Class information for:
Level 1: CONGENITAL CENTRAL HYPOVENTILATION SYNDROME//ONDINES CURSE//DIAPHRAGM PACING

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
15762 693 27.0 67%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
8 4 CARDIAC & CARDIOVASCULAR SYSTEM//PERIPHERAL VASCULAR DISEASES//CARDIOL 1276458
309 3       MECHANICAL VENTILATION//CRITICAL CARE MEDICINE//DELIRIUM 40181
802 2             NONINVASIVE VENTILATION//RESPIRATORY MUSCLES//DIAPHRAGM 12067
15762 1                   CONGENITAL CENTRAL HYPOVENTILATION SYNDROME//ONDINES CURSE//DIAPHRAGM PACING 693

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CONGENITAL CENTRAL HYPOVENTILATION SYNDROME authKW 2960882 12% 80% 84
2 ONDINES CURSE authKW 1511557 6% 84% 41
3 DIAPHRAGM PACING authKW 1468695 6% 83% 40
4 PHOX2B GENE authKW 1103161 4% 96% 26
5 PHOX2B authKW 726292 7% 35% 47
6 CCHS authKW 627209 3% 65% 22
7 HADDAD SYNDROME authKW 396551 1% 100% 9
8 CENTRAL HYPOVENTILATION authKW 392535 2% 64% 14
9 CENTRAL HYPOVENTILATION SYNDROME authKW 297409 1% 75% 9
10 DISEASE CONGENITAL CENTRAL HYPOVENTILATION SYNDROME authKW 264367 1% 100% 6

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Respiratory System 5901 24% 0% 168
2 Pediatrics 3954 26% 0% 183
3 Clinical Neurology 890 17% 0% 116
4 Critical Care Medicine 696 6% 0% 45
5 Physiology 301 8% 0% 56
6 Engineering, Biomedical 287 6% 0% 39
7 Surgery 270 13% 0% 87
8 Rehabilitation 166 4% 0% 25
9 Anesthesiology 87 2% 0% 17
10 Genetics & Heredity 86 6% 0% 42

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 AUTON MED PEDIAT 259176 1% 59% 10
2 NEUROL PHYSIOL DEV 213244 2% 44% 11
3 RUSH CHILDRENS HOSP 111517 1% 28% 9
4 AUTON MED PEDIAT PEDIAT 88122 0% 100% 2
5 FRENCH REFERENCE CENT HYPOVENTILAT 88122 0% 100% 2
6 NEUROL SCI BIOCHEM 88122 0% 100% 2
7 REFERENCE MALAD RA SYNDROME ONDINE 88122 0% 100% 2
8 SONO VENTILACAO 88122 0% 100% 2
9 UNITE RECH AD TAT PHYSIOL COMPORTEMENTALES 83476 1% 32% 6
10 INSERM E9935 74438 1% 24% 7

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PEDIATRIC PULMONOLOGY 13508 5% 1% 38
2 NEUROTRANSMITTER INTERACTIONS AND COGNITIVE FUNCTION 5506 0% 13% 1
3 RESPIRATORY PHYSIOLOGY & NEUROBIOLOGY 5438 3% 1% 18
4 SLEEP AND BREATHING 1460 1% 1% 6
5 AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE 1451 3% 0% 18
6 RESPIRATION PHYSIOLOGY 1361 1% 0% 9
7 PACE-PACING AND CLINICAL ELECTROPHYSIOLOGY 1257 2% 0% 16
8 PEDIATRIC RESEARCH 1212 2% 0% 16
9 AMERICAN REVIEW OF RESPIRATORY DISEASE 1188 2% 0% 13
10 PEDIATRICS AND NEONATOLOGY 766 0% 1% 3

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 CONGENITAL CENTRAL HYPOVENTILATION SYNDROME 2960882 12% 80% 84 Search CONGENITAL+CENTRAL+HYPOVENTILATION+SYNDROME Search CONGENITAL+CENTRAL+HYPOVENTILATION+SYNDROME
2 ONDINES CURSE 1511557 6% 84% 41 Search ONDINES+CURSE Search ONDINES+CURSE
3 DIAPHRAGM PACING 1468695 6% 83% 40 Search DIAPHRAGM+PACING Search DIAPHRAGM+PACING
4 PHOX2B GENE 1103161 4% 96% 26 Search PHOX2B+GENE Search PHOX2B+GENE
5 PHOX2B 726292 7% 35% 47 Search PHOX2B Search PHOX2B
6 CCHS 627209 3% 65% 22 Search CCHS Search CCHS
7 HADDAD SYNDROME 396551 1% 100% 9 Search HADDAD+SYNDROME Search HADDAD+SYNDROME
8 CENTRAL HYPOVENTILATION 392535 2% 64% 14 Search CENTRAL+HYPOVENTILATION Search CENTRAL+HYPOVENTILATION
9 CENTRAL HYPOVENTILATION SYNDROME 297409 1% 75% 9 Search CENTRAL+HYPOVENTILATION+SYNDROME Search CENTRAL+HYPOVENTILATION+SYNDROME
10 DISEASE CONGENITAL CENTRAL HYPOVENTILATION SYNDROME 264367 1% 100% 6 Search DISEASE+CONGENITAL+CENTRAL+HYPOVENTILATION+SYNDROME Search DISEASE+CONGENITAL+CENTRAL+HYPOVENTILATION+SYNDROME

