Class information for:
Level 2: AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE//POLYCYSTIC KIDNEY DISEASE//ADPKD

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
1566 6734 38.5 77%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 3)



ID, lev.
above
Publications Label for level above
102 71731 ACUTE PANCREATITIS//CHRONIC PANCREATITIS//PANCREATIC CANCER

Classes in level below (level 1)



ID, lev. below Publications Label for level below
892 2895 AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE//ADPKD//POLYCYSTIC KIDNEY DISEASE
2195 2250 JOUBERT SYNDROME//BARDET BIEDL SYNDROME//INTRAFLAGELLAR TRANSPORT
14076 729 UROMODULIN//TAMM HORSFALL PROTEIN//FAMILIAL JUVENILE HYPERURICEMIC NEPHROPATHY
14855 676 ELLIS VAN CREVELD SYNDROME//SHORT RIB POLYDACTYLY SYNDROME//JEUNE SYNDROME
32497 107 SCHIMKE IMMUNO OSSEOUS DYSPLASIA//SMARCAL1//SCHIMKE IMMUNOOSSEOUS DYSPLASIA
34178 77 WEISMANN NETTER STUHL SYNDROME//GLOMERULOCYSTIC KIDNEY//GLOMERULOCYSTIC KIDNEY DISEASE

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE Author keyword 352 68% 5% 311
2 POLYCYSTIC KIDNEY DISEASE Author keyword 341 56% 6% 410
3 ADPKD Author keyword 296 76% 3% 208
4 CILIOPATHY Author keyword 165 78% 2% 108
5 NEPHRONOPHTHISIS Author keyword 163 80% 2% 102
6 JOUBERT SYNDROME Author keyword 155 77% 2% 105
7 BARDET BIEDL SYNDROME Author keyword 152 72% 2% 121
8 ELLIS VAN CREVELD SYNDROME Author keyword 150 96% 1% 47
9 PRIMARY CILIA Author keyword 149 64% 2% 147
10 POLYCYSTIN 1 Author keyword 141 91% 1% 59

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE 352 68% 5% 311 Search AUTOSOMAL+DOMINANT+POLYCYSTIC+KIDNEY+DISEASE Search AUTOSOMAL+DOMINANT+POLYCYSTIC+KIDNEY+DISEASE
2 POLYCYSTIC KIDNEY DISEASE 341 56% 6% 410 Search POLYCYSTIC+KIDNEY+DISEASE Search POLYCYSTIC+KIDNEY+DISEASE
3 ADPKD 296 76% 3% 208 Search ADPKD Search ADPKD
4 CILIOPATHY 165 78% 2% 108 Search CILIOPATHY Search CILIOPATHY
5 NEPHRONOPHTHISIS 163 80% 2% 102 Search NEPHRONOPHTHISIS Search NEPHRONOPHTHISIS
6 JOUBERT SYNDROME 155 77% 2% 105 Search JOUBERT+SYNDROME Search JOUBERT+SYNDROME
7 BARDET BIEDL SYNDROME 152 72% 2% 121 Search BARDET+BIEDL+SYNDROME Search BARDET+BIEDL+SYNDROME
8 ELLIS VAN CREVELD SYNDROME 150 96% 1% 47 Search ELLIS+VAN+CREVELD+SYNDROME Search ELLIS+VAN+CREVELD+SYNDROME
9 PRIMARY CILIA 149 64% 2% 147 Search PRIMARY+CILIA Search PRIMARY+CILIA
10 POLYCYSTIN 1 141 91% 1% 59 Search POLYCYSTIN+1 Search POLYCYSTIN+1

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 INTRAFLAGELLAR TRANSPORT 345 56% 6% 421
2 POLYCYSTIC KIDNEY DISEASE 325 33% 12% 798
3 PKD1 290 79% 3% 188
4 ADPKD 282 87% 2% 141
5 BARDET BIEDL SYNDROME 243 48% 5% 369
6 PKD1 GENE 242 84% 2% 130
7 JOUBERT SYNDROME 191 54% 4% 247
8 PRIMARY CILIUM 191 43% 5% 340
9 KINESIN II 165 72% 2% 129
10 ARPKD 152 85% 1% 80

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Mechanisms of Disease: Ciliopathies 2011 278 77 94%
The primary cilium: a signalling centre during vertebrate development 2010 473 156 57%
Ciliogenesis: building the cell's antenna 2011 217 143 83%
Polycystic Kidney Disease 2009 241 95 88%
The Vertebrate Primary Cilium in Development, Homeostasis, and Disease 2009 280 107 68%
Novel therapeutic approaches to autosomal dominant polycystic kidney disease 2015 2 91 88%
The Primary cilium calcium channels and their role in flow sensing 2015 2 74 82%
Intraflagellar transport 2002 744 70 60%
The Primary Cilium as a Complex Signaling Center 2009 202 102 79%
Metabolic abnormalities in autosomal dominant polycystic kidney disease 2015 3 60 53%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 GENET TRANSLAT MED 16 65% 0.2% 15
2 RAINBOW CHILDHOOD PKD 16 65% 0.2% 15
3 HUMAN DIS MODELING 15 32% 0.6% 40
4 KIDNEY GENET GRP 15 73% 0.2% 11
5 EDUC ANIM MODELS HUMAN DIS 14 55% 0.3% 17
6 TRANSLAT CANC THER Y 8 75% 0.1% 6
7 SECT OPHTHALMOL NEUROSCI 8 28% 0.4% 25
8 DULBECCO TELETHON DIBIT 8 100% 0.1% 5
9 U574 8 27% 0.4% 25
10 CANALES ION 6 42% 0.2% 11

Related classes at same level (level 2)



Rank Relatedness score Related classes
1 0.0000034338 POLYCYSTIC LIVER DISEASE//BILIARY CYSTADENOCARCINOMA//BILIARY CYSTADENOMA
2 0.0000012399 KINESIN//DYNEIN//AXONEME
3 0.0000010233 RHOMBENCEPHALOSYNAPSIS//PONTOCEREBELLAR HYPOPLASIA//ARTHROGRYPOSIS
4 0.0000009425 AMELOBLASTOMAS//HEDGEHOG//ODONTOGENIC KERATOCYST
5 0.0000008724 HYPOTHALAMIC HAMARTOMA//GELASTIC SEIZURES//GELASTIC SEIZURE
6 0.0000008020 VESICO URETERAL REFLUX//URETEROCELE//HYDRONEPHROSIS
7 0.0000007043 ACHONDROPLASIA//HYPOCHONDROPLASIA//THANATOPHORIC DYSPLASIA
8 0.0000006594 BRONCHIECTASIS//PRIMARY CILIARY DYSKINESIA//MUCOCILIARY CLEARANCE
9 0.0000006545 KINETOCHORE//MITOSIS//CENTROSOME
10 0.0000006426 GJB2//CONNEXIN 26//USHER SYNDROME