Class information for:
Level 1: MAPLE SYRUP URINE DISEASE//BRANCHED CHAIN ALPHA KETO ACID DEHYDROGENASE COMPLEX//BCKDHA

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
8127 1216 30.6 60%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
1351 7837 MAPLE SYRUP URINE DISEASE//METHYLMALONIC ACIDEMIA//JOURNAL OF INHERITED METABOLIC DISEASE

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 MAPLE SYRUP URINE DISEASE Author keyword 151 71% 10% 122
2 BRANCHED CHAIN ALPHA KETO ACID DEHYDROGENASE COMPLEX Author keyword 41 87% 2% 20
3 BCKDHA Author keyword 31 92% 1% 12
4 BCKDHB Author keyword 20 100% 1% 9
5 BRANCHED CHAIN ALPHA KETOACID DEHYDROGENASE Author keyword 17 68% 1% 15
6 BRANCHED CHAIN KETO ACIDS Author keyword 15 77% 1% 10
7 MSUD Author keyword 12 58% 1% 14
8 BRANCHED CHAIN ALPHA KETO ACID DEHYDROGENASE Author keyword 12 63% 1% 12
9 BRANCHED CHAIN KETOACID DEHYDROGENASE Author keyword 12 86% 0% 6
10 BRANCHED CHAIN AMINO ACIDS Author keyword 11 14% 6% 78

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 MAPLE SYRUP URINE DISEASE 151 71% 10% 122 Search MAPLE+SYRUP+URINE+DISEASE Search MAPLE+SYRUP+URINE+DISEASE
2 BRANCHED CHAIN ALPHA KETO ACID DEHYDROGENASE COMPLEX 41 87% 2% 20 Search BRANCHED+CHAIN+ALPHA+KETO+ACID+DEHYDROGENASE+COMPLEX Search BRANCHED+CHAIN+ALPHA+KETO+ACID+DEHYDROGENASE+COMPLEX
3 BCKDHA 31 92% 1% 12 Search BCKDHA Search BCKDHA
4 BCKDHB 20 100% 1% 9 Search BCKDHB Search BCKDHB
5 BRANCHED CHAIN ALPHA KETOACID DEHYDROGENASE 17 68% 1% 15 Search BRANCHED+CHAIN+ALPHA+KETOACID+DEHYDROGENASE Search BRANCHED+CHAIN+ALPHA+KETOACID+DEHYDROGENASE
6 BRANCHED CHAIN KETO ACIDS 15 77% 1% 10 Search BRANCHED+CHAIN+KETO+ACIDS Search BRANCHED+CHAIN+KETO+ACIDS
7 MSUD 12 58% 1% 14 Search MSUD Search MSUD
8 BRANCHED CHAIN ALPHA KETO ACID DEHYDROGENASE 12 63% 1% 12 Search BRANCHED+CHAIN+ALPHA+KETO+ACID+DEHYDROGENASE Search BRANCHED+CHAIN+ALPHA+KETO+ACID+DEHYDROGENASE
9 BRANCHED CHAIN KETOACID DEHYDROGENASE 12 86% 0% 6 Search BRANCHED+CHAIN+KETOACID+DEHYDROGENASE Search BRANCHED+CHAIN+KETOACID+DEHYDROGENASE
10 BRANCHED CHAIN AMINO ACIDS 11 14% 6% 78 Search BRANCHED+CHAIN+AMINO+ACIDS Search BRANCHED+CHAIN+AMINO+ACIDS

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ALPHA KETOACID DEHYDROGENASE 41 55% 4% 51
2 SYRUP URINE DISEASE 29 26% 8% 97
3 MSUD 27 92% 1% 11
4 Y393N MUTATION 27 92% 1% 11
5 ACID DEHYDROGENASE COMPLEX 19 63% 2% 19
6 LARGE NEUTRAL AMINO 19 76% 1% 13
7 ACTIVITY STATE 18 50% 2% 26
8 KETOACID DEHYDROGENASE COMPLEX 17 75% 1% 12
9 2 OXO ACID DEHYDROGENASE 15 67% 1% 14
10 E1 BETA SUBUNIT 13 80% 1% 8

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Branched-chain amino acids in metabolic signalling and insulin resistance 2014 16 193 36%
Branch chain amino acids: biomarkers of health and disease 2014 4 13 85%
Interplay between Lipids and Branched-Chain Amino Acids in Development of Insulin Resistance 2012 116 49 24%
BRANCHED-CHAIN AMINO-ACID-METABOLISM 1984 534 75 60%
Studies on the regulation of the mitochondrial alpha-ketoacid dehydrogenase complexes and their kinases 1997 57 47 47%
Determination of branched-chain alpha-keto acid dehydrogenase activity state and branched-chain alpha-keto acid dehydrogenase kinase activity and protein in mammalian tissues 2000 17 24 88%
Emerging Perspectives on Essential Amino Acid Metabolism in Obesity and the Insulin-Resistant State 2011 73 121 40%
Mammalian branched-chain aminotransferases 2000 15 12 83%
Domino Liver Transplantation in Maple Syrup Urine Disease: A Case Report and Review of the Literature 2013 5 12 58%
DETERMINATION OF ACTIVITY AND ACTIVITY STATE OF BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE IN RAT-TISSUES 1988 31 18 94%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 PROGRAMA POS CB BIOQUIM 3 57% 0.3% 4
2 ALTHOUSE 2 33% 0.3% 4
3 MACROMOL CORE IL 1 50% 0.2% 2
4 NMR METABOL 1 18% 0.5% 6
5 NMR METAB 1 40% 0.2% 2
6 ANAESTHESIOL INTENS MED PAIN THER Y 1 50% 0.1% 1
7 BIOENERGETICA 1 50% 0.1% 1
8 CHUM ST LUC HOSP 1 50% 0.1% 1
9 CIENCIAS SAUDE ICS 1 50% 0.1% 1
10 CLIN CHEMFIM S 1 50% 0.1% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000155277 3 HYDROXYISOBUTYRATE DEHYDROGENASE//HIBCH//SERINE DEHYDROGENASE
2 0.0000122444 LIPOYL DOMAIN//PYRUVATE DEHYDROGENASE COMPLEX//DIHYDROLIPOAMIDE DEHYDROGENASE
3 0.0000102187 MUSCLE PROTEIN SYNTHESIS//LEUCINE//EXERCISE METAB GRP
4 0.0000084986 BETA HYDROXY BETA METHYLBUTYRATE//HMB//METAB TECHNOL INC
5 0.0000082693 CLIN MEDNUCLEO MED CIRURGIA EXPT//METAB HIDRO SALINO//PCRN
6 0.0000054734 L 3 HYDROXYBUTYRATE//FID GC FID//ACETOACETATE ESTERS
7 0.0000050035 METHYLMALONIC ACIDEMIA//PROPIONIC ACIDEMIA//METHYLMALONIC ACIDURIA
8 0.0000049030 LATE EVENING SNACK//NON PROTEIN RESPIRATORY QUOTIENT//BRANCHED CHAIN AMINO ACIDS
9 0.0000048772 IND PUBL RELAT//MULTIPHAS HLTH TESTING SERV//HLTH FUNDAMENTALS
10 0.0000047675 PURINE NUCLEOTIDE CYCLE//TRICARBOXYLIC ACID CYCLE INTERMEDIATES//GLYCOGEN SYNTHASE PHOSPHATASE