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 WEESE-MAYER, DE , BERRY-KRAVIS, EM , CECCHERINI, I , KEENS, TG , LOGHMANEE, DA , TRANG, H , (2010) AN OFFICIAL ATS CLINICAL POLICY STATEMENT: CONGENITAL CENTRAL HYPOVENTILATION SYNDROME GENETIC BASIS, DIAGNOSIS, AND MANAGEMENT.AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE. VOL. 181. ISSUE 6. P. 626 -644 106 87% 92
2 WEESE-MAYER, DE , BERRY-KRAVIS, EM , CECCHERINI, I , KEENS, TG , LOGHMANEE, DA , TRANG, H , (2013) FRENCH EDITION OF THE OFFICIAL DECLARATION OF THE CLINICAL POLICY OF THE AMERICAN THORACIC SOCIETY (ATS) ON CENTRAL CONGENITAL ALVEOLAR HYPOVENTILATION SYNDROME. GENETIC BASIS, DIAGNOSIS AND MANAGEMENT.REVUE DES MALADIES RESPIRATOIRES. VOL. 30. ISSUE 8. P. 706 -733 105 88% 1
3 CARROLL, MS , PATWARI, PP , WEESE-MAYER, DE , (2010) CARBON DIOXIDE CHEMORECEPTION AND HYPOVENTILATION SYNDROMES WITH AUTONOMIC DYSREGULATION.JOURNAL OF APPLIED PHYSIOLOGY. VOL. 108. ISSUE 4. P. 979 -988 77 89% 6
4 WEESE-MAYER, DE , RAND, CM , ZHOU, A , CARROLL, MS , HUNT, CE , (2017) CONGENITAL CENTRAL HYPOVENTILATION SYNDROME: A BEDSIDE-TO-BENCH SUCCESS STORY FOR ADVANCING EARLY DIAGNOSIS AND TREATMENT AND IMPROVED SURVIVAL AND QUALITY OF LIFE.PEDIATRIC RESEARCH. VOL. 81. ISSUE 1. P. 192 -201 66 74% 0
5 GRIGG-DAMBERGER, M , WELLS, A , (2009) CENTRAL CONGENITAL HYPOVENTILATION SYNDROME: CHANGING FACE OF A LESS MYSTERIOUS BUT MORE COMPLEX GENETIC DISORDER.SEMINARS IN RESPIRATORY AND CRITICAL CARE MEDICINE. VOL. 30. ISSUE 3. P. 262-274 60 94% 2
6 WEESE-MAYER, DE , RAND, CM , BERRY-KRAVIS, EM , JENNINGS, LJ , LOGHMANEE, DA , PATWARI, PP , CECCHERINI, I , (2009) CONGENITAL CENTRAL HYPOVENTILATION SYNDROME FROM PAST TO FUTURE: MODEL FOR TRANSLATIONAL AND TRANSITIONAL AUTONOMIC MEDICINE.PEDIATRIC PULMONOLOGY. VOL. 44. ISSUE 6. P. 521 -535 64 74% 27
7 PATWARI, PP , CARROLL, MS , RAND, CM , KUMAR, R , HARPER, R , WEESE-MAYER, DE , (2010) CONGENITAL CENTRAL HYPOVENTILATION SYNDROME AND THE PHOX2B GENE: A MODEL OF RESPIRATORY AND AUTONOMIC DYSREGULATION.RESPIRATORY PHYSIOLOGY & NEUROBIOLOGY. VOL. 173. ISSUE 3. P. 322-335 70 63% 20
8 HEALY, F , MARCUS, CL , (2011) CONGENITAL CENTRAL HYPOVENTILATION SYNDROME IN CHILDREN.PAEDIATRIC RESPIRATORY REVIEWS. VOL. 12. ISSUE 4. P. 253-263 46 87% 18
9 RAND, CM , CARROLL, MS , WEESE-MAYER, DE , (2014) CONGENITAL CENTRAL HYPOVENTILATION SYNDROME A NEUROCRISTOPATHY WITH DISORDERED RESPIRATORY CONTROL AND AUTONOMIC REGULATION.CLINICS IN CHEST MEDICINE. VOL. 35. ISSUE 3. P. 535 -+ 37 97% 3
10 BASU, SM , CHUNG, FF , ABDELHAKIM, SF , WONG, J , (2017) ANESTHETIC CONSIDERATIONS FOR PATIENTS WITH CONGENITAL CENTRAL HYPOVENTILATION SYNDROME: A SYSTEMATIC REVIEW OF THE LITERATURE.ANESTHESIA AND ANALGESIA. VOL. 124. ISSUE 1. P. 169 -178 33 92% 0

Classes with closest relation at Level 1



Rank Class id link
1 13342 LONG TERM FACILITATION//PHRENIC//RESPIRATORY PLASTICITY
2 15585 DIAPHRAGMATIC PARALYSIS//DIAPHRAGMATIC PLICATION//DIAPHRAGM PARALYSIS
3 10723 MECHANICAL INSUFFLATION EXSUFFLATION//NEUROMUSCULAR DISEASE//ASSISTED COUGH
4 34518 LONG TERM MONITORING LTM//SCALP SKULL BRAIN HEAD MODEL//AUTOMATIC STAGING
5 11097 ENTERIC NERVOUS SYSTEM//HIRSCHSPRUNGS DISEASE//HIRSCHSPRUNG DISEASE
6 778 PRE BOTZINGER COMPLEX//RETROTRAPEZOID NUCLEUS//RESPIRATORY RHYTHM
7 15995 DIAPHRAGM MUSCLE//P MUSCLE UNIT//RESPIRATORY MUSCLES
8 24494 OCULOPHARYNGEAL MUSCULAR DYSTROPHY//PABPN1//OPMD
9 11903 OBESITY HYPOVENTILATION SYNDROME//PICKWICKIAN SYNDROME//SLEEP RELATED HYPOXAEMIA
10 4045 RESPIRATORY MUSCLES//RESPIRATORY MUSCLE TRAINING//INSPIRATORY MUSCLE TRAINING

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