Class information for:
Level 2: THROMBOTIC THROMBOCYTOPENIC PURPURA//ADAMTS 13//HEMOLYTIC UREMIC SYNDROME

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
2079 4804 33.7 76%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 3)



ID, lev.
above
Publications Label for level above
623 10035 THROMBOTIC THROMBOCYTOPENIC PURPURA//RIBOSOME INACTIVATING PROTEINS//ADAMTS 13

Classes in level below (level 1)



ID, lev. below Publications Label for level below
1242 2666 THROMBOTIC THROMBOCYTOPENIC PURPURA//ADAMTS 13//TTP
4435 1713 SHIGA TOXIN//HEMOLYTIC UREMIC SYNDROME//SHIGA TOXIN B SUBUNIT
24607 257 UF SIDA//KODECYTE//ESA CNRS 6033
28482 168 T ACTIVATION//POLYAGGLUTINATION//ERYTHROCYTE CHARGE

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 THROMBOTIC THROMBOCYTOPENIC PURPURA Author keyword 864 75% 13% 632
2 ADAMTS 13 Author keyword 552 76% 8% 389
3 HEMOLYTIC UREMIC SYNDROME Author keyword 387 54% 10% 503
4 THROMBOTIC MICROANGIOPATHY Author keyword 128 41% 5% 244
5 TTP Author keyword 127 52% 4% 173
6 SHIGA TOXIN Author keyword 97 39% 4% 197
7 UPSHAW SCHULMAN SYNDROME Author keyword 86 96% 1% 26
8 THROMBOTIC THROMBOCYTOPENIC PURPURA TTP Author keyword 69 75% 1% 49
9 VON WILLEBRAND FACTOR CLEAVING PROTEASE Author keyword 67 85% 1% 35
10 MICROANGIOPATHIC HEMOLYTIC ANEMIA Author keyword 52 62% 1% 53

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 THROMBOTIC THROMBOCYTOPENIC PURPURA 864 75% 13% 632 Search THROMBOTIC+THROMBOCYTOPENIC+PURPURA Search THROMBOTIC+THROMBOCYTOPENIC+PURPURA
2 ADAMTS 13 552 76% 8% 389 Search ADAMTS+13 Search ADAMTS+13
3 HEMOLYTIC UREMIC SYNDROME 387 54% 10% 503 Search HEMOLYTIC+UREMIC+SYNDROME Search HEMOLYTIC+UREMIC+SYNDROME
4 THROMBOTIC MICROANGIOPATHY 128 41% 5% 244 Search THROMBOTIC+MICROANGIOPATHY Search THROMBOTIC+MICROANGIOPATHY
5 TTP 127 52% 4% 173 Search TTP Search TTP
6 SHIGA TOXIN 97 39% 4% 197 Search SHIGA+TOXIN Search SHIGA+TOXIN
7 UPSHAW SCHULMAN SYNDROME 86 96% 1% 26 Search UPSHAW+SCHULMAN+SYNDROME Search UPSHAW+SCHULMAN+SYNDROME
8 THROMBOTIC THROMBOCYTOPENIC PURPURA TTP 69 75% 1% 49 Search THROMBOTIC+THROMBOCYTOPENIC+PURPURA+TTP Search THROMBOTIC+THROMBOCYTOPENIC+PURPURA+TTP
9 VON WILLEBRAND FACTOR CLEAVING PROTEASE 67 85% 1% 35 Search VON+WILLEBRAND+FACTOR+CLEAVING+PROTEASE Search VON+WILLEBRAND+FACTOR+CLEAVING+PROTEASE
10 MICROANGIOPATHIC HEMOLYTIC ANEMIA 52 62% 1% 53 Search MICROANGIOPATHIC+HEMOLYTIC+ANEMIA Search MICROANGIOPATHIC+HEMOLYTIC+ANEMIA

