Class information for:
Level 1: BERNARD SOULIER SYNDROME//GPIB IX V COMPLEX//BERNARD SOULIER

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
16281 663 37.2 75%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
8 4 CARDIAC & CARDIOVASCULAR SYSTEM//PERIPHERAL VASCULAR DISEASES//CARDIOL 1276458
131 3       HEMATOLOGY//HAEMOPHILIA//TRANSFUSION 66936
697 2             MEAN PLATELET VOLUME//PLATELETS//HEMATOLOGY 13039
16281 1                   BERNARD SOULIER SYNDROME//GPIB IX V COMPLEX//BERNARD SOULIER 663

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BERNARD SOULIER SYNDROME authKW 1791158 10% 59% 66
2 GPIB IX V COMPLEX authKW 294749 1% 80% 8
3 BERNARD SOULIER authKW 282085 1% 88% 7
4 GLYCOPROTEIN IX authKW 276330 1% 100% 6
5 GLYCOPROTEIN IB IX V authKW 209330 2% 45% 10
6 HAZEL PIP PEL VASC BIOL address 207239 1% 50% 9
7 GLYCOPROTEIN IB authKW 203070 3% 21% 21
8 GIANT PLATELETS authKW 189819 2% 32% 13
9 GPIB IX COMPLEX authKW 164479 1% 71% 5
10 GPIB IX authKW 161186 1% 50% 7

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 19406 52% 0% 344
2 Peripheral Vascular Diseases 3877 23% 0% 151
3 Biochemistry & Molecular Biology 785 31% 0% 206
4 Biophysics 132 6% 0% 41
5 Cell Biology 90 8% 0% 53
6 Medicine, Research & Experimental 63 5% 0% 32
7 Biochemical Research Methods 7 2% 0% 14
8 CYTOLOGY & HISTOLOGY 4 0% 0% 1
9 Pathology 2 1% 0% 8
10 Medical Laboratory Technology 1 0% 0% 3

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HAZEL PIP PEL VASC BIOL 207239 1% 50% 9
2 U311 132975 3% 15% 19
3 ROON ARTERIOSCLEROSIS THROMBOSIS 112610 2% 16% 15
4 EFS ALSACE 68374 1% 21% 7
5 SERV IMMUNOTRASFUS ANAL CLIN 66984 1% 36% 4
6 KINET PARAMETER IL 61405 0% 67% 2
7 EXPT HEMOSTASIS THROMBOSIS 60153 1% 15% 9
8 PUGET SOUND BLOOD 54810 2% 12% 10
9 BIOCHEM IMS 46055 0% 100% 1
10 BIOMED DIAGNOSIS AUGUSTI PII SUNYE 46055 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 THROMBOSIS AND HAEMOSTASIS 20125 10% 1% 66
2 BLOOD 8989 12% 0% 82
3 JOURNAL OF THROMBOSIS AND HAEMOSTASIS 8557 4% 1% 27
4 PLATELETS 6912 2% 1% 16
5 THROMBOSIS RESEARCH 6464 6% 0% 38
6 JOURNAL OF BIOLOGICAL CHEMISTRY 1499 11% 0% 72
7 BRITISH JOURNAL OF HAEMATOLOGY 1478 3% 0% 21
8 BLOOD COAGULATION & FIBRINOLYSIS 1122 1% 0% 9
9 BLOOD CELLS 1098 1% 1% 4
10 SEMINARS IN CELL BIOLOGY 1069 0% 2% 1

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 BERNARD SOULIER SYNDROME 1791158 10% 59% 66 Search BERNARD+SOULIER+SYNDROME Search BERNARD+SOULIER+SYNDROME
2 GPIB IX V COMPLEX 294749 1% 80% 8 Search GPIB+IX+V+COMPLEX Search GPIB+IX+V+COMPLEX
3 BERNARD SOULIER 282085 1% 88% 7 Search BERNARD+SOULIER Search BERNARD+SOULIER
4 GLYCOPROTEIN IX 276330 1% 100% 6 Search GLYCOPROTEIN+IX Search GLYCOPROTEIN+IX
5 GLYCOPROTEIN IB IX V 209330 2% 45% 10 Search GLYCOPROTEIN+IB+IX+V Search GLYCOPROTEIN+IB+IX+V
6 GLYCOPROTEIN IB 203070 3% 21% 21 Search GLYCOPROTEIN+IB Search GLYCOPROTEIN+IB
7 GIANT PLATELETS 189819 2% 32% 13 Search GIANT+PLATELETS Search GIANT+PLATELETS
8 GPIB IX COMPLEX 164479 1% 71% 5 Search GPIB+IX+COMPLEX Search GPIB+IX+COMPLEX
9 GPIB IX 161186 1% 50% 7 Search GPIB+IX Search GPIB+IX
10 GLYCOPROTEIN V 147375 1% 80% 4 Search GLYCOPROTEIN+V Search GLYCOPROTEIN+V

