Class information for:
Level 1: KLIPPEL TRENAUNAY SYNDROME//KLIPPEL TRENAUNAY WEBER SYNDROME//PARKES WEBER SYNDROME

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
19108 521 19.9 61%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
391 3       ARTERIOVENOUS MALFORMATION//VERTEBROPLASTY//DURAL ARTERIOVENOUS FISTULA 30586
1399 2             HEMANGIOMA//LYMPHANGIOMA//INFANTILE HEMANGIOMA 8083
19108 1                   KLIPPEL TRENAUNAY SYNDROME//KLIPPEL TRENAUNAY WEBER SYNDROME//PARKES WEBER SYNDROME 521

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 KLIPPEL TRENAUNAY SYNDROME authKW 4945850 22% 74% 114
2 KLIPPEL TRENAUNAY WEBER SYNDROME authKW 1858851 8% 77% 41
3 PARKES WEBER SYNDROME authKW 652323 3% 70% 16
4 RASA1 authKW 337570 2% 48% 12
5 KLIPPEL TRENAUNAY WEBER authKW 301411 1% 86% 6
6 UNIT VASC MALFORMAT address 234432 1% 100% 4
7 AGGF1 authKW 234428 1% 67% 6
8 KLIPPEL TRENAUNAY authKW 209312 1% 71% 5
9 ANGIO OSTEOHYPERTROPHY SYNDROME authKW 187544 1% 80% 4
10 KLIPPEL TRENAUNAY SYNDROME KTS authKW 187544 1% 80% 4

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 1321 12% 0% 65
2 Peripheral Vascular Diseases 803 12% 0% 63
3 Surgery 744 22% 0% 113
4 Radiology, Nuclear Medicine & Medical Imaging 664 15% 0% 77
5 Pediatrics 579 12% 0% 64
6 Genetics & Heredity 198 9% 0% 49
7 Obstetrics & Gynecology 153 6% 0% 31
8 Clinical Neurology 126 8% 0% 43
9 Acoustics 110 3% 0% 16
10 Neuroimaging 107 2% 0% 10

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 UNIT VASC MALFORMAT 234432 1% 100% 4
2 VASC MALFORMAT CLIN 78143 0% 67% 2
3 ALIASGHAR PEDIAT 58608 0% 100% 1
4 ANGIODYSPLASIE SPRECHSTUNDE 58608 0% 100% 1
5 CENTER CARDIOVASC GENET MOL MED 58608 0% 100% 1
6 CHRISTIAN DU DUVE CELLULAR PATHOL 58608 0% 100% 1
7 CLIN MATERNO FETAL 58608 0% 100% 1
8 CLIN RADIODIAGNOST IMAGE TECH 58608 0% 100% 1
9 CONSULTAT MULTIDISCIPLINAIRE ANGIODYSPLASIES COMP 58608 0% 100% 1
10 HEMANGIOMA SURGHENAN PROV PEOPLES HOSP 58608 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 RONTGEN-BLATTER KLINIK UND PRAXIS 6510 0% 11% 1
2 PHLEBOLOGY 3031 2% 1% 8
3 PEDIATRIC DERMATOLOGY 2269 2% 0% 12
4 AMERICAN JOURNAL OF MEDICAL GENETICS PART A 1445 2% 0% 12
5 EUROPEAN JOURNAL OF MEDICAL GENETICS 1280 1% 0% 5
6 PHLEBOLOGIE-ANNALES VASCULAIRES 1198 0% 1% 2
7 JOURNAL OF VASCULAR SURGERY-VENOUS AND LYMPHATIC DISORDERS 1011 0% 1% 2
8 ANNALS OF VASCULAR SURGERY 951 2% 0% 8
9 VASA-JOURNAL OF VASCULAR DISEASES 761 1% 0% 5
10 JOURNAL OF VASCULAR SURGERY 760 2% 0% 12

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 KLIPPEL TRENAUNAY SYNDROME 4945850 22% 74% 114 Search KLIPPEL+TRENAUNAY+SYNDROME Search KLIPPEL+TRENAUNAY+SYNDROME
2 KLIPPEL TRENAUNAY WEBER SYNDROME 1858851 8% 77% 41 Search KLIPPEL+TRENAUNAY+WEBER+SYNDROME Search KLIPPEL+TRENAUNAY+WEBER+SYNDROME
3 PARKES WEBER SYNDROME 652323 3% 70% 16 Search PARKES+WEBER+SYNDROME Search PARKES+WEBER+SYNDROME
4 RASA1 337570 2% 48% 12 Search RASA1 Search RASA1
5 KLIPPEL TRENAUNAY WEBER 301411 1% 86% 6 Search KLIPPEL+TRENAUNAY+WEBER Search KLIPPEL+TRENAUNAY+WEBER
6 AGGF1 234428 1% 67% 6 Search AGGF1 Search AGGF1
7 KLIPPEL TRENAUNAY 209312 1% 71% 5 Search KLIPPEL+TRENAUNAY Search KLIPPEL+TRENAUNAY
8 ANGIO OSTEOHYPERTROPHY SYNDROME 187544 1% 80% 4 Search ANGIO+OSTEOHYPERTROPHY+SYNDROME Search ANGIO+OSTEOHYPERTROPHY+SYNDROME
9 KLIPPEL TRENAUNAY SYNDROME KTS 187544 1% 80% 4 Search KLIPPEL+TRENAUNAY+SYNDROME+KTS Search KLIPPEL+TRENAUNAY+SYNDROME+KTS
10 LOCALIZED INTRAVASCULAR COAGULATION 131867 1% 75% 3 Search LOCALIZED+INTRAVASCULAR+COAGULATION Search LOCALIZED+INTRAVASCULAR+COAGULATION

