Class information for: |
Basic class information |
Class id | #P | Avg. number of references |
Database coverage of references |
---|---|---|---|
18617 | 544 | 30.1 | 74% |
Hierarchy of classes |
The table includes all classes above and classes immediately below the current class. |
Cluster id | Level | Cluster label | #P |
---|---|---|---|
0 | 4 | BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY | 4064930 |
389 | 3 | PEROXISOME//CARNITINE//JOURNAL OF INHERITED METABOLIC DISEASE | 30841 |
3395 | 2 | PKAN//NBIA//PANTOTHENATE KINASE | 1632 |
18617 | 1 | PKAN//NBIA//HALLERVORDEN SPATZ SYNDROME | 544 |
Terms with highest relevance score |
rank | Term | termType | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|---|
1 | PKAN | authKW | 2041085 | 7% | 91% | 40 |
2 | NBIA | authKW | 1959692 | 8% | 78% | 45 |
3 | HALLERVORDEN SPATZ SYNDROME | authKW | 1653272 | 7% | 82% | 36 |
4 | HALLERVORDEN SPATZ DISEASE | authKW | 1562697 | 6% | 80% | 35 |
5 | PLA2G6 | authKW | 1203483 | 5% | 79% | 27 |
6 | NEURODEGENERATION WITH BRAIN IRON ACCUMULATION | authKW | 1174797 | 6% | 70% | 30 |
7 | PANTOTHENATE KINASE ASSOCIATED NEURODEGENERATION | authKW | 1076795 | 5% | 71% | 27 |
8 | PANK2 | authKW | 901197 | 3% | 94% | 17 |
9 | NEUROFERRITINOPATHY | authKW | 790694 | 3% | 78% | 18 |
10 | INFANTILE NEUROAXONAL DYSTROPHY | authKW | 718458 | 3% | 80% | 16 |
Web of Science journal categories |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|
1 | Clinical Neurology | 9547 | 57% | 0% | 311 |
2 | Neurosciences | 1383 | 31% | 0% | 166 |
3 | Pediatrics | 691 | 13% | 0% | 71 |
4 | Genetics & Heredity | 403 | 13% | 0% | 68 |
5 | Pathology | 345 | 8% | 0% | 42 |
6 | Neuroimaging | 278 | 3% | 0% | 16 |
7 | Radiology, Nuclear Medicine & Medical Imaging | 78 | 6% | 0% | 32 |
8 | Psychiatry | 51 | 5% | 0% | 25 |
9 | Biochemistry & Molecular Biology | 36 | 12% | 0% | 63 |
10 | Geriatrics & Gerontology | 8 | 1% | 0% | 5 |
Address terms |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|
1 | PIERFRANCO LUISA MARIANI STUDY MITOCHONDRIA | 144328 | 1% | 43% | 6 |
2 | MICROCITEMIA ANEMIE CONGENITE HAEMATOL | 112260 | 0% | 100% | 2 |
3 | MOL MED GENET PEDIAT NEUROL | 112260 | 0% | 100% | 2 |
4 | ILLING SECT CLIN MOL NEUROGENET | 96214 | 1% | 29% | 6 |
5 | NEUROMUSCULAR NEUROMETAB DISORDERS | 74839 | 0% | 67% | 2 |
6 | OSPED REG MICROCITEMIA | 74839 | 0% | 67% | 2 |
7 | ADVOCATE CHRIST HOSP MED | 56130 | 0% | 100% | 1 |
8 | ALBRECHT KOSSEL NEUROREGULAT | 56130 | 0% | 100% | 1 |
9 | ANIM MED SURGERY | 56130 | 0% | 100% | 1 |
10 | CATTEDRO UO NEUROL | 56130 | 0% | 100% | 1 |
Journals |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|
1 | MOVEMENT DISORDERS | 10527 | 6% | 1% | 35 |
2 | SEMINARS IN PEDIATRIC NEUROLOGY | 4715 | 1% | 2% | 5 |
3 | PEDIATRIC NEUROLOGY | 3376 | 3% | 0% | 16 |
4 | NEUROPEDIATRICS | 3330 | 2% | 1% | 11 |
5 | PARKINSONISM & RELATED DISORDERS | 2822 | 2% | 0% | 11 |
6 | BRAIN & DEVELOPMENT | 2596 | 2% | 0% | 13 |
7 | EUROPEAN JOURNAL OF PAEDIATRIC NEUROLOGY | 1822 | 1% | 1% | 6 |
8 | INTERNATIONAL REVIEW OF NEUROBIOLOGY | 1703 | 1% | 1% | 6 |
9 | ACTA NEUROPATHOLOGICA | 1610 | 2% | 0% | 13 |
10 | NEUROLOGY | 1496 | 4% | 0% | 24 |
Author Key Words |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
LCSH search | Wikipedia search |
---|---|---|---|---|---|---|---|
1 | PKAN | 2041085 | 7% | 91% | 40 | Search PKAN | Search PKAN |
2 | NBIA | 1959692 | 8% | 78% | 45 | Search NBIA | Search NBIA |
3 | HALLERVORDEN SPATZ SYNDROME | 1653272 | 7% | 82% | 36 | Search HALLERVORDEN+SPATZ+SYNDROME | Search HALLERVORDEN+SPATZ+SYNDROME |
4 | HALLERVORDEN SPATZ DISEASE | 1562697 | 6% | 80% | 35 | Search HALLERVORDEN+SPATZ+DISEASE | Search HALLERVORDEN+SPATZ+DISEASE |
