Class information for:
Level 1: BETA KETOTHIOLASE DEFICIENCY//MITOCHONDRIAL ACETOACETYL COA THIOLASE//THIOLASE

Basic class information
Class id #P Avg. number of
references		 Database coverage
of references
14230 783 31.3 65%


Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes
The table includes all classes above and classes immediately below the current class.


Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
389 3       PEROXISOME//CARNITINE//JOURNAL OF INHERITED METABOLIC DISEASE 30841
1356 2             PEROXISOME//ADRENOLEUKODYSTROPHY//ZELLWEGER SYNDROME 8277
14230 1                   BETA KETOTHIOLASE DEFICIENCY//MITOCHONDRIAL ACETOACETYL COA THIOLASE//THIOLASE 783

Terms with highest relevance score


rank Term termType Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 BETA KETOTHIOLASE DEFICIENCY authKW 584948 2% 100% 15
2 MITOCHONDRIAL ACETOACETYL COA THIOLASE authKW 393213 1% 92% 11
3 THIOLASE authKW 368351 3% 41% 23
4 DELTA3 DELTA2 ENOYL COA ISOMERASE authKW 354512 1% 91% 10
5 3 KETOTHIOLASE DEFICIENCY authKW 311972 1% 100% 8
6 SUCCINYL COA3 KETOACID COA TRANSFERASE authKW 249574 1% 80% 8
7 T2 DEFICIENCY authKW 233979 1% 100% 6
8 2 4 DIENOYL COA REDUCTASE authKW 226884 1% 73% 8
9 HSD10 DEFICIENCY authKW 194983 1% 100% 5
10 ERAB authKW 175481 1% 75% 6

Web of Science journal categories


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 Biochemistry & Molecular Biology 4625 63% 0% 490
2 Biophysics 1243 15% 0% 119
3 Genetics & Heredity 773 14% 0% 111
4 Medicine, Research & Experimental 562 11% 0% 86
5 Endocrinology & Metabolism 414 10% 0% 78
6 Cell Biology 156 9% 0% 72
7 Biochemical Research Methods 47 4% 0% 28
8 Medical Laboratory Technology 16 1% 0% 8
9 Pediatrics 12 2% 0% 19
10 Crystallography 10 2% 0% 13

Address terms


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 PHYSIOL CHEM ZELLBIOCHEM ABT 77993 0% 100% 2
2 SR SYST BIOL GRP 51994 0% 67% 2
3 BIO OULU 47923 5% 3% 42
4 AFDELINGEN FARMACOL 38997 0% 100% 1
5 ANIM GENOM BIOINFORRNAT 38997 0% 100% 1
6 BIO OULU MED BIOCHEM KAJAANINTIE 52 A 38997 0% 100% 1
7 CBE GHC 38997 0% 100% 1
8 CEMECOHOSP NINOS CORDOBA 38997 0% 100% 1
9 CHLCEPE 38997 0% 100% 1
10 FAK MED PHYSIOL CHEM ZELLBIOCHEM ABT 38997 0% 100% 1

Journals


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 JOURNAL OF INHERITED METABOLIC DISEASE 15896 5% 1% 43
2 JOURNAL OF BIOCHEMISTRY 4671 5% 0% 36
3 BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS 3248 2% 1% 15
4 MOLECULAR GENETICS AND METABOLISM 3175 2% 1% 16
5 JOURNAL OF BIOLOGICAL CHEMISTRY 1812 11% 0% 86
6 BIOCHEMISTRY 1767 6% 0% 50
7 BIOCHEMICAL JOURNAL 1591 4% 0% 35
8 BIOCHIMICA ET BIOPHYSICA ACTA-LIPIDS AND LIPID METABOLISM 1296 1% 1% 6
9 EUROPEAN JOURNAL OF BIOCHEMISTRY 1101 3% 0% 24
10 HUMAN MUTATION 780 1% 0% 9

Author Key Words


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class		 LCSH search Wikipedia search
1 BETA KETOTHIOLASE DEFICIENCY 584948 2% 100% 15 Search BETA+KETOTHIOLASE+DEFICIENCY Search BETA+KETOTHIOLASE+DEFICIENCY
2 MITOCHONDRIAL ACETOACETYL COA THIOLASE 393213 1% 92% 11 Search MITOCHONDRIAL+ACETOACETYL+COA+THIOLASE Search MITOCHONDRIAL+ACETOACETYL+COA+THIOLASE
3 THIOLASE 368351 3% 41% 23 Search THIOLASE Search THIOLASE
4 DELTA3 DELTA2 ENOYL COA ISOMERASE 354512 1% 91% 10 Search DELTA3+DELTA2+ENOYL+COA+ISOMERASE Search DELTA3+DELTA2+ENOYL+COA+ISOMERASE
5 3 KETOTHIOLASE DEFICIENCY 311972 1% 100% 8 Search 3+KETOTHIOLASE+DEFICIENCY Search 3+KETOTHIOLASE+DEFICIENCY
6 SUCCINYL COA3 KETOACID COA TRANSFERASE 249574 1% 80% 8 Search SUCCINYL+COA3+KETOACID+COA+TRANSFERASE Search SUCCINYL+COA3+KETOACID+COA+TRANSFERASE
7 T2 DEFICIENCY 233979 1% 100% 6 Search T2+DEFICIENCY Search T2+DEFICIENCY
8 2 4 DIENOYL COA REDUCTASE 226884 1% 73% 8 Search 2+4+DIENOYL+COA+REDUCTASE Search 2+4+DIENOYL+COA+REDUCTASE
9 HSD10 DEFICIENCY 194983 1% 100% 5 Search HSD10+DEFICIENCY Search HSD10+DEFICIENCY
10 ERAB 175481 1% 75% 6 Search ERAB Search ERAB

Core articles
The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.