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of publ.
in class
1 FACTOR CLEAVING PROTEASE 947 69% 17% 814
2 HEMOLYTIC UREMIC SYNDROME 470 27% 31% 1510
3 MICROANGIOPATHIES 302 83% 4% 172
4 THROMBOTIC THROMBOCYTOPENIC PURPURA 245 34% 12% 597
5 UPSHAW SCHULMAN SYNDROME 149 86% 2% 75
6 TTP 145 70% 2% 120
7 ADAMTS13 ACTIVITY 123 78% 2% 80
8 ADAMTS 13 122 52% 3% 164
9 VONWILLEBRAND FACTOR MULTIMERS 97 55% 3% 122
10 PLASMA EXCHANGE 83 18% 9% 431

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Mechanisms of disease - Thrombotic microangiopathies 2002 643 97 80%
Von Willebrand factor, ADAMTS13, and thrombotic thrombocytopenic purpura 2008 205 58 95%
Syndromes of Thrombotic Microangiopathy 2014 27 57 53%
The role of rituximab in the management of patients with acquired thrombotic thrombocytopenic purpura 2015 3 25 96%
Shiga toxins - from cell biology to biomedical applications 2010 145 160 73%
VWF excess and ADAMTS13 deficiency: a unifying pathomechanism linking inflammation to thrombosis in DIC, malaria, and TIP 2015 4 121 53%
How I treat patients with thrombotic thrombocytopenic purpura: 2010 2010 101 46 76%
How I treat thrombotic thrombocytopenic purpura and atypical haemolytic uraemic syndrome 2014 11 35 69%
ADAMTS13 and von Willebrand Factor in Thrombotic Thrombocytopenic Purpura 2015 2 86 86%
Natural history of Upshaw-Schulman syndrome based on ADAMTS13 gene analysis in Japan 2011 34 59 97%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 BLOOD TRANSFUS MED 40 46% 1.4% 65
2 SERV HEM HE E 15 88% 0.1% 7
3 PATOGENESIS INMUNOL PROC INFECCIOSOS 9 83% 0.1% 5
4 MOL INFECTIOL 9 39% 0.4% 18
5 CENT HEMATOL 9 14% 1.2% 59
6 UF SIDA 8 70% 0.1% 7
7 TRAF SIGNALISAT 8 60% 0.2% 9
8 REFERENCE MICROANGIOPATHIES THROMBOT 8 100% 0.1% 5
9 INFECT IMMUN INJURY REPAIR 7 48% 0.2% 11
10 FISIOPATOGENIA 7 36% 0.3% 16

Related classes at same level (level 2)



Rank Relatedness score Related classes
1 0.0000028545 STEC//EPEC//UROGUANYLIN
2 0.0000013192 RIBOSOME INACTIVATING PROTEINS//RICIN//TRICHOSANTHIN
3 0.0000011574 HAEMOPHILIA//HAEMOPHILIA A//VON WILLEBRAND DISEASE
4 0.0000010530 LDL APHERESIS//LOW DENSITY LIPOPROTEIN APHERESIS//APHERESIS
5 0.0000007648 COMPLEMENT//MANNOSE BINDING LECTIN//PAROXYSMAL NOCTURNAL HEMOGLOBINURIA
6 0.0000007536 IMMUNE THROMBOCYTOPENIA//IDIOPATHIC THROMBOCYTOPENIC PURPURA//IMMUNE THROMBOCYTOPENIC PURPURA
7 0.0000007413 POSTERIOR REVERSIBLE ENCEPHALOPATHY SYNDROME//REVERSIBLE POSTERIOR LEUKOENCEPHALOPATHY SYNDROME//HYPERTENSIVE ENCEPHALOPATHY
8 0.0000007408 PURPURA FULMINANS//SYMMETRICAL PERIPHERAL GANGRENE//CARCINOCYTHEMIA
9 0.0000006668 TINU SYNDROME//ACUTE INTERSTITIAL NEPHRITIS//PROPYLTHIOURACIL
10 0.0000005868 ANTIPHOSPHOLIPID SYNDROME//ANTIPHOSPHOLIPID ANTIBODIES//LUPUS ANTICOAGULANT