Class information for:
Level 1: HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS//HEMOPHAGOCYTIC SYNDROME//MACROPHAGE ACTIVATION SYNDROME

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
3749 1919 27.1 81%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
118 3       EPSTEIN BARR VIRUS//LYMPHOMA//HODGKINS DISEASE 69002
495 2             EPSTEIN BARR VIRUS//NASOPHARYNGEAL CARCINOMA//HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 15379
3749 1                   HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS//HEMOPHAGOCYTIC SYNDROME//MACROPHAGE ACTIVATION SYNDROME 1919

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS authKW 4317638 19% 76% 356
2 HEMOPHAGOCYTIC SYNDROME authKW 2648633 14% 63% 266
3 MACROPHAGE ACTIVATION SYNDROME authKW 1379508 7% 65% 133
4 HEMOPHAGOCYTOSIS authKW 1340587 7% 61% 138
5 HAEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS authKW 983742 4% 90% 69
6 FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS authKW 920825 3% 89% 65
7 HAEMOPHAGOCYTIC SYNDROME authKW 542982 2% 74% 46
8 LYMPHOHISTIOCYTOSIS authKW 413229 2% 84% 31
9 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS HLH authKW 341126 1% 79% 27
10 HLH authKW 323550 2% 54% 38

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 21534 32% 0% 623
2 Pediatrics 8738 24% 0% 455
3 Rheumatology 3472 8% 0% 153
4 Oncology 1722 17% 0% 329
5 Medicine, General & Internal 769 11% 0% 206
6 Pathology 715 6% 0% 117
7 Immunology 400 9% 0% 167
8 Infectious Diseases 307 5% 0% 87
9 Transplantation 249 3% 0% 53
10 Medical Laboratory Technology 109 2% 0% 29

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 IMMUNODEFICIENCY HISTIOCYTOSIS PROGRAM 50912 0% 80% 4
2 CHILDHOOD CANC UNIT 49264 2% 9% 36
3 UNITE RECH DEV NORMAL PATHOL SYST IMMUNITAIRE 45851 0% 41% 7
4 ONCO EMATOL PEDIAT 31821 0% 100% 2
5 PAEDIAT IHOBA 31821 0% 100% 2
6 ZENTRUM FRAUENHEILKUNDE KINDER JUGENDMED 31821 0% 100% 2
7 NORMAL PATHOL HOMEOSTASIS IMMUNE SYST 31817 0% 50% 4
8 BONE MARROW TRANSPLANT IMMUNE DEFICIENCY 26872 0% 24% 7
9 BONE MARROW TRANSPLANTAT IMMUNE DEFICIENCY 23845 1% 13% 12
10 MOL MED SURGCLIN GENET UNIT 21212 0% 67% 2

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PEDIATRIC HEMATOLOGY AND ONCOLOGY 13114 2% 2% 41
2 INTERNATIONAL JOURNAL OF HEMATOLOGY 11791 3% 1% 53
3 JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY 10908 3% 1% 50
4 PEDIATRIC BLOOD & CANCER 9823 3% 1% 53
5 INDIAN JOURNAL OF HEMATOLOGY AND BLOOD TRANSFUSION 7868 1% 3% 17
6 BRITISH JOURNAL OF HAEMATOLOGY 4600 3% 0% 63
7 PEDIATRIC RHEUMATOLOGY 2821 0% 2% 8
8 INTERNATIONAL JOURNAL OF PEDIATRIC HEMATOLOGY/ONCOLOGY 2620 0% 2% 7
9 TURKISH JOURNAL OF HEMATOLOGY 2582 0% 2% 8
10 BLOOD 2497 4% 0% 75

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 4317638 19% 76% 356 Search HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS Search HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS
2 HEMOPHAGOCYTIC SYNDROME 2648633 14% 63% 266 Search HEMOPHAGOCYTIC+SYNDROME Search HEMOPHAGOCYTIC+SYNDROME
3 MACROPHAGE ACTIVATION SYNDROME 1379508 7% 65% 133 Search MACROPHAGE+ACTIVATION+SYNDROME Search MACROPHAGE+ACTIVATION+SYNDROME
4 HEMOPHAGOCYTOSIS 1340587 7% 61% 138 Search HEMOPHAGOCYTOSIS Search HEMOPHAGOCYTOSIS
5 HAEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 983742 4% 90% 69 Search HAEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS Search HAEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS
6 FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 920825 3% 89% 65 Search FAMILIAL+HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS Search FAMILIAL+HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS
7 HAEMOPHAGOCYTIC SYNDROME 542982 2% 74% 46 Search HAEMOPHAGOCYTIC+SYNDROME Search HAEMOPHAGOCYTIC+SYNDROME
8 LYMPHOHISTIOCYTOSIS 413229 2% 84% 31 Search LYMPHOHISTIOCYTOSIS Search LYMPHOHISTIOCYTOSIS
9 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS HLH 341126 1% 79% 27 Search HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS+HLH Search HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS+HLH
10 HLH 323550 2% 54% 38 Search HLH Search HLH

