Class information for:
Level 1: KENNEDYS DISEASE//SPINAL AND BULBAR MUSCULAR ATROPHY//SBMA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
20207 471 38.7 79%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
21 4 UROLOGY & NEPHROLOGY//UROL//JOURNAL OF UROLOGY 229838
272 3       PROSTATE CANCER//PROSTATIC NEOPLASMS//UROL 43768
534 2             ANDROGEN RECEPTOR//PROSTATE CANCER//CASTRATION RESISTANT PROSTATE CANCER 14838
20207 1                   KENNEDYS DISEASE//SPINAL AND BULBAR MUSCULAR ATROPHY//SBMA 471

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 KENNEDYS DISEASE authKW 3771878 17% 73% 80
2 SPINAL AND BULBAR MUSCULAR ATROPHY authKW 3308988 15% 73% 70
3 SBMA authKW 868398 5% 56% 24
4 X LINKED SPINAL AND BULBAR MUSCULAR ATROPHY authKW 847109 3% 93% 14
5 X LINKED RECESSIVE BULBOSPINAL NEURONOPATHY authKW 583469 2% 100% 9
6 KENNEDY SYNDROME authKW 437597 2% 75% 9
7 SPINAL BULBAR MUSCULAR ATROPHY authKW 264716 1% 58% 7
8 INTERUNIV MALATTIE NEURODEGENERAT address 259316 1% 67% 6
9 SPINOBULBAR MUSCULAR ATROPHY authKW 238681 2% 41% 9
10 BULBOSPINAL NEURONOPATHY authKW 207454 1% 80% 4

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 5389 46% 0% 219
2 Neurosciences 2542 43% 0% 203
3 Genetics & Heredity 217 10% 0% 48
4 Pathology 166 6% 0% 28
5 Psychiatry 110 7% 0% 31
6 Biochemistry & Molecular Biology 108 17% 0% 79
7 Medicine, Research & Experimental 41 5% 0% 22
8 Medicine, General & Internal 24 5% 0% 24
9 Endocrinology & Metabolism 24 4% 0% 19
10 Cell Biology 23 6% 0% 27

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 INTERUNIV MALATTIE NEURODEGENERAT 259316 1% 67% 6
2 NEUROGENET BRANCH 198492 6% 11% 28
3 INTERUNIV NEURODEGENERAT DIS 147335 1% 45% 5
4 CLIN CENT PERIPHERAL DEGENERAT NEUROPATHIES UNI 132351 1% 29% 7
5 ECCELLENZA MALATTIE NEURODEGENERAT 129652 1% 33% 6
6 DULBECCO TELETHON NEURODEGENERAT DIS 97242 1% 50% 3
7 CENT NEUROPHYSIOL S 86439 0% 67% 2
8 DIPARTIMENTO SCI FARMACOL BIOMOL DISFEB 85295 1% 26% 5
9 SEZ BIOMED ENDOCRINOL 83349 1% 43% 3
10 BC BESTA NEUROL 64830 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF THE NEUROLOGICAL SCIENCES 5016 6% 0% 28
2 HUMAN MOLECULAR GENETICS 4822 6% 0% 27
3 JOURNAL OF MOLECULAR NEUROSCIENCE 3422 3% 0% 12
4 ZHURNAL NEVROPATOLOGII I PSIKHIATRII IMENI S S KORSAKOVA 3240 3% 0% 13
5 MUSCLE & NERVE 2627 4% 0% 17
6 NEUROMUSCULAR DISORDERS 2219 2% 0% 9
7 AMYOTROPHIC LATERAL SCLEROSIS 2216 1% 1% 5
8 NEUROLOGY 1735 5% 0% 24
9 AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEGENERATION 1610 1% 1% 3
10 JOURNAL OF NEUROLOGY 1276 2% 0% 11

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 KENNEDYS DISEASE 3771878 17% 73% 80 Search KENNEDYS+DISEASE Search KENNEDYS+DISEASE
2 SPINAL AND BULBAR MUSCULAR ATROPHY 3308988 15% 73% 70 Search SPINAL+AND+BULBAR+MUSCULAR+ATROPHY Search SPINAL+AND+BULBAR+MUSCULAR+ATROPHY
3 SBMA 868398 5% 56% 24 Search SBMA Search SBMA
4 X LINKED SPINAL AND BULBAR MUSCULAR ATROPHY 847109 3% 93% 14 Search X+LINKED+SPINAL+AND+BULBAR+MUSCULAR+ATROPHY Search X+LINKED+SPINAL+AND+BULBAR+MUSCULAR+ATROPHY
5 X LINKED RECESSIVE BULBOSPINAL NEURONOPATHY 583469 2% 100% 9 Search X+LINKED+RECESSIVE+BULBOSPINAL+NEURONOPATHY Search X+LINKED+RECESSIVE+BULBOSPINAL+NEURONOPATHY
6 KENNEDY SYNDROME 437597 2% 75% 9 Search KENNEDY+SYNDROME Search KENNEDY+SYNDROME
7 SPINAL BULBAR MUSCULAR ATROPHY 264716 1% 58% 7 Search SPINAL+BULBAR+MUSCULAR+ATROPHY Search SPINAL+BULBAR+MUSCULAR+ATROPHY
8 SPINOBULBAR MUSCULAR ATROPHY 238681 2% 41% 9 Search SPINOBULBAR+MUSCULAR+ATROPHY Search SPINOBULBAR+MUSCULAR+ATROPHY
9 BULBOSPINAL NEURONOPATHY 207454 1% 80% 4 Search BULBOSPINAL+NEURONOPATHY Search BULBOSPINAL+NEURONOPATHY
10 SPINOBULBAR MUSCULAR ATROPHY SBMA 194490 1% 100% 3 Search SPINOBULBAR+MUSCULAR+ATROPHY+SBMA Search SPINOBULBAR+MUSCULAR+ATROPHY+SBMA

