Class information for:
Level 1: HEREDITARY HEMORRHAGIC TELANGIECTASIA//PULMONARY ARTERIOVENOUS MALFORMATION//HEREDITARY HAEMORRHAGIC TELANGIECTASIA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
5947 1554 23.4 69%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
391 3       ARTERIOVENOUS MALFORMATION//VERTEBROPLASTY//DURAL ARTERIOVENOUS FISTULA 30586
2544 2             HEREDITARY HEMORRHAGIC TELANGIECTASIA//PULMONARY ARTERIOVENOUS MALFORMATION//HEMOPTYSIS 3747
5947 1                   HEREDITARY HEMORRHAGIC TELANGIECTASIA//PULMONARY ARTERIOVENOUS MALFORMATION//HEREDITARY HAEMORRHAGIC TELANGIECTASIA 1554

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HEREDITARY HEMORRHAGIC TELANGIECTASIA authKW 4045992 17% 76% 270
2 PULMONARY ARTERIOVENOUS MALFORMATION authKW 1919289 8% 75% 130
3 HEREDITARY HAEMORRHAGIC TELANGIECTASIA authKW 1226202 5% 81% 77
4 PULMONARY ARTERIOVENOUS FISTULA authKW 733102 3% 75% 50
5 RENDU OSLER WEBER DISEASE authKW 655810 3% 76% 44
6 HHT authKW 577579 4% 47% 63
7 RENDU OSLER WEBER SYNDROME authKW 533023 2% 94% 29
8 EPISTAXIS authKW 424184 8% 17% 126
9 OSLER WEBER RENDU authKW 399752 1% 88% 23
10 OSLER WEBER RENDU DISEASE authKW 361024 1% 88% 21

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Otorhinolaryngology 3210 10% 0% 154
2 Radiology, Nuclear Medicine & Medical Imaging 2848 17% 0% 271
3 Respiratory System 2123 10% 0% 157
4 Cardiac & Cardiovascular System 1453 13% 0% 203
5 Medicine, General & Internal 1239 14% 0% 223
6 Peripheral Vascular Diseases 678 7% 0% 106
7 Surgery 473 11% 0% 177
8 Gastroenterology & Hepatology 464 6% 0% 93
9 Critical Care Medicine 453 4% 0% 57
10 Genetics & Heredity 341 8% 0% 117

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HHT 226523 1% 82% 14
2 NHLI CARDIOVASC SCI 188614 1% 80% 12
3 UNIV INTER HHT 137535 0% 100% 7
4 HHTIC LONDON 117887 0% 100% 6
5 REFERENCE MALAD RENDU OSLER 106968 0% 78% 7
6 TORONTO HHT PIROL 58943 0% 100% 3
7 UNIV INTERDEPARTMENTAL HHT 58943 0% 100% 3
8 HHT SOLUT 44206 0% 75% 3
9 CATTEDRA MED URGENZA PRONTO SOCCORSO 39296 0% 100% 2
10 CLIN CHEM GENET 39296 0% 100% 2

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF VASCULAR AND INTERVENTIONAL RADIOLOGY 5538 2% 1% 36
2 CARDIOVASCULAR AND INTERVENTIONAL RADIOLOGY 3694 2% 1% 29
3 RHINOLOGY 3246 1% 1% 13
4 INTERNATIONAL FORUM OF ALLERGY & RHINOLOGY 2308 1% 1% 10
5 CHEST 2082 3% 0% 48
6 AMERICAN JOURNAL OF RHINOLOGY 1837 1% 1% 11
7 LARYNGOSCOPE 1595 2% 0% 33
8 CATHETERIZATION AND CARDIOVASCULAR INTERVENTIONS 1455 1% 0% 20
9 PEDIATRIC CARDIOLOGY 1191 1% 0% 16
10 ORPHANET JOURNAL OF RARE DISEASES 1117 1% 1% 8

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 HEREDITARY HEMORRHAGIC TELANGIECTASIA 4045992 17% 76% 270 Search HEREDITARY+HEMORRHAGIC+TELANGIECTASIA Search HEREDITARY+HEMORRHAGIC+TELANGIECTASIA
2 PULMONARY ARTERIOVENOUS MALFORMATION 1919289 8% 75% 130 Search PULMONARY+ARTERIOVENOUS+MALFORMATION Search PULMONARY+ARTERIOVENOUS+MALFORMATION
3 HEREDITARY HAEMORRHAGIC TELANGIECTASIA 1226202 5% 81% 77 Search HEREDITARY+HAEMORRHAGIC+TELANGIECTASIA Search HEREDITARY+HAEMORRHAGIC+TELANGIECTASIA
4 PULMONARY ARTERIOVENOUS FISTULA 733102 3% 75% 50 Search PULMONARY+ARTERIOVENOUS+FISTULA Search PULMONARY+ARTERIOVENOUS+FISTULA
5 RENDU OSLER WEBER DISEASE 655810 3% 76% 44 Search RENDU+OSLER+WEBER+DISEASE Search RENDU+OSLER+WEBER+DISEASE
6 HHT 577579 4% 47% 63 Search HHT Search HHT
7 RENDU OSLER WEBER SYNDROME 533023 2% 94% 29 Search RENDU+OSLER+WEBER+SYNDROME Search RENDU+OSLER+WEBER+SYNDROME
8 EPISTAXIS 424184 8% 17% 126 Search EPISTAXIS Search EPISTAXIS
9 OSLER WEBER RENDU 399752 1% 88% 23 Search OSLER+WEBER+RENDU Search OSLER+WEBER+RENDU
10 OSLER WEBER RENDU DISEASE 361024 1% 88% 21 Search OSLER+WEBER+RENDU+DISEASE Search OSLER+WEBER+RENDU+DISEASE

