Class information for:
Level 2: SPINOCEREBELLAR ATAXIA//HEREDITARY SPASTIC PARAPLEGIA//FRIEDREICHS ATAXIA

Basic class information
Class id #P Avg. number of
references		 Database coverage
of references
1711 6674 36.9 81%


Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes
The table includes all classes above and classes immediately below the current class.


Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
603 3       HUNTINGTONS DISEASE//SPINOCEREBELLAR ATAXIA//POLYGLUTAMINE 14359
1711 2             SPINOCEREBELLAR ATAXIA//HEREDITARY SPASTIC PARAPLEGIA//FRIEDREICHS ATAXIA 6674
2557 1                   SPINOCEREBELLAR ATAXIA//MACHADO JOSEPH DISEASE//SCA2 2208
3134 1                   FRATAXIN//FRIEDREICHS ATAXIA//FRIEDREICH ATAXIA 2056
9176 1                   HEREDITARY SPASTIC PARAPLEGIA//SPASTIN//SPG4 1181
18172 1                   RHOMBENCEPHALOSYNAPSIS//PONTOCEREBELLAR HYPOPLASIA//CEREBELLAR AGENESIS 563
22273 1                   ARSACS//AOA2//SENATAXIN 388
30096 1                   MARINESCO SJOGREN SYNDROME//SIL1//WARBURG MICRO SYNDROME 174
34928 1                   PERRAULT SYNDROME//HOLMES ATAXIA//BOUCHER NEUHAUSER SYNDROME 104

Terms with highest relevance score


rank Term termType Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 SPINOCEREBELLAR ATAXIA authKW 1014661 5% 63% 350
2 HEREDITARY SPASTIC PARAPLEGIA authKW 970434 4% 81% 261
3 FRIEDREICHS ATAXIA authKW 850533 4% 75% 247
4 FRIEDREICH ATAXIA authKW 748313 3% 82% 199
5 FRATAXIN authKW 685410 3% 86% 174
6 MACHADO JOSEPH DISEASE authKW 492616 2% 70% 155
7 SCA2 authKW 287836 1% 85% 74
8 SPASTIN authKW 278236 1% 82% 74
9 SPG4 authKW 251612 1% 98% 56
10 AUTOSOMAL DOMINANT CEREBELLAR ATAXIA authKW 248133 1% 94% 58

Web of Science journal categories


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with term
in class
1 Clinical Neurology 54469 40% 0% 2639
2 Genetics & Heredity 14715 20% 0% 1361
3 Neurosciences 8400 22% 0% 1492
4 Biochemistry & Molecular Biology 2861 21% 0% 1394
5 Neuroimaging 1299 2% 0% 125
6 Pediatrics 871 5% 0% 330
7 Cell Biology 757 8% 0% 501
8 Pathology 363 3% 0% 187
9 Psychiatry 255 3% 0% 226
10 Radiology, Nuclear Medicine & Medical Imaging 95 3% 0% 188

Address terms


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with term
in class
1 ZYTOBIOL ZYTOPATHOL 177529 1% 63% 62
2 UNIGENE 73125 1% 40% 40
3 BRUCE LEFROY GENET HLTH 70063 1% 33% 46
4 ZYTOBIOL 69733 0% 51% 30
5 NEUROL 64784 28% 1% 1894
6 GENET CYTOGENET 63816 1% 22% 63
7 GENET CYTOGENET EMBRYOL 43728 1% 26% 37
8 NEUROGENET BRANCH 37726 1% 18% 46
9 EVANS CHEM 35912 0% 30% 26
10 CELLULAR NEUROL UNIT 31166 0% 45% 15

Journals


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 CEREBELLUM 103211 2% 16% 143
2 NEUROGENETICS 35927 1% 11% 69
3 HUMAN MOLECULAR GENETICS 17743 3% 2% 196
4 JOURNAL OF THE NEUROLOGICAL SCIENCES 17148 3% 2% 196
5 JOURNAL OF NEUROLOGY 16512 2% 2% 149
6 MOVEMENT DISORDERS 16415 2% 2% 154
7 NEUROLOGY 13585 4% 1% 254
8 ARCHIVES OF NEUROLOGY 11002 2% 2% 127
9 AMERICAN JOURNAL OF HUMAN GENETICS 9127 2% 2% 128
10 ANNALS OF NEUROLOGY 7724 2% 1% 116

Author Key Words


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class		 LCSH search Wikipedia search
1 SPINOCEREBELLAR ATAXIA 1014661 5% 63% 350 Search SPINOCEREBELLAR+ATAXIA Search SPINOCEREBELLAR+ATAXIA
2 HEREDITARY SPASTIC PARAPLEGIA 970434 4% 81% 261 Search HEREDITARY+SPASTIC+PARAPLEGIA Search HEREDITARY+SPASTIC+PARAPLEGIA
3 FRIEDREICHS ATAXIA 850533 4% 75% 247 Search FRIEDREICHS+ATAXIA Search FRIEDREICHS+ATAXIA
4 FRIEDREICH ATAXIA 748313 3% 82% 199 Search FRIEDREICH+ATAXIA Search FRIEDREICH+ATAXIA
5 FRATAXIN 685410 3% 86% 174 Search FRATAXIN Search FRATAXIN
6 MACHADO JOSEPH DISEASE 492616 2% 70% 155 Search MACHADO+JOSEPH+DISEASE Search MACHADO+JOSEPH+DISEASE
7 SCA2 287836 1% 85% 74 Search SCA2 Search SCA2
8 SPASTIN 278236 1% 82% 74 Search SPASTIN Search SPASTIN
9 SPG4 251612 1% 98% 56 Search SPG4 Search SPG4
10 AUTOSOMAL DOMINANT CEREBELLAR ATAXIA 248133 1% 94% 58 Search AUTOSOMAL+DOMINANT+CEREBELLAR+ATAXIA Search AUTOSOMAL+DOMINANT+CEREBELLAR+ATAXIA

Core articles
The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.


