Class information for:
Level 2: PSEUDOXANTHOMA ELASTICUM//ABCC6//ANGIOID STREAKS

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
3172 1633 19.9 58%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 3)


ID, lev.
above		 Publications Label for level above
202 48600 JOURNAL OF HEART VALVE DISEASE//AORTIC STENOSIS//TRANSCATHETER AORTIC VALVE IMPLANTATION

Classes in level below (level 1)


ID, lev. below Publications Label for level below
14126 725 PSEUDOXANTHOMA ELASTICUM//ANGIOID STREAKS//ABCC6
15335 648 PENTALOGY OF CANTRELL//ECTOPIA CORDIS//STERNAL CLEFT
27402 189 CALCIFIED AMORPHOUS TUMOR//DYSTROPHIC CARDIAC CALCIFICATION//MYOCARDIAL CALCIFICATION
34435 71 INTRACARDIAC TUBERCULOMA//MALARIA ENDEMIC REGION//MSR NAGAR

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 PSEUDOXANTHOMA ELASTICUM Author keyword 292 81% 11% 174
2 ABCC6 Author keyword 110 90% 3% 47
3 ANGIOID STREAKS Author keyword 99 78% 4% 65
4 PENTALOGY OF CANTRELL Author keyword 74 78% 3% 49
5 ECTOPIA CORDIS Author keyword 65 71% 3% 52
6 MRP6 Author keyword 41 100% 1% 15
7 STERNAL CLEFT Author keyword 38 78% 2% 25
8 GENERALIZED ARTERIAL CALCIFICATION OF INFANCY Author keyword 35 89% 1% 16
9 CANTRELLS PENTALOGY Author keyword 33 100% 1% 13
10 PXE Author keyword 29 73% 1% 22

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 PSEUDOXANTHOMA ELASTICUM 292 81% 11% 174 Search PSEUDOXANTHOMA+ELASTICUM Search PSEUDOXANTHOMA+ELASTICUM
2 ABCC6 110 90% 3% 47 Search ABCC6 Search ABCC6
3 ANGIOID STREAKS 99 78% 4% 65 Search ANGIOID+STREAKS Search ANGIOID+STREAKS
4 PENTALOGY OF CANTRELL 74 78% 3% 49 Search PENTALOGY+OF+CANTRELL Search PENTALOGY+OF+CANTRELL
5 ECTOPIA CORDIS 65 71% 3% 52 Search ECTOPIA+CORDIS Search ECTOPIA+CORDIS
6 MRP6 41 100% 1% 15 Search MRP6 Search MRP6
7 STERNAL CLEFT 38 78% 2% 25 Search STERNAL+CLEFT Search STERNAL+CLEFT
8 GENERALIZED ARTERIAL CALCIFICATION OF INFANCY 35 89% 1% 16 Search GENERALIZED+ARTERIAL+CALCIFICATION+OF+INFANCY Search GENERALIZED+ARTERIAL+CALCIFICATION+OF+INFANCY
9 CANTRELLS PENTALOGY 33 100% 1% 13 Search CANTRELLS+PENTALOGY Search CANTRELLS+PENTALOGY
10 PXE 29 73% 1% 22 Search PXE Search PXE

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 MRP6 146 96% 3% 46
2 CHROMOSOME 16P131 91 94% 2% 32
3 ECTOPIC MINERALIZATION 69 93% 2% 26
4 ECTOPIA CORDIS 56 75% 2% 40
5 ABCC6 GENE 53 89% 1% 24
6 CONNECTIVE TISSUE MINERALIZATION 45 94% 1% 16
7 OF CANTRELL 38 93% 1% 14
8 CONGENITAL DIVERTICULUM 35 86% 1% 18
9 PXE 32 85% 1% 17
10 PSEUDOXANTHOMA ELASTICUM 28 30% 5% 77

Journals

Reviews


Title Publ. year Cit. Active
references		 % act. ref.
to same field
Pseudoxanthoma Elasticum: Genetics, Clinical Manifestations and Therapeutic Approaches 2009 49 93 78%
Pseudoxanthoma elasticum: a clinical, pathophysiological and genetic update including 11 novel ABCC6 mutations 2005 115 82 88%
Proposal for Updating the Pseudoxanthoma Elasticum Classification System and a Review of the Clinical Findings 2010 21 39 95%
Pentalogy of Cantrell: two patients and a review to determine prognostic factors for optimal approach 2008 31 32 97%
Pseudoxanthoma elasticum: clinical phenotypes, molecular genetics and putative pathomechanisms 2009 40 54 81%
Congenital left ventricular aneurysms and diverticula: Definition, pathophysiology, clinical relevance and treatment 2006 53 60 92%
Genetics in Arterial Calcification: Lessons Learned From Rare Diseases 2012 21 32 47%
Cantrell's syndrome: A challenge to the surgeon 1998 45 8 88%
Mineralization/Anti-Mineralization Networks in the Skin and Vascular Connective Tissues 2013 6 56 61%
Pseudoxanthoma elasticum: diagnostic features, classification and treatment options 2014 2 69 87%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 PXE CONSULTAT 8 100% 0.3% 5
2 JEFFERSON MOL MED 4 13% 1.9% 31
3 MATRIX PATHOBIOL 4 50% 0.4% 6
4 ANGERS MED 4 56% 0.3% 5
5 CONSULTAT MULTIDISCIPLINAIRE PXE 3 100% 0.2% 3
6 CONSULTAT PXE 3 100% 0.2% 3
7 HERZ DIABET ZENTRUM NORDRHEIN WESTFALEN 2 15% 0.9% 14
8 CARDIOVASC VITAK BV 2 67% 0.1% 2
9 S TRANSFUS MED 2 21% 0.4% 7
10 INVAS ELE OPHYSIOL 1 50% 0.1% 2

Related classes at same level (level 2)


Rank Relatedness score Related classes
1 0.0000025940 VENTRICULAR SEPTAL RUPTURE//LEFT VENTRICULAR PSEUDOANEURYSM//CARDIAC RUPTURE
2 0.0000020064 GASTROSCHISIS//OMPHALOCELE//ABDOMINAL WALL DEFECTS
3 0.0000016554 VASCULAR CALCIFICATION//FGF 23//CALCIPHYLAXIS
4 0.0000009288 MARFAN SYNDROME//FIBRILLIN//LYSYL OXIDASE
5 0.0000008950 MYOCARDITIS//COXSACKIEVIRUS B3//VIRAL MYOCARDITIS
6 0.0000007843 CARDIOMYOPLASTY//SKELETAL MUSCLE VENTRICLE//LEFT VENTRICULAR RECONSTRUCTION
7 0.0000007312 IRON OVERLOAD//THALASSEMIA//DEFERASIROX
8 0.0000006801 CARDIAC MYXOMAS//MYXOMA//PAPILLARY FIBROELASTOMA
9 0.0000006597 CLUB FOOT//PONSETI//LIMB BODY WALL COMPLEX
10 0.0000005228 HYPERTROPHIC CARDIOMYOPATHY//ARRHYTHMOGENIC RIGHT VENTRICULAR CARDIOMYOPATHY//ATHLETES HEART