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 STAR, A , FULLER, CE , LANDAS, SK , (2010) INTRACRANIAL ANEURYSMS IN KLIPPEL-TRENAUNAY/WEBER SYNDROMES: CASE REPORT.NEUROSURGERY. VOL. 66. ISSUE 5. P. E1027-E1028 58 82% 6
2 STEIN, SR , PERLOW, JH , SAWAI, SK , (2006) KLIPPEL-TRENAUNAY-TYPE SYNDROME IN PREGNANCY.OBSTETRICAL & GYNECOLOGICAL SURVEY. VOL. 61. ISSUE 3. P. 194-206 29 100% 8
3 VOLZ, KR , KANNER, CD , EVANS, J , EVANS, KD , (2016) KLIPPEL-TRENAUNAY SYNDROME NEED FOR CAREFUL CLINICAL CLASSIFICATION.JOURNAL OF ULTRASOUND IN MEDICINE. VOL. 35. ISSUE 9. P. 2057 -2065 25 83% 0
4 ODUBER, CNEU , VAN DER HORST, CMAM , HENNEKAM, RCM , (2008) KLIPPEL-TRENAUNAY SYNDROME - DIAGNOSTIC CRITERIA AND HYPOTHESIS ON ETIOLOGY.ANNALS OF PLASTIC SURGERY. VOL. 60. ISSUE 2. P. 217 -223 26 67% 55
5 PENG, HH , WANG, TH , CHAO, AS , CHANG, YL , SHIEH, SC , CHANG, SD , (2006) KLIPPEL-TRENAUNAY-WEBER SYNDROME INVOLVING FETAL THIGH: PRENATAL PRESENTATIONS AND OUTCOMES.PRENATAL DIAGNOSIS. VOL. 26. ISSUE 9. P. 825-830 20 100% 6
6 KIHICZAK, GG , MEINE, JG , SCHWARTZ, RA , JANNIGER, CK , (2006) KLIPPEL-TRENAUNAY SYNDROME: A MULTISYSTEM DISORDER POSSIBLY RESULTING FROM A PATHOGENIC GENE FOR VASCULAR AND TISSUE OVERGROWTH.INTERNATIONAL JOURNAL OF DERMATOLOGY. VOL. 45. ISSUE 8. P. 883-890 31 61% 34
7 SREEKAR, H , DAWRE, S , PETKAR, KS , SHETTY, RB , LAMBA, S , NAIK, S , GUPTA, AK , (2013) DIVERSE MANIFESTATIONS AND MANAGEMENT OPTIONS IN KLIPPEL-TRENAUNAY SYNDROME: A SINGLE CENTRE 10-YEAR EXPERIENCE.JOURNAL OF PLASTIC SURGERY AND HAND SURGERY. VOL. 47. ISSUE 4. P. 303-307 17 94% 2
8 ZOPPI, MA , IBBA, RM , FLORIS, M , PUTZOLU, M , CRISPONI, G , MONNI, G , (2001) PRENATAL SONOGRAPHIC DIAGNOSIS OF KLIPPEL-TRENAUNAY-WEBER SYNDROME WITH CARDIAC FAILURE.JOURNAL OF CLINICAL ULTRASOUND. VOL. 29. ISSUE 7. P. 422-426 22 100% 6
9 JANSON, M , JANSON, G , SANT'ANA, E , ALESSIO, LE , DE ALMEIDA, RR , (2010) OPEN-BITE ORTHODONTIC-SURGICAL TREATMENT IN THE KLIPPEL-TRENAUNAY-WEBER SYNDROME: A CASE REPORT.ORAL SURGERY ORAL MEDICINE ORAL PATHOLOGY ORAL RADIOLOGY AND ENDODONTOLOGY. VOL. 109. ISSUE 6. P. E17 -E25 18 95% 0
10 OZKAN, Y , SANAL, B , (2015) KLIPPEL-TRENAUNAY SYNDROME ACCOMPANIED BY THE FINDINGS OF SCOLIOSIS AND SPINAL NERVE ROOT COMPRESSION DUE TO AVM.TURKIYE FIZIKSEL TIP VE REHABILITASYON DERGISI-TURKISH JOURNAL OF PHYSICAL MEDICINE AND REHABILITATION. VOL. 61. ISSUE 2. P. 179 -183 15 100% 0

Classes with closest relation at Level 1



Rank Class id link
1 26383 ANASTOMOSING HEMANGIOMA//BLADDER HEMANGIOMA//ANGIOMA GENITOURINARY SYSTEM
2 14681 PROTEUS SYNDROME//MACRODACTYLY//ENCEPHALOCRANIOCUTANEOUS LIPOMATOSIS
3 24469 BLUE RUBBER BLEB NEVUS SYNDROME//BEAN SYNDROME//BRBNS
4 35832 ACROANGIODERMATITIS//STEWART BLUEFARB SYNDROME//PSEUDO KAPOSI SARCOMA
5 3092 VENOUS MALFORMATION//LYMPHATIC MALFORMATION//SCLEROTHERAPY
6 17613 STURGE WEBER SYNDROME//CHOROIDAL HEMANGIOMA//CIRCUMSCRIBED CHOROIDAL HEMANGIOMA
7 22311 TWIN SPOTTING//PHACOMATOSIS PIGMENTOVASCULARIS//MONGOLIAN SPOT
8 19553 APLASIA CUTIS CONGENITA//ADAMS OLIVER SYNDROME//CUTIS MARMORATA TELANGIECTATICA CONGENITA
9 11101 SPINAL DURAL ARTERIOVENOUS FISTULA//SPINAL ARTERIOVENOUS MALFORMATION//SPINAL ANGIOGRAPHY
10 2177 INFANTILE HEMANGIOMA//HEMANGIOMA//KAPOSIFORM HEMANGIOENDOTHELIOMA

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