Class information for:
Level 1: COLLAGEN VI//TYPE VI COLLAGEN//BETHLEM MYOPATHY

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
18862 533 35.6 78%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
593 3       JOURNAL OF THE AMERICAN LEATHER CHEMISTS ASSOCIATION//OSTEOGENESIS IMPERFECTA//JOURNAL OF THE SOCIETY OF LEATHER TECHNOLOGISTS AND CHEMISTS 14947
797 2             OSTEOGENESIS IMPERFECTA//EHLERS DANLOS SYNDROME//COLLAGEN 12085
18862 1                   COLLAGEN VI//TYPE VI COLLAGEN//BETHLEM MYOPATHY 533

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 COLLAGEN VI authKW 2104428 11% 61% 60
2 TYPE VI COLLAGEN authKW 1392051 10% 45% 54
3 BETHLEM MYOPATHY authKW 1265545 5% 82% 27
4 ULLRICH CONGENITAL MUSCULAR DYSTROPHY authKW 881352 4% 77% 20
5 COLLAGEN TYPE VI authKW 357684 3% 39% 16
6 COL6A2 authKW 286442 1% 100% 5
7 ULLRICHS DISEASE authKW 286442 1% 100% 5
8 COL6A1 authKW 187484 1% 55% 6
9 LONG SPACING COLLAGEN authKW 179023 1% 63% 5
10 COL6A1 GENE authKW 171865 1% 100% 3

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Biochemistry & Molecular Biology 945 37% 0% 196
2 Cell Biology 823 21% 0% 114
3 Clinical Neurology 566 15% 0% 82
4 Anatomy & Morphology 258 3% 0% 17
5 Genetics & Heredity 173 9% 0% 47
6 Neurosciences 101 11% 0% 56
7 Biophysics 70 5% 0% 28
8 Ophthalmology 63 4% 0% 19
9 Pathology 55 4% 0% 19
10 Orthopedics 35 3% 0% 15

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 MED SURG CLIN CARE 128898 1% 75% 3
2 SC MUSCULOSKELETAL CELL BIOL 87712 1% 22% 7
3 MUSCULOSKELETAL CELL BIOL 74829 2% 15% 9
4 HISTOL MICROBIOL MED BIOTECHNOL 73998 5% 5% 26
5 NEUROMUSCULAR NEUROGENET DISORDERS CHILDHOOD SE 66519 1% 19% 6
6 AMAGEN 57288 0% 100% 1
7 BIOMED DIABET METAB DISORDERS CIBERDEM 57288 0% 100% 1
8 CARREFOUR SANTE JONQUIRE 57288 0% 100% 1
9 CERVEAU MOELLE EPINIERE ICMUMR 7225 57288 0% 100% 1
10 CIHR GRP MOL MECH INFLAMMAT 57288 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 MATRIX BIOLOGY 12304 3% 1% 17
2 MATRIX 8172 1% 2% 6
3 NEUROMUSCULAR DISORDERS 4754 3% 1% 14
4 CONNECTIVE TISSUE RESEARCH 1572 1% 0% 7
5 JOURNAL OF INNATE IMMUNITY 1093 1% 1% 3
6 FRONTIERS IN AGING NEUROSCIENCE 841 1% 0% 4
7 HUMAN MOLECULAR GENETICS 827 2% 0% 12
8 EUROPEAN JOURNAL OF BIOCHEMISTRY 813 3% 0% 17
9 MOLECULAR THERAPY-NUCLEIC ACIDS 755 0% 1% 2
10 JOURNAL OF BIOLOGICAL CHEMISTRY 743 9% 0% 46

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 COLLAGEN VI 2104428 11% 61% 60 Search COLLAGEN+VI Search COLLAGEN+VI
2 TYPE VI COLLAGEN 1392051 10% 45% 54 Search TYPE+VI+COLLAGEN Search TYPE+VI+COLLAGEN
3 BETHLEM MYOPATHY 1265545 5% 82% 27 Search BETHLEM+MYOPATHY Search BETHLEM+MYOPATHY
4 ULLRICH CONGENITAL MUSCULAR DYSTROPHY 881352 4% 77% 20 Search ULLRICH+CONGENITAL+MUSCULAR+DYSTROPHY Search ULLRICH+CONGENITAL+MUSCULAR+DYSTROPHY
5 COLLAGEN TYPE VI 357684 3% 39% 16 Search COLLAGEN+TYPE+VI Search COLLAGEN+TYPE+VI
6 COL6A2 286442 1% 100% 5 Search COL6A2 Search COL6A2
7 ULLRICHS DISEASE 286442 1% 100% 5 Search ULLRICHS+DISEASE Search ULLRICHS+DISEASE
8 COL6A1 187484 1% 55% 6 Search COL6A1 Search COL6A1
9 LONG SPACING COLLAGEN 179023 1% 63% 5 Search LONG+SPACING+COLLAGEN Search LONG+SPACING+COLLAGEN
10 COL6A1 GENE 171865 1% 100% 3 Search COL6A1+GENE Search COL6A1+GENE

