Class information for:
Level 2: ADRENAL INSUFFICIENCY//AIRE//APECED

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
2373 4304 37.0 75%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
284 3       POLYCYSTIC OVARY SYNDROME//ENDOCRINOLOGY & METABOLISM//CORTISOL 42633
2373 2             ADRENAL INSUFFICIENCY//AIRE//APECED 4304
5236 1                   AIRE//APECED//AUTOIMMUNE REGULATOR 1652
10927 1                   ADRENAL INSUFFICIENCY//RELATIVE ADRENAL INSUFFICIENCY//FREE CORTISOL 1023
11660 1                   ADRENAL INSUFFICIENCY//ADDISONS DISEASE//ADRENAL CRISIS 964
19281 1                   HYPOPITUITARISM//POST TRAUMATIC HYPOPITUITARISM//PITUITARY DYSFUNCTION 513
31459 1                   AE TABOR SIBERIAN BRANCH//ANAT 1 GUSTAVE L LEVY PL//DERIVATIVE OF TENSION 152

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ADRENAL INSUFFICIENCY authKW 695198 6% 36% 273
2 AIRE authKW 558055 3% 68% 116
3 APECED authKW 510654 2% 86% 84
4 ADDISONS DISEASE authKW 328474 3% 38% 121
5 HYPOPITUITARISM authKW 175925 3% 17% 147
6 AUTOIMMUNE REGULATOR authKW 172515 1% 81% 30
7 RELATIVE ADRENAL INSUFFICIENCY authKW 161204 1% 78% 29
8 FOXN1 authKW 160896 1% 69% 33
9 CHRONIC MUCOCUTANEOUS CANDIDIASIS authKW 129669 1% 57% 32
10 AIRE GENE authKW 114899 0% 90% 18

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 Endocrinology & Metabolism 19267 26% 0% 1133
2 Critical Care Medicine 8577 9% 0% 387
3 Immunology 5218 18% 0% 776
4 Medicine, General & Internal 1798 11% 0% 470
5 Pediatrics 869 6% 0% 253
6 Anesthesiology 259 2% 0% 78
7 Medical Laboratory Technology 177 1% 0% 57
8 Surgery 172 6% 0% 248
9 Clinical Neurology 137 4% 0% 177
10 Medicine, Research & Experimental 128 3% 0% 141

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 DEV IMMUNOL 33112 1% 9% 55
2 GEN MOL PATHOL 29167 1% 15% 27
3 ENDOCRINOL 27984 10% 1% 427
4 FIRS S 27674 0% 23% 17
5 MEMPHIS LUNG PROGRAM 26728 0% 54% 7
6 INTERNAL MED ENDOCRINE METAB SCI 24953 0% 27% 13
7 CLIN NEUROENDOCRINOL GRP 23207 0% 55% 6
8 ABT ENDOKRINOL DIABETOL ERNAHRUNGSMED 21278 0% 100% 3
9 PAEDIAT IMMUNOL GENET OPERAT UNIT 21278 0% 100% 3
10 MOL IMMUNOGENET GRP 21260 0% 25% 12

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CLINICAL ENDOCRINOLOGY 27834 4% 2% 172
2 JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM 17849 6% 1% 246
3 EUROPEAN JOURNAL OF ENDOCRINOLOGY 14124 2% 2% 102
4 PITUITARY 8112 1% 4% 28
5 JOURNAL OF ENDOCRINOLOGICAL INVESTIGATION 5614 1% 1% 63
6 INTENSIVE CARE MEDICINE 5092 2% 1% 67
7 PEDIATRIC CRITICAL CARE MEDICINE 2845 1% 2% 25
8 CRITICAL CARE MEDICINE 2778 2% 1% 69
9 JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM 2657 1% 1% 37
10 ENDOCRINE PRACTICE 2545 0% 2% 20

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 ADRENAL INSUFFICIENCY 695198 6% 36% 273 Search ADRENAL+INSUFFICIENCY Search ADRENAL+INSUFFICIENCY
2 AIRE 558055 3% 68% 116 Search AIRE Search AIRE
3 APECED 510654 2% 86% 84 Search APECED Search APECED
4 ADDISONS DISEASE 328474 3% 38% 121 Search ADDISONS+DISEASE Search ADDISONS+DISEASE
5 HYPOPITUITARISM 175925 3% 17% 147 Search HYPOPITUITARISM Search HYPOPITUITARISM
6 AUTOIMMUNE REGULATOR 172515 1% 81% 30 Search AUTOIMMUNE+REGULATOR Search AUTOIMMUNE+REGULATOR
7 RELATIVE ADRENAL INSUFFICIENCY 161204 1% 78% 29 Search RELATIVE+ADRENAL+INSUFFICIENCY Search RELATIVE+ADRENAL+INSUFFICIENCY
8 FOXN1 160896 1% 69% 33 Search FOXN1 Search FOXN1
9 CHRONIC MUCOCUTANEOUS CANDIDIASIS 129669 1% 57% 32 Search CHRONIC+MUCOCUTANEOUS+CANDIDIASIS Search CHRONIC+MUCOCUTANEOUS+CANDIDIASIS
10 AIRE GENE 114899 0% 90% 18 Search AIRE+GENE Search AIRE+GENE

