Class information for:
Level 1: SHWACHMAN DIAMOND SYNDROME//SBDS//SHWACHMAN SYNDROME

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
19077 523 26.4 69%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
535 3       TAURINE//CHRONIC GRANULOMATOUS DISEASE//L FORMS 19480
4001 2             SHWACHMAN DIAMOND SYNDROME//SBDS//SHWACHMAN SYNDROME 687
19077 1                   SHWACHMAN DIAMOND SYNDROME//SBDS//SHWACHMAN SYNDROME 523

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SHWACHMAN DIAMOND SYNDROME authKW 3908714 15% 83% 81
2 SBDS authKW 1143885 4% 85% 23
3 SHWACHMAN SYNDROME authKW 762881 3% 93% 14
4 PANCREATIC STEATOSIS authKW 357600 1% 88% 7
5 FATTY PANCREAS authKW 286077 1% 70% 7
6 LIPOMATOUS PSEUDOHYPERTROPHY authKW 243265 1% 83% 5
7 SBDS GENE authKW 233536 1% 100% 4
8 SCHWACHMAN DIAMOND SYNDROME authKW 233536 1% 100% 4
9 PANCREATIC LIPOMATOSIS authKW 186827 1% 80% 4
10 SHWACHMAN DIAMOND authKW 186827 1% 80% 4

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 1835 19% 0% 97
2 Pediatrics 1386 18% 0% 96
3 Gastroenterology & Hepatology 1345 16% 0% 83
4 Radiology, Nuclear Medicine & Medical Imaging 822 16% 0% 85
5 Endocrinology & Metabolism 383 11% 0% 60
6 Oncology 116 10% 0% 51
7 Pathology 91 4% 0% 23
8 Nutrition & Dietetics 87 4% 0% 21
9 Genetics & Heredity 72 6% 0% 33
10 Transplantation 35 2% 0% 11

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 GASTROENTEROL NUTR PAEDIAT 116768 0% 100% 2
2 PROGRAM INTEGRAT BIOL 68103 1% 17% 7
3 MARROW FAILURE MYELODYSPLASIA PROGRAM 62270 1% 27% 4
4 BONE JOINT DISSNP 58384 0% 100% 1
5 CLIN EXPT MEDGASTROENTEROL HEPATOL SERV 58384 0% 100% 1
6 CLIN PEDIAT IRCCS BURLO GAROFOLO 58384 0% 100% 1
7 CRIT CARE UNIT CARDIOL 58384 0% 100% 1
8 DEP CHILHLTH 58384 0% 100% 1
9 GE CHINA CO LTD 58384 0% 100% 1
10 GENET UMANA MED 58384 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PANCREATOLOGY 3029 2% 1% 8
2 PANCREAS 2449 2% 0% 13
3 INTERNATIONAL JOURNAL OF PANCREATOLOGY 2268 1% 1% 6
4 PEDIATRIC BLOOD & CANCER 1844 2% 0% 12
5 JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION 1595 3% 0% 14
6 BRITISH JOURNAL OF HAEMATOLOGY 1086 3% 0% 16
7 MORFOLOGIA NORMAL Y PATOLOGICA SECCION B-ANATOMIA PATOLOGICA 776 0% 1% 1
8 JOURNAL OF THE KOREAN SURGICAL SOCIETY 729 1% 0% 3
9 JOURNAL OF CLINICAL ULTRASOUND 728 1% 0% 7
10 PEDIATRIC RADIOLOGY 691 2% 0% 9

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 SHWACHMAN DIAMOND SYNDROME 3908714 15% 83% 81 Search SHWACHMAN+DIAMOND+SYNDROME Search SHWACHMAN+DIAMOND+SYNDROME
2 SBDS 1143885 4% 85% 23 Search SBDS Search SBDS
3 SHWACHMAN SYNDROME 762881 3% 93% 14 Search SHWACHMAN+SYNDROME Search SHWACHMAN+SYNDROME
4 PANCREATIC STEATOSIS 357600 1% 88% 7 Search PANCREATIC+STEATOSIS Search PANCREATIC+STEATOSIS
5 FATTY PANCREAS 286077 1% 70% 7 Search FATTY+PANCREAS Search FATTY+PANCREAS
6 LIPOMATOUS PSEUDOHYPERTROPHY 243265 1% 83% 5 Search LIPOMATOUS+PSEUDOHYPERTROPHY Search LIPOMATOUS+PSEUDOHYPERTROPHY
7 SBDS GENE 233536 1% 100% 4 Search SBDS+GENE Search SBDS+GENE
8 SCHWACHMAN DIAMOND SYNDROME 233536 1% 100% 4 Search SCHWACHMAN+DIAMOND+SYNDROME Search SCHWACHMAN+DIAMOND+SYNDROME
9 PANCREATIC LIPOMATOSIS 186827 1% 80% 4 Search PANCREATIC+LIPOMATOSIS Search PANCREATIC+LIPOMATOSIS
10 SHWACHMAN DIAMOND 186827 1% 80% 4 Search SHWACHMAN+DIAMOND Search SHWACHMAN+DIAMOND