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 RAMOS-CASALS, M , BRITO-ZERON, P , LOPEZ-GUILLERMO, A , KHAMASHTA, MA , BOSCH, X , (2014) ADULT HAEMOPHAGOCYTIC SYNDROME.LANCET. VOL. 383. ISSUE 9927. P. 1503 -1516 93 86% 74
2 USMANI, GN , WODA, BA , NEWBURGER, PE , (2013) ADVANCES IN UNDERSTANDING THE PATHOGENESIS OF HLH.BRITISH JOURNAL OF HAEMATOLOGY. VOL. 161. ISSUE 5. P. 609-622 94 85% 48
3 ROSADO, FGN , KIM, AS , (2013) HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS AN UPDATE ON DIAGNOSIS AND PATHOGENESIS.AMERICAN JOURNAL OF CLINICAL PATHOLOGY. VOL. 139. ISSUE 6. P. 713-727 98 81% 49
4 FILIPPONE, EJ , FARBER, JL , (2016) HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS: AN UPDATE FOR NEPHROLOGISTS.INTERNATIONAL UROLOGY AND NEPHROLOGY. VOL. 48. ISSUE 8. P. 1291 -1304 106 83% 0
5 ZHANG, L , ZHOU, J , SOKOL, L , (2014) HEREDITARY AND ACQUIRED HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS.CANCER CONTROL. VOL. 21. ISSUE 4. P. 301 -312 98 87% 5
6 GUPTA, S , WEITZMAN, S , (2010) PRIMARY AND SECONDARY HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS: CLINICAL FEATURES, PATHOGENESIS AND THERAPY.EXPERT REVIEW OF CLINICAL IMMUNOLOGY. VOL. 6. ISSUE 1. P. 137-154 114 70% 68
7 HENTER, JI , HORNE, A , ARICO, M , EGELER, RM , FILIPOVICH, AH , IMASHUKU, S , LADISCH, S , MCCLAIN, K , WEBB, D , WINIARSKI, J , ET AL (2007) HLH-2004: DIAGNOSTIC AND THERAPEUTIC GUIDELINES FOR HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS.PEDIATRIC BLOOD & CANCER. VOL. 48. ISSUE 2. P. 124-131 47 92% 998
8 JANKA, GE , (2007) FAMILIAL AND ACQUIRED HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS.EUROPEAN JOURNAL OF PEDIATRICS. VOL. 166. ISSUE 2. P. 95-109 87 81% 208
9 JORDAN, MB , ALLEN, CE , WEITZMAN, S , FILIPOVICH, AH , MCCLAIN, KL , (2011) HOW I TREAT HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS.BLOOD. VOL. 118. ISSUE 15. P. 4041-4052 67 82% 163
10 HAYDEN, A , PARK, S , GIUSTINI, D , LEE, AYY , CHEN, LYC , (2016) HEMOPHAGOCYTIC SYNDROMES (HPSS) INCLUDING HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS (HLH) IN ADULTS: A SYSTEMATIC SCOPING REVIEW.BLOOD REVIEWS. VOL. 30. ISSUE 6. P. 411 -420 69 90% 2

Classes with closest relation at Level 1



Rank Class id link
1 22954 CHRONIC ACTIVE EPSTEIN BARR VIRUS INFECTION//HYPERSENSITIVITY TO MOSQUITO BITES//HYDROA VACCINIFORME
2 15548 ADULT ONSET STILLS DISEASE//STILLS DISEASE//ADULT STILLS DISEASE
3 20278 CHEDIAK HIGASHI SYNDROME//GRISCELLI SYNDROME//LYST
4 15071 XLP//X LINKED LYMPHOPROLIFERATIVE DISEASE//2B4
5 17024 FOLLICULAR DENDRITIC CELL SARCOMA//HISTIOCYTIC SARCOMA//INTERDIGITATING DENDRITIC CELL SARCOMA
6 11125 PANNICULITIS//SUBCUTANEOUS PANNICULITIS LIKE T CELL LYMPHOMA//WEBER CHRISTIAN DISEASE
7 15374 INTRAVASCULAR LYMPHOMA//INTRAVASCULAR LYMPHOMATOSIS//INTRAVASCULAR LARGE B CELL LYMPHOMA
8 2247 JUVENILE IDIOPATHIC ARTHRITIS//JUVENILE RHEUMATOID ARTHRITIS//JUVENILE CHRONIC ARTHRITIS
9 11559 INFECTIOUS MONONUCLEOSIS//EPSTEIN BARR VIRUS//MONONUCLEOSIS
10 3875 GRANZYME//GRANZYME B//PERFORIN

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