 522199 2% 85% 248 Search ADPKD Search ADPKD
5 CILIOPATHY 361615 2% 75% 194 Search CILIOPATHY Search CILIOPATHY
6 GLI 315167 1% 71% 179 Search GLI Search GLI
7 PRIMARY CILIA 308658 1% 68% 182 Search PRIMARY+CILIA Search PRIMARY+CILIA
8 SMOOTHENED 288446 1% 73% 160 Search SMOOTHENED Search SMOOTHENED
9 HEDGEHOG SIGNALING 287926 2% 62% 187 Search HEDGEHOG+SIGNALING Search HEDGEHOG+SIGNALING
10 BARDET BIEDL SYNDROME 263517 1% 78% 136 Search BARDET+BIEDL+SYNDROME Search BARDET+BIEDL+SYNDROME

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 BRISCOE, J , THEROND, PP , (2013) THE MECHANISMS OF HEDGEHOG SIGNALLING AND ITS ROLES IN DEVELOPMENT AND DISEASE.NATURE REVIEWS MOLECULAR CELL BIOLOGY. VOL. 14. ISSUE 7. P. 416-429 161 77% 320
2 TEGLUND, S , TOFTGARD, R , (2010) HEDGEHOG BEYOND MEDULLOBLASTOMA AND BASAL CELL CARCINOMA.BIOCHIMICA ET BIOPHYSICA ACTA-REVIEWS ON CANCER. VOL. 1805. ISSUE 2. P. 181 -208 280 67% 198
3 ROBBINS, DJ , FEI, DL , RIOBO, NA , (2012) THE HEDGEHOG SIGNAL TRANSDUCTION NETWORK.SCIENCE SIGNALING. VOL. 5. ISSUE 246. P. - 196 87% 98
4 PANDOLFI, S , STECCA, B , (2015) COOPERATIVE INTEGRATION BETWEEN HEDGEHOG-GLI SIGNALLING AND OTHER ONCOGENIC PATHWAYS: IMPLICATIONS FOR CANCER THERAPY.EXPERT REVIEWS IN MOLECULAR MEDICINE. VOL. 17. ISSUE . P. - 232 80% 8
5 TORRES, VE , HARRIS, PC , PIRSON, Y , (2007) AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE.LANCET. VOL. 369. ISSUE 9569. P. 1287 -1301 166 87% 361
6 GOETZ, SC , ANDERSON, KV , (2010) THE PRIMARY CILIUM: A SIGNALLING CENTRE DURING VERTEBRATE DEVELOPMENT.NATURE REVIEWS GENETICS. VOL. 11. ISSUE 5. P. 331 -344 119 76% 612
7 YANG, L , XIE, G , FAN, Q , XIE, J , (2010) ACTIVATION OF THE HEDGEHOG-SIGNALING PATHWAY IN HUMAN CANCER AND THE CLINICAL IMPLICATIONS.ONCOGENE. VOL. 29. ISSUE 4. P. 469 -481 169 86% 125
8 QUINLAN, RJ , TOBIN, JL , BEALES, PL , (2008) MODELING CILIOPATHIES: PRIMARY CILIA IN DEVELOPMENT AND DISEASE.MOUSE MODELS OF DEVELOPMENTAL GENETIC DISEASE. VOL. 84. ISSUE . P. 249-+ 223 79% 66
9 WILSON, CW , CHUANG, PT , (2010) MECHANISM AND EVOLUTION OF CYTOSOLIC HEDGEHOG SIGNAL TRANSDUCTION.DEVELOPMENT. VOL. 137. ISSUE 13. P. 2079 -2094 178 88% 77
10 MADHIVANAN, K , AGUILAR, RC , (2014) CILIOPATHIES: THE TRAFFICKING CONNECTION.TRAFFIC. VOL. 15. ISSUE 10. P. 1031 -1056 179 84% 15

Classes with closest relation at Level 3



Rank Class id link
1 27 DEVELOPMENTAL BIOLOGY//DEVELOPMENT//AGR2
2 365 MICROTUBULES//MITOSIS//KINETOCHORE
3 465 RENAL CELL CARCINOMA//ANGIOMYOLIPOMA//TUBEROUS SCLEROSIS
4 360 RETINA//OPHTHALMOLOGY//PHOTORECEPTOR
5 212 GASTROENTEROLOGY & HEPATOLOGY//LAPAROSCOPIC CHOLECYSTECTOMY//PRIMARY BILIARY CIRRHOSIS
6 447 TCTP//TRANSLATIONALLY CONTROLLED TUMOR PROTEIN//GENETIC EPIDEMIOLOGY
7 474 CLEFT PALATE-CRANIOFACIAL JOURNAL//CLEFT PALATE//CRANIOSYNOSTOSIS
8 298 UROLOGY & NEPHROLOGY//PROTEINURIA//NEPHROTIC SYNDROME
9 370 ACUTE PANCREATITIS//PANCREATIC CANCER//CHRONIC PANCREATITIS
10 361 UROLOGY & NEPHROLOGY//VESICOURETERAL REFLUX//RENAL ARTERY STENOSIS

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