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 BURROUGHS, L , WOOLFREY, A , SHIMAMURA, A , (2009) SHWACHMAN-DIAMOND SYNDROME: A REVIEW OF THE CLINICAL PRESENTATION,, MOLECULAR PATHOGENESIS, DIAGNOSIS, AND TREATMENT.HEMATOLOGY-ONCOLOGY CLINICS OF NORTH AMERICA. VOL. 23. ISSUE 2. P. 233-+ 55 85% 41
2 DROR, Y , (2005) SHWACHMAN-DIAMOND SYNDROME.PEDIATRIC BLOOD & CANCER. VOL. 45. ISSUE 7. P. 892-901 58 82% 56
3 DROR, Y , DONADIEU, J , KOGLMEIER, J , DODGE, J , TOIVIAINEN-SALO, S , MAKITIE, O , KERR, E , ZEIDLER, C , SHIMAMURA, A , SHAH, N , ET AL (2011) DRAFT CONSENSUS GUIDELINES FOR DIAGNOSIS AND TREATMENT OF SHWACHMAN-DIAMOND SYNDROME.ANNALS MEETING REPORTS. VOL. 1242. ISSUE . P. 40-55 48 84% 24
4 SHIMAMURA, A , (2006) SHWACHMAN-DIAMOND SYNDROME.SEMINARS IN HEMATOLOGY. VOL. 43. ISSUE 3. P. 178 -188 52 81% 37
5 CATANZARO, R , CUFFARI, B , ITALIA, A , MAROTTA, F , (2016) EXPLORING THE METABOLIC SYNDROME: NONALCOHOLIC FATTY PANCREAS DISEASE.WORLD JOURNAL OF GASTROENTEROLOGY. VOL. 22. ISSUE 34. P. 7660 -7675 78 44% 0
6 DROR, Y , FREEDMAN, MH , (2002) SHWACHMAN-DIAMOND SYNDROME.BRITISH JOURNAL OF HAEMATOLOGY. VOL. 118. ISSUE 3. P. 701 -713 47 84% 83
7 DONADIEU, J , FENNETEAU, O , BEAUPAIN, B , BEAUFILS, S , BELLANGER, F , MAHLAOUI, N , LAMBILLIOTTE, A , ALADJIDI, N , BERTRAND, Y , MIALOU, V , ET AL (2012) CLASSIFICATION OF AND RISK FACTORS FOR HEMATOLOGIC COMPLICATIONS IN A FRENCH NATIONAL COHORT OF 102 PATIENTS WITH SHWACHMAN-DIAMOND SYNDROME.HAEMATOLOGICA-THE HEMATOLOGY JOURNAL. VOL. 97. ISSUE 9. P. 1312 -1319 38 81% 20
8 MYERS, KC , DAVIES, SM , SHIMAMURA, A , (2013) CLINICAL AND MOLECULAR PATHOPHYSIOLOGY OF SHWACHMAN-DIAMOND SYNDROME: AN UPDATE.HEMATOLOGY-ONCOLOGY CLINICS OF NORTH AMERICA. VOL. 27. ISSUE 1. P. 117-+ 36 77% 13
9 SCHABALLIE, H , RENARD, M , VERMYLEN, C , SCHEERS, I , REVENCU, N , REGAL, L , CASSIMAN, D , SEVENANTS, L , HOFFMAN, I , CORVELEYN, A , ET AL (2013) MISDIAGNOSIS AS ASPHYXIATING THORACIC DYSTROPHY AND CMV-ASSOCIATED HAEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS IN SHWACHMAN-DIAMOND SYNDROME.EUROPEAN JOURNAL OF PEDIATRICS. VOL. 172. ISSUE 5. P. 613-622 30 91% 3
10 SMITS, MM , VAN GEENEN, EJM , (2011) THE CLINICAL SIGNIFICANCE OF PANCREATIC STEATOSIS.NATURE REVIEWS GASTROENTEROLOGY & HEPATOLOGY. VOL. 8. ISSUE 3. P. 169 -177 52 48% 30

Classes with closest relation at Level 1



Rank Class id link
1 15513 DIAMOND BLACKFAN ANEMIA//RPS19//DIAMOND BLACKFAN ANAEMIA
2 9288 SEVERE CONGENITAL NEUTROPENIA//CYCLIC NEUTROPENIA//CONGENITAL NEUTROPENIA
3 11716 DISTAL INTESTINAL OBSTRUCTION SYNDROME//MECONIUM ILEUS//FIBROSING COLONOPATHY
4 13233 FAT QUANTIFICATION//WATER FAT SEPARATION//FAT SUPPRESSION
5 18087 DYSKERATOSIS CONGENITA//DYSKERIN//HOYERAAL HREIDARSSON SYNDROME
6 9046 EXOCRINE PANCREATIC INSUFFICIENCY//STEATORRHEA//PANCREATIC INSUFFICIENCY
7 22758 ARGINYLATION//JOHANSON BLIZZARD SYNDROME//N END RULE
8 10222 PANCREAS DIVISUM//MRCP//MAGNETIC RESONANCE CHOLANGIOPANCREATOGRAPHY
9 17423 JUVENILE MYELOMONOCYTIC LEUKEMIA//JMML//JUVENILE MYELOMONOCYTIC LEUKAEMIA
10 13410 PANCREAS NEOPLASMS//PANCREAS CT//PANCREAS MR

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