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 SAVOIA, A , KUNISHIMA, S , DE ROCCO, D , ZIEGER, B , RAND, ML , PUJOL-MOIX, N , CALISKAN, U , TOKGOZ, H , PECCI, A , NORIS, P , ET AL (2014) SPECTRUM OF THE MUTATIONS IN BERNARD-SOULIER SYNDROME.HUMAN MUTATION. VOL. 35. ISSUE 9. P. 1033 -1045 88 80% 11
2 LOPEZ, JA , ANDREWS, RK , AFSHAR-KHARGHAN, V , BERNDT, MC , (1998) BERNARD-SOULIER SYNDROME.BLOOD. VOL. 91. ISSUE 12. P. 4397 -4418 106 55% 306
3 LANZA, F , (2006) BERNARD-SOULIER SYNDROME (HEMORRHAGIPAROUS THROMBOCYTIC DYSTROPHY).ORPHANET JOURNAL OF RARE DISEASES. VOL. 1. ISSUE . P. - 64 85% 40
4 LI, R , EMSLEY, J , (2013) THE ORGANIZING PRINCIPLE OF THE PLATELET GLYCOPROTEIN IBIXV COMPLEX.JOURNAL OF THROMBOSIS AND HAEMOSTASIS. VOL. 11. ISSUE 4. P. 605-614 62 65% 22
5 YAMAMOTO, N , AKAMATSU, N , SAKURABA, H , MATSUNO, K , HOSOYA, R , NOGAMI, H , KASAHARA, K , MITSUYAMA, S , ARAI, M , (2013) NOVEL BERNARD-SOULIER SYNDROME VARIANTS CAUSED BY COMPOUND HETEROZYGOUS MUTATIONS (CASE I) OR A CYTOPLASMIC TAIL TRUNCATION (CASE II) OF GPIB ALPHA.THROMBOSIS RESEARCH. VOL. 131. ISSUE 4. P. E160-E167 49 84% 1
6 KUNISHIMA, S , KAMIYA, T , SAITO, H , (2002) GENETIC ABNORMALITIES OF BERNARD-SOULIER SYNDROME.INTERNATIONAL JOURNAL OF HEMATOLOGY. VOL. 76. ISSUE 4. P. 319-327 70 73% 36
7 STRASSEL, C , DAVID, T , ECKLY, A , BAAS, MJ , MOOG, S , RAVANAT, C , TRZECIAK, MC , VINCIGUERRA, C , CAZENAVE, JP , GACHET, C , ET AL (2006) SYNTHESIS OF GPIB BETA WITH NOVEL TRANSMEMBRANE AND CYTOPLASMIC SEQUENCES IN A BERNARD-SOULIER PATIENT RESULTING IN GPIB-DEFECTIVE SIGNALING IN CHO CELLS.JOURNAL OF THROMBOSIS AND HAEMOSTASIS. VOL. 4. ISSUE 1. P. 217-228 42 89% 17
8 WARE, J , (1998) MOLECULAR ANALYSES OF THE PLATELET GLYCOPROTEIN IB-IX-V RECEPTOR.THROMBOSIS AND HAEMOSTASIS. VOL. 79. ISSUE 3. P. 466 -478 77 54% 50
9 ZHOU, L , YANG, W , LI, R , (2014) ANALYSIS OF INTER-SUBUNIT CONTACTS REVEALS THE STRUCTURAL MALLEABILITY OF EXTRACELLULAR DOMAINS IN PLATELET GLYCOPROTEIN IB-IX COMPLEX.JOURNAL OF THROMBOSIS AND HAEMOSTASIS. VOL. 12. ISSUE 1. P. 82 -89 25 93% 5
10 MO, X , LIU, L , LOPEZ, JA , LI, R , (2012) TRANSMEMBRANE DOMAINS ARE CRITICAL TO THE INTERACTION BETWEEN PLATELET GLYCOPROTEIN V AND GLYCOPROTEIN IB-IX COMPLEX.JOURNAL OF THROMBOSIS AND HAEMOSTASIS. VOL. 10. ISSUE 9. P. 1875-1886 28 82% 5

Classes with closest relation at Level 1



Rank Class id link
1 15313 MAY HEGGLIN ANOMALY//INHERITED THROMBOCYTOPENIA//EPSTEIN SYNDROME
2 17085 OPEN CANALICULAR SYSTEM//FIBRINOGEN GOLD//2E4 KAPTIN
3 5175 GLANZMANN THROMBASTHENIA//GLANZMANNS THROMBASTHENIA//THROMBASTHENIA
4 20646 PLATELET GLYCOPROTEIN//PLATELET RECEPTOR POLYMORPHISMS//GPIA
5 4132 GLYCOPROTEIN VI//GPVI//PLATELETS
6 639 VON WILLEBRAND DISEASE//VON WILLEBRAND FACTOR//VWD
7 29194 PLATELET APOPTOSIS//COATED PLATELET//STUDY HUMAN OPERATOR PERFORMANCE
8 15142 DISINTEGRIN//C TYPE LECTIN LIKE PROTEIN//ECHISTATIN
9 17609 FILAMIN A//FILAMIN//FLNA
10 24651 GEA 3175//MESOIONIC 3 ARYL SUBSTITUTED OXATRIAZOLES//NEUTROPHIL DERIVED RELAXING FACTOR

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