Rank Reference # ref. in
cl.		 Shr. of ref. in
cl.		 Citations
1 HORI, T , YAMAGUCHI, S , SHINKAKU, H , HORIKAWA, R , SHIGEMATSU, Y , TAKAYANAGI, M , FUKAO, T , (2015) INBORN ERRORS OF KETONE BODY UTILIZATION.PEDIATRICS INTERNATIONAL. VOL. 57. ISSUE 1. P. 41 -48 53 100% 0
2 FUKAO, T , MITCHELL, G , SASS, J , HORI, T , ORII, K , AOYAMA, Y , (2014) KETONE BODY METABOLISM AND ITS DEFECTS.JOURNAL OF INHERITED METABOLIC DISEASE. VOL. 37. ISSUE 4. P. 541 -551 46 68% 17
3 HILTUNEN, JK , FILPPULA, SA , KOIVURANTA, KT , SIIVARI, K , QIN, YM , HAYRINEN, HM , (1996) PEROXISOMAL BETA-OXIDATION AND POLYUNSATURATED FATTY ACIDS.PEROXISOMES: BIOLOGY AND ROLE IN TOXICOLOGY AND DISEASE. VOL. 804. ISSUE . P. 116 -128 57 80% 23
4 YANG, SY , HE, XY , SCHULZ, H , (2005) 3-HYDROXYACYL-COA DEHYDROGENASE AND SHORT CHAIN 3-HYDROXYACYL-COA DEHYDROGENASE IN HUMAN HEALTH AND DISEASE.FEBS JOURNAL. VOL. 272. ISSUE 19. P. 4874 -4883 44 69% 47
5 VILARDO, E , ROSSMANITH, W , (2015) MOLECULAR INSIGHTS INTO HSD10 DISEASE: IMPACT OF SDR5C1 MUTATIONS ON THE HUMAN MITOCHONDRIAL RNASE P COMPLEX.NUCLEIC ACIDS RESEARCH. VOL. 43. ISSUE 10. P. 5112 -5119 29 73% 5
6 HILTUNEN, JK , QIN, YM , (2000) BETA-OXIDATION - STRATEGIES FOR THE METABOLISM OF A WIDE VARIETY OF ACYL-COA ESTERS.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS. VOL. 1484. ISSUE 2-3. P. 117 -128 54 57% 75
7 KASARAGOD, P , SCHMITZ, W , HILTUNEN, JK , WIERENGA, RK , (2013) THE ISOMERASE AND HYDRATASE REACTION MECHANISM OF THE CROTONASE ACTIVE SITE OF THE MULTIFUNCTIONAL ENZYME (TYPE-1), AS DEDUCED FROM STRUCTURES OF COMPLEXES WITH 3S-HYDROXY-ACYL-COA.FEBS JOURNAL. VOL. 280. ISSUE 13. P. 3160-3175 34 65% 6
8 POIRIER, Y , ANTONENKOV, VD , GLUMOFF, T , HILTUNEN, JK , (2006) PEROXISOMAL BETA-OXIDATION - A METABOLIC PATHWAY WITH MULTIPLE FUNCTIONS.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH. VOL. 1763. ISSUE 12. P. 1413 -1426 47 45% 142
9 ZSCHOCKE, J , (2012) HSD10 DISEASE: CLINICAL CONSEQUENCES OF MUTATIONS IN THE HSD17B10 GENE.JOURNAL OF INHERITED METABOLIC DISEASE. VOL. 35. ISSUE 1. P. 81-89 28 76% 13
10 KUNAU, WH , DOMMES, V , SCHULZ, H , (1995) BETA-OXIDATION OF FATTY ACIDS IN MITOCHONDRIA, PEROXISOMES, AND BACTERIA: A CENTURY OF CONTINUED PROGRESS.PROGRESS IN LIPID RESEARCH. VOL. 34. ISSUE 4. P. 267 -342 131 20% 292

Classes with closest relation at Level 1


Rank Class id link
1 17561 ELECTRON TRANSFERRING FLAVOPROTEIN//ISOVALERIC ACIDEMIA//ACYL COA DEHYDROGENASE
2 27804 ACYL COA THIOESTERASE//ACETYL COA HYDROLASE//ACYL COA HYDROLASE
3 30827 DODECANEDIOIC ACID//DIETHYL SEBACATE//AZELAIC ACID
4 24942 3 HYDROXY 3 METHYLGLUTARIC ACIDURIA//3 METHYLGLUTACONIC ACIDURIA//3 METHYLGLUTARIC ACID
5 2721 PEROXISOME//PEROXIN//PEROXISOME BIOGENESIS
6 2388 NEWBORN SCREENING//MEDIUM CHAIN ACYL COA DEHYDROGENASE DEFICIENCY//UNIT MOL MED
7 1912 ADRENOLEUKODYSTROPHY//X LINKED ADRENOLEUKODYSTROPHY//PHYTANIC ACID
8 7161 ENOYL ACP REDUCTASE//ACYL CARRIER PROTEIN//FABH
9 8921 CARNITINE PALMITOYLTRANSFERASE//CARNITINE PALMITOYLTRANSFERASE I//CARNITINE PALMITOYLTRANSFERASE DEFICIENCY
10 17356 GLYOXYSOME//GLYOXYLATE CYCLE//BIOCHEM 117 WEITZER HALL

Go to start page