Class information for:
Level 1: ALPORT SYNDROME//GOODPASTURES SYNDROME//GOODPASTURES DISEASE

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
3158 2051 31.4 71%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
307 3       INTEGRIN//ALPORT SYNDROME//LAMININ 40384
1878 2             ALPORT SYNDROME//LAMININ//BASEMENT MEMBRANE 6010
3158 1                   ALPORT SYNDROME//GOODPASTURES SYNDROME//GOODPASTURES DISEASE 2051

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ALPORT SYNDROME authKW 3587599 14% 81% 297
2 GOODPASTURES SYNDROME authKW 965900 5% 67% 97
3 GOODPASTURES DISEASE authKW 509699 2% 80% 43
4 HEREDITARY NEPHRITIS authKW 467286 2% 83% 38
5 GLOMERULAR BASEMENT MEMBRANE authKW 385107 4% 29% 90
6 COL4A5 authKW 379367 1% 88% 29
7 TYPE IV COLLAGEN authKW 345772 6% 20% 116
8 ANTI GBM ANTIBODIES authKW 334926 1% 75% 30
9 THIN BASEMENT MEMBRANE NEPHROPATHY authKW 333441 1% 80% 28
10 ANTI GLOMERULAR BASEMENT MEMBRANE DISEASE authKW 332937 2% 57% 39

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Urology & Nephrology 31078 36% 0% 738
2 Transplantation 1903 7% 0% 137
3 Pathology 1854 9% 0% 186
4 Pediatrics 793 8% 0% 158
5 Ophthalmology 561 5% 0% 104
6 Genetics & Heredity 404 7% 0% 148
7 Medicine, General & Internal 384 8% 0% 163
8 Biochemistry & Molecular Biology 309 15% 0% 300
9 Medicine, Research & Experimental 136 4% 0% 87
10 Microscopy 116 1% 0% 19

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ULTRASTRUCT BIOL 211712 1% 89% 16
2 MED NO HLTH 66985 0% 75% 6
3 NO HOSP 52920 0% 44% 8
4 UNIT RENAL MORPHOL 44659 0% 100% 3
5 UNIT DEV NEPHROL FCT 725 33493 0% 75% 3
6 MERHEIM MED INTERNAL MED 1 29773 0% 100% 2
7 COLOGNE GEN HOSP 28621 0% 38% 5
8 MED NORTHERN HLTH 26793 0% 60% 3
9 MATRIX BIOL 25911 1% 6% 27
10 REFERENCE MALAD RENALES HEREDITAI ENFANT 23519 0% 23% 7

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 KIDNEY INTERNATIONAL 20601 7% 1% 142
2 PEDIATRIC NEPHROLOGY 15650 4% 1% 80
3 NEPHROLOGY DIALYSIS TRANSPLANTATION 14464 5% 1% 110
4 JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY 8853 3% 1% 66
5 CLINICAL NEPHROLOGY 8090 3% 1% 52
6 AMERICAN JOURNAL OF KIDNEY DISEASES 6679 3% 1% 62
7 COLLAGEN AND RELATED RESEARCH 4706 0% 3% 10
8 AMERICAN JOURNAL OF NEPHROLOGY 2396 1% 1% 23
9 SEMINARS IN NEPHROLOGY 2213 1% 1% 17
10 NEPHRON 2209 1% 1% 27

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 ALPORT SYNDROME 3587599 14% 81% 297 Search ALPORT+SYNDROME Search ALPORT+SYNDROME
2 GOODPASTURES SYNDROME 965900 5% 67% 97 Search GOODPASTURES+SYNDROME Search GOODPASTURES+SYNDROME
3 GOODPASTURES DISEASE 509699 2% 80% 43 Search GOODPASTURES+DISEASE Search GOODPASTURES+DISEASE
4 HEREDITARY NEPHRITIS 467286 2% 83% 38 Search HEREDITARY+NEPHRITIS Search HEREDITARY+NEPHRITIS
5 GLOMERULAR BASEMENT MEMBRANE 385107 4% 29% 90 Search GLOMERULAR+BASEMENT+MEMBRANE Search GLOMERULAR+BASEMENT+MEMBRANE
6 COL4A5 379367 1% 88% 29 Search COL4A5 Search COL4A5
7 TYPE IV COLLAGEN 345772 6% 20% 116 Search TYPE+IV+COLLAGEN Search TYPE+IV+COLLAGEN
8 ANTI GBM ANTIBODIES 334926 1% 75% 30 Search ANTI+GBM+ANTIBODIES Search ANTI+GBM+ANTIBODIES
9 THIN BASEMENT MEMBRANE NEPHROPATHY 333441 1% 80% 28 Search THIN+BASEMENT+MEMBRANE+NEPHROPATHY Search THIN+BASEMENT+MEMBRANE+NEPHROPATHY
10 ANTI GLOMERULAR BASEMENT MEMBRANE DISEASE 332937 2% 57% 39 Search ANTI+GLOMERULAR+BASEMENT+MEMBRANE+DISEASE Search ANTI+GLOMERULAR+BASEMENT+MEMBRANE+DISEASE

