Class information for:
Level 1: ALVEOLAR CAPILLARY DYSPLASIA//ABCA3//PULMONARY INTERSTITIAL GLYCOGENOSIS

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
18469 550 31.6 79%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
501 3       SYSTEMIC SCLEROSIS//SCLERODERMA//IDIOPATHIC PULMONARY FIBROSIS 22108
968 2             IDIOPATHIC PULMONARY FIBROSIS//INTERSTITIAL LUNG DISEASE//PULMONARY FIBROSIS 10678
18469 1                   ALVEOLAR CAPILLARY DYSPLASIA//ABCA3//PULMONARY INTERSTITIAL GLYCOGENOSIS 550

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ALVEOLAR CAPILLARY DYSPLASIA authKW 2083676 8% 89% 42
2 ABCA3 authKW 1212538 6% 70% 31
3 PULMONARY INTERSTITIAL GLYCOGENOSIS authKW 614963 2% 92% 12
4 CHILDHOOD INTERSTITIAL LUNG DISEASE authKW 499659 2% 100% 9
5 MISALIGNMENT OF PULMONARY VEINS authKW 388624 1% 100% 7
6 NEUROENDOCRINE CELL HYPERPLASIA OF INFANCY authKW 388624 1% 100% 7
7 PEDIATRIC INTERSTITIAL LUNG DISEASE authKW 388624 1% 100% 7
8 ACDMPV authKW 333106 1% 100% 6
9 SURFACTANT PROTEIN C authKW 299086 5% 22% 25
10 CONGENITAL ALVEOLAR CAPILLARY DYSPLASIA authKW 285518 1% 86% 6

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Pediatrics 10537 47% 0% 261
2 Respiratory System 7069 30% 0% 163
3 Critical Care Medicine 562 7% 0% 36
4 Pathology 500 9% 0% 50
5 Genetics & Heredity 90 7% 0% 37
6 Radiology, Nuclear Medicine & Medical Imaging 90 6% 0% 34
7 Allergy 66 2% 0% 10
8 Obstetrics & Gynecology 48 4% 0% 20
9 Cell Biology 23 5% 0% 30
10 Medicine, General & Internal 17 4% 0% 24

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PEDIAT PULM SECT 167925 2% 28% 11
2 BUR PUBL HLTH POLICY 111035 0% 100% 2
3 CHILDRENS HOSP LUDWIG 111035 0% 100% 2
4 PEDIATPEDIAT PULM SECT 111035 0% 100% 2
5 PULM CRIT CARE LUNG EPITHELIAL CELL BIOL LA 111035 0% 100% 2
6 EDWARD MALLINCKRODT PEDIAT 90653 3% 9% 19
7 SECT NEONATOL PERINATAL PULM BIOL 87743 1% 23% 7
8 UMR S U938 83274 1% 50% 3
9 ABT EPIDEMIOL KINDES JUGENDALTERS 55518 0% 100% 1
10 AZIENDA OSPEDAL UNIV OSPED RIUNITI ANCONA 55518 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PEDIATRIC PULMONOLOGY 30728 9% 1% 51
2 PEDIATRIC ALLERGY IMMUNOLOGY AND PULMONOLOGY 5822 1% 2% 5
3 PEDIATRIC AND ADOLESCENT MEDICINE 4625 0% 8% 1
4 PEDIATRIC AND DEVELOPMENTAL PATHOLOGY 4208 2% 1% 10
5 PAEDIATRIC RESPIRATORY REVIEWS 3370 1% 1% 6
6 JOURNAL OF PERINATOLOGY 2867 2% 1% 10
7 FETAL AND PEDIATRIC PATHOLOGY 2438 1% 1% 5
8 ORPHANET JOURNAL OF RARE DISEASES 2437 1% 1% 7
9 RESPIRATORY RESEARCH 1978 1% 0% 8
10 JOURNAL OF PEDIATRICS 1967 4% 0% 22

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 ALVEOLAR CAPILLARY DYSPLASIA 2083676 8% 89% 42 Search ALVEOLAR+CAPILLARY+DYSPLASIA Search ALVEOLAR+CAPILLARY+DYSPLASIA
2 ABCA3 1212538 6% 70% 31 Search ABCA3 Search ABCA3
3 PULMONARY INTERSTITIAL GLYCOGENOSIS 614963 2% 92% 12 Search PULMONARY+INTERSTITIAL+GLYCOGENOSIS Search PULMONARY+INTERSTITIAL+GLYCOGENOSIS
4 CHILDHOOD INTERSTITIAL LUNG DISEASE 499659 2% 100% 9 Search CHILDHOOD+INTERSTITIAL+LUNG+DISEASE Search CHILDHOOD+INTERSTITIAL+LUNG+DISEASE
5 MISALIGNMENT OF PULMONARY VEINS 388624 1% 100% 7 Search MISALIGNMENT+OF+PULMONARY+VEINS Search MISALIGNMENT+OF+PULMONARY+VEINS
6 NEUROENDOCRINE CELL HYPERPLASIA OF INFANCY 388624 1% 100% 7 Search NEUROENDOCRINE+CELL+HYPERPLASIA+OF+INFANCY Search NEUROENDOCRINE+CELL+HYPERPLASIA+OF+INFANCY
7 PEDIATRIC INTERSTITIAL LUNG DISEASE 388624 1% 100% 7 Search PEDIATRIC+INTERSTITIAL+LUNG+DISEASE Search PEDIATRIC+INTERSTITIAL+LUNG+DISEASE
8 ACDMPV 333106 1% 100% 6 Search ACDMPV Search ACDMPV
9 SURFACTANT PROTEIN C 299086 5% 22% 25 Search SURFACTANT+PROTEIN+C Search SURFACTANT+PROTEIN+C
10 CONGENITAL ALVEOLAR CAPILLARY DYSPLASIA 285518 1% 86% 6 Search CONGENITAL+ALVEOLAR+CAPILLARY+DYSPLASIA Search CONGENITAL+ALVEOLAR+CAPILLARY+DYSPLASIA