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 BORNSTEIN, SR , ALLOLIO, B , ARLT, W , BARTHEL, A , DON-WAUCHOPE, A , HAMMER, GD , HUSEBYE, ES , MERKE, DP , MURAD, MH , STRATAKIS, CA , ET AL (2016) DIAGNOSIS AND TREATMENT OF PRIMARY ADRENAL INSUFFICIENCY: AN ENDOCRINE SOCIETY CLINICAL PRACTICE GUIDELINE.JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM. VOL. 101. ISSUE 2. P. 364 -389 115 73% 24
2 KISAND, K , PETERSON, P , (2015) AUTOIMMUNE POLYENDOCRINOPATHY CANDIDIASIS ECTODERMAL DYSTROPHY.JOURNAL OF CLINICAL IMMUNOLOGY. VOL. 35. ISSUE 5. P. 463 -478 126 89% 5
3 MATHIS, D , BENOIST, C , (2009) AIRE.ANNUAL REVIEW OF IMMUNOLOGY. VOL. 27. ISSUE . P. 287-312 102 71% 300
4 ABRAMSON, J , HUSEBYE, ES , (2016) AUTOIMMUNE REGULATOR AND SELF-TOLERANCE - MOLECULAR AND CLINICAL ASPECTS.IMMUNOLOGICAL REVIEWS. VOL. 271. ISSUE 1. P. 127 -140 84 83% 5
5 ANDERSON, MS , SU, MA , (2016) AIRE EXPANDS: NEW ROLES IN IMMUNE TOLERANCE AND BEYOND.NATURE REVIEWS IMMUNOLOGY. VOL. 16. ISSUE 4. P. 247 -258 79 87% 5
6 NITTA, T , SUZUKI, H , (2016) THYMIC STROMAL CELL SUBSETS FOR T CELL DEVELOPMENT.CELLULAR AND MOLECULAR LIFE SCIENCES. VOL. 73. ISSUE 5. P. 1021 -1037 136 62% 0
7 KISAND, K , PETERSON, P , (2011) AUTOIMMUNE POLYENDOCRINOPATHY CANDIDIASIS ECTODERMAL DYSTROPHY: KNOWN AND NOVEL ASPECTS OF THE SYNDROME.YEAR IN HUMAN AND MEDICAL GENETICS: INBORN ERRORS OF IMMUNITY II. VOL. 1246. ISSUE . P. 77 -91 104 83% 23
8 PETERSON, P , ORG, T , REBANE, A , (2008) TRANSCRIPTIONAL REGULATION BY AIRE: MOLECULAR MECHANISMS OF CENTRAL TOLERANCE.NATURE REVIEWS IMMUNOLOGY. VOL. 8. ISSUE 12. P. 948-957 104 79% 92
9 ARSTILA, TP , JARVE, H , (2013) HUMAN APECED; A SICK THYMUS SYNDROME?.FRONTIERS IN IMMUNOLOGY. VOL. 4. ISSUE . P. - 84 94% 12
10 PERNIOLA, R , MUSCO, G , (2014) THE BIOPHYSICAL AND BIOCHEMICAL PROPERTIES OF THE AUTOIMMUNE REGULATOR (AIRE) PROTEIN.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE. VOL. 1842. ISSUE 2. P. 326 -337 96 77% 8

Classes with closest relation at Level 2



Rank Class id link
1 3208 DEHYDROEPIANDROSTERONE//DHEA//DEHYDROEPIANDROSTERONE SULFATE
2 2727 11 BETA HYDROXYSTEROID DEHYDROGENASE//11 BETA HYDROXYSTEROID DEHYDROGENASE TYPE 1//11 BETA HSD1
3 1915 IMMUNOSENESCENCE//INTERLEUKIN 7//IL 7
4 380 PITUITARY ADENOMA//ACROMEGALY//CRANIOPHARYNGIOMA
5 721 SUPERANTIGEN//IMMUNOLOGY//T CELL RECEPTOR
6 3243 PSEUDOHYPOPARATHYROIDISM//FAHRS DISEASE//MENINGIOANGIOMATOSIS
7 789 TYPE 1 DIABETES//BARBARA DAVIS CHILDHOOD DIABET//PTPN22
8 909 CONGENITAL ADRENAL HYPERPLASIA//21 HYDROXYLASE DEFICIENCY//ENDOCRINE RESEARCH
9 856 HYPOTHYROIDISM//SUBCLINICAL HYPOTHYROIDISM//HYPERTHYROIDISM
10 744 SEPSIS//SEPTIC SHOCK//HYDROXYETHYL STARCH

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