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 COTTIN, V , DUPUIS-GIROD, S , LESCA, G , CORDIER, JF , (2007) PULMONARY VASCULAR MANIFESTATIONS OF HEREDITARY HEMORRHAGIC TELANGIECTASIA (RENDU-OSLER DISEASE).RESPIRATION. VOL. 74. ISSUE 4. P. 361 -378 109 84% 68
2 RIMMER, J , LUND, VJ , (2015) HEREDITARY HAEMORRHAGIC TELANGIECTASIA.RHINOLOGY. VOL. 53. ISSUE 3. P. 195 -203 83 93% 0
3 FAUGHNAN, ME , PALDA, VA , GARCIA-TSAO, G , GEISTHOFF, UW , MCDONALD, J , PROCTOR, DD , SPEARS, J , BROWN, DH , BUSCARINI, E , CHESNUTT, MS , ET AL (2011) INTERNATIONAL GUIDELINES FOR THE DIAGNOSIS AND MANAGEMENT OF HEREDITARY HAEMORRHAGIC TELANGIECTASIA.JOURNAL OF MEDICAL GENETICS. VOL. 48. ISSUE 2. P. 73-87 75 68% 221
4 SHOVLIN, CL , (2010) HEREDITARY HAEMORRHAGIC TELANGIECTASIA PATHOPHYSIOLOGY, DIAGNOSIS AND TREATMENT.BLOOD REVIEWS. VOL. 24. ISSUE 6. P. 203 -219 100 63% 136
5 COTTIN, V , CHINET, T , LAVOLE, A , CORRE, R , MARCHAND, E , REYNAUD-GAITHERT, M , PLAUCHU, H , CORDIER, JF , (2007) PULMONARY ARTERIOVENOUS MALFORMATIONS IN HEREDITARY HEMORRHAGIC TELANGIECTASIA - A SERIES OF 126 PATIENTS.MEDICINE. VOL. 86. ISSUE 1. P. 1 -17 85 87% 75
6 CARTIN-CEBA, R , SWANSON, KL , KROWKA, MJ , (2013) PULMONARY ARTERIOVENOUS MALFORMATIONS.CHEST. VOL. 144. ISSUE 3. P. 1033-1044 69 86% 29
7 MCDONALD, J , BAYRAK-TOYDEMIR, P , PYERITZ, RE , (2011) HEREDITARY HEMORRHAGIC TELANGIECTASIA: AN OVERVIEW OF DIAGNOSIS, MANAGEMENT, AND PATHOGENESIS.GENETICS IN MEDICINE. VOL. 13. ISSUE 7. P. 607 -616 70 82% 72
8 LARSON, AM , (2003) LIVER DISEASE IN HEREDITARY HEMORRHAGIC TELANGIECTASIA.JOURNAL OF CLINICAL GASTROENTEROLOGY. VOL. 36. ISSUE 2. P. 149-158 101 71% 30
9 GARCIA-TSAO, G , (2007) LIVER INVOLVEMENT IN HEREDITARY HEMORRHAGIC TELANGIECTASIA (HHT).JOURNAL OF HEPATOLOGY. VOL. 46. ISSUE 3. P. 499-507 62 93% 59
10 GOSSAGE, JR , KANJ, G , (1998) PULMONARY ARTERIOVENOUS MALFORMATIONS - A STATE OF THE ART REVIEW.AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE. VOL. 158. ISSUE 2. P. 643 -661 64 86% 232

Classes with closest relation at Level 1



Rank Class id link
1 14371 ENDOGLIN//CD105//TRC105
2 37641 PANCREATIC ARTERIOVENOUS MALFORMATION//ARTERIOVENOUS ANGIOGRAPHY//ARTERIOVENOUS MALFORMATION OF PANCREAS
3 12926 ANGIODYSPLASIA//GASTRIC ANTRAL VASCULAR ECTASIA//WATERMELON STOMACH
4 15064 HEMOPTYSIS//BRONCHIAL ARTERY//BRONCHIAL ARTERY EMBOLIZATION
5 23788 ARTERIOPORTAL FISTULA//SPLENIC ARTERIOVENOUS FISTULA//EXTRAHEPATIC ARTERIOPORTAL FISTULA
6 10504 EPISTAXIS//NASAL PACKING//SPHENOPALATINE ARTERY
7 26579 EXTRAPLEURAL HEMATOMA//EXTRAPLEURAL FAT SIGN//ARTERIO ARTERIAL FISTULA
8 11496 HEPATOPULMONARY SYNDROME//PORTOPULMONARY HYPERTENSION//CONTRAST ENHANCED ECHOCARDIOGRAPHY
9 17298 VEIN OF GALEN//VEIN OF GALEN MALFORMATION//VEIN OF GALEN ANEURYSMAL MALFORMATION
10 2597 PATENT FORAMEN OVALE//PARADOXICAL EMBOLISM//CRYPTOGENIC STROKE

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