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 LAMPE, AK , BUSHBY, KMD , (2005) COLLAGEN VI RELATED MUSCLE DISORDERS.JOURNAL OF MEDICAL GENETICS. VOL. 42. ISSUE 9. P. 673-685 88 77% 191
2 BONNEMANN, CG , (2011) THE COLLAGEN VI-RELATED MYOPATHIES: MUSCLE MEETS ITS MATRIX.NATURE REVIEWS NEUROLOGY. VOL. 7. ISSUE 7. P. 379 -390 81 74% 62
3 ALLAMAND, V , BRINAS, L , RICHARD, P , STOJKOVIC, T , QUIJANO-ROY, S , BONNE, G , (2011) COLVI MYOPATHIES: WHERE DO WE STAND, WHERE DO WE GO?.SKELETAL MUSCLE. VOL. 1. ISSUE . P. - 76 74% 32
4 CESCON, M , GATTAZZO, F , CHEN, PW , BONALDO, P , (2015) COLLAGEN VI AT A GLANCE.JOURNAL OF CELL SCIENCE. VOL. 128. ISSUE 19. P. 3525 -3531 68 76% 5
5 BUSHBY, KMD , COLLINS, J , HICKS, D , (2014) COLLAGEN TYPE VI MYOPATHIES.PROGRESS IN HERITABLE SOFT CONNECTIVE TISSUE DISEASES. VOL. 802. ISSUE . P. 185 -199 50 74% 16
6 BERNARDI, P , BONALDO, P , (2013) MITOCHONDRIAL DYSFUNCTION AND DEFECTIVE AUTOPHAGY IN THE PATHOGENESIS OF COLLAGEN VI MUSCULAR DYSTROPHIES.COLD SPRING HARBOR PERSPECTIVES IN BIOLOGY. VOL. 5. ISSUE 5. P. - 52 69% 12
7 LAMPE, AK , ZOU, Y , SUDANO, D , O'BRIEN, KK , HICKS, D , LAVAL, SH , CHARLTON, R , JIMENEZ-MALLEBRERA, C , ZHANG, RZ , FINKEL, RS , ET AL (2008) EXON SKIPPING MUTATIONS IN COLLAGEN VI ARE COMMON AND ARE PREDICTIVE FOR SEVERITY AND INHERITANCE.HUMAN MUTATION. VOL. 29. ISSUE 6. P. 809-822 41 91% 39
8 YONEKAWA, T , NISHINO, I , (2015) ULLRICH CONGENITAL MUSCULAR DYSTROPHY: CLINICOPATHOLOGICAL FEATURES, NATURAL HISTORY AND PATHOMECHANISM(S).JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY. VOL. 86. ISSUE 3. P. 280 -287 42 75% 3
9 TAGLIAVINI, F , PELLEGRINI, C , SARDONE, F , SQUARZONI, S , PAULSSON, M , WAGENER, R , GUALANDI, F , TRABANELLI, C , FERLINI, A , MERLINI, L , ET AL (2014) DEFECTIVE COLLAGEN VI ALPHA 6 CHAIN EXPRESSION IN THE SKELETAL MUSCLE OF PATIENTS WITH COLLAGEN VI-RELATED MYOPATHIES.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE. VOL. 1842. ISSUE 9. P. 1604 -1612 37 82% 8
10 BRINAS, L , RICHARD, P , QUIJANO-ROY, S , GARTIOUX, C , LEDEUIL, C , LACENE, E , MAKRI, S , FERREIRO, A , MAUGENRE, S , TOPALOGLU, H , ET AL (2010) EARLY ONSET COLLAGEN VI MYOPATHIES: GENETIC AND CLINICAL CORRELATIONS.ANNALS OF NEUROLOGY. VOL. 68. ISSUE 4. P. 511-520 31 97% 30

Classes with closest relation at Level 1



Rank Class id link
1 8944 TYPE V COLLAGEN//COLLAGEN XII//TYPE XI COLLAGEN
2 36499 RIGID SPINE SYNDROME//RIGID SPINE//1ST AFFILIATED HOSP NEUROL
3 6620 CONGENITAL MUSCULAR DYSTROPHY//DYSTROGLYCAN//WALKER WARBURG SYNDROME
4 22228 SYNOVIAL LINING CELLS//URIDINE DIPHOSPHOGLUCOSE DEHYDROGENASE//DOG SYNOVIAL MEMBRANE
5 8640 DYSFERLIN//LIMB GIRDLE MUSCULAR DYSTROPHY//SARCOGLYCAN
6 11104 LARP6//COLLAGEN GENES//ALPHA 2I COLLAGEN
7 9776 STRUCT BIOPHYS GRP//KERATOCYTES//MACULAR CORNEAL DYSTROPHY
8 20535 PSEUDOACHONDROPLASIA//MULTIPLE EPIPHYSEAL DYSPLASIA//MATRILIN
9 13420 NG2 PROTEOGLYCAN//PERICYTE ENDOTHELIAL CELL INTERACTION//POLYVALENT ANTIGEN
10 2309 MARFAN SYNDROME//FIBRILLIN//FBN1

Go to start page