Class information for:
Level 1: BERNARD SOULIER SYNDROME//MAY HEGGLIN ANOMALY//EPSTEIN SYNDROME

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
7379 1295 36.5 73%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
202 20434 CLOPIDOGREL//PRASUGREL//ASPIRIN RESISTANCE

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 BERNARD SOULIER SYNDROME Author keyword 136 79% 7% 88
2 MAY HEGGLIN ANOMALY Author keyword 76 88% 3% 36
3 EPSTEIN SYNDROME Author keyword 64 100% 2% 21
4 FECHTNER SYNDROME Author keyword 38 89% 1% 17
5 GIANT PLATELETS Author keyword 35 76% 2% 25
6 MYH9 RELATED DISEASE Author keyword 33 83% 1% 19
7 INHERITED THROMBOCYTOPENIAS Author keyword 30 100% 1% 12
8 MACROTHROMBOCYTOPENIA Author keyword 29 58% 3% 33
9 INHERITED PLATELET DISORDERS Author keyword 25 77% 1% 17
10 MYH9 GENE Author keyword 23 76% 1% 16

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 BERNARD SOULIER SYNDROME 136 79% 7% 88 Search BERNARD+SOULIER+SYNDROME Search BERNARD+SOULIER+SYNDROME
2 MAY HEGGLIN ANOMALY 76 88% 3% 36 Search MAY+HEGGLIN+ANOMALY Search MAY+HEGGLIN+ANOMALY
3 EPSTEIN SYNDROME 64 100% 2% 21 Search EPSTEIN+SYNDROME Search EPSTEIN+SYNDROME
4 FECHTNER SYNDROME 38 89% 1% 17 Search FECHTNER+SYNDROME Search FECHTNER+SYNDROME
5 GIANT PLATELETS 35 76% 2% 25 Search GIANT+PLATELETS Search GIANT+PLATELETS
6 MYH9 RELATED DISEASE 33 83% 1% 19 Search MYH9+RELATED+DISEASE Search MYH9+RELATED+DISEASE
7 INHERITED THROMBOCYTOPENIAS 30 100% 1% 12 Search INHERITED+THROMBOCYTOPENIAS Search INHERITED+THROMBOCYTOPENIAS
8 MACROTHROMBOCYTOPENIA 29 58% 3% 33 Search MACROTHROMBOCYTOPENIA Search MACROTHROMBOCYTOPENIA
9 INHERITED PLATELET DISORDERS 25 77% 1% 17 Search INHERITED+PLATELET+DISORDERS Search INHERITED+PLATELET+DISORDERS
10 MYH9 GENE 23 76% 1% 16 Search MYH9+GENE Search MYH9+GENE

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 LEUKOCYTE INCLUSIONS 122 78% 6% 81
2 BERNARD SOULIER SYNDROME 121 51% 13% 169
3 FECHTNER SYNDROME 59 71% 4% 48
4 AUTOSOMAL DOMINANT MACROTHROMBOCYTOPENIA 52 75% 3% 38
5 GIANT PLATELETS 44 88% 2% 21
6 IX COMPLEX 42 49% 5% 63
7 LEUCINE RICH GLYCOPROTEINS 39 68% 3% 34
8 EPSTEIN SYNDROME 37 81% 2% 22
9 MACROTHROMBOCYTOPENIA 35 53% 4% 46
10 MYH9 RELATED DISEASE 35 60% 3% 38

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Bernard-Soulier syndrome 1998 293 192 60%
Recent advances in the understanding and management of MYH9-related inherited thrombocytopenias 2011 49 66 80%
Bernard-Soulier syndrome (Hemorrhagiparous thrombocytic dystrophy) 2006 35 75 87%
The organizing principle of the platelet glycoprotein IbIXV complex 2013 15 96 65%
Bernard Soulier syndrome in pregnancy: a systematic review 2010 21 20 85%
Inherited thrombocytopenias frequently diagnosed in adults 2013 12 68 62%
What is the role of genetic testing in the investigation of patients with suspected platelet function disorders? 2014 4 54 61%
Congenital macrothrombocytopenias 2006 29 58 71%
Genetics of familial forms of thrombocytopenia 2012 22 77 45%
Mechanisms of platelet activation by thrombin: A short history 2012 18 25 52%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 PLATELET PATHOL UNIT 12 86% 0.5% 6
2 REPROD DEV SCI PUBL MED SCI 6 80% 0.3% 4
3 AZIENDA SANTOBONO PAUSILIPON 6 71% 0.4% 5
4 ADV DIAG 6 34% 1.2% 15
5 HAZEL PIP PEL VASC BIOL 6 50% 0.7% 9
6 ADULT HAEMOPHILIA 6 100% 0.3% 4
7 IRCCS POLICLIN SAN MATTEO FDN 5 25% 1.2% 16
8 HAEMATOL ONCOLPROGRAM CELL BIOL 4 75% 0.2% 3
9 HEMOSTASIS THROMBOSISNAKA KU 4 75% 0.2% 3
10 SEKT INNERE MED 1 4 75% 0.2% 3

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000201694 GLANZMANN THROMBASTHENIA//GLANZMANNS THROMBASTHENIA//THROMBASTHENIA
2 0.0000134366 GLYCOPROTEIN VI//GPVI//CLEC 2
3 0.0000114898 VON WILLEBRAND DISEASE//VON WILLEBRAND FACTOR//VWD
4 0.0000110574 HERMANSKY PUDLAK SYNDROME//CHEDIAK HIGASHI SYNDROME//LYST
5 0.0000106933 C TYPE LECTIN LIKE PROTEIN//ANTICOAGULATION FACTOR I//ANTICOAGULATION FACTOR II
6 0.0000091558 JACOBSEN SYNDROME//11Q SYNDROME//11Q TERMINAL DELETION DISORDER
7 0.0000084677 DESMOPRESSIN//DDAVP//PHARMACOLOGY DESMOPRESSIN
8 0.0000075198 PLATELET APOPTOSIS//COATED PLATELET//STUDY HUMAN OPERATOR PERFORMANCE
9 0.0000064355 ASPIRIN RESISTANCE//PFA 100//THROMBOSTAT
10 0.0000062960 THROMBOPOIETIN//C MPL//MEGAKARYOCYTE