5 | PLA2G6 | 1203483 | 5% | 79% | 27 | Search PLA2G6 | Search PLA2G6 |
6 | NEURODEGENERATION WITH BRAIN IRON ACCUMULATION | 1174797 | 6% | 70% | 30 | Search NEURODEGENERATION+WITH+BRAIN+IRON+ACCUMULATION | Search NEURODEGENERATION+WITH+BRAIN+IRON+ACCUMULATION |
7 | PANTOTHENATE KINASE ASSOCIATED NEURODEGENERATION | 1076795 | 5% | 71% | 27 | Search PANTOTHENATE+KINASE+ASSOCIATED+NEURODEGENERATION | Search PANTOTHENATE+KINASE+ASSOCIATED+NEURODEGENERATION |
8 | PANK2 | 901197 | 3% | 94% | 17 | Search PANK2 | Search PANK2 |
9 | NEUROFERRITINOPATHY | 790694 | 3% | 78% | 18 | Search NEUROFERRITINOPATHY | Search NEUROFERRITINOPATHY |
10 | INFANTILE NEUROAXONAL DYSTROPHY | 718458 | 3% | 80% | 16 | Search INFANTILE+NEUROAXONAL+DYSTROPHY | Search INFANTILE+NEUROAXONAL+DYSTROPHY |
Core articles |
The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c: (1) Number of references referring to publications in the class. (2) Share of total number of active references referring to publications in the class. (3) Age of the article. New articles get higher score than old articles. (4) Citation rate, normalized to year. |
Rank | Reference | # ref. in cl. |
Shr. of ref. in cl. |
Citations |
---|---|---|---|---|
1 | LEVI, S , FINAZZI, D , (2014) NEURODEGENERATION WITH BRAIN IRON ACCUMULATION: UPDATE ON PATHOGENIC MECHANISMS.FRONTIERS IN PHARMACOLOGY. VOL. 5. ISSUE . P. - | 81 | 50% | 24 |
2 | KURIAN, MA , HAYFLICK, SJ , (2013) PANTOTHENATE KINASE-ASSOCIATED NEURODEGENERATION (PKAN) AND PLA2G6-ASSOCIATED NEURODEGENERATION (PLAN): REVIEW OF TWO MAJOR NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA) PHENOTYPES.METAL RELATED NEURODEGENERATIVE DISEASE. VOL. 110. ISSUE . P. 49-71 | 51 | 89% | 16 |
3 | SCHNEIDER, SA , (2016) NEURODEGENERATION WITH BRAIN IRON ACCUMULATION.CURRENT NEUROLOGY AND NEUROSCIENCE REPORTS. VOL. 16. ISSUE 1. P. - | 62 | 76% | 0 |
4 | SCHNEIDER, SA , DUSEK, P , HARDY, J , WESTENBERGER, A , JANKOVIC, J , BHATIA, KP , (2013) GENETICS AND PATHOPHYSIOLOGY OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA).CURRENT NEUROPHARMACOLOGY. VOL. 11. ISSUE 1. P. 59 -79 | 83 | 50% | 30 |
5 | SCHNEIDER, SA , BHATIA, KP , (2012) SYNDROMES OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION.SEMINARS IN PEDIATRIC NEUROLOGY. VOL. 19. ISSUE 2. P. 57 -66 | 56 | 69% | 24 |
6 | SCHNEIDER, SA , ZORZI, G , NARDOCCI, N , (2013) PATHOPHYSIOLOGY AND TREATMENT OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION IN THE PEDIATRIC POPULATION.CURRENT TREATMENT OPTIONS IN NEUROLOGY. VOL. 15. ISSUE 5. P. 652 -667 | 56 | 67% | 6 |
7 | SCHNEIDER, SA , BHATIA, KP , (2013) EXCESS IRON HARMS THE BRAIN: THE SYNDROMES OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA).JOURNAL OF NEURAL TRANSMISSION. VOL. 120. ISSUE 4. P. 695 -703 | 55 | 63% | 14 |
8 | ARBER, CE , LI, A , HOULDEN, H , WRAY, S , (2016) REVIEW: INSIGHTS INTO MOLECULAR MECHANISMS OF DISEASE IN NEURODEGENERATION WITH BRAIN IRON ACCUMULATION: UNIFYING THEORIES.NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY. VOL. 42. ISSUE 3. P. 220 -241 | 58 | 41% | 7 |
9 | SCHNEIDER, SA , HARDY, J , BHATIA, KP , (2012) SYNDROMES OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA): AN UPDATE ON CLINICAL PRESENTATIONS, HISTOLOGICAL AND GENETIC UNDERPINNINGS, AND TREATMENT CONSIDERATIONS.MOVEMENT DISORDERS. VOL. 27. ISSUE 1. P. 42 -53 | 50 | 63% | 45 |
10 | KURIAN, MA , MCNEILL, A , LIN, JP , MAHER, ER , (2011) CHILDHOOD DISORDERS OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA).DEVELOPMENTAL MEDICINE AND CHILD NEUROLOGY. VOL. 53. ISSUE 5. P. 394 -404 | 39 | 83% | 34 |
Classes with closest relation at Level 1 |