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 HERTZ, JM , (2009) ALPORT SYNDROME MOLECULAR GENETIC ASPECTS.DANISH MEDICAL BULLETIN. VOL. 56. ISSUE 3. P. 105-152 258 78% 11
2 KASHTAN, CE , (1999) ALPORT SYNDROME - AN INHERITED DISORDER OF RENAL, OCULAR, AND COCHLEAR BASEMENT MEMBRANES.MEDICINE. VOL. 78. ISSUE 5. P. 338 -360 160 91% 85
3 MAO, M , ALAVI, MV , LABELLE-DUMAIS, C , GOULD, DB , (2015) TYPE IV COLLAGENS AND BASEMENT MEMBRANE DISEASES: CELL BIOLOGY AND PATHOGENIC MECHANISMS.BASEMENT MEMBRANES. VOL. 76. ISSUE . P. 61 -116 152 54% 1
4 BORZA, DB , HUDSON, BG , (2003) MOLECULAR CHARACTERIZATION OF THE TARGET ANTIGENS OF ANTI-GLOMERULAR BASEMENT MEMBRANE ANTIBODY DISEASE.SPRINGER SEMINARS IN IMMUNOPATHOLOGY. VOL. 24. ISSUE 4. P. 345-361 110 96% 16
5 HUDSON, BG , TRYGGVASON, K , SUNDARAMOORTHY, M , NEILSON, EG , (2003) ALPORT'S SYNDROME, GOODPASTURE'S SYNDROME, AND TYPE IV COLLAGEN.NEW ENGLAND JOURNAL OF MEDICINE. VOL. 348. ISSUE 25. P. 2543-2556 95 75% 396
6 KASHTAN, CE , MICHAEL, AF , (1996) ALPORT SYNDROME.KIDNEY INTERNATIONAL. VOL. 50. ISSUE 5. P. 1445 -1463 119 90% 104
7 HUDSON, BG , (2004) THE MOLECULAR BASIS OF GOODPASTURE AND ALPORT SYNDROMES: BEACONS FOR THE DISCOVERY OF THE COLLAGEN IV FAMILY.JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY. VOL. 15. ISSUE 10. P. 2514-2527 82 94% 65
8 CUI, Z , ZHAO, MH , (2011) ADVANCES IN HUMAN ANTIGLOMERULAR BASEMENT MEMBRANE DISEASE.NATURE REVIEWS NEPHROLOGY. VOL. 7. ISSUE 12. P. 697-705 76 83% 18
9 TRYGGVASON, K , PATRAKKA, J , (2006) THIN BASEMENT MEMBRANE NEPHROPATHY.JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY. VOL. 17. ISSUE 3. P. 813-822 75 95% 36
10 HEIDET, L , GUBLER, MC , (2016) ALPORT SYNDROME: HEREDITARY NEPHROPATHY ASSOCIATED WITH MUTATIONS IN GENES CODING FOR TYPE IV COLLAGEN CHAINS.NEPHROLOGIE & THERAPEUTIQUE. VOL. 12. ISSUE 7. P. 544 -551 62 93% 0

Classes with closest relation at Level 1



Rank Class id link
1 9452 ANIONIC SITES//GLOMERULAR BASEMENT MEMBRANE//CATIONIC COLLOIDAL GOLD
2 22007 PERIRENAL PSEUDOCYST//GLOMERULOCYSTIC KIDNEY DISEASE//JUVENILE NEPHROPATHY
3 31365 NEPHROPTOSIS//LOIN PAIN HAEMATURIA SYNDROME//NEPHROPEXY
4 23749 NAIL PATELLA SYNDROME//LMX1B//COLLAGENOFIBROTIC GLOMERULOPATHY
5 2796 LAMININ//BASEMENT MEMBRANE//LAMININ 5
6 7566 GLOMERULONEPHRITIS//INFLAMMATORY DIS//NEPHROTOXIC NEPHRITIS
7 30823 ABT WERPUNKT NEPHROL 4//ANCA ASSOCIATED RENAL DISEASE//CUSTODY OF HABITUAL CRIMINALS AND CRIMINALLY INSANE
8 23079 RECURRENT GLOMERULONEPHRITIS//RECURRENT IGA NEPHROPATHY//DE NOVO GLOMERULONEPHRITIS
9 25623 MATH THEORET STAT//1 1 2 TRICHLORO 1 2 2 TRIFLUOROETHANE FC 113//AEROSP MED HOSP
10 21917 ENT DIS HEAD NECK SURG//CARCINOMA CELL INVASION//PATHOBIOCHEM INTERNAL MED 4

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