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 KATSUNO, M , TANAKA, F , ADACHI, H , BANNO, H , SUZUKI, K , WATANABE, H , SOBUE, G , (2012) PATHOGENESIS AND THERAPY OF SPINAL AND BULBAR MUSCULAR ATROPHY (SBMA).PROGRESS IN NEUROBIOLOGY. VOL. 99. ISSUE 3. P. 246-256 90 70% 34
2 BEITEL, LK , ALVARADO, C , MOKHTAR, S , PALIOURAS, M , TRIFIRO, M , (2013) MECHANISMS MEDIATING SPINAL AND BULBAR MUSCULAR ATROPHY: INVESTIGATIONS INTO POLYGLUTAMINE-EXPANDED ANDROGEN RECEPTOR FUNCTION AND DYSFUNCTION.FRONTIERS IN NEUROLOGY. VOL. 4. ISSUE . P. - 88 61% 10
3 FINSTERER, J , (2010) PERSPECTIVES OF KENNEDY'S DISEASE.JOURNAL OF THE NEUROLOGICAL SCIENCES. VOL. 298. ISSUE 1-2. P. 1-10 57 81% 18
4 CHUA, JP , LIEBERMAN, AP , (2013) PATHOGENIC MECHANISMS AND THERAPEUTIC STRATEGIES IN SPINOBULBAR MUSCULAR ATROPHY.CNS & NEUROLOGICAL DISORDERS-DRUG TARGETS. VOL. 12. ISSUE 8. P. 1146 -1156 84 51% 3
5 PENNUTO, M , GREENSMITH, L , PRADAT, PF , SORARU, G , (2015) 210TH ENMC INTERNATIONAL WORKSHOP: RESEARCH AND CLINICAL MANAGEMENT OF PATIENTS WITH SPINAL AND BULBAR MUSCULAR ATROPHY, 27-29 MARCH, 2015, NAARDEN, THE NETHERLANDS.NEUROMUSCULAR DISORDERS. VOL. 25. ISSUE 10. P. 802 -812 54 66% 2
6 RINALDI, C , MALIK, B , GREENSMITH, L , (2016) TARGETED MOLECULAR THERAPIES FOR SBMA.JOURNAL OF MOLECULAR NEUROSCIENCE. VOL. 58. ISSUE 3. P. 335 -342 48 69% 1
7 FINSTERER, J , SORARU, G , (2016) ONSET MANIFESTATIONS OF SPINAL AND BULBAR MUSCULAR ATROPHY (KENNEDY'S DISEASE).JOURNAL OF MOLECULAR NEUROSCIENCE. VOL. 58. ISSUE 3. P. 321 -329 36 97% 0
8 ROCCHI, A , PENNUTO, M , (2013) NEW ROUTES TO THERAPY FOR SPINAL AND BULBAR MUSCULAR ATROPHY.JOURNAL OF MOLECULAR NEUROSCIENCE. VOL. 50. ISSUE 3. P. 514 -523 53 67% 7
9 GIORGETTI, E , RUSMINI, P , CRIPPA, V , CRISTOFANI, R , BONCORAGLIO, A , CICARDI, ME , GALBIATI, M , POLETTI, A , (2015) SYNERGIC PRODEGRADATIVE ACTIVITY OF BICALUTAMIDE AND TREHALOSE ON THE MUTANT ANDROGEN RECEPTOR RESPONSIBLE FOR SPINAL AND BULBAR MUSCULAR ATROPHY.HUMAN MOLECULAR GENETICS. VOL. 24. ISSUE 1. P. 64 -75 44 72% 5
10 ZAJAC, JA , FUI, MNT , (2012) KENNEDY'S DISEASE CLINICAL SIGNIFICANCE OF TANDEM REPEATS IN THE ANDROGEN RECEPTOR.TANDEM REPEAT POLYMORPHISMS: GENETIC PLASTICITY, NEURAL DIVERSITY AND DISEASE. VOL. 769. ISSUE . P. 153-168 52 69% 2

Classes with closest relation at Level 1



Rank Class id link
1 15439 CAG REPEAT//ANDROGEN RECEPTOR GENE//ANDROGEN RECEPTOR
2 19332 SPINAL NUCLEUS OF THE BULBOCAVERNOSUS//BULBOCAVERNOSUS//BHRP
3 377 HUNTINGTONS DISEASE//HUNTINGTIN//POLYGLUTAMINE
4 11214 ANDROGEN INSENSITIVITY SYNDROME//ANDROGEN INSENSITIVITY//TESTICULAR FEMINIZATION
5 2557 SPINOCEREBELLAR ATAXIA//MACHADO JOSEPH DISEASE//SCA2
6 16834 SECT GENE STRUCT DIS//REPEAT INSTABILITY//MUTS BETA
7 1876 ANDROGEN RECEPTOR//GEORGE WHIPPLE CANC//CASTRATION RESISTANT PROSTATE CANCER
8 7068 AMYOTROPHIC LATERAL SCLEROSIS//PRIMARY LATERAL SCLEROSIS//MOTOR NEURON DISEASE
9 32627 IGHMBP2//SMARD1//SPINAL MUSCULAR ATROPHY WITH RESPIRATORY DISTRESS
10 4018 SPINAL MUSCULAR ATROPHY//SMN//SURVIVAL MOTOR NEURON

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