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 ELLIOTT, EJ , JAFFE, A , HIME, NJ , ZURYNSKI, Y , FITZGERALD, D , SELVADURAI, H , PHU, A , DEVERELL, M , (2015) CHILDHOOD INTERSTITIAL LUNG DISEASE: A SYSTEMATIC REVIEW.PEDIATRIC PULMONOLOGY. VOL. 50. ISSUE 12. P. 1383 -1392 46 90% 9
2 SPAGNOLO, P , BUSH, A , (2016) INTERSTITIAL LUNG DISEASE IN CHILDREN YOUNGER THAN 2 YEARS.PEDIATRICS. VOL. 137. ISSUE 6. P. - 60 71% 1
3 PECA, D , CUTRERA, R , MASOTTI, A , BOLDRINI, R , DANHAIVE, O , (2015) ABCA3, A KEY PLAYER IN NEONATAL RESPIRATORY TRANSITION AND GENETIC DISORDERS OF THE SURFACTANT SYSTEM.BIOCHEMICAL SOCIETY TRANSACTIONS. VOL. 43. ISSUE . P. 913 -919 43 90% 3
4 KUO, CS , YOUNG, LR , (2014) INTERSTITIAL LUNG DISEASE IN CHILDREN.CURRENT OPINION IN PEDIATRICS. VOL. 26. ISSUE 3. P. 320 -327 40 83% 7
5 KURLAND, G , DETERDING, RR , HAGOOD, JS , YOUNG, LR , BRODY, AS , CASTILE, RG , DELL, S , FAN, LL , HAMVAS, A , HILMAN, BC , ET AL (2013) AN OFFICIAL AMERICAN THORACIC SOCIETY CLINICAL PRACTICE GUIDELINE: CLASSIFICATION, EVALUATION, AND MANAGEMENT OF CHILDHOOD INTERSTITIAL LUNG DISEASE IN INFANCY.AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE. VOL. 188. ISSUE 3. P. 376 -394 72 39% 48
6 LEE, EY , (2013) INTERSTITIAL LUNG DISEASE IN INFANTS: NEW CLASSIFICATION SYSTEM, IMAGING TECHNIQUE, CLINICAL PRESENTATION AND IMAGING FINDINGS.PEDIATRIC RADIOLOGY. VOL. 43. ISSUE 1. P. 3-13 47 71% 5
7 BISHOP, NB , STANKIEWICZ, P , STEINHORN, RH , (2011) ALVEOLAR CAPILLARY DYSPLASIA.AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE. VOL. 184. ISSUE 2. P. 172 -179 41 76% 35
8 WAMBACH, JA , CASEY, AM , FISHMAN, MP , WEGNER, DJ , WERT, SE , COLE, FS , HAMVAS, A , NOGEE, LM , (2014) GENOTYPE-PHENOTYPE CORRELATIONS FOR INFANTS AND CHILDREN WITH ABCA3 DEFICIENCY.AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE. VOL. 189. ISSUE 12. P. 1538 -1543 28 97% 21
9 LANGSTON, C , DISHOP, MK , (2009) DIFFUSE LUNG DISEASE IN INFANCY: A PROPOSED CLASSIFICATION APPLIED TO 259 DIAGNOSTIC BIOPSIES.PEDIATRIC AND DEVELOPMENTAL PATHOLOGY. VOL. 12. ISSUE 6. P. 421-437 39 76% 21
10 GUPTA, A , ZHENG, SL , (2017) GENETIC DISORDERS OF SURFACTANT PROTEIN DYSFUNCTION: WHEN TO CONSIDER AND HOW TO INVESTIGATE.ARCHIVES OF DISEASE IN CHILDHOOD. VOL. 102. ISSUE 1. P. 84 -90 35 74% 0

Classes with closest relation at Level 1



Rank Class id link
1 15258 PULMONARY ALVEOLAR PROTEINOSIS//WHOLE LUNG LAVAGE//ALVEOLAR PROTEINOSIS
2 31869 FAMILIAL BRITISH DEMENTIA//FAMILIAL DANISH DEMENTIA//BRI2
3 783 IDIOPATHIC PULMONARY FIBROSIS//USUAL INTERSTITIAL PNEUMONIA//IDIOPATHIC INTERSTITIAL PNEUMONIA
4 468 PULMONARY SURFACTANT//RESPIRATORY DISTRESS SYNDROME//LUNG SURFACTANT
5 37140 SEGMENTAL INTESTINAL DILATATION//SEGMENTAL DILATATION//SEGMENTAL DILATATION OF ILEUM
6 9717 LUNG DEVELOPMENT//LUNG MORPHOGENESIS//BRANCHING MORPHOGENESIS
7 14232 THYROID DYSGENESIS//THYROID HEMIAGENESIS//BENIGN HEREDITARY CHOREA
8 18316 LARYNGOMALACIA//SUPRAGLOTTOPLASTY//STRIDOR
9 15208 SHRINKING LUNG SYNDROME//IDIOPATHIC PULMONARY HEMOSIDEROSIS//PULMONARY HEMOSIDEROSIS
10 25461 PULMONARY VENO OCCLUSIVE DISEASE//PULMONARY CAPILLARY HEMANGIOMATOSIS//PULMONARY CAPILLARY HAEMANGIOMATOSIS

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