Rank Reference # ref. in
cl.		 Shr. of ref. in
cl.		 Citations
1 SANTOS, R , LEFEVRE, S , SLIWA, D , SEGUIN, A , CAMADRO, JM , LESUISSE, E , (2010) FRIEDREICH ATAXIA: MOLECULAR MECHANISMS, REDOX CONSIDERATIONS, AND THERAPEUTIC OPPORTUNITIES.ANTIOXIDANTS & REDOX SIGNALING. VOL. 13. ISSUE 5. P. 651 -690 264 87% 59
2 MAIO, N , ROUAULT, TA , (2015) IRON-SULFUR CLUSTER BIOGENESIS IN MAMMALIAN CELLS: NEW INSIGHTS INTO THE MOLECULAR MECHANISMS OF CLUSTER DELIVERY.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH. VOL. 1853. ISSUE 6. P. 1493 -1512 191 61% 29
3 SEIDEL, K , SISWANTO, S , BRUNT, ERP , DEN DUNNEN, W , KORF, HW , RUB, U , (2012) BRAIN PATHOLOGY OF SPINOCEREBELLAR ATAXIAS.ACTA NEUROPATHOLOGICA. VOL. 124. ISSUE 1. P. 1 -21 151 83% 75
4 XU, XM , MOLLER, SG , (2011) IRON-SULFUR CLUSTERS: BIOGENESIS, MOLECULAR MECHANISMS, AND THEIR FUNCTIONAL SIGNIFICANCE.ANTIOXIDANTS & REDOX SIGNALING. VOL. 15. ISSUE 1. P. 271 -307 220 66% 40
5 MARMOLINO, D , (2011) FRIEDREICH'S ATAXIA: PAST, PRESENT AND FUTURE.BRAIN RESEARCH REVIEWS. VOL. 67. ISSUE 1-2. P. 311 -330 157 91% 47
6 ROCHE, B , AUSSEL, L , EZRATY, B , MANDIN, P , PY, B , BARRAS, F , (2013) IRON/SULFUR PROTEINS BIOGENESIS IN PROKARYOTES: FORMATION, REGULATION AND DIVERSITY.BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS. VOL. 1827. ISSUE 3. P. 455-469 144 73% 79
7 LO GIUDICE, T , LOMBARDI, F , SANTORELLI, FM , KAWARAI, T , ORLACCHIO, A , (2014) HEREDITARY SPASTIC PARAPLEGIA: CLINICAL-GENETIC CHARACTERISTICS AND EVOLVING MOLECULAR MECHANISMS.EXPERIMENTAL NEUROLOGY. VOL. 261. ISSUE . P. 518 -539 152 67% 42
8 LILL, R , HOFFMANN, B , MOLIK, S , PIERIK, AJ , RIETZSCHEL, N , STEHLING, O , UZARSKA, MA , WEBERT, H , WILBRECHT, C , MUHLENHOFF, U , (2012) THE ROLE OF MITOCHONDRIA IN CELLULAR IRON-SULFUR PROTEIN BIOGENESIS AND IRON METABOLISM.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH. VOL. 1823. ISSUE 9. P. 1491 -1508 144 61% 164
9 FINK, JK , (2013) HEREDITARY SPASTIC PARAPLEGIA: CLINICO-PATHOLOGIC FEATURES AND EMERGING MOLECULAR MECHANISMS.ACTA NEUROPATHOLOGICA. VOL. 126. ISSUE 3. P. 307-328 141 67% 85
10 KLEBE, S , STEVANIN, G , DEPIENNE, C , (2015) CLINICAL AND GENETIC HETEROGENEITY IN HEREDITARY SPASTIC PARAPLEGIAS: FROM SPG1 TO SPG72 AND STILL COUNTING.REVUE NEUROLOGIQUE. VOL. 171. ISSUE 6-7. P. 505 -530 150 76% 8

Classes with closest relation at Level 2


Rank Class id link
1 1645 HUNTINGTONS DISEASE//HUNTINGTIN//POLYGLUTAMINE
2 1532 CEREBELLUM//PURKINJE CELL//INFERIOR OLIVE
3 2003 MYOTONIC DYSTROPHY//MYOTONIA//MYOTONIC DYSTROPHY TYPE 1
4 3395 PKAN//NBIA//PANTOTHENATE KINASE
5 3382 LISSENCEPHALY//SECKEL SYNDROME//LIS1
6 1735 SPINAL MUSCULAR ATROPHY//CHARCOT MARIE TOOTH DISEASE//NEUROFILAMENT
7 3244 COENZYME Q10//UBIQUINONE//COENZYME Q
8 1262 HYDROGENASE//FERREDOXIN//FEFE HYDROGENASE
9 2520 ESSENTIAL TREMOR//TREMOR//ORTHOSTATIC TREMOR
10 3549 ARTHROGRYPOSIS//FREEMAN SHELDON SYNDROME//DISTAL ARTHROGRYPOSIS

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